Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
1PYR-3OH-5COOH [mitochondrial matrix]
Stable Identifier
R-ALL-9929425
Type
Chemical Compound [SimpleEntity]
Compartment
mitochondrial matrix
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Saccharomyces cerevisiae
Schizosaccharomyces pombe
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of amino acids and derivatives (Bos taurus)
Glyoxylate metabolism and glycine degradation (Bos taurus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Bos taurus)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Bos taurus)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Bos taurus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Bos taurus)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Bos taurus)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Caenorhabditis elegans)
Metabolism of amino acids and derivatives (Caenorhabditis elegans)
Glyoxylate metabolism and glycine degradation (Caenorhabditis elegans)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Caenorhabditis elegans)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Caenorhabditis elegans)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Caenorhabditis elegans)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Canis familiaris)
Metabolism of amino acids and derivatives (Canis familiaris)
Glyoxylate metabolism and glycine degradation (Canis familiaris)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Canis familiaris)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Canis familiaris)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Canis familiaris)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Canis familiaris)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Canis familiaris)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Danio rerio)
Metabolism of amino acids and derivatives (Danio rerio)
Glyoxylate metabolism and glycine degradation (Danio rerio)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Danio rerio)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Danio rerio)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Danio rerio)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Dictyostelium discoideum)
Metabolism of amino acids and derivatives (Dictyostelium discoideum)
Glyoxylate metabolism and glycine degradation (Dictyostelium discoideum)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Dictyostelium discoideum)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Dictyostelium discoideum)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Dictyostelium discoideum)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Drosophila melanogaster)
Metabolism of amino acids and derivatives (Drosophila melanogaster)
Glyoxylate metabolism and glycine degradation (Drosophila melanogaster)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Drosophila melanogaster)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Drosophila melanogaster)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Drosophila melanogaster)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Gallus gallus)
Metabolism of amino acids and derivatives (Gallus gallus)
Glyoxylate metabolism and glycine degradation (Gallus gallus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Gallus gallus)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Gallus gallus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Gallus gallus)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Glyoxylate metabolism and glycine degradation (Homo sapiens)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Homo sapiens)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Homo sapiens)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Homo sapiens)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Homo sapiens)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Homo sapiens)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Mus musculus)
Metabolism of amino acids and derivatives (Mus musculus)
Glyoxylate metabolism and glycine degradation (Mus musculus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Mus musculus)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Mus musculus)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Mus musculus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Mus musculus)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Mus musculus)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Rattus norvegicus)
Metabolism of amino acids and derivatives (Rattus norvegicus)
Glyoxylate metabolism and glycine degradation (Rattus norvegicus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Rattus norvegicus)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Rattus norvegicus)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Rattus norvegicus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Rattus norvegicus)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Rattus norvegicus)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Saccharomyces cerevisiae)
Metabolism of amino acids and derivatives (Saccharomyces cerevisiae)
Glyoxylate metabolism and glycine degradation (Saccharomyces cerevisiae)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Saccharomyces cerevisiae)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Saccharomyces cerevisiae)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Saccharomyces cerevisiae)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Schizosaccharomyces pombe)
Metabolism of amino acids and derivatives (Schizosaccharomyces pombe)
Glyoxylate metabolism and glycine degradation (Schizosaccharomyces pombe)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Schizosaccharomyces pombe)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Schizosaccharomyces pombe)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Schizosaccharomyces pombe)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Sus scrofa)
Metabolism of amino acids and derivatives (Sus scrofa)
Glyoxylate metabolism and glycine degradation (Sus scrofa)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Sus scrofa)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Sus scrofa)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Sus scrofa)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Sus scrofa)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Sus scrofa)
1PYR-3OH-5COOH [mitochondrial matrix]
Metabolism (Xenopus tropicalis)
Metabolism of amino acids and derivatives (Xenopus tropicalis)
Glyoxylate metabolism and glycine degradation (Xenopus tropicalis)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Xenopus tropicalis)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Xenopus tropicalis)
1PYR-3OH-5COOH [mitochondrial matrix]
Proline catabolism (Xenopus tropicalis)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Xenopus tropicalis)
1PYR-3OH-5COOH [mitochondrial matrix]
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Xenopus tropicalis)
1PYR-3OH-5COOH [mitochondrial matrix]
External Reference Information
External Reference
(3R,5S)-1-pyrroline-3-hydroxy-5-carboxylate [ChEBI:62612]
Participates
as an input of
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Gallus gallus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Xenopus tropicalis)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Danio rerio)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Sus scrofa)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Bos taurus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Canis familiaris)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Rattus norvegicus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Mus musculus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Homo sapiens)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Gallus gallus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Xenopus tropicalis)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Danio rerio)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Sus scrofa)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Bos taurus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Canis familiaris)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Rattus norvegicus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Mus musculus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Homo sapiens)
as an output of
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Saccharomyces cerevisiae)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Schizosaccharomyces pombe)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Dictyostelium discoideum)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Caenorhabditis elegans)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Drosophila melanogaster)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Xenopus tropicalis)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Sus scrofa)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Bos taurus)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Canis familiaris)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Rattus norvegicus)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Mus musculus)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Homo sapiens)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Saccharomyces cerevisiae)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Schizosaccharomyces pombe)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Dictyostelium discoideum)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Caenorhabditis elegans)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Drosophila melanogaster)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Xenopus tropicalis)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Sus scrofa)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Bos taurus)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Canis familiaris)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Rattus norvegicus)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Mus musculus)
PRODH2 oxidises HPRO to 1PYR-3OH-5COOH (Homo sapiens)
Cross References
AraCyc
PYRROLINE-HYDROXY-CARBOXYLATE
PubChem Compound
46926300
ZINC
ZINC000003870184
KEGG Gene
C04281
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text