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chondroitin(2)-DCN [Golgi lumen]
Stable Identifier
R-HSA-2063993
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
Golgi lumen
Synonyms
_DCN, Decorin, PGS2_HUMAN, DCN
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of glycosylation (Homo sapiens)
Diseases associated with glycosaminoglycan metabolism (Homo sapiens)
Defective CHSY1 causes TPBS (Homo sapiens)
Defective CHSY1 does not transfer GalNAc to chondroitin (Homo sapiens)
chondroitin(2)-core proteins [Golgi lumen] (Homo sapiens)
chondroitin(2)-DCN [Golgi lumen] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
Chondroitin sulfate biosynthesis (Homo sapiens)
CHPF,CHPF2,CHSY3 transfer GlcA to chondroitin (Homo sapiens)
chondroitin(2)-core proteins [Golgi lumen] (Homo sapiens)
chondroitin(2)-DCN [Golgi lumen] (Homo sapiens)
CHPF,CHSY3 transfer GalNAc to chondroitin (Homo sapiens)
chondroitin(2)-core proteins [Golgi lumen] (Homo sapiens)
chondroitin(2)-DCN [Golgi lumen] (Homo sapiens)
CHSY1 transfers GalNAc to chondroitin (Homo sapiens)
chondroitin(2)-core proteins [Golgi lumen] (Homo sapiens)
chondroitin(2)-DCN [Golgi lumen] (Homo sapiens)
CHSY1 transfers GlcA to chondroitin (Homo sapiens)
chondroitin(2)-core proteins [Golgi lumen] (Homo sapiens)
chondroitin(2)-DCN [Golgi lumen] (Homo sapiens)
External Reference Information
External Reference
UniProt:P07585 DCN
Gene Names
DCN, SLRR1B
Chain
signal peptide:1-16, propeptide:17-30, chain:31-359
Reference Genes
BioGPS Gene:1634 DCN
COSMIC (genes):DCN DCN
CTD Gene:1634 DCN
dbSNP Gene:1634 DCN
ENSEMBL:ENSG00000011465 DCN
HGNC:2705 DCN
KEGG Gene (Homo sapiens):1634 DCN
Monarch:1634 DCN
NCBI Gene:1634 DCN
OMIM:125255 DCN
UCSC:P07585 DCN
Reference Transcript
RefSeq:XM_006719270.1 DCN
RefSeq:NM_133506.3 DCN
RefSeq:XM_005268693.1 DCN
RefSeq:XM_017018917.1 DCN
RefSeq:NM_133507.3 DCN
RefSeq:NM_001920.4 DCN
RefSeq:NM_133504.3 DCN
RefSeq:NM_133505.3 DCN
RefSeq:NM_133503.3 DCN
Other Identifiers
0001410239
0006130131
11736001_s_at
11736002_s_at
11757283_s_at
1634
201893_x_at
209335_3p_at
209335_at
211813_3p_x_at
211813_x_at
211896_s_at
239786_at
3465263
3465265
3465267
3465269
3465271
3465273
3465275
3465276
3465277
3465278
3465279
3465280
3465281
3465282
3465283
3465284
3465288
3465290
3465292
3465293
3465295
3465307
3465308
3465309
3465310
3465314
49560_at
66521_at
7965410
A_23_P64873
A_33_P3382856
GE469763
GE502543
GE61148
GO:0000003
GO:0001822
GO:0001890
GO:0003674
GO:0003723
GO:0005198
GO:0005515
GO:0005518
GO:0005539
GO:0005575
GO:0005576
GO:0005589
GO:0005615
GO:0005622
GO:0005737
GO:0005764
GO:0005773
GO:0005794
GO:0005796
GO:0006464
GO:0006790
GO:0006914
GO:0006950
GO:0007005
GO:0007165
GO:0007519
GO:0007568
GO:0008150
GO:0009056
GO:0009058
GO:0009612
GO:0009887
GO:0010508
GO:0010596
GO:0014068
GO:0016239
GO:0016525
GO:0019800
GO:0030021
GO:0030198
GO:0030206
GO:0030207
GO:0030208
GO:0031012
GO:0032496
GO:0032991
GO:0034641
GO:0040011
GO:0042060
GO:0042592
GO:0043202
GO:0043226
GO:0044281
GO:0045944
GO:0047485
GO:0048646
GO:0048856
GO:0048870
