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MT-CO2 [mitochondrial inner membrane]
Stable Identifier
R-HSA-164302
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
Cytochrome c oxidase subunit 2, Cytochrome c oxidase polypeptide II
Icon
Locations in the PathwayBrowser
Expand all
Cellular responses to stimuli (Homo sapiens)
Cellular responses to stress (Homo sapiens)
Cellular response to chemical stress (Homo sapiens)
Cytoprotection by HMOX1 (Homo sapiens)
CO binds to Cytochrome c oxidase (Homo sapiens)
Cytochrome c oxidase [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
MT-CO2:CuA [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
Cytochrome c oxidase:CO [mitochondrial inner membrane] (Homo sapiens)
Cytochrome c oxidase [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
MT-CO2:CuA [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
Cytochrome c oxidase [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
MT-CO2:CuA [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
Cytochrome c oxidase:CO [mitochondrial inner membrane] (Homo sapiens)
Cytochrome c oxidase [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
MT-CO2:CuA [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
Gene expression (Transcription) (Homo sapiens)
RNA Polymerase II Transcription (Homo sapiens)
Generic Transcription Pathway (Homo sapiens)
Transcriptional Regulation by TP53 (Homo sapiens)
TP53 Regulates Metabolic Genes (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
Cytochrome c oxidase [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
MT-CO2:CuA [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
Cytochrome c oxidase:CO [mitochondrial inner membrane] (Homo sapiens)
Cytochrome c oxidase [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
MT-CO2:CuA [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
Cytochrome c oxidase [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
MT-CO2:CuA [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
Cytochrome c oxidase:CO [mitochondrial inner membrane] (Homo sapiens)
Cytochrome c oxidase [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
MT-CO2:CuA [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Mitochondrial protein degradation (Homo sapiens)
YME1L1 binds mitochondrial inner membrane proteins (Homo sapiens)
Substrate of YME1L1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
YME1L1:substrate protein (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
Substrate of YME1L1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
YME1L1 degrades mitochondrial inner membrane proteins (Homo sapiens)
YME1L1:substrate protein (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
Substrate of YME1L1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
MT-CO2 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:P00403 MT-CO2
Gene Names
MT-CO2, COII, COX2, COXII, MTCO2
Chain
chain:1-227
Reference Genes
BioGPS Gene:4513 MT-CO2
COSMIC (genes):MT-CO2 MT-CO2
CTD Gene:4513 MT-CO2
dbSNP Gene:4513 MT-CO2
ENSEMBL:ENSG00000198712 MT-CO2
ENSEMBL_homo_sapiens_GENE:ENSG00000198712.1 MT-CO2
HGNC:7421 MT-CO2
KEGG Gene (Homo sapiens):4513 MT-CO2
Monarch:4513 MT-CO2
NCBI Gene:4513 MT-CO2
OMIM:516040 MT-CO2
Reference Transcript
RefSeq:NC_012920.1 MT-CO2
Other Identifiers
11758423_s_at
11762922_s_at
11762923_x_at
1553567_3p_s_at
1553567_PM_s_at
1553567_s_at
1553569_PM_at
1553569_at
1553570_PM_x_at
1553570_x_at
17100659
17100661
17100663
17100665
17100667
17126266
17126268
2315231
2315232
2315316
2315317
2315318
2315319
2492706
2492708
2868799
4037628
4037629
4037631
4037633
4037634
4037635
4037637
4037639
4037640
4037641
4037642
4037643
4037644
4037645
4037646
4037647
4037648
4037649
4037651
4513
7896750
7896752
8043375
8113356
8165663
8165665
8165667
8165669
8165672
A_23_P337726
A_23_P402751
A_33_P3410700
GO:0001666
GO:0003824
GO:0004129
GO:0005215
GO:0005507
GO:0005515
GO:0005739
GO:0005743
GO:0005751
GO:0006091
GO:0006123
GO:0007595
GO:0016020
GO:0016491
GO:0022900
GO:0031966
GO:0042773
GO:0043226
GO:0045277
GO:0045333
GO:0046872
GO:0048856
GO:0055085
GO:0070469
GO:1902600
HMNXSV003022003
HMNXSV003032141
HMNXSV003041642
Hs2Affx.1.41.S1_3p_s_at
Hs2Affx.1.43.S1_3p_x_at
PH_hs_0033947
PH_hs_0036541
RNA143496|tRNA_413_70
RNA143539|tRNA_456_68
TC01000013.hg
TC0M000005.hg
TC0M000006.hg
TC0M000021.hg
TC0M000022.hg
p26926
Participates
as a member of
Substrate of YME1L1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
as a component of
MT-CO2:CuA [mitochondrial inner membrane] (Homo sapiens)
Cytochrome c oxidase [mitochondrial inner membrane] (Homo sapiens)
Inferred To
mt-co2 [mitochondrial inner membrane]
(Xenopus tropicalis)
Ghost homologue of MT-CO2 [mitochondrial inner membrane]
(Canis familiaris)
MT-CO2 [mitochondrial inner membrane]
(Bos taurus)
MT-CO2 [mitochondrial inner membrane]
(Danio rerio)
MT-CO2 [mitochondrial inner membrane]
(Drosophila melanogaster)
MT-CO2 [mitochondrial inner membrane]
(Gallus gallus)
MT-CO2 [mitochondrial inner membrane]
(Mus musculus)
MT-CO2 [mitochondrial inner membrane]
(Rattus norvegicus)
MT-CO2 [mitochondrial inner membrane]
(Sus scrofa)
Cross References
RefSeq
YP_003024029.1
ZINC - World Drugs
COX2_HUMAN
OpenTargets
ENSG00000198712
ZINC - Substances
COX2_HUMAN
ZINC - Biogenic
COX2_HUMAN
ZINC target
P00403
PRO
P00403
PDB
3VRJ
,
5Z62
ZINC - Metabolites
COX2_HUMAN
GeneCards
P00403
HPA
ENSG00000198712-MT-CO2
Ensembl
ENSP00000354876
,
ENSG00000198712
,
ENST00000361739
Pharos - Targets
P00403
Orphanet
16472
ZINC - Predictions - Purchasable
COX2_HUMAN
HMDB Protein
HMDBP07035
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P13569 CFTR
17
PolyUb-CFTR [clathrin-coated endocytic vesicle membrane]
(R-HSA-8869104)
PolyUb-CFTR [plasma membrane]
(R-HSA-8867595)
CFTR [lysosomal membrane]
(R-HSA-5627279)
CFTR [Golgi-associated vesicle membrane]
(R-HSA-5627079)
CFTR [endosome membrane]
(R-HSA-6782965)
PolyUb-CFTR [endosome membrane]
(R-HSA-6782976)
CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866834)
ub-CFTR F508del [cytosol]
(R-HSA-8866838)
ub-CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866842)
CFTR G542* [plasma membrane]
(R-HSA-5678986)
CFTR G551D [plasma membrane]
(R-HSA-5678977)
CFTR W1282* [plasma membrane]
(R-HSA-5678976)
CFTR F508del [plasma membrane]
(R-HSA-5678978)
CFTR N1303K [plasma membrane]
(R-HSA-5678983)
CFTR [plasma membrane]
(R-HSA-383188)
CFTR [endoplasmic reticulum membrane]
(R-HSA-8866837)
misfolded CFTR [endoplasmic reticulum membrane]
(R-HSA-8868730)
0.483
7
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