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What is Reactome ?
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Team
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Our Logo
License Agreement
Privacy Notice
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Table of Contents
DOIs
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FAD [mitochondrial matrix]
Stable Identifier
R-ALL-113596
Type
Chemical Compound [SimpleEntity]
Compartment
mitochondrial matrix
Synonyms
Flavin adenine dinucleotide
Icon
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Plasmodium falciparum
Rattus norvegicus
Saccharomyces cerevisiae
Schizosaccharomyces pombe
Sus scrofa
Xenopus tropicalis
Expand all
Cellular responses to external stimuli (Bos taurus)
Cellular responses to stress (Bos taurus)
Detoxification of Reactive Oxygen Species (Bos taurus)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Bos taurus)
GSR dimer [mitochondrial matrix] (Bos taurus)
GSR holoenzyme [mitochondrial matrix] (Bos taurus)
FAD [mitochondrial matrix]
Metabolism (Bos taurus)
Metabolism of amino acids and derivatives (Bos taurus)
Branched-chain amino acid catabolism (Bos taurus)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Bos taurus)
FAD [mitochondrial matrix]
IVD tetramer [mitochondrial matrix] (Bos taurus)
FAD [mitochondrial matrix]
Choline catabolism (Bos taurus)
CHDH oxidises Cho to BETALD (Bos taurus)
FAD [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Bos taurus)
SARDH:FAD [mitochondrial matrix] (Bos taurus)
FAD [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Bos taurus)
Glycine degradation (Bos taurus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Bos taurus)
DLD dimer:2xFAD [mitochondrial matrix] (Bos taurus)
FAD [mitochondrial matrix]
Metabolism of lipids (Bos taurus)
Fatty acid metabolism (Bos taurus)
Mitochondrial Fatty Acid Beta-Oxidation (Bos taurus)
ACAD10 dehydrogenates S-2MPDA-CoA (Bos taurus)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Bos taurus)
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Bos taurus)
Decanoyl-CoA+FAD<=>trans-Dec-2-enoyl-CoA+FADH2 (Bos taurus)
FAD [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Bos taurus)
lauroyl-CoA+FAD<=>2-trans-Dodecenoyl-CoA+FADH2 (Bos taurus)
FAD [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Bos taurus)
myristoyl-CoA+FAD<=>trans-Tetradec-2-enoyl-CoA+FADH2 (Bos taurus)
FAD [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Bos taurus)
Octanoyl-CoA+FAD<=>trans-Oct-2-enoyl-CoA+FADH2 (Bos taurus)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Bos taurus)
dehydrogenation of 4-cis-decenoyl-CoA to form 2-trans-4-cis-decadienoyl-CoA (Bos taurus)
FAD [mitochondrial matrix]
The citric acid (TCA) cycle and respiratory electron transport (Bos taurus)
Pyruvate metabolism and Citric Acid (TCA) cycle (Bos taurus)
Interconversion of 2-oxoglutarate and 2-hydroxyglutarate (Bos taurus)
(R)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Bos taurus)
FAD [mitochondrial matrix]
(S)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Bos taurus)
FAD [mitochondrial matrix]
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Bos taurus)
Respiratory electron transport (Bos taurus)
Complex I biogenesis (Bos taurus)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Bos taurus)
815kDa complex [mitochondrial inner membrane] (Bos taurus)
550kDa complex [mitochondrial inner membrane] (Bos taurus)
315kDa subcomplex [mitochondrial inner membrane] (Bos taurus)
Intermediate 2 [mitochondrial inner membrane] (Bos taurus)
Intermediate 1 [mitochondrial inner membrane] (Bos taurus)
IP subcomplex [mitochondrial matrix] (Bos taurus)
NDUFA9:FAD [mitochondrial matrix] (Bos taurus)
FAD [mitochondrial matrix]
980kDa complex [mitochondrial inner membrane] (Bos taurus)
815kDa complex [mitochondrial inner membrane] (Bos taurus)
550kDa complex [mitochondrial inner membrane] (Bos taurus)
315kDa subcomplex [mitochondrial inner membrane] (Bos taurus)
Intermediate 2 [mitochondrial inner membrane] (Bos taurus)
Intermediate 1 [mitochondrial inner membrane] (Bos taurus)
IP subcomplex [mitochondrial matrix] (Bos taurus)
NDUFA9:FAD [mitochondrial matrix] (Bos taurus)
FAD [mitochondrial matrix]
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Bos taurus)
315kDa subcomplex [mitochondrial inner membrane] (Bos taurus)
Intermediate 2 [mitochondrial inner membrane] (Bos taurus)
Intermediate 1 [mitochondrial inner membrane] (Bos taurus)
IP subcomplex [mitochondrial matrix] (Bos taurus)
NDUFA9:FAD [mitochondrial matrix] (Bos taurus)
FAD [mitochondrial matrix]
550kDa complex [mitochondrial inner membrane] (Bos taurus)
315kDa subcomplex [mitochondrial inner membrane] (Bos taurus)
Intermediate 2 [mitochondrial inner membrane] (Bos taurus)
Intermediate 1 [mitochondrial inner membrane] (Bos taurus)
IP subcomplex [mitochondrial matrix] (Bos taurus)
NDUFA9:FAD [mitochondrial matrix] (Bos taurus)
FAD [mitochondrial matrix]
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Bos taurus)
Complex I [mitochondrial inner membrane] (Bos taurus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Bos taurus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Bos taurus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Bos taurus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Bos taurus)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Bos taurus)
NDUFA9:FAD [mitochondrial matrix] (Bos taurus)
FAD [mitochondrial matrix]
Cellular responses to external stimuli (Caenorhabditis elegans)
Cellular responses to stress (Caenorhabditis elegans)
Detoxification of Reactive Oxygen Species (Caenorhabditis elegans)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Caenorhabditis elegans)
GSR dimer [mitochondrial matrix] (Caenorhabditis elegans)
GSR holoenzyme [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Caenorhabditis elegans)
TXNRD2 dimer [mitochondrial matrix] (Caenorhabditis elegans)
TXNRD2 holoenzyme [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Metabolism (Caenorhabditis elegans)
Metabolism of amino acids and derivatives (Caenorhabditis elegans)
Branched-chain amino acid catabolism (Caenorhabditis elegans)
BCKDH transfers CoA group from CoA-SH to BCAAs (Caenorhabditis elegans)
lipo-BCKDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Caenorhabditis elegans)
FAD [mitochondrial matrix]
ACADSB tetramer [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Caenorhabditis elegans)
FAD [mitochondrial matrix]
ACAD8 tetramer [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Caenorhabditis elegans)
FAD [mitochondrial matrix]
IVD tetramer [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Choline catabolism (Caenorhabditis elegans)
CHDH oxidises Cho to BETALD (Caenorhabditis elegans)
FAD [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Caenorhabditis elegans)
DMGDH:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Caenorhabditis elegans)
Glycine degradation (Caenorhabditis elegans)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Caenorhabditis elegans)
DLD dimer:2xFAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
LIPT1 transfers lipoyl group from lipoyl-GCSH to DHs (Caenorhabditis elegans)
DHs [mitochondrial matrix] (Caenorhabditis elegans)
BCKDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
PDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
aKGDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
lipoylated DHs [mitochondrial matrix] (Caenorhabditis elegans)
lipo-BCKDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
lipo-aKGDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Lysine catabolism (Caenorhabditis elegans)
alpha-ketoadipate + CoASH + NAD+ => glutaryl-CoA + CO2 + NADH + H+ (Caenorhabditis elegans)
lipo-aKGDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Caenorhabditis elegans)
FAD [mitochondrial matrix]
GCDH tetramer [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Metabolism of lipids (Caenorhabditis elegans)
Fatty acid metabolism (Caenorhabditis elegans)
Mitochondrial Fatty Acid Beta-Oxidation (Caenorhabditis elegans)
ACAD10 dehydrogenates S-2MPDA-CoA (Caenorhabditis elegans)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Caenorhabditis elegans)
