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SCO1 [mitochondrial matrix]
Stable Identifier
R-HSA-5336170
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Protein SCO1 homolog, mitochondrial, SCO1_HUMAN
Locations in the PathwayBrowser
Expand all
Cellular responses to stimuli (Homo sapiens)
Cellular responses to stress (Homo sapiens)
Cellular response to chemical stress (Homo sapiens)
Cytoprotection by HMOX1 (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
COX ancilliary proteins [mitochondrial matrix] (Homo sapiens)
SCO1 [mitochondrial matrix] (Homo sapiens)
Gene expression (Transcription) (Homo sapiens)
RNA Polymerase II Transcription (Homo sapiens)
Generic Transcription Pathway (Homo sapiens)
Transcriptional Regulation by TP53 (Homo sapiens)
TP53 Regulates Metabolic Genes (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
COX ancilliary proteins [mitochondrial matrix] (Homo sapiens)
SCO1 [mitochondrial matrix] (Homo sapiens)
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
COX ancilliary proteins [mitochondrial matrix] (Homo sapiens)
SCO1 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:O75880 SCO1
Gene Names
SCO1, SCOD1
Chain
transit peptide:1-67, chain:68-301
Reference Genes
BioGPS Gene:6341 SCO1
COSMIC (genes):SCO1 SCO1
CTD Gene:6341 SCO1
dbSNP Gene:6341 SCO1
ENSEMBL:ENSG00000133028 SCO1
ENSEMBL_homo_sapiens_GENE:ENSG00000133028.12 SCO1
HGNC:10603 SCO1
KEGG Gene (Homo sapiens):6341 SCO1
Monarch:6341 SCO1
NCBI Gene:6341 SCO1
OMIM:603644 SCO1
UCSC:O75880 SCO1
Reference Transcript
RefSeq:NM_004589.3 SCO1
RefSeq:XM_005256751.3 SCO1
Other Identifiers
11728242_a_at
16841425
223221_PM_at
223221_at
3745492
3745494
3745495
3745496
3745498
3745500
3745501
3745502
3745503
3745505
3745506
3745507
3745508
3745511
3745512
3745513
3745514
3745516
3745520
3745521
55225_at
63237_at
6341
65440_at
8012823
85831_r_at
A_23_P15466
GE54210
GO:0005507
GO:0005515
GO:0005739
GO:0005743
GO:0006878
GO:0007005
GO:0008535
GO:0016020
GO:0016531
GO:0030016
GO:0033617
GO:0043226
GO:0046872
GO:0055065
GO:0065003
GO:0140104
HMNXSV003011990
ILMN_1728975
PH_hs_0001375
PH_hs_0009448
TC17001136.hg
g9963786_3p_at
Participates
as a member of
COX ancilliary proteins [mitochondrial matrix] (Homo sapiens)
Inferred To
SCO1 [mitochondrial matrix]
(Bos taurus)
SCO1 [mitochondrial matrix]
(Canis familiaris)
SCO1 [mitochondrial matrix]
(Drosophila melanogaster)
SCO1 [mitochondrial matrix]
(Gallus gallus)
SCO1 [mitochondrial matrix]
(Mus musculus)
SCO1 [mitochondrial matrix]
(Rattus norvegicus)
SCO1 [mitochondrial matrix]
(Sus scrofa)
Cross References
RefSeq
XP_005256808.1
,
NP_004580.1
OpenTargets
ENSG00000133028
GeneCards
O75880
HPA
ENSG00000133028-SCO1
Ensembl
ENSP00000255390
,
ENSG00000133028
,
ENST00000255390
PRO
O75880
Pharos - Targets
O75880
Orphanet
15259
HMDB Protein
HMDBP08256
PDB
2GGT
,
2HRN
,
2GVP
,
2GQM
,
2HRF
,
2GQK
,
2GT6
,
2GQL
,
2GT5
,
1WP0
Interactors (2)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q8NEZ3 WDR19
2
WDR19 [ciliary tip]
(R-HSA-5625347)
WDR19 [cilium]
(R-HSA-5610446)
0.508
2
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.483
3
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