Reactome: A Curated Pathway Database
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Peroxisomal lipid metabolism

Stable Identifier
R-HSA-390918
Type
Pathway
Species
Homo sapiens
Locations in the PathwayBrowser
Summation

In humans, the catabolism of phytanate, pristanate, and very long chain fatty acids as well as the first four steps of the biosynthesis of plasmalogens are catalyzed by peroxisomal enzymes. Defects in any of these enzymes or in the assembly of peroxisomes are associated with severe developmental disorders (Wanders and Watherham 2006).

Literature References
PubMed ID Title Journal Year
16756494 Biochemistry of mammalian peroxisomes revisited Annu Rev Biochem 2006
Participants
Participant Of
Orthologous Events