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2xMUT:AdoCbl [mitochondrial matrix]
Stable Identifier
R-HSA-70999
Type
Complex
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
MUT dimer:adenosylcobalamin, methylmalonyl-CoA mutase, homodimer
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Mitochondrial Fatty Acid Beta-Oxidation (Homo sapiens)
Propionyl-CoA catabolism (Homo sapiens)
MUT isomerises L-MM-CoA to SUCC-CoA (Homo sapiens)
2xMUT:AdoCbl [mitochondrial matrix] (Homo sapiens)
Literature References
PubMed ID
Title
Journal
Year
13934212
Metabolism of propionic acid in animal tissues. X. Methylmalonyl coenzyme A mutase holoenzyme
Sasakawa, T
,
Ochoa, S
,
Mazumder, R
J Biol Chem
1963
The Metabolic and Molecular Bases of Inherited Disease, 8th ed
Beaudet, AL
,
Scriver, CR
,
Sly, WS
,
Valle, D
2001
Participants
components
AdoCbl [mitochondrial matrix]
x 2
MUT [mitochondrial matrix]
(Homo sapiens)
Inferred To
2xMUT:AdoCbl [mitochondrial matrix]
(Bos taurus)
2xMUT:AdoCbl [mitochondrial matrix]
(Caenorhabditis elegans)
2xMUT:AdoCbl [mitochondrial matrix]
(Canis familiaris)
2xMUT:AdoCbl [mitochondrial matrix]
(Danio rerio)
2xMUT:AdoCbl [mitochondrial matrix]
(Gallus gallus)
2xMUT:AdoCbl [mitochondrial matrix]
(Mus musculus)
2xMUT:AdoCbl [mitochondrial matrix]
(Rattus norvegicus)
2xMUT:AdoCbl [mitochondrial matrix]
(Sus scrofa)
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