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PITRM1 [mitochondrial matrix]
Stable Identifier
R-HSA-8986159
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Presequence protease, mitochondrial, PREP_HUMAN
Locations in the PathwayBrowser
Expand all
Protein localization (Homo sapiens)
Mitochondrial protein import (Homo sapiens)
PITRM1 proteolyzes mitochondrial targeting peptides (presequences) (Homo sapiens)
PITRM1 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q5JRX3 PITRM1
Gene Names
PITRM1, KIAA1104, MP1, PREP
Chain
transit peptide:1-28, chain:29-1037
Reference Genes
BioGPS Gene:10531 PITRM1
COSMIC (genes):PITRM1 PITRM1
COSMIC (genes):PREP PITRM1
CTD Gene:10531 PITRM1
dbSNP Gene:10531 PITRM1
ENSEMBL:ENSG00000107959 PITRM1
HGNC:17663 PITRM1
KEGG:hsa:10531 PITRM1
Monarch:10531 PITRM1
NCBI Gene:10531 PITRM1
OMIM:618211 PITRM1
UCSC:Q5JRX3 PITRM1
Reference Transcript
RefSeq:NM_001242309.1 PITRM1
RefSeq:NM_001242307.2 PITRM1
RefSeq:NM_014889.3 PITRM1
Other Identifiers
10531
11725613_x_at
11745253_a_at
11745942_a_at
11746526_a_at
16711205
205273_PM_s_at
205273_s_at
3274174
3274175
3274176
3274177
3274178
3274179
3274180
3274181
3274182
3274183
3274184
3274185
3274186
3274187
3274188
3274189
3274190
3274191
3274192
3274193
3274194
3274195
3274196
3274197
3274198
3274199
3274200
3274201
3274202
3274204
3274205
3274206
3274207
3274208
3274210
3274211
3274212
3274213
3274214
3274215
3274216
3274217
3274218
3274219
3274220
3274221
3274222
3274223
3274224
3274225
34839_at
7931778
A_23_P52402
A_33_P3265104
GO:0003824
GO:0004222
GO:0005515
GO:0005739
GO:0005759
GO:0006508
GO:0006626
GO:0008047
GO:0008237
GO:0008270
GO:0016485
GO:0016787
GO:0043226
GO:0046872
GO:0051604
GO:0098772
GO:0140096
HMNXSV003017887
HMNXSV003052348
ILMN_1698072
PH_hs_0022064
TC10000975.hg
g7662487_3p_s_at
Inferred To
CYM1 [mitochondrial matrix]
(Saccharomyces cerevisiae)
ucr-2.2 [mitochondrial matrix]
(Caenorhabditis elegans)
PITRM1 [mitochondrial matrix]
(Bos taurus)
PITRM1 [mitochondrial matrix]
(Canis familiaris)
PITRM1 [mitochondrial matrix]
(Drosophila melanogaster)
PITRM1 [mitochondrial matrix]
(Gallus gallus)
PITRM1 [mitochondrial matrix]
(Sus scrofa)
cym1 [mitochondrial matrix]
(Schizosaccharomyces pombe)
pitrm1 [mitochondrial matrix]
(Danio rerio)
pitrm1 [mitochondrial matrix]
(Dictyostelium discoideum)
pitrm1 [mitochondrial matrix]
(Xenopus tropicalis)
Pitrm1 [mitochondrial matrix]
(Mus musculus)
Pitrm1 [mitochondrial matrix]
(Rattus norvegicus)
Cross References
RefSeq
NP_001229236.1
,
NP_001229238.1
,
NP_055704.2
ENSEMBL
ENST00000224949
,
ENST00000451104
,
ENST00000380989
,
ENSG00000107959
,
ENSP00000401201
,
ENSP00000224949
,
ENSP00000370377
OpenTargets
ENSG00000107959
GeneCards
PITRM1
HPA
ENSG00000107959-PITRM1
ZINC target
Q5JRX3
PRO
Q5JRX3
Pharos - Targets
Q5JRX3
GlyGen
Q5JRX3
PDB
6XOT
,
6XOS
,
6XOU
,
4L3T
,
6XOV
,
4RPU
,
4NGE
,
6XOW
Interactors (5)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P0DTC5 M
10
M [plasma membrane]
(R-COV-9755780)
N-glycan M [virion membrane]
(R-COV-9694385)
M [virion membrane]
(R-COV-9694320)
M [endocytic vesicle membrane]
(R-COV-9694563)
N-glycan M [endocytic vesicle membrane]
(R-COV-9694738)
M [endoplasmic reticulum-Golgi intermediate compartment membrane]
(R-COV-9694439)
N-glycan M [endoplasmic reticulum-Golgi intermediate compartment membrane]
(R-COV-9694446)
M [endoplasmic reticulum membrane]
(R-COV-9767620)
nascent M [endoplasmic reticulum lumen]
(R-COV-9694279)
N-glycan M [endoplasmic reticulum membrane]
(R-COV-9694684)
0.643
3
UniProt:Q9HB09 B2L12
0.527
2
UniProt:Q80H93 8b
1
8b [cytosol]
(R-COV-9678168)
0.527
2
UniProt:A6NGG8 PCARE
0.508
2
UniProt:Q83D60 Q83D60
0.488
2
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