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NDUFB1 [mitochondrial inner membrane]
Stable Identifier
R-HSA-60214
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase MNLL subunit , Complex I-MNLL, CI-MNLL
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB1 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O75438 NDUFB1
Gene Names
NDUFB1
Chain
initiator methionine:, chain:2-58
Reference Genes
BioGPS Gene:4707 NDUFB1
COSMIC (genes):NDUFB1 NDUFB1
CTD Gene:4707 NDUFB1
dbSNP Gene:4707 NDUFB1
ENSEMBL:ENSG00000183648 NDUFB1
ENSEMBL_homo_sapiens_GENE:ENSG00000183648.11 NDUFB1
HGNC:7695 NDUFB1
KEGG Gene (Homo sapiens):4707 NDUFB1
Monarch:4707 NDUFB1
NCBI Gene:4707 NDUFB1
OMIM:603837 NDUFB1
UCSC:O75438 NDUFB1
Reference Transcript
RefSeq:NM_004545.3 NDUFB1
Other Identifiers
11721296_a_at
16796048
206790_PM_s_at
206790_s_at
3576938
3576939
3576940
3576943
3576946
3576949
3576950
3576951
3576952
3576954
3576955
3576956
38605_at
4707
7980955
A_23_P140423
GE61076
GO:0003824
GO:0005215
GO:0005634
GO:0005654
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0007005
GO:0008137
GO:0009060
GO:0016020
GO:0016491
GO:0016607
GO:0032981
GO:0042776
GO:0043226
GO:0055086
GO:0065003
GO:0070469
GO:1901135
HMNXSV003055510
ILMN_1724367
PH_hs_0010822
TC14001447.hg
g4758775_3p_a_at
Participates
as a component of
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
Inferred To
Ndufb1 [mitochondrial inner membrane]
(Mus musculus)
NDUFB1 [mitochondrial inner membrane]
(Bos taurus)
NDUFB1 [mitochondrial inner membrane]
(Canis familiaris)
NDUFB1 [mitochondrial inner membrane]
(Gallus gallus)
NDUFB1 [mitochondrial inner membrane]
(Sus scrofa)
Ghost homologue of NDUFB1 [mitochondrial inner membrane]
(Caenorhabditis elegans)
Ghost homologue of NDUFB1 [mitochondrial inner membrane]
(Danio rerio)
Ghost homologue of NDUFB1 [mitochondrial inner membrane]
(Rattus norvegicus)
ND-MNLL [mitochondrial inner membrane]
(Drosophila melanogaster)
ndufb1 [mitochondrial inner membrane]
(Xenopus tropicalis)
Cross References
RefSeq
NP_004536.2
OpenTargets
ENSG00000183648
GeneCards
O75438
HPA
ENSG00000183648-NDUFB1
Ensembl
ENSP00000450776
,
ENSP00000451090
,
ENST00000555441
,
ENST00000553514
,
ENST00000617122
,
ENSP00000475170
,
ENSP00000483888
,
ENST00000329559
,
ENST00000605997
,
ENSP00000330787
,
ENSG00000183648
PRO
O75438
Pharos - Targets
O75438
Orphanet
24744
PDB
5XTH
,
5XTC
,
5XTD
,
5XTI
HMDB Protein
HMDBP00118
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.527
5
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