Cytosolic gamma-butyrobetaine hydroxylase dimer (BBOX1), a dioxygenase, catalyzes the reaction of oxygen, 4-trimethylammoniobutanoate (TEABT), and 2-oxoglutarate (2OG)to form CO2, succinate (SUCCA), and carnitine (CAR) (Lindstedt and Nordin 1984; Vaz et al. 1998).
Vaz, FM, van Gool, S, Ofman, R, Ijlst, L
Lindstedt, S, Nordin, I
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