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COQ5 [mitochondrial matrix]
Stable Identifier
R-HSA-2162210
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
2-methoxy-6-polyprenyl-1,4-benzoquinol methylase, mitochondrial ecNumber2.1.1.201/ecNumber, COQ5_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of cofactors (Homo sapiens)
Ubiquinol biosynthesis (Homo sapiens)
COQ3 methylates DHDB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ5 [mitochondrial matrix] (Homo sapiens)
COQ3 methylates DeMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ5 [mitochondrial matrix] (Homo sapiens)
COQ5 methylates MDMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ5 [mitochondrial matrix] (Homo sapiens)
COQ5 [mitochondrial matrix] (Homo sapiens)
COQ6 hydroxylates DHB (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ5 [mitochondrial matrix] (Homo sapiens)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Homo sapiens)
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
COQ5 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q5HYK3 COQ5
Gene Names
COQ5
Chain
transit peptide:1-42, chain:43-327
Reference Genes
BioGPS Gene:84274 COQ5
COSMIC (genes):COQ5 COQ5
CTD Gene:84274 COQ5
dbSNP Gene:84274 COQ5
ENSEMBL:ENSG00000110871 COQ5
ENSEMBL_homo_sapiens_GENE:ENSG00000110871.15 COQ5
HGNC:28722 COQ5
KEGG Gene (Homo sapiens):84274 COQ5
Monarch:84274 COQ5
NCBI Gene:84274 COQ5
OMIM:616359 COQ5
UCSC:Q5HYK3 COQ5
Reference Transcript
RefSeq:NM_032314.3 COQ5
Other Identifiers
11744112_a_at
11744113_s_at
11751667_a_at
16771322
223114_PM_at
223114_at
3474580
3474581
3474582
3474584
3474586
3474587
3474588
3474589
3474590
3474598
44743_at
7967072
84274
A_23_P105625
A_33_P3243128
GE56974
GO:0003824
GO:0005515
GO:0005739
GO:0005743
GO:0005759
GO:0006744
GO:0008168
GO:0008757
GO:0016020
GO:0016740
GO:0031314
GO:0032259
GO:0032991
GO:0043226
GO:0043333
GO:0043430
GO:0110142
GO:1901663
HMNXSV003024385
ILMN_1770936
PH_hs_0001563
TC12002047.hg
g13436220_3p_at
Participates
as a component of
COQ3:COQ4:COQ5:COQ6:COQ7:COQ9 [mitochondrial inner membrane] (Homo sapiens)
Inferred To
COQ5 [mitochondrial matrix]
(Bos taurus)
COQ5 [mitochondrial matrix]
(Caenorhabditis elegans)
COQ5 [mitochondrial matrix]
(Canis familiaris)
COQ5 [mitochondrial matrix]
(Danio rerio)
COQ5 [mitochondrial matrix]
(Dictyostelium discoideum)
COQ5 [mitochondrial matrix]
(Drosophila melanogaster)
COQ5 [mitochondrial matrix]
(Gallus gallus)
COQ5 [mitochondrial matrix]
(Mus musculus)
COQ5 [mitochondrial matrix]
(Rattus norvegicus)
COQ5 [mitochondrial matrix]
(Saccharomyces cerevisiae)
COQ5 [mitochondrial matrix]
(Schizosaccharomyces pombe)
COQ5 [mitochondrial matrix]
(Sus scrofa)
COQ5 [mitochondrial matrix]
(Xenopus tropicalis)
Cross References
RefSeq
NP_115690.3
OpenTargets
ENSG00000110871
GeneCards
Q5HYK3
HPA
ENSG00000110871-COQ5
Ensembl
ENSG00000110871
,
ENST00000288532
,
ENSP00000288532
PRO
Q5HYK3
Pharos - Targets
Q5HYK3
Orphanet
24434
HMDB Protein
HMDBP07419
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