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Caenorhabditis elegans)
Decanoyl-CoA+FAD<=>trans-Dec-2-enoyl-CoA+FADH2 (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Caenorhabditis elegans)
Octanoyl-CoA+FAD<=>trans-Oct-2-enoyl-CoA+FADH2 (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Caenorhabditis elegans)
palmitoyl-CoA+FAD<=>trans-Hexadec-2-enoyl-CoA+FADH2 (Caenorhabditis elegans)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Caenorhabditis elegans)
dehydrogenation of 4-cis-decenoyl-CoA to form 2-trans-4-cis-decadienoyl-CoA (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Phospholipid metabolism (Caenorhabditis elegans)
Glycerophospholipid biosynthesis (Caenorhabditis elegans)
Synthesis of PA (Caenorhabditis elegans)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Triglyceride metabolism (Caenorhabditis elegans)
Triglyceride catabolism (Caenorhabditis elegans)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Caenorhabditis elegans)
Electron transport from NADPH to Ferredoxin (Caenorhabditis elegans)
FDXR transfers electrons to FDX1,2 (FDX1L) (Caenorhabditis elegans)
FDXR:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
NADPH transfers electrons to FDXR (Caenorhabditis elegans)
FDXR:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
The citric acid (TCA) cycle and respiratory electron transport (Caenorhabditis elegans)
Pyruvate metabolism and Citric Acid (TCA) cycle (Caenorhabditis elegans)
Citric acid cycle (TCA cycle) (Caenorhabditis elegans)
alpha-ketoglutarate + CoASH + NAD+ => succinyl-CoA + CO2 + NADH + H+ (Caenorhabditis elegans)
lipo-aKGDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Interconversion of 2-oxoglutarate and 2-hydroxyglutarate (Caenorhabditis elegans)
(S)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Pyruvate metabolism (Caenorhabditis elegans)
Regulation of pyruvate dehydrogenase (PDH) complex (Caenorhabditis elegans)
PDK isoforms phosphorylate lipo-PDH (Caenorhabditis elegans)
lipo-PDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
PDP dephosphorylates p-lipo-PDH (Caenorhabditis elegans)
PDP [mitochondrial matrix] (Caenorhabditis elegans)
PDP1 complex [mitochondrial matrix] (Caenorhabditis elegans)
PDPr:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
PDP2 complex [mitochondrial matrix] (Caenorhabditis elegans)
PDPr:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
lipo-PDH decarboxylates PYR to Ac-CoA (Caenorhabditis elegans)
lipo-PDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Caenorhabditis elegans)
Respiratory electron transport (Caenorhabditis elegans)
Complex I biogenesis (Caenorhabditis elegans)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Caenorhabditis elegans)
IP subcomplex [mitochondrial matrix] (Caenorhabditis elegans)
NDUFA9:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Intermediate 1 [mitochondrial inner membrane] (Caenorhabditis elegans)
IP subcomplex [mitochondrial matrix] (Caenorhabditis elegans)
NDUFA9:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Caenorhabditis elegans)
Intermediate 1 [mitochondrial inner membrane] (Caenorhabditis elegans)
IP subcomplex [mitochondrial matrix] (Caenorhabditis elegans)
NDUFA9:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Intermediate 2 [mitochondrial inner membrane] (Caenorhabditis elegans)
Intermediate 1 [mitochondrial inner membrane] (Caenorhabditis elegans)
IP subcomplex [mitochondrial matrix] (Caenorhabditis elegans)
NDUFA9:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
NDUF subunits bind to form the IP subcomplex (Caenorhabditis elegans)
IP subcomplex [mitochondrial matrix] (Caenorhabditis elegans)
NDUFA9:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
NDUFA9:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to QH2 (Caenorhabditis elegans)
ETF:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Reducing equivalents from beta-oxidation of fatty acids transfer to ETF (Caenorhabditis elegans)
FAD [mitochondrial matrix]
ETF:FAD [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Signal Transduction (Caenorhabditis elegans)
Signaling by Nuclear Receptors (Caenorhabditis elegans)
Signaling by Retinoic Acid (Caenorhabditis elegans)
PDK isoforms phosphorylate lipo-PDH (Caenorhabditis elegans)
lipo-PDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 dimer [mitochondrial matrix] (Caenorhabditis elegans)
aKADH E3 [mitochondrial matrix] (Caenorhabditis elegans)
FAD [mitochondrial matrix]
Cellular responses to external stimuli (Canis familiaris)
Cellular responses to stress (Canis familiaris)
Detoxification of Reactive Oxygen Species (Canis familiaris)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Canis familiaris)
GSR dimer [mitochondrial matrix] (Canis familiaris)
GSR holoenzyme [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Canis familiaris)
TXNRD2 dimer [mitochondrial matrix] (Canis familiaris)
TXNRD2 holoenzyme [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Metabolism (Canis familiaris)
Metabolism of amino acids and derivatives (Canis familiaris)
Branched-chain amino acid catabolism (Canis familiaris)
BCKDH transfers CoA group from CoA-SH to BCAAs (Canis familiaris)
lipo-BCKDH [mitochondrial matrix] (Canis familiaris)
aKADH E3 dimer [mitochondrial matrix] (Canis familiaris)
aKADH E3 [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
BCKDK phosphorylates BCKDH (Canis familiaris)
lipo-BCKDH [mitochondrial matrix] (Canis familiaris)
aKADH E3 dimer [mitochondrial matrix] (Canis familiaris)
aKADH E3 [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
p-BCKDH [mitochondrial matrix] (Canis familiaris)
aKADH E3 dimer [mitochondrial matrix] (Canis familiaris)
aKADH E3 [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
PPM1K dephosphorylates p-BCKDH (Canis familiaris)
lipo-BCKDH [mitochondrial matrix] (Canis familiaris)
aKADH E3 dimer [mitochondrial matrix] (Canis familiaris)
aKADH E3 [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
p-BCKDH [mitochondrial matrix] (Canis familiaris)
aKADH E3 dimer [mitochondrial matrix] (Canis familiaris)
aKADH E3 [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
ACADSB tetramer [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
ACAD8 tetramer [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
IVD tetramer [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Choline catabolism (Canis familiaris)
CHDH oxidises Cho to BETALD (Canis familiaris)
FAD [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Canis familiaris)
DMGDH:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Canis familiaris)
SARDH:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Canis familiaris)
LIPT1 transfers lipoyl group from lipoyl-GCSH to DHs (Canis familiaris)
DHs [mitochondrial matrix] (Canis familiaris)
BCKDH [mitochondrial matrix] (Canis familiaris)
aKADH E3 dimer [mitochondrial matrix] (Canis familiaris)
aKADH E3 [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
lipoylated DHs [mitochondrial matrix] (Canis familiaris)
lipo-BCKDH [mitochondrial matrix] (Canis familiaris)
aKADH E3 dimer [mitochondrial matrix] (Canis familiaris)
aKADH E3 [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Lysine catabolism (Canis familiaris)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Canis familiaris)
FAD [mitochondrial matrix]
GCDH tetramer [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Metabolism of lipids (Canis familiaris)
Fatty acid metabolism (Canis familiaris)
Mitochondrial Fatty Acid Beta-Oxidation (Canis familiaris)
ACAD11 dehydrogenates BH-CoA (Canis familiaris)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Canis familiaris)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Canis familiaris)
Butanoyl-CoA+FAD<=>Crotonoyl-CoA+FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Canis familiaris)
Decanoyl-CoA+FAD<=>trans-Dec-2-enoyl-CoA+FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Canis familiaris)
Hexanoyl-CoA+FAD<=>trans-Hex-2-enoyl-CoA+FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Canis familiaris)
