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SAE1 [nucleoplasm]
Stable Identifier
R-HSA-947697
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
nucleoplasm
Synonyms
SUMO-activating enzyme subunit 1, SAE1_HUMAN
Icon
Locations in the PathwayBrowser
Expand all
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
SUMOylation (Homo sapiens)
Processing and activation of SUMO (Homo sapiens)
SUMO is conjugated to E1 (UBA2:SAE1) (Homo sapiens)
Conjugation of SUMO1 to UBA2:SAE1 (Homo sapiens)
SUMO1:UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
Conjugation of SUMO2 to UBA2:SAE1 (Homo sapiens)
SUMO2:UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
Conjugation of SUMO3 to UBA2:SAE1 (Homo sapiens)
SUMO3:UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
SUMO is transferred from E1 to E2 (UBE2I, UBC9) (Homo sapiens)
Transfer of SUMO1 from E1 to UBE2I (UBC9) (Homo sapiens)
SUMO1:UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
Transfer of SUMO2 from E1 to UBE2I (UBC9) (Homo sapiens)
SUMO2:UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
Transfer of SUMO3 from E1 to UBE2I (UBC9) (Homo sapiens)
SUMO3:UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
UBA2:SAE1 [nucleoplasm] (Homo sapiens)
SAE1 [nucleoplasm] (Homo sapiens)
Literature References
PubMed ID
Title
Journal
Year
11481243
Expression and regulation of the mammalian SUMO-1 E1 enzyme
Azuma, Y
,
Tan, SH
,
Cavenagh, MM
,
Ainsztein, AM
,
Saitoh, H
,
Dasso, M
FASEB J.
2001
External Reference Information
External Reference
UniProt:Q9UBE0 SAE1
Gene Names
SAE1, AOS1, SUA1, UBLE1A
Chain
initiator methionine:1, chain:1-346, chain:2-346
Reference Genes
BioGPS Gene:10055 SAE1
COSMIC (genes):SAE1 SAE1
CTD Gene:10055 SAE1
dbSNP Gene:10055 SAE1
ENSEMBL:ENSG00000142230 SAE1
HGNC:30660 SAE1
KEGG Gene (Homo sapiens):10055 SAE1
Monarch:10055 SAE1
NCBI Gene:10055 SAE1
OMIM:613294 SAE1
UCSC:Q9UBE0 SAE1
Reference Transcript
RefSeq:NM_001145713.1 SAE1
RefSeq:NM_005500.2 SAE1
RefSeq:NM_001145714.1 SAE1
Other Identifiers
0000060338
10055
11737533_a_at
11744108_x_at
11751729_a_at
11751730_x_at
1555618_s_at
16863551
217946_s_at
3353524
3353529
3837140
3837141
3837142
3837143
3837146
3837147
3837148
3837150
3837151
3837152
3837162
3837164
3837167
3837168
3837169
3837170
3837171
3837172
3837173
3837174
3837175
3837176
45712_at
51084_at
8029884
A_14_P101357
A_23_P16337
A_24_P194000
GE61854
GO:0003674
GO:0004839
GO:0005515
GO:0005575
GO:0005622
GO:0005634
GO:0005654
GO:0005737
GO:0006464
GO:0006605
GO:0006810
GO:0007005
GO:0008022
GO:0008047
GO:0008150
GO:0008641
GO:0015031
GO:0016567
GO:0016874
GO:0016925
GO:0019899
GO:0019948
GO:0030234
GO:0031510
GO:0032446
GO:0032991
GO:0033235
