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CS [mitochondrial matrix]
Stable Identifier
R-HSA-70972
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
citrate synthase, Citrate synthase, mitochondrial precursor
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Citric acid cycle (TCA cycle) (Homo sapiens)
Maturation of TCA enzymes and regulation of TCA cycle (Homo sapiens)
CSKMT methylates Citrate Synthase (Homo sapiens)
Methylated(n) CS dimer [mitochondrial matrix] (Homo sapiens)
CS dimer [mitochondrial matrix] (Homo sapiens)
CS [mitochondrial matrix] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Mitochondrial protein degradation (Homo sapiens)
CLPXP binds mitochondrial matrix proteins (Homo sapiens)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Homo sapiens)
CS [mitochondrial matrix] (Homo sapiens)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Homo sapiens)
CS [mitochondrial matrix] (Homo sapiens)
CLPXP degrades mitochondrial matrix proteins (Homo sapiens)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Homo sapiens)
CS [mitochondrial matrix] (Homo sapiens)
LONP1 binds mitochondrial matrix proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
CS [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
CS [mitochondrial matrix] (Homo sapiens)
LONP1 degrades mitochondrial matrix proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
CS [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:O75390 CS
Gene Names
CS
Chain
transit peptide:1-27, chain:28-466
Reference Genes
BioGPS Gene:1431 CS
COSMIC (genes):CS CS
CTD Gene:1431 CS
dbSNP Gene:1431 CS
ENSEMBL:ENSG00000062485 CS
ENSEMBL_homo_sapiens_GENE:ENSG00000062485.19 CS
HGNC:2422 CS
KEGG Gene (Homo sapiens):1431 CS
Monarch:1431 CS
NCBI Gene:1431 CS
OMIM:118950 CS
UCSC:O75390 CS
Reference Transcript
RefSeq:NM_004077.2 CS
Other Identifiers
11748037_s_at
11748038_s_at
1431
16766001
17121958
208660_PM_at
208660_at
3457613
3457615
3457616
3457617
3457618
3457619
3457620
3457621
3457622
3457624
3457626
3457627
3457629
3457630
3457633
3457635
3457636
3457637
3457638
3457641
3457654
3457655
3457656
3824754
3824755
3824756
3824758
3824759
3824764
3824768
41314_at
7964064
A_23_P47818
A_33_P3215078
GE61606
GO:0003723
GO:0003824
GO:0004108
GO:0005576
GO:0005615
GO:0005634
GO:0005739
GO:0005759
GO:0005975
GO:0006091
GO:0006099
GO:0006101
GO:0016740
GO:0036440
GO:0043226
GO:0046912
GO:0070062
HMNXSV003037834
ILMN_1706057
ILMN_2396410
TC12003213.hg
g12652712_3p_at
Participates
as a member of
Substrate of LONP1 (mitochondrial matrix) [mitochondrial matrix] (Homo sapiens)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Homo sapiens)
as a component of
CS dimer [mitochondrial matrix] (Homo sapiens)
Other forms of this molecule
CS(1-466) [mitochondrial intermembrane space]
CS(1-466) [cytosol]
N6,N6-dimethyl-K395-CS [mitochondrial matrix]
N6-methyl-K395-CS [mitochondrial matrix]
N6,N6,N6-trimethyl-K395-CS [mitochondrial matrix]
Inferred To
cs [mitochondrial matrix]
(Danio rerio)
cs [mitochondrial matrix]
(Dictyostelium discoideum)
cs [mitochondrial matrix]
(Xenopus tropicalis)
cts-1 [mitochondrial matrix]
(Caenorhabditis elegans)
CIT1 [mitochondrial matrix]
(Saccharomyces cerevisiae)
CS [mitochondrial matrix]
(Bos taurus)
CS [mitochondrial matrix]
(Canis familiaris)
CS [mitochondrial matrix]
(Gallus gallus)
CS [mitochondrial matrix]
(Plasmodium falciparum)
CS [mitochondrial matrix]
(Sus scrofa)
kdn [mitochondrial matrix]
(Drosophila melanogaster)
Cs [mitochondrial matrix]
(Mus musculus)
Cs [mitochondrial matrix]
(Rattus norvegicus)
cit1 [mitochondrial matrix]
(Schizosaccharomyces pombe)
Cross References
RefSeq
NP_004068.2
OpenTargets
ENSG00000062485
IntEnz
2.3.3.1
GeneCards
O75390
HPA
ENSG00000062485-CS
Ensembl
ENSG00000062485
,
ENSP00000342056
,
ENST00000351328
PRO
O75390
Pharos - Targets
O75390
HMDB Protein
HMDBP00043
PDB
5UZQ
,
5UZP
,
5UZR
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