lauroyl-CoA+FAD<=>2-trans-Dodecenoyl-CoA+FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Canis familiaris)
myristoyl-CoA+FAD<=>trans-Tetradec-2-enoyl-CoA+FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Canis familiaris)
Octanoyl-CoA+FAD<=>trans-Oct-2-enoyl-CoA+FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Canis familiaris)
palmitoyl-CoA+FAD<=>trans-Hexadec-2-enoyl-CoA+FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Canis familiaris)
dehydrogenation of 4-cis-decenoyl-CoA to form 2-trans-4-cis-decadienoyl-CoA (Canis familiaris)
FAD [mitochondrial matrix]
Phospholipid metabolism (Canis familiaris)
Glycerophospholipid biosynthesis (Canis familiaris)
Synthesis of PA (Canis familiaris)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Canis familiaris)
FAD [mitochondrial matrix]
Triglyceride metabolism (Canis familiaris)
Triglyceride catabolism (Canis familiaris)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Canis familiaris)
FAD [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Canis familiaris)
Electron transport from NADPH to Ferredoxin (Canis familiaris)
FDXR transfers electrons to FDX1,2 (FDX1L) (Canis familiaris)
FDXR:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
NADPH transfers electrons to FDXR (Canis familiaris)
FDXR:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
The citric acid (TCA) cycle and respiratory electron transport (Canis familiaris)
Pyruvate metabolism and Citric Acid (TCA) cycle (Canis familiaris)
Interconversion of 2-oxoglutarate and 2-hydroxyglutarate (Canis familiaris)
(R)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
(S)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Canis familiaris)
FAD [mitochondrial matrix]
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Canis familiaris)
Respiratory electron transport (Canis familiaris)
Complex I biogenesis (Canis familiaris)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Canis familiaris)
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Intermediate 2 [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Canis familiaris)
315kDa subcomplex [mitochondrial inner membrane] (Canis familiaris)
Intermediate 2 [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Intermediate 2 [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Canis familiaris)
550kDa complex [mitochondrial inner membrane] (Canis familiaris)
315kDa subcomplex [mitochondrial inner membrane] (Canis familiaris)
Intermediate 2 [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
815kDa complex [mitochondrial inner membrane] (Canis familiaris)
550kDa complex [mitochondrial inner membrane] (Canis familiaris)
315kDa subcomplex [mitochondrial inner membrane] (Canis familiaris)
Intermediate 2 [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
NDUF subunits bind to form the IP subcomplex (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Canis familiaris)
815kDa complex [mitochondrial inner membrane] (Canis familiaris)
550kDa complex [mitochondrial inner membrane] (Canis familiaris)
315kDa subcomplex [mitochondrial inner membrane] (Canis familiaris)
Intermediate 2 [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
980kDa complex [mitochondrial inner membrane] (Canis familiaris)
815kDa complex [mitochondrial inner membrane] (Canis familiaris)
550kDa complex [mitochondrial inner membrane] (Canis familiaris)
315kDa subcomplex [mitochondrial inner membrane] (Canis familiaris)
Intermediate 2 [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Canis familiaris)
315kDa subcomplex [mitochondrial inner membrane] (Canis familiaris)
Intermediate 2 [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
550kDa complex [mitochondrial inner membrane] (Canis familiaris)
315kDa subcomplex [mitochondrial inner membrane] (Canis familiaris)
Intermediate 2 [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Canis familiaris)
980kDa complex [mitochondrial inner membrane] (Canis familiaris)
815kDa complex [mitochondrial inner membrane] (Canis familiaris)
550kDa complex [mitochondrial inner membrane] (Canis familiaris)
315kDa subcomplex [mitochondrial inner membrane] (Canis familiaris)
Intermediate 2 [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 [mitochondrial inner membrane] (Canis familiaris)
IP subcomplex [mitochondrial matrix] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Complex I [mitochondrial inner membrane] (Canis familiaris)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Canis familiaris)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Canis familiaris)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Canis familiaris)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Canis familiaris)
Complex I [mitochondrial inner membrane] (Canis familiaris)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Canis familiaris)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Canis familiaris)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Canis familiaris)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Canis familiaris)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Canis familiaris)
NDUFA9:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to QH2 (Canis familiaris)
ETF:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Reducing equivalents from beta-oxidation of fatty acids transfer to ETF (Canis familiaris)
FAD [mitochondrial matrix]
ETF:FAD [mitochondrial matrix] (Canis familiaris)
FAD [mitochondrial matrix]
Cellular responses to external stimuli (Danio rerio)
Cellular responses to stress (Danio rerio)
Detoxification of Reactive Oxygen Species (Danio rerio)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Danio rerio)
GSR dimer [mitochondrial matrix] (Danio rerio)
GSR holoenzyme [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Danio rerio)
TXNRD2 dimer [mitochondrial matrix] (Danio rerio)
TXNRD2 holoenzyme [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Metabolism (Danio rerio)
Metabolism of amino acids and derivatives (Danio rerio)
Branched-chain amino acid catabolism (Danio rerio)
BCKDH transfers CoA group from CoA-SH to BCAAs (Danio rerio)
lipo-BCKDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
BCKDK phosphorylates BCKDH (Danio rerio)
lipo-BCKDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
p-BCKDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
PPM1K dephosphorylates p-BCKDH (Danio rerio)
lipo-BCKDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
p-BCKDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Danio rerio)
FAD [mitochondrial matrix]
ACADSB tetramer [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Danio rerio)
FAD [mitochondrial matrix]
ACAD8 tetramer [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Danio rerio)
FAD [mitochondrial matrix]
IVD tetramer [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Choline catabolism (Danio rerio)
CHDH oxidises Cho to BETALD (Danio rerio)
FAD [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Danio rerio)
DMGDH:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Danio rerio)
SARDH:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Danio rerio)
Glycine degradation (Danio rerio)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Danio rerio)
DLD dimer:2xFAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
LIPT1 transfers lipoyl group from lipoyl-GCSH to DHs (Danio rerio)
DHs [mitochondrial matrix] (Danio rerio)
BCKDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
PDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
aKGDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
lipoylated DHs [mitochondrial matrix] (Danio rerio)
lipo-BCKDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
lipo-aKGDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Lysine catabolism (Danio rerio)
alpha-ketoadipate + CoASH + NAD+ => glutaryl-CoA + CO2 + NADH + H+ (Danio rerio)
lipo-aKGDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Danio rerio)
FAD [mitochondrial matrix]
GCDH tetramer [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Metabolism of lipids (Danio rerio)
Fatty acid metabolism (Danio rerio)
Mitochondrial Fatty Acid Beta-Oxidation (Danio rerio)
