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AUH [mitochondrial matrix]
Stable Identifier
R-HSA-70775
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
methylglutaconyl-CoA hydratase, AU RNA binding protein
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of amino acids and derivatives (Homo sapiens)
Branched-chain amino acid catabolism (Homo sapiens)
beta-methylglutaconyl-CoA + H2O <=> beta-hydroxy-beta-methylglutaryl-CoA (Homo sapiens)
AUH hexamer [mitochondrial matrix] (Homo sapiens)
AUH [mitochondrial matrix] (Homo sapiens)
Literature References
PubMed ID
Title
Journal
Year
11738050
Crystal structure of human AUH protein, a single-stranded RNA binding homolog of enoyl-CoA hydratase
Kurimoto, K
,
Fukai, S
,
Nureki, O
,
Muto, Y
,
Yokoyama, S
Structure
2001
External Reference Information
External Reference
UniProt:Q13825 AUH
Gene Names
AUH
Chain
transit peptide:1-67, chain:68-339
Reference Genes
BioGPS Gene:549 AUH
COSMIC (genes):AUH AUH
CTD Gene:549 AUH
dbSNP Gene:549 AUH
ENSEMBL:ENSG00000148090 AUH
HGNC:890 AUH
KEGG Gene (Homo sapiens):549 AUH
Monarch:549 AUH
NCBI Gene:549 AUH
OMIM:600529 AUH
UCSC:Q13825 AUH
Reference Transcript
RefSeq:NM_001306190.1 AUH
RefSeq:NM_001698.2 AUH
Other Identifiers
0006550377
11745450_a_at
11749988_x_at
17095686
205052_at
3214373
3214374
3214375
3214378
3214380
3214385
3214386
3214400
3214401
3214405
3214406
3214415
3214416
3214420
3214421
3214422
3214423
3214424
37616_at
549
8162264
A_23_P20852
GE60058
GO:0003674
GO:0003723
GO:0003729
GO:0003730
GO:0003824
GO:0004300
GO:0004490
GO:0005575
GO:0005622
GO:0005737
GO:0005739
GO:0005759
GO:0006520
GO:0006552
GO:0006629
GO:0006635
GO:0008150
GO:0009056
GO:0009083
GO:0016829
GO:0043226
GO:0044281
GO:0050011
ILMN_1740349
ILMN_2231911
PH_hs_0004678
TC09001324.hg
X79888_at
g4502326_3p_at
Participant Of
hasComponent
AUH hexamer [mitochondrial matrix]
Inferred To
auh [mitochondrial matrix] (Danio rerio)
auh [mitochondrial matrix] (Dictyostelium discoideum)
auh [mitochondrial matrix] (Xenopus tropicalis)
Auh [mitochondrial matrix] (Mus musculus)
Auh [mitochondrial matrix] (Rattus norvegicus)
AUH [mitochondrial matrix] (Bos taurus)
AUH [mitochondrial matrix] (Canis familiaris)
AUH [mitochondrial matrix] (Gallus gallus)
AUH [mitochondrial matrix] (Plasmodium falciparum)
AUH [mitochondrial matrix] (Sus scrofa)
Dmel\CG8778 [mitochondrial matrix] (Drosophila melanogaster)
ech-5 [mitochondrial matrix] (Caenorhabditis elegans)
Cross References
RefSeq
NP_001293119.1
,
NP_001689.1
OpenTargets
ENSG00000148090
IntEnz
4.2.1.56
HPA
ENSG00000148090-AUH
GeneCards
Q13825
Ensembl
ENSP00000364883
,
ENSG00000148090
,
ENST00000303617
,
ENSP00000307334
,
ENST00000375731
PRO
Q13825
Orphanet
15342
HMDB Protein
HMDBP00982
PDB
1HZD
,
2ZQQ
,
2ZQR
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