In human liver and kidney tissue, monomeric peroxisomal ACOX2 (bound to FAD cofactor) catalyzes the reaction of (2S)-pristanoyl-CoA and O2 to form trans-2,3-dehydropristanoyl-CoA and H2O2 (Vanhove et al. 1993; Baumgart et al. 1996). A putative acyl-coenzyme A oxidase-like protein ACOXL could catalyse this type of reaction but its activity has not yet been determined.
Vanhove, GF, Van Veldhoven, PP, Fransen, M, Denis, S, Eyssen, HJ, Wanders, RJ, Mannaerts, GP
Baumgart, E, Vanhooren, JC, Fransen, M, Marynen, P, Puype, M, Vandekerckhove, J, Leunissen, JA, Fahimi, HD, Mannaerts, GP, Van Veldhoven, PP
pristanoyl-CoA oxidase activity of ACOX2:FAD, ACOXL:FAD [peroxisomal matrix]
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