ACAD11 dehydrogenates BH-CoA (Danio rerio)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Danio rerio)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Danio rerio)
Butanoyl-CoA+FAD<=>Crotonoyl-CoA+FADH2 (Danio rerio)
FAD [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Danio rerio)
Decanoyl-CoA+FAD<=>trans-Dec-2-enoyl-CoA+FADH2 (Danio rerio)
FAD [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Danio rerio)
Hexanoyl-CoA+FAD<=>trans-Hex-2-enoyl-CoA+FADH2 (Danio rerio)
FAD [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Danio rerio)
lauroyl-CoA+FAD<=>2-trans-Dodecenoyl-CoA+FADH2 (Danio rerio)
FAD [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Danio rerio)
myristoyl-CoA+FAD<=>trans-Tetradec-2-enoyl-CoA+FADH2 (Danio rerio)
FAD [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Danio rerio)
Octanoyl-CoA+FAD<=>trans-Oct-2-enoyl-CoA+FADH2 (Danio rerio)
FAD [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Danio rerio)
palmitoyl-CoA+FAD<=>trans-Hexadec-2-enoyl-CoA+FADH2 (Danio rerio)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Danio rerio)
dehydrogenation of 4-cis-decenoyl-CoA to form 2-trans-4-cis-decadienoyl-CoA (Danio rerio)
FAD [mitochondrial matrix]
Phospholipid metabolism (Danio rerio)
Glycerophospholipid biosynthesis (Danio rerio)
Synthesis of PA (Danio rerio)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Danio rerio)
FAD [mitochondrial matrix]
Triglyceride metabolism (Danio rerio)
Triglyceride catabolism (Danio rerio)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Danio rerio)
FAD [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Danio rerio)
Electron transport from NADPH to Ferredoxin (Danio rerio)
FDXR transfers electrons to FDX1,2 (FDX1L) (Danio rerio)
FDXR:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
NADPH transfers electrons to FDXR (Danio rerio)
FDXR:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
The citric acid (TCA) cycle and respiratory electron transport (Danio rerio)
Pyruvate metabolism and Citric Acid (TCA) cycle (Danio rerio)
Citric acid cycle (TCA cycle) (Danio rerio)
alpha-ketoglutarate + CoASH + NAD+ => succinyl-CoA + CO2 + NADH + H+ (Danio rerio)
lipo-aKGDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Interconversion of 2-oxoglutarate and 2-hydroxyglutarate (Danio rerio)
(R)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Danio rerio)
FAD [mitochondrial matrix]
(S)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Danio rerio)
FAD [mitochondrial matrix]
Pyruvate metabolism (Danio rerio)
Regulation of pyruvate dehydrogenase (PDH) complex (Danio rerio)
PDK isoforms phosphorylate lipo-PDH (Danio rerio)
lipo-PDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
PDP dephosphorylates p-lipo-PDH (Danio rerio)
PDP [mitochondrial matrix] (Danio rerio)
PDP1 complex [mitochondrial matrix] (Danio rerio)
PDPr:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
PDP2 complex [mitochondrial matrix] (Danio rerio)
PDPr:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
lipo-PDH decarboxylates PYR to Ac-CoA (Danio rerio)
lipo-PDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Danio rerio)
Respiratory electron transport (Danio rerio)
Complex I biogenesis (Danio rerio)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Danio rerio)
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Intermediate 2 [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Danio rerio)
315kDa subcomplex [mitochondrial inner membrane] (Danio rerio)
Intermediate 2 [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Intermediate 2 [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Danio rerio)
550kDa complex [mitochondrial inner membrane] (Danio rerio)
315kDa subcomplex [mitochondrial inner membrane] (Danio rerio)
Intermediate 2 [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
815kDa complex [mitochondrial inner membrane] (Danio rerio)
550kDa complex [mitochondrial inner membrane] (Danio rerio)
315kDa subcomplex [mitochondrial inner membrane] (Danio rerio)
Intermediate 2 [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
NDUF subunits bind to form the IP subcomplex (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Danio rerio)
815kDa complex [mitochondrial inner membrane] (Danio rerio)
550kDa complex [mitochondrial inner membrane] (Danio rerio)
315kDa subcomplex [mitochondrial inner membrane] (Danio rerio)
Intermediate 2 [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
980kDa complex [mitochondrial inner membrane] (Danio rerio)
815kDa complex [mitochondrial inner membrane] (Danio rerio)
550kDa complex [mitochondrial inner membrane] (Danio rerio)
315kDa subcomplex [mitochondrial inner membrane] (Danio rerio)
Intermediate 2 [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Danio rerio)
315kDa subcomplex [mitochondrial inner membrane] (Danio rerio)
Intermediate 2 [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
550kDa complex [mitochondrial inner membrane] (Danio rerio)
315kDa subcomplex [mitochondrial inner membrane] (Danio rerio)
Intermediate 2 [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Danio rerio)
980kDa complex [mitochondrial inner membrane] (Danio rerio)
815kDa complex [mitochondrial inner membrane] (Danio rerio)
550kDa complex [mitochondrial inner membrane] (Danio rerio)
315kDa subcomplex [mitochondrial inner membrane] (Danio rerio)
Intermediate 2 [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 [mitochondrial inner membrane] (Danio rerio)
IP subcomplex [mitochondrial matrix] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Complex I [mitochondrial inner membrane] (Danio rerio)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Danio rerio)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Danio rerio)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Danio rerio)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Danio rerio)
Complex I [mitochondrial inner membrane] (Danio rerio)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Danio rerio)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Danio rerio)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Danio rerio)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Danio rerio)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Danio rerio)
NDUFA9:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to QH2 (Danio rerio)
ETF:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Reducing equivalents from beta-oxidation of fatty acids transfer to ETF (Danio rerio)
FAD [mitochondrial matrix]
ETF:FAD [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Signal Transduction (Danio rerio)
Signaling by Nuclear Receptors (Danio rerio)
Signaling by Retinoic Acid (Danio rerio)
PDK isoforms phosphorylate lipo-PDH (Danio rerio)
lipo-PDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Danio rerio)
aKADH E3 dimer [mitochondrial matrix] (Danio rerio)
aKADH E3 [mitochondrial matrix] (Danio rerio)
FAD [mitochondrial matrix]
Cellular responses to external stimuli (Dictyostelium discoideum)
Cellular responses to stress (Dictyostelium discoideum)
Detoxification of Reactive Oxygen Species (Dictyostelium discoideum)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Dictyostelium discoideum)
GSR dimer [mitochondrial matrix] (Dictyostelium discoideum)
GSR holoenzyme [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Metabolism (Dictyostelium discoideum)
Metabolism of amino acids and derivatives (Dictyostelium discoideum)
Branched-chain amino acid catabolism (Dictyostelium discoideum)
BCKDH transfers CoA group from CoA-SH to BCAAs (Dictyostelium discoideum)
lipo-BCKDH [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 dimer [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Dictyostelium discoideum)
FAD [mitochondrial matrix]
ACADSB tetramer [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Dictyostelium discoideum)
FAD [mitochondrial matrix]
ACAD8 tetramer [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Dictyostelium discoideum)
FAD [mitochondrial matrix]
IVD tetramer [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Choline catabolism (Dictyostelium discoideum)
CHDH oxidises Cho to BETALD (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Dictyostelium discoideum)
