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ACO2 [mitochondrial matrix]
Stable Identifier
R-BTA-70968
Type
Protein [EntityWithAccessionedSequence]
Species
Bos taurus
Compartment
mitochondrial matrix
Synonyms
P20004
Locations in the PathwayBrowser
Expand all
Metabolism (Bos taurus)
Aerobic respiration and respiratory electron transport (Bos taurus)
Citric acid cycle (TCA cycle) (Bos taurus)
ACO2 isomerizes citrate (Bos taurus)
ACO2:3Fe-4S [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
ACO2:4Fe-4S [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
Maturation of TCA enzymes and regulation of TCA cycle (Bos taurus)
Frataxin transfers Fe2+ to ACO2 (Bos taurus)
ACO2:3Fe-4S [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
ACO2:4Fe-4S [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
ROS,RNS oxidize ACO2:4Fe-4S (Bos taurus)
ACO2:3Fe-4S [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
ACO2:4Fe-4S [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
Metabolism of proteins (Bos taurus)
Mitochondrial protein degradation (Bos taurus)
CLPXP binds mitochondrial matrix proteins (Bos taurus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
CLPXP degrades mitochondrial matrix proteins (Bos taurus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
LONP1 binds mitochondrial matrix proteins (Bos taurus)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
LONP1 degrades mitochondrial matrix proteins (Bos taurus)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
ACO2 [mitochondrial matrix] (Bos taurus)
External Reference Information
External Reference
UniProt:P20004
Reference Genes
BioGPS Gene:280976
ENSEMBL:ENSBTAG00000006429
ENSEMBL:ENSBTAG00000006429.5
KEGG Gene (Bos taurus):280976
Monarch:280976
NCBI Gene:280976
Reference Transcript
RefSeq:NM_173977.3
Other Identifiers
280976
GO:0003824
GO:0003994
GO:0005506
GO:0005739
GO:0005829
GO:0006091
GO:0006099
GO:0006101
GO:0008198
GO:0016829
GO:0043226
GO:0046872
GO:0047780
GO:0051536
GO:0051538
GO:0051539
Participates
as a member of
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Bos taurus)
as a component of
ACO2:3Fe-4S [mitochondrial matrix] (Bos taurus)
ACO2:4Fe-4S [mitochondrial matrix] (Bos taurus)
Inferred From
ACO2 [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_776402.1
IntEnz
4.2.1.3
Ensembl
ENSBTAP00000008431
,
ENSBTAT00000008431
,
ENSBTAG00000006429
VGNC
25546
PDB
1NIS
,
1AMI
,
1C96
,
1AMJ
,
1ACO
,
1C97
,
1FGH
,
8ACN
,
1NIT
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