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PQBP1 [nucleoplasm]
Stable Identifier
R-HSA-8867889
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
nucleoplasm
Synonyms
Polyglutamine-binding protein 1, PQBP1_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism of RNA (Homo sapiens)
Processing of Capped Intron-Containing Pre-mRNA (Homo sapiens)
mRNA Splicing (Homo sapiens)
mRNA Splicing - Major Pathway (Homo sapiens)
Disassembly of the Intron Lariat Spliceosome (new) (Homo sapiens)
Intron Lariat Spliceosome (ILS) [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Formation of the Spliceosomal B complex (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Spliceosomal B complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Formation of the Spliceosomal B* complex (Homo sapiens)
Spliceosomal B* complex [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Spliceosomal Bact complex [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Formation of the Spliceosomal Bact complex (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Spliceosomal B complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Spliceosomal Bact complex [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Formation of the Spliceosomal C complex containing intron lariat (Homo sapiens)
Spliceosomal B* complex [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Spliceosomal C complex [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Formation of the Spliceosomal C* complex (Homo sapiens)
Spliceosomal C complex [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Spliceosomal C* complex [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Formation of the Spliceosomal P complex and exon ligation (Homo sapiens)
Spliceosomal C* complex [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Spliceosomal P complex [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Spliceosomal P complex dissociates yielding the intron-containing complex (ILS) and the spliced mRNP (new) (Homo sapiens)
Intron Lariat Spliceosome (ILS) [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
Spliceosomal P complex [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
PQBP1 [nucleoplasm] (Homo sapiens)
External Reference Information
External Reference
UniProt:O60828 PQBP1
Gene Names
PQBP1, NPW38, JM26
Chain
initiator methionine:, chain:2-265
Reference Genes
BioGPS Gene:10084 PQBP1
COSMIC (genes):PQBP1 PQBP1
CTD Gene:10084 PQBP1
dbSNP Gene:10084 PQBP1
ENSEMBL:ENSG00000102103 PQBP1
HGNC:9330 PQBP1
KEGG:hsa:10084 PQBP1
Monarch:10084 PQBP1
NCBI Gene:10084 PQBP1
OMIM:300463 PQBP1
UCSC:O60828 PQBP1
Reference Transcript
RefSeq:NM_001167989.1 PQBP1
RefSeq:NM_001167992.1 PQBP1
RefSeq:NM_001167990.1 PQBP1
RefSeq:NM_001032384.1 PQBP1
RefSeq:NM_001032382.1 PQBP1
RefSeq:XM_005272572.4 PQBP1
RefSeq:NM_144495.2 PQBP1
RefSeq:NM_001032383.1 PQBP1
RefSeq:NM_005710.2 PQBP1
RefSeq:NM_001032381.1 PQBP1
RefSeq:XM_005272571.3 PQBP1
RefSeq:XM_017029207.1 PQBP1
RefSeq:XM_011543884.2 PQBP1
Other Identifiers
10084
11730026_x_at
11753989_x_at
11756030_a_at
11761355_a_at
11761356_x_at
17103509
207769_PM_s_at
207769_s_at
210499_3p_s_at
210499_PM_s_at
210499_s_at
214527_PM_s_at
214527_s_at
34325_at
3976931
3976932
3976933
3976934
3976935
3976936
3976937
3976938
3976939
3976940
3976941
3976942
3976943
3976944
3976945
3976946
3976947
3976948
3976949
8167412
A_14_P111129
A_14_P139896
A_23_P62139
A_33_P3224371
A_33_P3325933
A_33_P3325935
GE55166
GO:0000380
GO:0002218
GO:0002230
GO:0002376
GO:0003677
GO:0003690
GO:0003713
GO:0005515
GO:0005634
GO:0005654
GO:0005737