Glycine degradation (Dictyostelium discoideum)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Dictyostelium discoideum)
DLD dimer:2xFAD [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
LIPT1 transfers lipoyl group from lipoyl-GCSH to DHs (Dictyostelium discoideum)
DHs [mitochondrial matrix] (Dictyostelium discoideum)
BCKDH [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 dimer [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
PDH [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 dimer [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
aKGDH [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 dimer [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
lipoylated DHs [mitochondrial matrix] (Dictyostelium discoideum)
lipo-BCKDH [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 dimer [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 dimer [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
lipo-aKGDH [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 dimer [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Lysine catabolism (Dictyostelium discoideum)
alpha-ketoadipate + CoASH + NAD+ => glutaryl-CoA + CO2 + NADH + H+ (Dictyostelium discoideum)
lipo-aKGDH [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 dimer [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Dictyostelium discoideum)
FAD [mitochondrial matrix]
GCDH tetramer [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Metabolism of lipids (Dictyostelium discoideum)
Phospholipid metabolism (Dictyostelium discoideum)
Glycerophospholipid biosynthesis (Dictyostelium discoideum)
Synthesis of PA (Dictyostelium discoideum)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Triglyceride metabolism (Dictyostelium discoideum)
Triglyceride catabolism (Dictyostelium discoideum)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Dictyostelium discoideum)
Electron transport from NADPH to Ferredoxin (Dictyostelium discoideum)
FDXR transfers electrons to FDX1,2 (FDX1L) (Dictyostelium discoideum)
FDXR:FAD [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
NADPH transfers electrons to FDXR (Dictyostelium discoideum)
FDXR:FAD [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
The citric acid (TCA) cycle and respiratory electron transport (Dictyostelium discoideum)
Pyruvate metabolism and Citric Acid (TCA) cycle (Dictyostelium discoideum)
Citric acid cycle (TCA cycle) (Dictyostelium discoideum)
alpha-ketoglutarate + CoASH + NAD+ => succinyl-CoA + CO2 + NADH + H+ (Dictyostelium discoideum)
lipo-aKGDH [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 dimer [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Interconversion of 2-oxoglutarate and 2-hydroxyglutarate (Dictyostelium discoideum)
(S)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Pyruvate metabolism (Dictyostelium discoideum)
lipo-PDH decarboxylates PYR to Ac-CoA (Dictyostelium discoideum)
lipo-PDH [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 dimer [mitochondrial matrix] (Dictyostelium discoideum)
aKADH E3 [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Dictyostelium discoideum)
Respiratory electron transport (Dictyostelium discoideum)
Complex I biogenesis (Dictyostelium discoideum)
NDUF subunits bind to form the IP subcomplex (Dictyostelium discoideum)
IP subcomplex [mitochondrial matrix] (Dictyostelium discoideum)
NDUFA9:FAD [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
NDUFA9:FAD [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to QH2 (Dictyostelium discoideum)
ETF:FAD [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Reducing equivalents from beta-oxidation of fatty acids transfer to ETF (Dictyostelium discoideum)
FAD [mitochondrial matrix]
ETF:FAD [mitochondrial matrix] (Dictyostelium discoideum)
FAD [mitochondrial matrix]
Metabolism (Drosophila melanogaster)
Metabolism of amino acids and derivatives (Drosophila melanogaster)
Branched-chain amino acid catabolism (Drosophila melanogaster)
BCKDH transfers CoA group from CoA-SH to BCAAs (Drosophila melanogaster)
lipo-BCKDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Drosophila melanogaster)
FAD [mitochondrial matrix]
ACADSB tetramer [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Drosophila melanogaster)
FAD [mitochondrial matrix]
IVD tetramer [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Choline catabolism (Drosophila melanogaster)
CHDH oxidises Cho to BETALD (Drosophila melanogaster)
FAD [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Drosophila melanogaster)
SARDH:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Drosophila melanogaster)
Glycine degradation (Drosophila melanogaster)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Drosophila melanogaster)
DLD dimer:2xFAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
LIPT1 transfers lipoyl group from lipoyl-GCSH to DHs (Drosophila melanogaster)
DHs [mitochondrial matrix] (Drosophila melanogaster)
BCKDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
PDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
aKGDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
lipoylated DHs [mitochondrial matrix] (Drosophila melanogaster)
lipo-BCKDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
lipo-aKGDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Lysine catabolism (Drosophila melanogaster)
alpha-ketoadipate + CoASH + NAD+ => glutaryl-CoA + CO2 + NADH + H+ (Drosophila melanogaster)
lipo-aKGDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Drosophila melanogaster)
FAD [mitochondrial matrix]
GCDH tetramer [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Metabolism of lipids (Drosophila melanogaster)
Fatty acid metabolism (Drosophila melanogaster)
Mitochondrial Fatty Acid Beta-Oxidation (Drosophila melanogaster)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Drosophila melanogaster)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Drosophila melanogaster)
Butanoyl-CoA+FAD<=>Crotonoyl-CoA+FADH2 (Drosophila melanogaster)
FAD [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Drosophila melanogaster)
Decanoyl-CoA+FAD<=>trans-Dec-2-enoyl-CoA+FADH2 (Drosophila melanogaster)
FAD [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Drosophila melanogaster)
Hexanoyl-CoA+FAD<=>trans-Hex-2-enoyl-CoA+FADH2 (Drosophila melanogaster)
FAD [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Drosophila melanogaster)
Octanoyl-CoA+FAD<=>trans-Oct-2-enoyl-CoA+FADH2 (Drosophila melanogaster)
FAD [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Drosophila melanogaster)
palmitoyl-CoA+FAD<=>trans-Hexadec-2-enoyl-CoA+FADH2 (Drosophila melanogaster)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Drosophila melanogaster)
dehydrogenation of 4-cis-decenoyl-CoA to form 2-trans-4-cis-decadienoyl-CoA (Drosophila melanogaster)
FAD [mitochondrial matrix]
Phospholipid metabolism (Drosophila melanogaster)
Glycerophospholipid biosynthesis (Drosophila melanogaster)
Synthesis of PA (Drosophila melanogaster)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Drosophila melanogaster)
FAD [mitochondrial matrix]
Triglyceride metabolism (Drosophila melanogaster)
Triglyceride catabolism (Drosophila melanogaster)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Drosophila melanogaster)
FAD [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Drosophila melanogaster)
Electron transport from NADPH to Ferredoxin (Drosophila melanogaster)
FDXR transfers electrons to FDX1,2 (FDX1L) (Drosophila melanogaster)
FDXR:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
NADPH transfers electrons to FDXR (Drosophila melanogaster)
FDXR:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
The citric acid (TCA) cycle and respiratory electron transport (Drosophila melanogaster)
Pyruvate metabolism and Citric Acid (TCA) cycle (Drosophila melanogaster)
Citric acid cycle (TCA cycle) (Drosophila melanogaster)
alpha-ketoglutarate + CoASH + NAD+ => succinyl-CoA + CO2 + NADH + H+ (Drosophila melanogaster)
lipo-aKGDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Interconversion of 2-oxoglutarate and 2-hydroxyglutarate (Drosophila melanogaster)