GO:0043008
GO:0043085
GO:0043226
GO:0044388
GO:0046982
GO:1903955
Hs2.279868.2.S1_3p_s_at
ILMN_1657204
PH_hs_0022094
TC19000672.hg
TC19002180.hg
g7705472_3p_s_at
Participant Of
hasComponent
SUMO1:UBA2:SAE1 [nucleoplasm]
SUMO2:UBA2:SAE1 [nucleoplasm]
SUMO3:UBA2:SAE1 [nucleoplasm]
UBA2:SAE1 [nucleoplasm]
Inferred To
Aos1 [nucleoplasm] (Drosophila melanogaster)
Homologues of SAE1 [nucleoplasm] (Plasmodium falciparum)
Sae1 [nucleoplasm] (Mus musculus)
Sae1 [nucleoplasm] (Rattus norvegicus)
AOS1 [nucleoplasm] (Saccharomyces cerevisiae)
sae1 [nucleoplasm] (Danio rerio)
sae1 [nucleoplasm] (Dictyostelium discoideum)
sae1 [nucleoplasm] (Xenopus tropicalis)
aos-1 [nucleoplasm] (Caenorhabditis elegans)
SAE1 [nucleoplasm] (Canis familiaris)
SAE1 [nucleoplasm] (Gallus gallus)
SAE1 [nucleoplasm] (Plasmodium falciparum)
SAE1 [nucleoplasm] (Sus scrofa)
Cross References
RefSeq
NP_001139186.1
,
NP_005491.1
,
NP_001139185.1
OpenTargets
ENSG00000142230
ZINC - Substances
SAE1_HUMAN
ZINC target
Q9UBE0
ZINC - Biogenic
SAE1_HUMAN
PRO
Q9UBE0
PDB
1Y8Q
,
6CWZ
,
3KYC
,
6CWY
,
1Y8R
,
3KYD
ZINC - Metabolites
SAE1_HUMAN
GeneCards
Q9UBE0
HPA
ENSG00000142230-SAE1
Ensembl
ENSP00000270225
,
ENSG00000142230
,
ENSP00000416557
,
ENSP00000440818
,
ENST00000392776
,
ENST00000270225
,
ENST00000413379
ZINC - Predictions - Purchasable
SAE1_HUMAN
HMDB Protein
HMDBP11566
Interactors (4)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P63279 UBE2I
8
UBE2I [nuclear envelope]
(R-HSA-4655408)
SUMO1-K14-UBE2I [nucleoplasm]
(R-HSA-4085358)
UBE2I [cytosol]
(R-HSA-4655342)
SUMO1-C93-UBE2I [cytosol]
(R-HSA-4656909)
SUMO3-C93-UBE2I [nucleoplasm]
(R-HSA-3730629)
SUMO2-C93-UBE2I [nucleoplasm]
(R-HSA-3730619)
UBE2I [nucleoplasm]
(R-HSA-912481)
SUMO1-C93-UBE2I [nucleoplasm]
(R-HSA-3730617)
0.669
3
UniProt:P63165 SUMO1
155
TOPORS-G97-SUMO1 [nucleoplasm]
(R-HSA-4551623)
K14-UBE2I-G97-SUMO1 [nucleoplasm]
(R-HSA-4085334)
PIAS4-G97-SUMO1 [nucleoplasm]
(R-HSA-3968375)
K2592-RANBP2-G97-SUMO1 [nuclear envelope]
(R-HSA-4551627)
K2723-RANBP2-G97-SUMO1 [nuclear envelope]
(R-HSA-4551737)
K2650-RANBP2-G97-SUMO1 [nuclear envelope]
(R-HSA-4551591)
K196-VHL-G97-SUMO1 [nucleoplasm]
(R-HSA-4551630)
K171-VHL-G97-SUMO1 [nucleoplasm]
(R-HSA-4551632)
K159-VHL-G97-SUMO1 [nucleoplasm]
(R-HSA-4551713)
MDM-G97-SUMO1 [nucleoplasm]
(R-HSA-3730829)
K575-TRIM28-G97-SUMO1 [nucleoplasm]
(R-HSA-4090305)
K804-TRIM28-G97-SUMO1 [nucleoplasm]
(R-HSA-3782561)
K750-TRIM28-G97-SUMO1 [nucleoplasm]
(R-HSA-4090298)
K676-TRIM28-G97-SUMO1 [nucleoplasm]
(R-HSA-4090396)
K554-TRIM28-G97-SUMO1 [nucleoplasm]
(R-HSA-3782555)
K779-TRIM28-G97-SUMO1 [nucleoplasm]
(R-HSA-3782585)
ING2-G97-SUMO1 [nucleoplasm]
(R-HSA-4086096)
K788-Ncoa2-G97-SUMO1 [nucleoplasm]