GO:0006355
GO:0006397
GO:0008380
GO:0010494
GO:0016071
GO:0016604
GO:0016607
GO:0031175
GO:0032481
GO:0043021
GO:0043226
GO:0043484
GO:0045087
GO:0045893
GO:0048814
GO:0051607
GO:0060090
GO:0071360
GO:0071598
GO:0098542
GO:0140110
HMNXSV003037667
Hs.30570.4.S1_3p_a_at
Hs.30570.4.S1_3p_x_at
ILMN_1692429
ILMN_1711596
ILMN_2325234
PH_hs_0002613
TC0X000263.hg
g10801589_3p_a_at
g10801589_3p_at
g10801589_3p_x_at
Participates
as an input of
Formation of the Spliceosomal B complex (Homo sapiens)
as an output of
Formation of the Spliceosomal Bact complex (Homo sapiens)
as a component of
Spliceosomal B complex [nucleoplasm] (Homo sapiens)
PRP19-CDC5L complex [nucleoplasm] (Homo sapiens)
Inferred To
pqbp-1.1 [nucleoplasm]
(Caenorhabditis elegans)
Pqbp1 [nucleoplasm]
(Mus musculus)
Pqbp1 [nucleoplasm]
(Rattus norvegicus)
PQBP1 [nucleoplasm]
(Bos taurus)
PQBP1 [nucleoplasm]
(Canis familiaris)
PQBP1 [nucleoplasm]
(Sus scrofa)
pqbp1 [nucleoplasm]
(Danio rerio)
pqbp1 [nucleoplasm]
(Xenopus tropicalis)
Ghost homologue of PQBP1 [nucleoplasm]
(Dictyostelium discoideum)
Ghost homologue of PQBP1 [nucleoplasm]
(Drosophila melanogaster)
Ghost homologue of PQBP1 [nucleoplasm]
(Gallus gallus)
Ghost homologue of PQBP1 [nucleoplasm]
(Plasmodium falciparum)
Ghost homologue of PQBP1 [nucleoplasm]
(Schizosaccharomyces pombe)
Cross References
RefSeq
XP_016884696.1
,
NP_001161462.1
,
NP_652766.1
,
NP_001161464.1
,
NP_001161461.1
,
NP_001027553.1
,
NP_001027556.1
,
XP_005272628.1
,
XP_005272629.1
,
NP_001027554.1
,
NP_005701.1
,
XP_011542186.1
,
NP_001027555.1
OpenTargets
ENSG00000102103
ENSEMBL
ENST00000396763
,
ENST00000710033
,
ENST00000710035
,
ENST00000710038
,
ENST00000218224
,
ENST00000710037
,
ENST00000692023
,
ENST00000470062
,
ENSP00000518007
,
ENST00000710039
,
ENSP00000518009
,
ENSP00000518006
,
ENSP00000518008
,
ENSP00000518005
,
ENSP00000509191
,
ENST00000376563
,
ENSP00000509874
,
ENSP00000508445
,
ENSP00000414861
,
ENST00000376566
,
ENST00000710032
,
ENST00000447146
,
ENST00000465859
,
ENST00000443648
,
ENST00000651767
,
ENST00000710049
,
ENST00000710046
,
ENST00000710044
,
ENSP00000509927
,
ENSP00000518017
,
ENSP00000518014
,
ENST00000247140
,
ENSP00000498362
,
ENSP00000365747
,
ENSP00000518013
,
ENSP00000518015
,
ENSP00000247140
,
ENST00000710042
,
ENST00000710041
,
ENST00000472742
,
ENSP00000379985
,
ENSP00000218224
,
ENSP00000365750
,
ENSP00000518012
,
ENSP00000518010
,
ENSP00000518011
,
ENST00000710043
,
ENSP00000391759
HPA
ENSG00000102103-PQBP1
PRO
O60828
Pharos - Targets
O60828
GlyGen
O60828
Orphanet
PQBP1
PDB
4BWS
,
4CDO
,
4BWQ
Interactors (10)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q9Y2W2 WBP11
1
WBP11 [nucleoplasm]
(R-HSA-8867887)
0.797
13
UniProt:Q15691 MAPRE1
1
MAPRE1 [cytosol]
(R-HSA-376240)
0.718
6
UniProt:Q9BRK4 LZTS2
0.718
6
UniProt:Q08379 GOLGA2
3
p-S37-GOLGA2 [Golgi membrane]
(R-HSA-2172179)
GOLGA2 [endoplasmic reticulum-Golgi intermediate compartment membrane]
(R-HSA-2167933)
GOLGA2 [Golgi membrane]
(R-HSA-6808764)
0.718
6
UniProt:P42858 HTT
1
HTT [nucleoplasm]
(R-HSA-9023590)
0.556
3
UniProt:P54253 ATX1
0.556
3
UniProt:Q16630 CPSF6
2
CPSF6(1-490)-FGFR1(429-822) fusion [cytosol]
(R-HSA-1614368)
CPSF6(1-490)-p-FGFR1(429-822) fusion [cytosol]
(R-HSA-1838987)
0.527
2
UniProt:P62140 PPP1CB
4
PPP1CB [cytosol]
(R-HSA-163405)
PPP1CB P49R [cytosol]
(R-HSA-9660547)
PPP1CB A56P [cytosol]
(R-HSA-9660543)
PPP1CB [nucleoplasm]
(R-HSA-62003)
0.508
2
UniProt:Q15435 PP1R7
0.508
2
UniProt:P62136 PPP1CA
1
PPP1CA [cytosol]
(R-HSA-163525)
0.508
2
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