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hex-1 [lysosomal lumen]
Stable Identifier
R-CEL-1605605
Type
Protein [EntityWithAccessionedSequence]
Species
Caenorhabditis elegans
Compartment
lysosomal lumen
Synonyms
HEXB(316-556), Q22492
Locations in the PathwayBrowser
Expand all
Metabolism (Caenorhabditis elegans)
Metabolism of carbohydrates (Caenorhabditis elegans)
Glycosaminoglycan metabolism (Caenorhabditis elegans)
Chondroitin sulfate/dermatan sulfate metabolism (Caenorhabditis elegans)
CS/DS degradation (Caenorhabditis elegans)
HEXA cleaves the terminal GalNAc from DS (Caenorhabditis elegans)
bHEXA [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
HEXB cleaves the terminal GalNAc from DS (Caenorhabditis elegans)
bHEXB [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
Hyaluronan metabolism (Caenorhabditis elegans)
Hyaluronan uptake and degradation (Caenorhabditis elegans)
HEXA cleaves the terminal GalNAc from small HA fragments (Caenorhabditis elegans)
bHEXA [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
HEXB cleaves the terminal GalNAc from small HA fragments (Caenorhabditis elegans)
bHEXB [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
Keratan sulfate/keratin metabolism (Caenorhabditis elegans)
Keratan sulfate degradation (Caenorhabditis elegans)
HEXA cleaves the terminal GalNAc from keratan sulfate (Caenorhabditis elegans)
bHEXA [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
HEXB cleaves the terminal GalNAc from keratan sulfate (Caenorhabditis elegans)
bHEXB [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
Metabolism of lipids (Caenorhabditis elegans)
Sphingolipid metabolism (Caenorhabditis elegans)
Glycosphingolipid metabolism (Caenorhabditis elegans)
Glycosphingolipid catabolism (Caenorhabditis elegans)
bHEXA hydrolyzes GM2A:GM2 to GM2A:GM3 (Caenorhabditis elegans)
bHEXA [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
bHEXA,bHEXB hydrolyze GM2A:GA2 to GM2A:LacCer (Caenorhabditis elegans)
bHEXA,bHEXB [lysosomal lumen] (Caenorhabditis elegans)
bHEXA [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
bHEXB [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
bHEXA,bHEXB hydrolyze PSAP(195-273):Gb4Cer:PE (Caenorhabditis elegans)
bHEXA,bHEXB [lysosomal lumen] (Caenorhabditis elegans)
bHEXA [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
bHEXB [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
bHEXA,bHEXS hydrolyze GM2A:SM2 (Caenorhabditis elegans)
bHEXA,bHEXS [lysosomal lumen] (Caenorhabditis elegans)
bHEXA [lysosomal lumen] (Caenorhabditis elegans)
HEXB dimer [lysosomal lumen] (Caenorhabditis elegans)
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
hex-1 [lysosomal lumen] (Caenorhabditis elegans)
External Reference Information
External Reference
UniProt:Q22492
Gene Names
hex-1
Reference Genes
BioGPS Gene:180533 hex-1
CTD Gene:180533 hex-1
ENSEMBL:WBGene00020509
Monarch:180533 hex-1
NCBI Gene:180533 hex-1
UCSC:Q22492 hex-1
Wormbase:WBGene00020509
Reference Transcript
RefSeq:NM_076008.6 hex-1
Other Identifiers
173287_s_at
180533
18615777
192747_at
A_12_P106940
A_12_P157825
CE07499
CE_WBGene00020509_A
CE_WBGene00020509_B
CE_WBGene00020509_C
CGZ0035178
GO:0003824
GO:0004553
GO:0004563
GO:0005975
GO:0016787
T14F9.3
T14F9.3_1157-1216_0.921_8_B
T14F9.3_1305-1364_0.921_7_A
T14F9.3_818-877_0.898_17_C
T14F9_3P00339
T14F9_3P00946
T14F9_3P01415
WBGene00020509
cea2.c.47924
Participates
as a component of
Mature HEXB [lysosomal lumen] (Caenorhabditis elegans)
Other forms of this molecule
hex-1 [extracellular region]
hex-1 [extracellular region]
hex-1 [azurophil granule lumen]
hex-1 [azurophil granule lumen]
hex-1 [lysosomal lumen]
hex-1 [lysosomal lumen]
hex-1 [lysosomal lumen]
hex-1 [lysosomal lumen]
Inferred From
HEXB(316-556) [lysosomal lumen]
(Homo sapiens)
Modified Residues
Name
Inter-chain Crosslink via L-cystine (cross-link) at 360 and 309 (in Homo sapiens)
Coordinate
360
PsiMod Name
L-cystine (cross-link)
PsiMod Definition
A protein modification that effectively cross-links two L-cysteine residues to form L-cystine.
Cross References
RefSeq
NP_508409.1
IntEnz
3.2.1.52
PRO
Q22492
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