(S)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Drosophila melanogaster)
FAD [mitochondrial matrix]
Pyruvate metabolism (Drosophila melanogaster)
Regulation of pyruvate dehydrogenase (PDH) complex (Drosophila melanogaster)
PDK isoforms phosphorylate lipo-PDH (Drosophila melanogaster)
lipo-PDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
PDP dephosphorylates p-lipo-PDH (Drosophila melanogaster)
PDP [mitochondrial matrix] (Drosophila melanogaster)
PDP1 complex [mitochondrial matrix] (Drosophila melanogaster)
PDPr:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
PDP2 complex [mitochondrial matrix] (Drosophila melanogaster)
PDPr:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
lipo-PDH decarboxylates PYR to Ac-CoA (Drosophila melanogaster)
lipo-PDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Drosophila melanogaster)
Respiratory electron transport (Drosophila melanogaster)
Complex I biogenesis (Drosophila melanogaster)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Intermediate 1 [mitochondrial inner membrane] (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Drosophila melanogaster)
Intermediate 1 [mitochondrial inner membrane] (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Intermediate 2 [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 1 [mitochondrial inner membrane] (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Drosophila melanogaster)
315kDa subcomplex [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 2 [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 1 [mitochondrial inner membrane] (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Intermediate 2 [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 1 [mitochondrial inner membrane] (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Drosophila melanogaster)
550kDa complex [mitochondrial inner membrane] (Drosophila melanogaster)
315kDa subcomplex [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 2 [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 1 [mitochondrial inner membrane] (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
815kDa complex [mitochondrial inner membrane] (Drosophila melanogaster)
550kDa complex [mitochondrial inner membrane] (Drosophila melanogaster)
315kDa subcomplex [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 2 [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 1 [mitochondrial inner membrane] (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
NDUF subunits bind to form the IP subcomplex (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Drosophila melanogaster)
315kDa subcomplex [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 2 [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 1 [mitochondrial inner membrane] (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
550kDa complex [mitochondrial inner membrane] (Drosophila melanogaster)
315kDa subcomplex [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 2 [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 1 [mitochondrial inner membrane] (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Drosophila melanogaster)
980kDa complex [mitochondrial inner membrane] (Drosophila melanogaster)
815kDa complex [mitochondrial inner membrane] (Drosophila melanogaster)
550kDa complex [mitochondrial inner membrane] (Drosophila melanogaster)
315kDa subcomplex [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 2 [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 1 [mitochondrial inner membrane] (Drosophila melanogaster)
IP subcomplex [mitochondrial matrix] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Complex I [mitochondrial inner membrane] (Drosophila melanogaster)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Drosophila melanogaster)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Drosophila melanogaster)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Drosophila melanogaster)
Complex I [mitochondrial inner membrane] (Drosophila melanogaster)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Drosophila melanogaster)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Drosophila melanogaster)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Drosophila melanogaster)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Drosophila melanogaster)
NDUFA9:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to QH2 (Drosophila melanogaster)
ETF:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Reducing equivalents from beta-oxidation of fatty acids transfer to ETF (Drosophila melanogaster)
FAD [mitochondrial matrix]
ETF:FAD [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Signal Transduction (Drosophila melanogaster)
Signaling by Nuclear Receptors (Drosophila melanogaster)
Signaling by Retinoic Acid (Drosophila melanogaster)
PDK isoforms phosphorylate lipo-PDH (Drosophila melanogaster)
lipo-PDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 dimer [mitochondrial matrix] (Drosophila melanogaster)
aKADH E3 [mitochondrial matrix] (Drosophila melanogaster)
FAD [mitochondrial matrix]
Cellular responses to external stimuli (Gallus gallus)
Cellular responses to stress (Gallus gallus)
Detoxification of Reactive Oxygen Species (Gallus gallus)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Gallus gallus)
GSR dimer [mitochondrial matrix] (Gallus gallus)
GSR holoenzyme [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Gallus gallus)
TXNRD2 dimer [mitochondrial matrix] (Gallus gallus)
TXNRD2 holoenzyme [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Metabolism (Gallus gallus)
Metabolism of amino acids and derivatives (Gallus gallus)
Branched-chain amino acid catabolism (Gallus gallus)
BCKDH transfers CoA group from CoA-SH to BCAAs (Gallus gallus)
lipo-BCKDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
PPM1K dephosphorylates p-BCKDH (Gallus gallus)
lipo-BCKDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
p-BCKDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Gallus gallus)
FAD [mitochondrial matrix]
ACADSB tetramer [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Gallus gallus)
FAD [mitochondrial matrix]
ACAD8 tetramer [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Gallus gallus)
FAD [mitochondrial matrix]
IVD tetramer [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Choline catabolism (Gallus gallus)
CHDH oxidises Cho to BETALD (Gallus gallus)
FAD [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Gallus gallus)
DMGDH:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Gallus gallus)
SARDH:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Gallus gallus)
Glycine degradation (Gallus gallus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Gallus gallus)
DLD dimer:2xFAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
LIPT1 transfers lipoyl group from lipoyl-GCSH to DHs (Gallus gallus)
DHs [mitochondrial matrix] (Gallus gallus)
BCKDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
PDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
aKGDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
lipoylated DHs [mitochondrial matrix] (Gallus gallus)
lipo-BCKDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
lipo-aKGDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Lysine catabolism (Gallus gallus)
alpha-ketoadipate + CoASH + NAD+ => glutaryl-CoA + CO2 + NADH + H+ (Gallus gallus)
lipo-aKGDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Gallus gallus)
FAD [mitochondrial matrix]
GCDH tetramer [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Metabolism of lipids (Gallus gallus)
Fatty acid metabolism (Gallus gallus)
Mitochondrial Fatty Acid Beta-Oxidation (Gallus gallus)
ACAD11 dehydrogenates BH-CoA (Gallus gallus)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Gallus gallus)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Gallus gallus)
Butanoyl-CoA+FAD<=>Crotonoyl-CoA+FADH2 (Gallus gallus)
FAD [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Gallus gallus)
Decanoyl-CoA+FAD<=>trans-Dec-2-enoyl-CoA+FADH2 (Gallus gallus)
FAD [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Gallus gallus)
Hexanoyl-CoA+FAD<=>trans-Hex-2-enoyl-CoA+FADH2 (Gallus gallus)
