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NDUFB11 [mitochondrial inner membrane]
Stable Identifier
R-HSA-163933
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase ESSS subunit
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB11 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9NX14 NDUFB11
Gene Names
NDUFB11, UNQ111/PRO1064
Chain
transit peptide:1-29, chain:30-153
Reference Genes
BioGPS Gene:54539 NDUFB11
COSMIC (genes):NDUFB11 NDUFB11
CTD Gene:54539 NDUFB11
dbSNP Gene:54539 NDUFB11
ENSEMBL:ENSG00000147123 NDUFB11
HGNC:20372 NDUFB11
KEGG Gene (Homo sapiens):54539 NDUFB11
Monarch:54539 NDUFB11
NCBI Gene:54539 NDUFB11
OMIM:300403 NDUFB11
UCSC:Q9NX14 NDUFB11
Reference Transcript
RefSeq:NM_001135998.2 NDUFB11
RefSeq:NM_019056.6 NDUFB11
Other Identifiers
11717251_s_at
11717252_x_at
17110429
218320_s_at
3386460
4007010
4007011
4007013
4007014
4007017
4007018
4007019
54539
56467_s_at
8172296
A_23_P22765
GE55524
GO:0003674
GO:0005515
GO:0005575
GO:0005622
GO:0005737
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0007005
GO:0008150
GO:0016020
GO:0016021
GO:0022607
GO:0032981
GO:0032991
GO:0043226
GO:0055114
GO:0065003
GO:0070469
ILMN_1749709
PH_hs_0020112
TC0X000994.hg
TC0X002052.hg
g9506682_3p_s_at
Participant Of
hasComponent
HP subcomplex [mitochondrial inner membrane]
Inferred To
NDUFB11 [mitochondrial inner membrane] (Bos taurus)
NDUFB11 [mitochondrial inner membrane] (Caenorhabditis elegans)
NDUFB11 [mitochondrial inner membrane] (Canis familiaris)
NDUFB11 [mitochondrial inner membrane] (Sus scrofa)
NP15.6 [mitochondrial inner membrane] (Drosophila melanogaster)
Ghost homologue of NDUFB11 [mitochondrial inner membrane] (Gallus gallus)
Ghost homologue of NDUFB11 [mitochondrial inner membrane] (Xenopus tropicalis)
Ndufb11 [mitochondrial inner membrane] (Mus musculus)
Ndufb11 [mitochondrial inner membrane] (Rattus norvegicus)
ndufb11 [mitochondrial inner membrane] (Danio rerio)
Cross References
RefSeq
NP_001129470.1
,
NP_061929.2
Target Pathogen
5b354852be737e166372eadd
OpenTargets
ENSG00000147123
HPA
ENSG00000147123-NDUFB11
GeneCards
Q9NX14
Ensembl
ENST00000276062
,
ENSP00000367042
,
ENST00000377811
,
ENSG00000147123
,
ENSP00000276062
PRO
Q9NX14
Orphanet
23222
HMDB Protein
HMDBP01106
PDB
5XTC
,
5XTI
,
5XTD
,
5XTH
Interactors (4)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q15125 EBP
1
EBP [endoplasmic reticulum membrane]
(R-HSA-195697)
0.556
3
UniProt:Q9NPL8 TIMMDC1
1
TIMMDC1 [mitochondrial inner membrane]
(R-HSA-5689720)
0.556
3
UniProt:P08034 GJB1
2
GJB1 [endoplasmic reticulum-Golgi intermediate compartment]
(R-HSA-190636)
GJB1 [endoplasmic reticulum membrane]
(R-HSA-190656)
0.556
3
UniProt:O75489 NDUFS3
1
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
0.527
4
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