(R-HSA-4085297)
K731-Ncoa2-G97-SUMO1 [nucleoplasm]
(R-HSA-4085312)
K239-Ncoa2-G97-SUMO1 [nucleoplasm]
(R-HSA-4085320)
K239-NCOA2-G97-SUMO1 [nucleoplasm]
(R-HSA-4085299)
K731-NCOA2-G97-SUMO1 [nucleoplasm]
(R-HSA-4085290)
K788-NCOA2-G97-SUMO1 [nucleoplasm]
(R-HSA-4085308)
NPM1-G97-SUMO1 [nucleoplasm]
(R-HSA-4086019)
NCOR2-G97-SUMO1 [nucleoplasm]
(R-HSA-3927883)
DDX17-G97-SUMO1 [nucleoplasm]
(R-HSA-3900210)
PARK7-G97-SUMO1 [nucleoplasm]
(R-HSA-4085344)
K1033-CREBBP-G97-SUMO1 [nucleoplasm]
(R-HSA-3927910)
K1056-CREBBP-G97-SUMO1 [nucleoplasm]
(R-HSA-3927954)
K998-CREBBP-G97-SUMO1 [nucleoplasm]
(R-HSA-3927822)
K1154-NRIP1-G97-SUMO1 [nucleoplasm]
(R-HSA-4086067)
K756-NRIP1-G97-SUMO1 [nucleoplasm]
(R-HSA-4086034)
DDX5-G97-SUMO1 [nucleoplasm]
(R-HSA-3900212)
CASP8AP2-G97-SUMO1 [nucleoplasm]
(R-HSA-3927863)
K1024-EP300-G97-SUMO1 [nucleoplasm]
(R-HSA-3899298)
K1020-EP300-G97-SUMO1 [nucleoplasm]
(R-HSA-3899290)
CTBP1-G97-SUMO1 [nucleoplasm]
(R-HSA-3730764)
K231-SAFB-G97-SUMO1 [nucleoplasm]
(R-HSA-4085364)
K294-SAFB-G97-SUMO1 [nucleoplasm]
(R-HSA-4085341)
K624-MKL1-G97-SUMO1 [nucleoplasm]
(R-HSA-3900128)
K576-MKL1-G97-SUMO1 [nucleoplasm]
(R-HSA-3900225)
K499-MKL1-G97-SUMO1 [nucleoplasm]
(R-HSA-3900219)
K631-DAXX-G97-SUMO1 [nucleoplasm]
(R-HSA-4086044)
K630-DAXX-G97-SUMO1 [nucleoplasm]
(R-HSA-4086012)
SIN3A-G97-SUMO1 [nucleoplasm]
(R-HSA-4086058)
PPARGC1A-G97-SUMO1 [nucleoplasm]
(R-HSA-3903014)
HIPK2-G97-SUMO1 [nucleoplasm]
(R-HSA-4090362)
K774-NCOA1-G97-SUMO1 [nucleoplasm]
(R-HSA-4085292)
K732-NCOA1-G97-SUMO1 [nucleoplasm]
(R-HSA-4085278)
K538-MBD1-G97-SUMO1 [nucleoplasm]
(R-HSA-4090416)
K499-MBD1-G97-SUMO1 [nucleoplasm]
(R-HSA-4090332)
ZNF131-G97-SUMO1 [nucleoplasm]
(R-HSA-3730875)
K90-NFKB2-G97-SUMO1 [cytosol]
(R-HSA-4755511)
K689-NFKB2-G97-SUMO1 [cytosol]
(R-HSA-4755446)
K863-NFKB2-G97-SUMO1 [cytosol]
(R-HSA-4755412)
K298-NFKB2-G97-SUMO1 [cytosol]
(R-HSA-4755505)
p-S172-IKBKE-G97-SUMO1 [nucleoplasm]
(R-HSA-4755408)
K309-IKBKG-G97-SUMO1 [nucleoplasm]
(R-HSA-4755404)
K277-IKBKG-G97-SUMO1 [nucleoplasm]
(R-HSA-4755531)
NFKBIA-G97-SUMO1 [nucleoplasm]
(R-HSA-4656987)
AURKA-G97-SUMO1 [cytosol]
(R-HSA-4655413)
TOP2B-G97-SUMO1 [nucleoplasm]
(R-HSA-4641311)
TOP1-G97-SUMO1 [nucleoplasm]
(R-HSA-4641306)
TOP2A-G97-SUMO1 [nucleoplasm]
(R-HSA-4641341)
K254-PCNA-G97-SUMO1 [nucleoplasm]
(R-HSA-4615853)
K-PCNA-G97-SUMO1 [nucleoplasm]
(R-HSA-4615836)
K164-PCNA-G97-SUMO1 [nucleoplasm]
(R-HSA-4615951)
MDC1-G97-SUMO1 [nucleoplasm]
(R-HSA-4570527)
STAG2-G97-SUMO1 [nucleoplasm]
(R-HSA-3826645)
RAD21-G97-SUMO1 [nucleoplasm]
(R-HSA-3826574)
K411-RAD52-G97-SUMO1 [nucleoplasm]
(R-HSA-4568857)
K412-RAD52-G97-SUMO1 [nucleoplasm]
(R-HSA-4568850)
K414-RAD52-G97-SUMO1 [nucleoplasm]
