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PXLP-K391-ALAS2 [mitochondrial matrix]
Stable Identifier
R-BTA-1022083
Type
Protein [EntityWithAccessionedSequence]
Species
Bos taurus
Compartment
mitochondrial matrix
Synonyms
Q3ZC31
Locations in the PathwayBrowser
Expand all
Metabolism (Bos taurus)
Metabolism of porphyrins (Bos taurus)
Heme biosynthesis (Bos taurus)
ALAS condenses SUCC-CoA and Gly to form dALA (Bos taurus)
ALAS1,2 [mitochondrial matrix] (Bos taurus)
ALAS2 homodimer (pyridoxal phosphate cofactor) [mitochondrial matrix] (Bos taurus)
PXLP-K391-ALAS2 [mitochondrial matrix] (Bos taurus)
External Reference Information
External Reference
UniProt:Q3ZC31
Reference Genes
BioGPS Gene:511791
ENSEMBL:ENSBTAG00000013178
ENSEMBL:ENSBTAG00000013178.4
KEGG Gene (Bos taurus):511791
Monarch:511791
NCBI Gene:511791
Reference Transcript
RefSeq:NM_001035103.2
Other Identifiers
511791
GO:0003824
GO:0003870
GO:0005739
GO:0005759
GO:0006778
GO:0009058
GO:0016740
GO:0030170
GO:0033014
GO:0043226
Participates
as a component of
ALAS2 homodimer (pyridoxal phosphate cofactor) [mitochondrial matrix] (Bos taurus)
Inferred From
PXLP-K391-ALAS2 [mitochondrial matrix]
(Homo sapiens)
Modified Residues
Name
N6-pyridoxal phosphate-L-lysine at 391 (in Homo sapiens)
Coordinate
391
PsiMod Name
N6-pyridoxal phosphate-L-lysine [MOD:00128]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-pyridoxal phosphate-L-lysine.
Cross References
RefSeq
NP_001030275.1
IntEnz
2.3.1.37
Ensembl
ENSBTAP00000017538
,
ENSBTAG00000013178
,
ENSBTAT00000017538
VGNC
25804
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