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MT-ND6 [mitochondrial inner membrane]
Stable Identifier
R-HSA-60569
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase chain 6 (EC 1.6.5.3)
Icon
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
ND2, ND3, ND6, NDUFB6 bind the MCIA complex to form a 370kDa subcomplex (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND6 [mitochondrial inner membrane] (Homo sapiens)
MT-ND6 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND6 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND6 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND6 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND6 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND6 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND6 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MT-ND6 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex (-MCIA complex) [mitochondrial inner membrane] (Homo sapiens)
MT-ND6 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex (-MCIA complex) [mitochondrial inner membrane] (Homo sapiens)
MT-ND6 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:P03923 MT-ND6
Gene Names
MT-ND6, MTND6, NADH6, ND6
Chain
chain:1-174
Reference Genes
BioGPS Gene:4541 MT-ND6
COSMIC (genes):MT-ND6 MT-ND6
CTD Gene:4541 MT-ND6
dbSNP Gene:4541 MT-ND6
ENSEMBL:ENSG00000198695 MT-ND6
HGNC:7462 MT-ND6
KEGG Gene (Homo sapiens):4541 MT-ND6
Monarch:4541 MT-ND6
NCBI Gene:4541 MT-ND6
OMIM:516006 MT-ND6
Reference Transcript
RefSeq:NC_012920.1 MT-ND6
Other Identifiers
0001090670
1553575_at
17100697
17100699
2867408
4037743
4037744
4037745
4037746
4037747
4037748
4037749
4037750
4037751
4037752
4037753
4037754
4541
8113120
8165705
8165707
A_23_P317056
GO:0003674
GO:0005575
GO:0005622
GO:0005737
GO:0005739
GO:0005743
GO:0006091
GO:0006120
GO:0007005
GO:0008137
GO:0008150
GO:0016020
GO:0016021
GO:0016491
GO:0022607
GO:0031966
GO:0032981
GO:0043226
GO:0055114
GO:0065003
GO:0070469
Hs2Affx.1.46.S1_3p_at
ILMN_3308961
Participant Of
input
ND2, ND3, ND6, NDUFB6 bind the MCIA complex to form a 370kDa subcomplex
hasComponent
370 kDa subcomplex (-MCIA complex) [mitochondrial inner membrane]
370 kDa subcomplex [mitochondrial inner membrane]
Inferred To
nd6 [mitochondrial inner membrane] (Xenopus tropicalis)
Mtnd6 [mitochondrial inner membrane] (Mus musculus)
Mtnd6 [mitochondrial inner membrane] (Rattus norvegicus)
mt:ND6 [mitochondrial inner membrane] (Drosophila melanogaster)
MT-ND6 [mitochondrial inner membrane] (Bos taurus)
MT-ND6 [mitochondrial inner membrane] (Canis familiaris)
MT-ND6 [mitochondrial inner membrane] (Gallus gallus)
MT-ND6 [mitochondrial inner membrane] (Sus scrofa)
mt-nd6 [mitochondrial inner membrane] (Danio rerio)
Cross References
RefSeq
YP_003024037.1
Target Pathogen
5b354852be737e166372e6ed
OpenTargets
ENSG00000198695
HPA
ENSG00000198695-MT-ND6
GeneCards
P03923
Ensembl
ENST00000361681
,
ENSP00000354665
,
ENSG00000198695
PRO
P03923
Orphanet
16484
HMDB Protein
HMDBP00189
PDB
5XTD
,
5XTC
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:O75489 NDUFS3
1
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
0.527
2
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