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ACO2 [mitochondrial matrix]
Stable Identifier
R-HSA-70968
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
aconitase 2, mitochondrial, Aconitate hydratase, mitochondrial precursor , Citrate hydro-lyase, Aconitase
External Reference Information
External Reference
UniProt:Q99798 ACO2
Gene Names
ACO2
Chain
transit peptide:1-27, chain:28-780
Reference Genes
BioGPS Gene:50 ACO2
COSMIC (genes):ACO2 ACO2
CTD Gene:50 ACO2
dbSNP Gene:50 ACO2
ENSEMBL:ENSG00000100412 ACO2
ENSEMBL_homo_sapiens_GENE:ENSG00000100412.17 ACO2
HGNC:118 ACO2
KEGG Gene (Homo sapiens):50 ACO2
Monarch:50 ACO2
NCBI Gene:50 ACO2
OMIM:100850 ACO2
UCSC:Q99798 ACO2
Reference Transcript
RefSeq:NM_001098.2 ACO2
Other Identifiers
11743048_s_at
11752649_s_at
160044_g_at
16930635
200793_PM_s_at
200793_s_at
2386712
3946890
3946891
3946898
3946899
3946901
3946904
3946905
3946908
3946909
3946911
3946918
3946920
3946921
3946922
3946923
3946928
3946929
3946930
3946931
3946932
3946933
3958966
3958972
50
8073430
89636_f_at
A_23_P103149
A_23_P305481
GO:0001889
GO:0003824
GO:0003994
GO:0005506
GO:0005739
GO:0005759
GO:0005829
GO:0006091
GO:0006099
GO:0006101
GO:0006102
GO:0016829
GO:0035900
GO:0043226
GO:0046872
GO:0047780
GO:0048856
GO:0051536
GO:0051538
GO:0051539
HMNXSV003034821
PH_hs_0032150
TC22000337.hg
U80040_at
g4501866_3p_at
g4501866_3p_x_at
Participates
as a member of
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Homo sapiens)
as a component of
ACO2:3Fe-4S [mitochondrial matrix] (Homo sapiens)
ACO2:4Fe-4S [mitochondrial matrix] (Homo sapiens)
Other forms of this molecule
ACO2(1-780) [mitochondrial intermembrane space]
ACO2(1-780) [cytosol]
Inferred To
ACO2 [mitochondrial matrix]
(Bos taurus)
ACO2 [mitochondrial matrix]
(Caenorhabditis elegans)
ACO2 [mitochondrial matrix]
(Canis familiaris)
ACO2 [mitochondrial matrix]
(Dictyostelium discoideum)
ACO2 [mitochondrial matrix]
(Gallus gallus)
ACO2 [mitochondrial matrix]
(Mus musculus)
ACO2 [mitochondrial matrix]
(Rattus norvegicus)
ACO2 [mitochondrial matrix]
(Saccharomyces cerevisiae)
ACO2 [mitochondrial matrix]
(Schizosaccharomyces pombe)
ACO2 [mitochondrial matrix]
(Sus scrofa)
aco2 [mitochondrial matrix]
(Xenopus tropicalis)
wu:fa10e03 [mitochondrial matrix]
(Danio rerio)
mAcon1 [mitochondrial matrix]
(Drosophila melanogaster)
Cross References
RefSeq
NP_001089.1
OpenTargets
ENSG00000100412
IntEnz
4.2.1.3
HPA
ENSG00000100412-ACO2
GeneCards
Q99798
Ensembl
ENSP00000216254
,
ENSG00000100412
,
ENST00000216254
PRO
Q99798
Pharos - Targets
Q99798
Orphanet
21595
HMDB Protein
HMDBP00725
Interactors (2)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P19320 VCAM1
1
VCAM1 [plasma membrane]
(R-HSA-197834)
0.527
4
UniProt:Q8IWL3 HSCB
5
HSCB [mitochondrial matrix]
(R-HSA-1299438)
HSCB [mitochondrial inner membrane]
(R-HSA-1299447)
HSCB(1-235) [mitochondrial inner membrane]
(R-HSA-1299443)
HSCB(1-30) [mitochondrial matrix]
(R-HSA-8986120)
HSCB(1-235) [mitochondrial intermembrane space]
(R-HSA-1299456)
0.462
2
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