Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
q-BH2 [cytosol]
Stable Identifier
R-ALL-1497857
Type
Chemical Compound [SimpleEntity]
Compartment
cytosol
Synonyms
L-erythro-7,8-dihydrobiopterin, dihydrobiopterin, 7,8-dihydrobiopterin
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Plasmodium falciparum
Rattus norvegicus
Saccharomyces cerevisiae
Schizosaccharomyces pombe
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of lipids (Bos taurus)
Triglyceride metabolism (Bos taurus)
Triglyceride biosynthesis (Bos taurus)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Bos taurus)
q-BH2 [cytosol]
Metabolism of nitric oxide: NOS3 activation and regulation (Bos taurus)
eNOS activation (Bos taurus)
BH2 binding can lead to eNOS uncoupling (Bos taurus)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Bos taurus)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Bos taurus)
Metabolism of cofactors (Bos taurus)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Bos taurus)
BH2 binding can lead to eNOS uncoupling (Bos taurus)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Bos taurus)
q-BH2 [cytosol]
Metabolism (Caenorhabditis elegans)
Metabolism of lipids (Caenorhabditis elegans)
Triglyceride metabolism (Caenorhabditis elegans)
Triglyceride biosynthesis (Caenorhabditis elegans)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Caenorhabditis elegans)
q-BH2 [cytosol]
Metabolism of nitric oxide: NOS3 activation and regulation (Caenorhabditis elegans)
eNOS activation (Caenorhabditis elegans)
BH2 binding can lead to eNOS uncoupling (Caenorhabditis elegans)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Caenorhabditis elegans)
Metabolism of cofactors (Caenorhabditis elegans)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Caenorhabditis elegans)
BH2 binding can lead to eNOS uncoupling (Caenorhabditis elegans)
q-BH2 [cytosol]
Metabolism (Canis familiaris)
Metabolism of lipids (Canis familiaris)
Triglyceride metabolism (Canis familiaris)
Triglyceride biosynthesis (Canis familiaris)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Canis familiaris)
q-BH2 [cytosol]
Metabolism of nitric oxide: NOS3 activation and regulation (Canis familiaris)
eNOS activation (Canis familiaris)
Salvage - Sepiapterin is reduced to q-BH2 (Canis familiaris)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Canis familiaris)
Metabolism of cofactors (Canis familiaris)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Canis familiaris)
Salvage - Sepiapterin is reduced to q-BH2 (Canis familiaris)
q-BH2 [cytosol]
Metabolism (Danio rerio)
Metabolism of lipids (Danio rerio)
Triglyceride metabolism (Danio rerio)
Triglyceride biosynthesis (Danio rerio)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Danio rerio)
q-BH2 [cytosol]
Metabolism of nitric oxide: NOS3 activation and regulation (Danio rerio)
eNOS activation (Danio rerio)
Salvage - Sepiapterin is reduced to q-BH2 (Danio rerio)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Danio rerio)
Metabolism of cofactors (Danio rerio)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Danio rerio)
Salvage - Sepiapterin is reduced to q-BH2 (Danio rerio)
q-BH2 [cytosol]
Metabolism (Dictyostelium discoideum)
Metabolism of lipids (Dictyostelium discoideum)
Triglyceride metabolism (Dictyostelium discoideum)
Triglyceride biosynthesis (Dictyostelium discoideum)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Dictyostelium discoideum)
q-BH2 [cytosol]
Metabolism of nitric oxide: NOS3 activation and regulation (Dictyostelium discoideum)
eNOS activation (Dictyostelium discoideum)
BH2 binding can lead to eNOS uncoupling (Dictyostelium discoideum)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Dictyostelium discoideum)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Dictyostelium discoideum)
Metabolism of cofactors (Dictyostelium discoideum)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Dictyostelium discoideum)
BH2 binding can lead to eNOS uncoupling (Dictyostelium discoideum)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Dictyostelium discoideum)
q-BH2 [cytosol]
Metabolism (Drosophila melanogaster)
Metabolism of nitric oxide: NOS3 activation and regulation (Drosophila melanogaster)
eNOS activation (Drosophila melanogaster)
BH2 binding can lead to eNOS uncoupling (Drosophila melanogaster)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Drosophila melanogaster)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Drosophila melanogaster)
Metabolism of cofactors (Drosophila melanogaster)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Drosophila melanogaster)