GO:0050840
GO:0051901
GO:0062023
GO:0090141
GO:1900747
Hs.27864.0.A1_3p_at
Hs.76152.0.A2_3p_a_at
Hs.76152.1.A2_3p_at
Hs.76152.1.A2_3p_s_at
ILMN_1666672
ILMN_1683194
ILMN_1701748
ILMN_1768227
ILMN_1838575
ILMN_2347145
PH_hs_0022710
TC12001804.hg
g7381210_3p_s_at
g7381210_3p_x_at
Participant Of
hasMember
chondroitin(2)-core proteins [Golgi lumen]
Other forms of this molecule
DCN(31-?) [extracellular region]
DCN(?-359) [extracellular region]
DCN [extracellular region]
D2,4,4(S)3-DCN [lysosomal lumen]
D2,4(S)2-DCN [lysosomal lumen]
D4S-DCN [lysosomal lumen]
DCN [lysosomal lumen]
CSE-DCN [lysosomal lumen]
C6S-DCN [lysosomal lumen]
C4S-DCN [lysosomal lumen]
CSE-DCN [extracellular region]
C6S-DCN [extracellular region]
C4S-DCN [extracellular region]
CSE-DCN [Golgi lumen]
C6S-DCN [Golgi lumen]
D4S-DCN [extracellular region]
D2,4(S)2-DCN [extracellular region]
D2,4,4(S)3-DCN [extracellular region]
chondroitin(1)-DCN [Golgi lumen]
C4S-DCN [Golgi lumen]
chondroitin(3)-DCN [Golgi lumen]
D2,4,4(S)3-DCN [Golgi lumen]
D4S-DCN [Golgi lumen]
dermatan-DCN [Golgi lumen]
D2,4(S)2-DCN [Golgi lumen]
GlcA-Gal-Gal-Xyl-DCN [Golgi lumen]
Gal-Gal-Xyl-DCN [Golgi lumen]
DCN [Golgi lumen]
Gal-Xyl-DCN [Golgi lumen]
XylS-DCN [Golgi lumen]
Inferred To
DCN [Golgi lumen] (Bos taurus)
DCN [Golgi lumen] (Canis familiaris)
DCN [Golgi lumen] (Sus scrofa)
Dcn [Golgi lumen] (Mus musculus)
Dcn [Golgi lumen] (Rattus norvegicus)
DS05899.7 [Golgi lumen] (Drosophila melanogaster)
dcn [Golgi lumen] (Danio rerio)
chondroitin(2)-DCN [Golgi lumen] (Xenopus tropicalis)
Modified Residues
Name
O-xylosyl-L-serine (ChEBI:63509) at unknown position
Modification
beta-D-GlcA-(1->3)-beta-D-GalNAc-(1->4)-beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group
PsiMod Name
O-xylosyl-L-serine
PsiMod Definition
A protein modification that effectively converts an L-serine residue to O3-xylosylserine.
Cross References
RefSeq
NP_598010.1
,
XP_006719333.1
,
NP_598011.1
,
NP_598012.1
,
NP_598013.1
,
NP_598014.1
,
NP_001911.1
,
XP_005268750.1
,
XP_016874406.1
OpenTargets
ENSG00000011465
GeneCards
P07585
HPA
ENSG00000011465-DCN
Ensembl
ENSP00000447654
,
ENST00000425043
,
ENST00000552962
,
ENST00000420120
,
ENST00000052754
,
ENSP00000398514
,
ENSP00000401021
,
ENSP00000052754
,
ENSP00000376862
,
ENST00000393155
,
ENST00000456569
,
ENSG00000011465
,
ENST00000441303
,
ENSP00000413723
,
ENSP00000399815
,
ENST00000547568
,
ENSP00000447674
PRO
P07585
Orphanet
15853
Interactors (3)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:O75063 XYLK
0.623
4
UniProt:P02751 FN1
8
FN1(32-271) [extracellular region]
(R-HSA-3787935)
FN1(32-2386) [platelet alpha granule lumen]
(R-HSA-114620)
FN1(272-2386) [extracellular region]
(R-HSA-3788024)
FN1(32-?) [extracellular region]
(R-HSA-2533850)
FN1(?-2386) [extracellular region]
(R-HSA-2533841)
p-FN1 [endoplasmic reticulum lumen]
(R-HSA-8956937)
FN1 [endoplasmic reticulum lumen]
(R-HSA-8956708)
FN1(32-2386) [extracellular region]
(R-HSA-54851)
0.602
9
UniProt:P13497-2 BMP1
0.558
2
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