FAD [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Gallus gallus)
lauroyl-CoA+FAD<=>2-trans-Dodecenoyl-CoA+FADH2 (Gallus gallus)
FAD [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Gallus gallus)
myristoyl-CoA+FAD<=>trans-Tetradec-2-enoyl-CoA+FADH2 (Gallus gallus)
FAD [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Gallus gallus)
Octanoyl-CoA+FAD<=>trans-Oct-2-enoyl-CoA+FADH2 (Gallus gallus)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Gallus gallus)
dehydrogenation of 4-cis-decenoyl-CoA to form 2-trans-4-cis-decadienoyl-CoA (Gallus gallus)
FAD [mitochondrial matrix]
Phospholipid metabolism (Gallus gallus)
Glycerophospholipid biosynthesis (Gallus gallus)
Synthesis of PA (Gallus gallus)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Gallus gallus)
FAD [mitochondrial matrix]
Triglyceride metabolism (Gallus gallus)
Triglyceride catabolism (Gallus gallus)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Gallus gallus)
FAD [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Gallus gallus)
Electron transport from NADPH to Ferredoxin (Gallus gallus)
NADPH transfers electrons to FDXR (Gallus gallus)
FDXR:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
The citric acid (TCA) cycle and respiratory electron transport (Gallus gallus)
Pyruvate metabolism and Citric Acid (TCA) cycle (Gallus gallus)
Citric acid cycle (TCA cycle) (Gallus gallus)
alpha-ketoglutarate + CoASH + NAD+ => succinyl-CoA + CO2 + NADH + H+ (Gallus gallus)
lipo-aKGDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Interconversion of 2-oxoglutarate and 2-hydroxyglutarate (Gallus gallus)
(R)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Gallus gallus)
FAD [mitochondrial matrix]
(S)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Gallus gallus)
FAD [mitochondrial matrix]
Pyruvate metabolism (Gallus gallus)
Regulation of pyruvate dehydrogenase (PDH) complex (Gallus gallus)
PDK isoforms phosphorylate lipo-PDH (Gallus gallus)
lipo-PDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
PDP dephosphorylates p-lipo-PDH (Gallus gallus)
PDP [mitochondrial matrix] (Gallus gallus)
PDP1 complex [mitochondrial matrix] (Gallus gallus)
PDPr:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
PDP2 complex [mitochondrial matrix] (Gallus gallus)
PDPr:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
lipo-PDH decarboxylates PYR to Ac-CoA (Gallus gallus)
lipo-PDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Gallus gallus)
Respiratory electron transport (Gallus gallus)
Complex I biogenesis (Gallus gallus)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Gallus gallus)
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Intermediate 2 [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Gallus gallus)
315kDa subcomplex [mitochondrial inner membrane] (Gallus gallus)
Intermediate 2 [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Intermediate 2 [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Gallus gallus)
550kDa complex [mitochondrial inner membrane] (Gallus gallus)
315kDa subcomplex [mitochondrial inner membrane] (Gallus gallus)
Intermediate 2 [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
815kDa complex [mitochondrial inner membrane] (Gallus gallus)
550kDa complex [mitochondrial inner membrane] (Gallus gallus)
315kDa subcomplex [mitochondrial inner membrane] (Gallus gallus)
Intermediate 2 [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
NDUF subunits bind to form the IP subcomplex (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Gallus gallus)
815kDa complex [mitochondrial inner membrane] (Gallus gallus)
550kDa complex [mitochondrial inner membrane] (Gallus gallus)
315kDa subcomplex [mitochondrial inner membrane] (Gallus gallus)
Intermediate 2 [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
980kDa complex [mitochondrial inner membrane] (Gallus gallus)
815kDa complex [mitochondrial inner membrane] (Gallus gallus)
550kDa complex [mitochondrial inner membrane] (Gallus gallus)
315kDa subcomplex [mitochondrial inner membrane] (Gallus gallus)
Intermediate 2 [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Gallus gallus)
315kDa subcomplex [mitochondrial inner membrane] (Gallus gallus)
Intermediate 2 [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
550kDa complex [mitochondrial inner membrane] (Gallus gallus)
315kDa subcomplex [mitochondrial inner membrane] (Gallus gallus)
Intermediate 2 [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Gallus gallus)
980kDa complex [mitochondrial inner membrane] (Gallus gallus)
815kDa complex [mitochondrial inner membrane] (Gallus gallus)
550kDa complex [mitochondrial inner membrane] (Gallus gallus)
315kDa subcomplex [mitochondrial inner membrane] (Gallus gallus)
Intermediate 2 [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 [mitochondrial inner membrane] (Gallus gallus)
IP subcomplex [mitochondrial matrix] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Complex I [mitochondrial inner membrane] (Gallus gallus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Gallus gallus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Gallus gallus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Gallus gallus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Gallus gallus)
Complex I [mitochondrial inner membrane] (Gallus gallus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Gallus gallus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Gallus gallus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Gallus gallus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Gallus gallus)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Gallus gallus)
NDUFA9:FAD [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Signal Transduction (Gallus gallus)
Signaling by Nuclear Receptors (Gallus gallus)
Signaling by Retinoic Acid (Gallus gallus)
PDK isoforms phosphorylate lipo-PDH (Gallus gallus)
lipo-PDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Gallus gallus)
aKADH E3 dimer [mitochondrial matrix] (Gallus gallus)
aKADH E3 [mitochondrial matrix] (Gallus gallus)
FAD [mitochondrial matrix]
Cellular responses to external stimuli (Homo sapiens)
Cellular responses to stress (Homo sapiens)
Detoxification of Reactive Oxygen Species (Homo sapiens)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Homo sapiens)
GSR dimer [mitochondrial matrix] (Homo sapiens)
GSR holoenzyme [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Homo sapiens)
TXNRD2 dimer [mitochondrial matrix] (Homo sapiens)
TXNRD2 holoenzyme [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Branched-chain amino acid catabolism (Homo sapiens)
BCKDH transfers CoA group from CoA-SH to BCAAs (Homo sapiens)
lipo-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
BCKDK phosphorylates BCKDH (Homo sapiens)
lipo-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
p-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
PPM1K dephosphorylates p-BCKDH (Homo sapiens)
lipo-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
p-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
ACADSB tetramer [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
ACAD8 tetramer [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
IVD tetramer [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Choline catabolism (Homo sapiens)
CHDH oxidises Cho to BETALD (Homo sapiens)
FAD [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Homo sapiens)
DMGDH:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Homo sapiens)
SARDH:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Homo sapiens)
Glycine degradation (Homo sapiens)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Homo sapiens)
DLD dimer:2xFAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
LIPT1 transfers lipoyl group from lipoyl-GCSH to DHs (Homo sapiens)
DHs [mitochondrial matrix] (Homo sapiens)
BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
aKGDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
lipoylated DHs [mitochondrial matrix] (Homo sapiens)
lipo-BCKDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
lipo-aKGDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Lysine catabolism (Homo sapiens)