BH2 binding can lead to eNOS uncoupling (Drosophila melanogaster)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Drosophila melanogaster)
q-BH2 [cytosol]
Metabolism (Gallus gallus)
Metabolism of lipids (Gallus gallus)
Triglyceride metabolism (Gallus gallus)
Triglyceride biosynthesis (Gallus gallus)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Gallus gallus)
q-BH2 [cytosol]
Metabolism of nitric oxide: NOS3 activation and regulation (Gallus gallus)
eNOS activation (Gallus gallus)
BH2 binding can lead to eNOS uncoupling (Gallus gallus)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Gallus gallus)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Gallus gallus)
Metabolism of cofactors (Gallus gallus)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Gallus gallus)
BH2 binding can lead to eNOS uncoupling (Gallus gallus)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Gallus gallus)
q-BH2 [cytosol]
Metabolism (Homo sapiens)
Metabolism of lipids (Homo sapiens)
Triglyceride metabolism (Homo sapiens)
Triglyceride biosynthesis (Homo sapiens)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Homo sapiens)
q-BH2 [cytosol]
Metabolism of nitric oxide: NOS3 activation and regulation (Homo sapiens)
eNOS activation (Homo sapiens)
BH2 binding can lead to eNOS uncoupling (Homo sapiens)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Homo sapiens)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of cofactors (Homo sapiens)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Homo sapiens)
BH2 binding can lead to eNOS uncoupling (Homo sapiens)
q-BH2 [cytosol]
Salvage - BH2 is reduced to BH4 by DHFR (Homo sapiens)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Homo sapiens)
q-BH2 [cytosol]
The BH3 radical can decay to dihydrobiopterin (BH2) (Homo sapiens)
q-BH2 [cytosol]
Metabolism (Mus musculus)
Metabolism of lipids (Mus musculus)
Triglyceride metabolism (Mus musculus)
Triglyceride biosynthesis (Mus musculus)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Mus musculus)
q-BH2 [cytosol]
Metabolism of nitric oxide: NOS3 activation and regulation (Mus musculus)
eNOS activation (Mus musculus)
BH2 binding can lead to eNOS uncoupling (Mus musculus)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Mus musculus)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Mus musculus)
Metabolism of cofactors (Mus musculus)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Mus musculus)
BH2 binding can lead to eNOS uncoupling (Mus musculus)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Mus musculus)
q-BH2 [cytosol]
Metabolism (Plasmodium falciparum)
Metabolism of nitric oxide: NOS3 activation and regulation (Plasmodium falciparum)
eNOS activation (Plasmodium falciparum)
BH2 binding can lead to eNOS uncoupling (Plasmodium falciparum)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Plasmodium falciparum)
Metabolism of cofactors (Plasmodium falciparum)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Plasmodium falciparum)
BH2 binding can lead to eNOS uncoupling (Plasmodium falciparum)
q-BH2 [cytosol]
Metabolism (Rattus norvegicus)
Metabolism of lipids (Rattus norvegicus)
Triglyceride metabolism (Rattus norvegicus)
Triglyceride biosynthesis (Rattus norvegicus)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Rattus norvegicus)
q-BH2 [cytosol]
Metabolism of nitric oxide: NOS3 activation and regulation (Rattus norvegicus)
eNOS activation (Rattus norvegicus)
BH2 binding can lead to eNOS uncoupling (Rattus norvegicus)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Rattus norvegicus)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Rattus norvegicus)
Metabolism of cofactors (Rattus norvegicus)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Rattus norvegicus)
BH2 binding can lead to eNOS uncoupling (Rattus norvegicus)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Rattus norvegicus)
q-BH2 [cytosol]
Metabolism (Saccharomyces cerevisiae)
Metabolism of nitric oxide: NOS3 activation and regulation (Saccharomyces cerevisiae)
eNOS activation (Saccharomyces cerevisiae)
BH2 binding can lead to eNOS uncoupling (Saccharomyces cerevisiae)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Saccharomyces cerevisiae)
Metabolism of cofactors (Saccharomyces cerevisiae)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Saccharomyces cerevisiae)
BH2 binding can lead to eNOS uncoupling (Saccharomyces cerevisiae)
q-BH2 [cytosol]
Metabolism (Schizosaccharomyces pombe)
Metabolism of nitric oxide: NOS3 activation and regulation (Schizosaccharomyces pombe)
