Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Overlays
DisGeNET
Web
API
Advanced Data Search
Site Search
Community
Icon Library
Outreach
Events
Training
Publications
Partners
Contributors
Papers Citing Us
Resources Guide
Collaboration
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Overlays
DisGeNET
Web
API
Advanced Data Search
Site Search
Community
Icon Library
Outreach
Events
Training
Publications
Partners
Contributors
Papers Citing Us
Resources Guide
Collaboration
Download
Search ...
Go!
FH [mitochondrial matrix]
Stable Identifier
R-BTA-70980
Type
Protein [EntityWithAccessionedSequence]
Species
Bos taurus
Compartment
mitochondrial matrix
Synonyms
FH, Q148D3
Locations in the PathwayBrowser
Expand all
Metabolism (Bos taurus)
Aerobic respiration and respiratory electron transport (Bos taurus)
Citric acid cycle (TCA cycle) (Bos taurus)
FH tetramer hydrates fumarate to L-malate (Bos taurus)
FH tetramer [mitochondrial matrix] (Bos taurus)
FH [mitochondrial matrix] (Bos taurus)
Metabolism of proteins (Bos taurus)
Mitochondrial protein degradation (Bos taurus)
CLPXP binds mitochondrial matrix proteins (Bos taurus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Bos taurus)
FH [mitochondrial matrix] (Bos taurus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Bos taurus)
FH [mitochondrial matrix] (Bos taurus)
CLPXP degrades mitochondrial matrix proteins (Bos taurus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Bos taurus)
FH [mitochondrial matrix] (Bos taurus)
LONP1 binds mitochondrial matrix proteins (Bos taurus)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
FH [mitochondrial matrix] (Bos taurus)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
FH [mitochondrial matrix] (Bos taurus)
LONP1 degrades mitochondrial matrix proteins (Bos taurus)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
FH [mitochondrial matrix] (Bos taurus)
External Reference Information
External Reference
UniProt:Q148D3
Gene Names
FH
Reference Genes
BioGPS Gene:520260 FH
ENSEMBL:ENSBTAG00000021688.5
KEGG Gene (Bos taurus):520260 FH
Monarch:520260 FH
NCBI Gene:520260 FH
Reference Transcript
RefSeq:NM_001075803.2 FH
Other Identifiers
520260
GO:0003824
GO:0004333
GO:0005739
GO:0005759
GO:0006091
GO:0006099
GO:0006106
GO:0006108
GO:0016829
GO:0043226
GO:0045239
GO:0048873
GO:0120162
Participates
as a member of
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Bos taurus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Bos taurus)
as a component of
FH tetramer [mitochondrial matrix] (Bos taurus)
Inferred From
FH [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_001069271.1
OpenTargets
ENSG00000091483
Ensembl
ENSBTAG00000021688
,
ENSBTAP00000028902
,
ENSBTAT00000028902
VGNC
28995
© 2024
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text