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HEXB [lysosomal lumen]
Stable Identifier
R-BTA-1605777
Type
Protein [EntityWithAccessionedSequence]
Species
Bos taurus
Compartment
lysosomal lumen
Synonyms
HEXB(122-311), H7BWW2
Locations in the PathwayBrowser
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Chondroitin sulfate/dermatan sulfate metabolism (Bos taurus)
CS/DS degradation (Bos taurus)
HEXA cleaves the terminal GalNAc from DS (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
HEXB cleaves the terminal GalNAc from DS (Bos taurus)
bHEXB [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
Hyaluronan metabolism (Bos taurus)
Hyaluronan uptake and degradation (Bos taurus)
HEXA cleaves the terminal GalNAc from small HA fragments (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
HEXB cleaves the terminal GalNAc from small HA fragments (Bos taurus)
bHEXB [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
Keratan sulfate/keratin metabolism (Bos taurus)
Keratan sulfate degradation (Bos taurus)
HEXA cleaves the terminal GalNAc from keratan sulfate (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
HEXB cleaves the terminal GalNAc from keratan sulfate (Bos taurus)
bHEXB [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
Metabolism of lipids (Bos taurus)
Sphingolipid metabolism (Bos taurus)
Glycosphingolipid metabolism (Bos taurus)
Glycosphingolipid catabolism (Bos taurus)
bHEXA hydrolyzes GM2A:GM2 to GM2A:GM3 (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
bHEXA,bHEXB hydrolyze GM2A:GA2 to GM2A:LacCer (Bos taurus)
bHEXA,bHEXB [lysosomal lumen] (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
bHEXB [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
bHEXA,bHEXB hydrolyze PSAP(195-273):Gb4Cer:PE (Bos taurus)
bHEXA,bHEXB [lysosomal lumen] (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
bHEXB [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
bHEXA,bHEXS hydrolyze GM2A:SM2 (Bos taurus)
bHEXA,bHEXS [lysosomal lumen] (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXB dimer [lysosomal lumen] (Bos taurus)
Mature HEXB [lysosomal lumen] (Bos taurus)
HEXB [lysosomal lumen] (Bos taurus)
External Reference Information
External Reference
UniProt:H7BWW2
Gene Names
HEXB
Reference Genes
BioGPS Gene:618571 HEXB
ENSEMBL:ENSBTAG00000015512.6
KEGG Gene (Bos taurus):618571 HEXB
Monarch:618571 HEXB
NCBI Gene:618571 HEXB
Reference Transcript
RefSeq:NM_001076510.2 HEXB
Other Identifiers
618571
GO:0003824
GO:0004553
GO:0004563
GO:0005764
GO:0005773
GO:0005975
GO:0006629
GO:0006689
GO:0008152
GO:0016020
GO:0016787
GO:0016798
GO:0030203
GO:0043226
GO:0102148
GO:1901135
Participates
as a component of
Mature HEXB [lysosomal lumen] (Bos taurus)
Other forms of this molecule
HEXB [extracellular region]
HEXB [extracellular region]
HEXB [azurophil granule lumen]
HEXB [azurophil granule lumen]
HEXB [lysosomal lumen]
HEXB [lysosomal lumen]
Inferred From
HEXB(122-311) [lysosomal lumen]
(Homo sapiens)
Modified Residues
Name
Inter-chain Crosslink via L-cystine (cross-link) at 137 and 93 (in Homo sapiens)
Coordinate
137
PsiMod Name
L-cystine (cross-link)
PsiMod Definition
A protein modification that effectively cross-links two L-cysteine residues to form L-cystine.
Name
Inter-chain Crosslink via L-cystine (cross-link) at 309 and 360 (in Homo sapiens)
Coordinate
309
PsiMod Name
L-cystine (cross-link)
PsiMod Definition
A protein modification that effectively cross-links two L-cysteine residues to form L-cystine.
Cross References
RefSeq
NP_001069978.2
OpenTargets
ENSG00000049860
Ensembl
ENSBTAP00000045456
,
ENSBTAG00000015512
,
ENSBTAT00000048411
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