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PXLP-K357-ABAT [mitochondrial matrix]
Stable Identifier
R-HSA-916848
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
4-aminobutyrate aminotransferase, mitochondrial, GABT_HUMAN
Locations in the PathwayBrowser
Expand all
Neuronal System (Homo sapiens)
Transmission across Chemical Synapses (Homo sapiens)
Neurotransmitter release cycle (Homo sapiens)
GABA synthesis, release, reuptake and degradation (Homo sapiens)
Degradation of GABA (Homo sapiens)
PXLP-K357-ABAT dimer:2Fe-2S transforms GABA to SUCCSA (Homo sapiens)
PXLP-K357-ABAT dimer:2Fe-2S [mitochondrial matrix] (Homo sapiens)
PXLP-K357-ABAT [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:P80404 ABAT
Gene Names
ABAT, GABAT
Chain
transit peptide:1-28, chain:29-500
Reference Genes
BioGPS Gene:18 ABAT
COSMIC (genes):ABAT ABAT
CTD Gene:18 ABAT
dbSNP Gene:18 ABAT
ENSEMBL:ENSG00000183044 ABAT
ENSEMBL_homo_sapiens_GENE:ENSG00000183044.12 ABAT
HGNC:23 ABAT
KEGG Gene (Homo sapiens):18 ABAT
Monarch:18 ABAT
NCBI Gene:18 ABAT
OMIM:137150 ABAT
Reference Transcript
RefSeq:XM_011522401.2 ABAT
RefSeq:NM_020686.5 ABAT
RefSeq:NM_001127448.1 ABAT
RefSeq:XM_011522400.2 ABAT
RefSeq:NM_000663.4 ABAT
Other Identifiers
11736387_a_at
11739130_a_at
16815735
18
206527_PM_at
206527_at
209459_PM_s_at
209459_s_at
209460_PM_at
209460_at
33446_at
36364_at
3647422
3647446
3647450
3647451
3647453
3647454
3647456
3647457
3647459
3647462
3647465
3647467
3647468
3647469
3647472
3647473
3647474
3647475
3647477
3647480
3647481
3647482
3647483
3647484
3647485
68707_at
7993126
A_14_P131650
A_23_P152505
A_24_P330684
A_33_P3268487
A_33_P3366161
GE57720
GE82563
GE87635
GO:0001666
GO:0003012
GO:0003013
GO:0003824
GO:0003867
GO:0005739
GO:0005759
GO:0006520
GO:0007620
GO:0007626
GO:0008483
GO:0009410
GO:0009448
GO:0009449
GO:0009450
GO:0010039
GO:0014053
GO:0016740
GO:0021549
GO:0022414
GO:0023052
GO:0030170
GO:0031652
GO:0032024
GO:0032144
GO:0032145
GO:0033602
GO:0034386
GO:0035094
GO:0035640
GO:0042220
GO:0042802
GO:0043226
GO:0045471
GO:0045776
GO:0045964
GO:0046872
GO:0047298
GO:0048148
GO:0048856
GO:0050877
GO:0051536
GO:0070474
GO:0097151
GO:1902722
GO:1904450
HMNXSV003033166
ILMN_1670117
ILMN_1805104
ILMN_2404407
L32961_at
PH_hs_0000214
PH_hs_0014662
S75578_s_at
TC16000148.hg
U80226_s_at
g4501846_3p_at
g9963907_3p_s_at
Participates
as a component of
PXLP-K357-ABAT dimer:2Fe-2S [mitochondrial matrix] (Homo sapiens)
Inferred To
cb880 [mitochondrial matrix]
(Danio rerio)
ABAT [mitochondrial matrix]
(Bos taurus)
ABAT [mitochondrial matrix]
(Canis familiaris)
ABAT [mitochondrial matrix]
(Gallus gallus)
ABAT [mitochondrial matrix]
(Sus scrofa)
Homologues of PXLP-K357-ABAT [mitochondrial matrix]
(Sus scrofa)
Gabat [mitochondrial matrix]
(Drosophila melanogaster)
PXLP-K357-ABAT [mitochondrial matrix]
(Caenorhabditis elegans)
PXLP-K357-ABAT [mitochondrial matrix]
(Dictyostelium discoideum)
PXLP-K357-ABAT [mitochondrial matrix]
(Mus musculus)
PXLP-K357-ABAT [mitochondrial matrix]
(Rattus norvegicus)
PXLP-K357-ABAT [mitochondrial matrix]
(Saccharomyces cerevisiae)
PXLP-K357-ABAT [mitochondrial matrix]
(Schizosaccharomyces pombe)
PXLP-K357-ABAT [mitochondrial matrix]
(Sus scrofa)
abat [mitochondrial matrix]
(Xenopus tropicalis)
Modified Residues
Name
N6-pyridoxal phosphate-L-lysine at 357
Coordinate
357
PsiMod Name
N6-pyridoxal phosphate-L-lysine [MOD:00128]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-pyridoxal phosphate-L-lysine.
Cross References
RefSeq
NP_000654.2
,
XP_011520702.1
,
NP_065737.2
,
NP_001120920.1
,
XP_011520703.1
Guide to Pharmacology - Targets
2464
OpenTargets
ENSG00000183044
ZINC - Substances
GABT_HUMAN
ZINC target
P80404
PRO
P80404
IntEnz
2.6.1.22
HPA
ENSG00000183044-ABAT
GeneCards
P80404
Ensembl
ENSP00000379845
,
ENSG00000183044
,
ENST00000425191
,
ENST00000396600
,
ENSP00000411916
,
ENSP00000268251
,
ENST00000268251
Pharos - Targets
P80404
ZINC - Predictions - Purchasable
GABT_HUMAN
Orphanet
15048
HMDB Protein
HMDBP00248
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