alpha-ketoadipate + CoASH + NAD+ => glutaryl-CoA + CO2 + NADH + H+ (Homo sapiens)
lipo-aKGDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Homo sapiens)
FAD [mitochondrial matrix]
GCDH tetramer [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Mitochondrial Fatty Acid Beta-Oxidation (Homo sapiens)
ACAD10 dehydrogenates S-2MPDA-CoA (Homo sapiens)
FAD [mitochondrial matrix]
ACAD11 dehydrogenates BH-CoA (Homo sapiens)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Homo sapiens)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Homo sapiens)
Butanoyl-CoA+FAD<=>Crotonoyl-CoA+FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Homo sapiens)
Decanoyl-CoA+FAD<=>trans-Dec-2-enoyl-CoA+FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Homo sapiens)
Hexanoyl-CoA+FAD<=>trans-Hex-2-enoyl-CoA+FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Homo sapiens)
lauroyl-CoA+FAD<=>2-trans-Dodecenoyl-CoA+FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Homo sapiens)
myristoyl-CoA+FAD<=>trans-Tetradec-2-enoyl-CoA+FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Homo sapiens)
Octanoyl-CoA+FAD<=>trans-Oct-2-enoyl-CoA+FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Homo sapiens)
palmitoyl-CoA+FAD<=>trans-Hexadec-2-enoyl-CoA+FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Homo sapiens)
Linoleoyl-CoA is converted to cis,cis-3,6- dodecadienoyl-CoA by three cycles of beta-oxidation (Homo sapiens)
FAD [mitochondrial matrix]
Trans,cis-lauro-2,6-dienoyl-CoA is converted to cis,cis-3,6- 4-cis-decenoyl-CoA by one cycle of beta-oxidation (Homo sapiens)
FAD [mitochondrial matrix]
dehydrogenation of 4-cis-decenoyl-CoA to form 2-trans-4-cis-decadienoyl-CoA (Homo sapiens)
FAD [mitochondrial matrix]
Phospholipid metabolism (Homo sapiens)
Glycerophospholipid biosynthesis (Homo sapiens)
Synthesis of PA (Homo sapiens)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Homo sapiens)
FAD [mitochondrial matrix]
Triglyceride metabolism (Homo sapiens)
Triglyceride catabolism (Homo sapiens)
Gly-3-P+FAD->DHAP+FADH2 (catalyzed by mitochondrial Gly-Phos dehydrogenase) (Homo sapiens)
FAD [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Homo sapiens)
Electron transport from NADPH to Ferredoxin (Homo sapiens)
FDXR transfers electrons to FDX1,2 (FDX1L) (Homo sapiens)
FDXR:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
NADPH transfers electrons to FDXR (Homo sapiens)
FDXR:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Pyruvate metabolism and Citric Acid (TCA) cycle (Homo sapiens)
Citric acid cycle (TCA cycle) (Homo sapiens)
alpha-ketoglutarate + CoASH + NAD+ => succinyl-CoA + CO2 + NADH + H+ (Homo sapiens)
lipo-aKGDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Interconversion of 2-oxoglutarate and 2-hydroxyglutarate (Homo sapiens)
(R)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
(S)-2-hydroxyglutarate + FAD => 2-oxoglutarate + FADH2 (Homo sapiens)
FAD [mitochondrial matrix]
Pyruvate metabolism (Homo sapiens)
Regulation of pyruvate dehydrogenase (PDH) complex (Homo sapiens)
PDK isoforms phosphorylate lipo-PDH (Homo sapiens)
lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
PDP dephosphorylates p-lipo-PDH (Homo sapiens)
PDP [mitochondrial matrix] (Homo sapiens)
PDP1 complex [mitochondrial matrix] (Homo sapiens)
PDPr:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
PDP2 complex [mitochondrial matrix] (Homo sapiens)
PDPr:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
lipo-PDH decarboxylates PYR to Ac-CoA (Homo sapiens)
lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
NDUF subunits bind to form the IP subcomplex (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 [mitochondrial inner membrane] (Homo sapiens)
IP subcomplex [mitochondrial matrix] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
NDUFA9:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to QH2 (Homo sapiens)
ETF:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Reducing equivalents from beta-oxidation of fatty acids transfer to ETF (Homo sapiens)
FAD [mitochondrial matrix]
ETF:FAD [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Signal Transduction (Homo sapiens)
Signaling by Nuclear Receptors (Homo sapiens)
Signaling by Retinoic Acid (Homo sapiens)
PDK isoforms phosphorylate lipo-PDH (Homo sapiens)
lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
p-lipo-PDH [mitochondrial matrix] (Homo sapiens)
aKADH E3 dimer [mitochondrial matrix] (Homo sapiens)
aKADH E3 [mitochondrial matrix] (Homo sapiens)
FAD [mitochondrial matrix]
Cellular responses to external stimuli (Mus musculus)
Cellular responses to stress (Mus musculus)
Detoxification of Reactive Oxygen Species (Mus musculus)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Mus musculus)
GSR dimer [mitochondrial matrix] (Mus musculus)
GSR holoenzyme [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Mus musculus)
TXNRD2 dimer [mitochondrial matrix] (Mus musculus)
TXNRD2 holoenzyme [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
Metabolism (Mus musculus)
Metabolism of amino acids and derivatives (Mus musculus)
Branched-chain amino acid catabolism (Mus musculus)
BCKDH transfers CoA group from CoA-SH to BCAAs (Mus musculus)
lipo-BCKDH [mitochondrial matrix] (Mus musculus)
aKADH E3 dimer [mitochondrial matrix] (Mus musculus)
aKADH E3 [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
BCKDK phosphorylates BCKDH (Mus musculus)
lipo-BCKDH [mitochondrial matrix] (Mus musculus)
aKADH E3 dimer [mitochondrial matrix] (Mus musculus)
aKADH E3 [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
p-BCKDH [mitochondrial matrix] (Mus musculus)
aKADH E3 dimer [mitochondrial matrix] (Mus musculus)
aKADH E3 [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
PPM1K dephosphorylates p-BCKDH (Mus musculus)
lipo-BCKDH [mitochondrial matrix] (Mus musculus)
aKADH E3 dimer [mitochondrial matrix] (Mus musculus)
aKADH E3 [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
p-BCKDH [mitochondrial matrix] (Mus musculus)
aKADH E3 dimer [mitochondrial matrix] (Mus musculus)
aKADH E3 [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Mus musculus)
FAD [mitochondrial matrix]
ACADSB tetramer [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Mus musculus)
FAD [mitochondrial matrix]
ACAD8 tetramer [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Mus musculus)
FAD [mitochondrial matrix]
IVD tetramer [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
Choline catabolism (Mus musculus)
CHDH oxidises Cho to BETALD (Mus musculus)
FAD [mitochondrial matrix]
DMGDH:FAD oxidatively demethylates DMGLY to SARC (Mus musculus)
DMGDH:FAD [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
SARDH:FAD oxidatively demethylates SARC to Gly (Mus musculus)
SARDH:FAD [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Mus musculus)
Glycine degradation (Mus musculus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Mus musculus)
DLD dimer:2xFAD [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
LIPT1 transfers lipoyl group from lipoyl-GCSH to DHs (Mus musculus)
DHs [mitochondrial matrix] (Mus musculus)
BCKDH [mitochondrial matrix] (Mus musculus)
aKADH E3 dimer [mitochondrial matrix] (Mus musculus)
aKADH E3 [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
PDH [mitochondrial matrix] (Mus musculus)
aKADH E3 dimer [mitochondrial matrix] (Mus musculus)
aKADH E3 [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
aKGDH [mitochondrial matrix] (Mus musculus)
aKADH E3 dimer [mitochondrial matrix] (Mus musculus)
aKADH E3 [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
lipoylated DHs [mitochondrial matrix] (Mus musculus)
lipo-BCKDH [mitochondrial matrix] (Mus musculus)
aKADH E3 dimer [mitochondrial matrix] (Mus musculus)
aKADH E3 [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
lipo-PDH [mitochondrial matrix] (Mus musculus)
aKADH E3 dimer [mitochondrial matrix] (Mus musculus)
aKADH E3 [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]
lipo-aKGDH [mitochondrial matrix] (Mus musculus)
aKADH E3 dimer [mitochondrial matrix] (Mus musculus)
aKADH E3 [mitochondrial matrix] (Mus musculus)
FAD [mitochondrial matrix]