eNOS activation (Schizosaccharomyces pombe)
BH2 binding can lead to eNOS uncoupling (Schizosaccharomyces pombe)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Schizosaccharomyces pombe)
Metabolism of cofactors (Schizosaccharomyces pombe)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Schizosaccharomyces pombe)
BH2 binding can lead to eNOS uncoupling (Schizosaccharomyces pombe)
q-BH2 [cytosol]
Metabolism (Sus scrofa)
Metabolism of lipids (Sus scrofa)
Triglyceride metabolism (Sus scrofa)
Triglyceride biosynthesis (Sus scrofa)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Sus scrofa)
q-BH2 [cytosol]
Metabolism of nitric oxide: NOS3 activation and regulation (Sus scrofa)
eNOS activation (Sus scrofa)
BH2 binding can lead to eNOS uncoupling (Sus scrofa)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Sus scrofa)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Sus scrofa)
Metabolism of cofactors (Sus scrofa)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Sus scrofa)
BH2 binding can lead to eNOS uncoupling (Sus scrofa)
q-BH2 [cytosol]
Salvage - Sepiapterin is reduced to q-BH2 (Sus scrofa)
q-BH2 [cytosol]
Metabolism (Xenopus tropicalis)
Metabolism of lipids (Xenopus tropicalis)
Triglyceride metabolism (Xenopus tropicalis)
Triglyceride biosynthesis (Xenopus tropicalis)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Xenopus tropicalis)
q-BH2 [cytosol]
Metabolism of nitric oxide: NOS3 activation and regulation (Xenopus tropicalis)
eNOS activation (Xenopus tropicalis)
Salvage - Sepiapterin is reduced to q-BH2 (Xenopus tropicalis)
q-BH2 [cytosol]
Metabolism of vitamins and cofactors (Xenopus tropicalis)
Metabolism of cofactors (Xenopus tropicalis)
Tetrahydrobiopterin (BH4) synthesis, recycling, salvage and regulation (Xenopus tropicalis)
Salvage - Sepiapterin is reduced to q-BH2 (Xenopus tropicalis)
q-BH2 [cytosol]
External Reference Information
External Reference
L-erythro-7,8-dihydrobiopterin [ChEBI:43029]
Participates
as an output of
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Dictyostelium discoideum)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Caenorhabditis elegans)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Gallus gallus)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Xenopus tropicalis)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Danio rerio)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Sus scrofa)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Bos taurus)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Canis familiaris)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Rattus norvegicus)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Mus musculus)
AGMO cleaves alkylglycerol into fatty aldehyde and glycerol (Homo sapiens)
The BH3 radical can decay to dihydrobiopterin (BH2) (Homo sapiens)
Salvage - Sepiapterin is reduced to q-BH2 (Dictyostelium discoideum)
Salvage - Sepiapterin is reduced to q-BH2 (Drosophila melanogaster)
Salvage - Sepiapterin is reduced to q-BH2 (Gallus gallus)
Salvage - Sepiapterin is reduced to q-BH2 (Xenopus tropicalis)
Salvage - Sepiapterin is reduced to q-BH2 (Sus scrofa)
Salvage - Sepiapterin is reduced to q-BH2 (Bos taurus)
Salvage - Sepiapterin is reduced to q-BH2 (Canis familiaris)
Salvage - Sepiapterin is reduced to q-BH2 (Rattus norvegicus)
Salvage - Sepiapterin is reduced to q-BH2 (Mus musculus)
Salvage - Sepiapterin is reduced to q-BH2 (Homo sapiens)
Salvage - Sepiapterin is reduced to q-BH2 (Danio rerio)
as an input of
Salvage - BH2 is reduced to BH4 by Dhfr (Mus musculus)
Salvage - BH2 is reduced to BH4 by DHFR (Homo sapiens)
BH2 binding can lead to eNOS uncoupling (Plasmodium falciparum)
BH2 binding can lead to eNOS uncoupling (Saccharomyces cerevisiae)
BH2 binding can lead to eNOS uncoupling (Schizosaccharomyces pombe)
BH2 binding can lead to eNOS uncoupling (Dictyostelium discoideum)
BH2 binding can lead to eNOS uncoupling (Caenorhabditis elegans)
BH2 binding can lead to eNOS uncoupling (Drosophila melanogaster)
BH2 binding can lead to eNOS uncoupling (Gallus gallus)
BH2 binding can lead to eNOS uncoupling (Sus scrofa)
BH2 binding can lead to eNOS uncoupling (Bos taurus)
BH2 binding can lead to eNOS uncoupling (Rattus norvegicus)
BH2 binding can lead to eNOS uncoupling (Mus musculus)
BH2 binding can lead to eNOS uncoupling (Homo sapiens)
Other forms of this molecule
q-BH2 [plasma membrane]
sepiapterin [cytosol]
Cross References
HMDB Metabolite
HMDB0000038
ZINC
ZINC000018181336
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text