Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
CHIT1 [extracellular region]
Stable Identifier
R-HSA-6786396
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
extracellular region
Synonyms
Chitotriosidase-1 ecNumber3.2.1.14/ecNumber, CHIT1_HUMAN
Locations in the PathwayBrowser for interactor UniProt:P43353 ALDH3B1
Expand all
Digestion and absorption (Homo sapiens)
Digestion (Homo sapiens)
Digestion of dietary carbohydrate (Homo sapiens)
CHIT1 hydrolyses CHIT to 3xADGP (Homo sapiens)
CHIT1 [extracellular region] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q13231 CHIT1
Gene Names
CHIT1
Chain
signal peptide:1-21, chain:22-466
Reference Genes
BioGPS Gene:1118 CHIT1
COSMIC (genes):CHIT1 CHIT1
CTD Gene:1118 CHIT1
dbSNP Gene:1118 CHIT1
ENSEMBL:ENSG00000133063 CHIT1
HGNC:1936 CHIT1
KEGG:hsa:1118 CHIT1
Monarch:1118 CHIT1
NCBI Gene:1118 CHIT1
OMIM:600031 CHIT1
UCSC:Q13231 CHIT1
Reference Transcript
RefSeq:NM_003465.3 CHIT1
RefSeq:NM_001256125.2 CHIT1
Other Identifiers
1118
11756970_a_at
16698200
208168_PM_s_at
208168_s_at
2451617
2451618
2451619
2451620
2451621
2451622
2451623
2451624
2451625
2451626
2451627
2451628
2451629
2451630
2451631
2451632
2451636
2451638
2451639
2451640
2451642
2451643
2451644
2451649
2451650
2451651
2451652
2451653
37061_at
7923562
A_23_P126278
A_33_P3388501
A_33_P3411333
GE61928
GE852216
GO:0000272
GO:0002376
GO:0004553
GO:0004568
GO:0005515
GO:0005576
GO:0005615
GO:0005764
GO:0005975
GO:0006032
GO:0006955
GO:0008061
GO:0008843
GO:0009617
GO:0016787
GO:0016798
GO:0035580
GO:0044245
GO:1901135
GO:1904724
HMNXSV003046926
HMNXSV003055166
PH_hs_0022990
PH_hs_0032147
U29615_at
g4502808_3p_a_at
Participates
as a member of
Specific granule lumen proteins [extracellular region] (Homo sapiens)
Tertiary granule lumen proteins [extracellular region] (Homo sapiens)
Other forms of this molecule
CHIT1 [tertiary granule lumen]
CHIT1 [specific granule lumen]
Inferred To
Cht7 [extracellular region]
(Drosophila melanogaster)
cht-3 [extracellular region]
(Caenorhabditis elegans)
Idgf5 [extracellular region]
(Drosophila melanogaster)
Idgf3 [extracellular region]
(Drosophila melanogaster)
CHT1 [extracellular region]
(Plasmodium falciparum)
chia.4 [extracellular region]
(Danio rerio)
chia.2 [extracellular region]
(Danio rerio)
chia.6 [extracellular region]
(Danio rerio)
Cht11 [extracellular region]
(Drosophila melanogaster)
Idgf1 [extracellular region]
(Drosophila melanogaster)
Chit1 [extracellular region]
(Mus musculus)
Chit1 [extracellular region]
(Rattus norvegicus)
cht-1 [extracellular region]
(Caenorhabditis elegans)
CTS2 [extracellular region]
(Saccharomyces cerevisiae)
Cht2 [extracellular region]
(Drosophila melanogaster)
Cht8 [extracellular region]
(Drosophila melanogaster)
Cht6 [extracellular region]
(Drosophila melanogaster)
Cht4 [extracellular region]
(Drosophila melanogaster)
CHIT1 [extracellular region]
(Sus scrofa)
chia.1 [extracellular region]
(Danio rerio)
cht-4 [extracellular region]
(Caenorhabditis elegans)
Idgf4 [extracellular region]
(Drosophila melanogaster)
Idgf6 [extracellular region]
(Drosophila melanogaster)
Cht12 [extracellular region]
(Drosophila melanogaster)
chia.3 [extracellular region]
(Danio rerio)
Homologues of CHIT1 [extracellular region]
(Caenorhabditis elegans)
Homologues of CHIT1 [extracellular region]
(Danio rerio)
Homologues of CHIT1 [extracellular region]
(Drosophila melanogaster)
Cht10 [extracellular region]
(Drosophila melanogaster)
Idgf2 [extracellular region]
(Drosophila melanogaster)
Cht9 [extracellular region]
(Drosophila melanogaster)
Cht5 [extracellular region]
(Drosophila melanogaster)
Cross References
RefSeq
NP_003456.1
,
NP_001243054.2
Guide to Pharmacology - Targets
3187
OpenTargets
ENSG00000133063
ENSEMBL
ENST00000255427
,
ENST00000367229
,
ENST00000491855
,
ENSP00000356198
,
ENSP00000255427
,
ENSP00000423778
,
ENSG00000133063
ZINC - Substances
CHIT1_HUMAN
ZINC target
Q13231
PRO
Q13231
PDB
1HKM
,
1LQ0
,
4WKH
,
1LG1
,
5NRA
,
4WK9
,
4WJX
,
4WKA
,
1HKI
,
1WB0
,
5NRF
,
1LG2
,
1HKK
,
1HKJ
,
4WKF
,
1GUV
,
6JJR
,
6SO0
,
5HBF
,
6ZE8
,
6JK6
,
5NR8
,
1WAW
IntEnz
3.2.1.14
HPA
ENSG00000133063-CHIT1
GeneCards
CHIT1
Pharos - Targets
Q13231
HMDB Protein
HMDBP01031
Interactors (3)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P43353 ALDH3B1
3
ALDH3B1 [plasma membrane]
(R-HSA-5696096)
ALDH3B1 [secretory granule membrane]
(R-HSA-6801023)
ALDH3B1 [specific granule membrane]
(R-HSA-6799510)
0.527
2
UniProt:Q96DB5 RMD1
0.527
2
UniProt:P40337 VHL
3
VHL [cytosol]
(R-HSA-391423)
VHL [nucleoplasm]
(R-HSA-1234127)
monoSUMO1-K159,171,196-VHL [nucleoplasm]
(R-HSA-4551697)
0.499
2
© 2026
Reactome
This website requires cookies and the limited processing of your personal data in order to function. By using the site you are agreeing to this as outlined in our
Privacy Notice
.
I agree, dismiss this banner
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text