(R-HSA-4568900)
XRCC4-G97-SUMO1 [nucleoplasm]
(R-HSA-4568869)
K160-PML-G97-SUMO1 [nucleoplasm]
(R-HSA-3730884)
K490-PML-G97-SUMO1 [nucleoplasm]
(R-HSA-3730833)
K65-PML-G97-SUMO1 [nucleoplasm]
(R-HSA-3730879)
K203-PARP1-G97-SUMO1 [nucleoplasm]
(R-HSA-4551625)
K486-PARP1-G97-SUMO1 [nucleoplasm]
(R-HSA-4551748)
K496-WRN-G97-SUMO1 [nucleoplasm]
(R-HSA-4568906)
K898-WRN-G97-SUMO1 [nucleoplasm]
(R-HSA-4568893)
K356-WRN-G97-SUMO1 [nucleoplasm]
(R-HSA-4568845)
RNF168-SUMO1 [nucleoplasm]
(R-HSA-4551631)
XPC-G97-SUMO1 [nucleoplasm]
(R-HSA-4570452)
TDG-G97-SUMO1 [nucleoplasm]
(R-HSA-4551682)
SP100-G97-SUMO1 [nucleoplasm]
(R-HSA-3730794)
BRCA1-G97-SUMO1 [nucleoplasm]
(R-HSA-3730735)
RXRA-G97-SUMO1 [nucleoplasm]
(R-HSA-4341090)
NR5A2-G97-SUMO1 [nucleoplasm]
(R-HSA-4755424)
K386-AR-G97-SUMO1 [nucleoplasm]
(R-HSA-4090321)
K520-AR-G97-SUMO1 [nucleoplasm]
(R-HSA-4090352)
K293-NR3C1-G97-SUMO1 [nucleoplasm]
(R-HSA-4341110)
K277-NR3C1-G97-SUMO1 [nucleoplasm]
(R-HSA-4341057)
K389-THRA-G97-SUMO1 [nucleoplasm]
(R-HSA-4719415)
K283-THRA-G97-SUMO1 [nucleoplasm]
(R-HSA-4719434)
K399-NR3C2-G97-SUMO1 [nucleoplasm]
(R-HSA-4341020)
K428-NR3C2-G97-SUMO1 [nucleoplasm]
(R-HSA-4341035)
K494-NR3C2-G97-SUMO1 [nucleoplasm]
(R-HSA-4341093)
K89-NR3C2-G97-SUMO1 [nucleoplasm]
(R-HSA-4341058)
K119-NR5A1-G97-SUMO1 [nucleoplasm]
(R-HSA-4546379)
K194-NR5A1-G97-SUMO1 [nucleoplasm]
(R-HSA-4546380)
NR2C1-G97-SUMO1 [nucleoplasm]
(R-HSA-4717492)
K303-ESR1-G97-SUMO1 [nucleoplasm]
(R-HSA-4090373)
K266-ESR1-G97-SUMO1 [nucleoplasm]
(R-HSA-4090359)
K302-ESR1-G97-SUMO1 [nucleoplasm]
(R-HSA-4090363)
K299-ESR1-G97-SUMO1 [nucleoplasm]
(R-HSA-4090349)
K268-ESR1-G97-SUMO1 [nucleoplasm]
(R-HSA-4090414)
K531-PGR-G97-SUMO1 [nucleoplasm]
(R-HSA-4341021)
K7-PGR-G97-SUMO1 [nucleoplasm]
(R-HSA-4341052)
K388-PGR-G97-SUMO1 [nucleoplasm]
(R-HSA-4341056)
K132-NR1H4-G97-SUMO1 [nucleoplasm]
(R-HSA-9610527)
NR1H4-G97-SUMO1 [nucleoplasm]
(R-HSA-4755434)
PPARG-G97-SUMO1 [nucleoplasm]
(R-HSA-4717445)
K395-PPARG-G97-SUMO1 [nucleoplasm]
(R-HSA-4717446)
PPARA-G97-SUMO1 [nucleoplasm]
(R-HSA-4341069)
K443-THRB-G97-SUMO1 [nucleoplasm]
(R-HSA-4719431)
K146-THRB-G97-SUMO1 [nucleoplasm]
(R-HSA-4719410)
K50-THRB-G97-SUMO1 [nucleoplasm]
(R-HSA-4719401)
RORA-G97-SUMO1 [nucleoplasm]
(R-HSA-4719426)
HIC1-G97-SUMO1 [nucleoplasm]
(R-HSA-4570544)
TP53BP1-G97-SUMO1 [nucleoplasm]
(R-HSA-3730731)
SP3-G97-SUMO1 [nucleoplasm]
(R-HSA-3730646)
K423-MITF-G97-SUMO1 [nucleoplasm]
(R-HSA-3730755)
K289-MITF-G97-SUMO1 [nucleoplasm]
(R-HSA-3730738)
K25-FOXL2-G97-SUMO1 [nucleoplasm]
(R-HSA-3968400)
K150-FOXL2-G97-SUMO1 [nucleoplasm]
(R-HSA-3968382)
K114-FOXL2-G97-SUMO1 [nucleoplasm]
(R-HSA-3968396)
HNRNPC-G97-SUMO1 [nucleoplasm]
(R-HSA-4570515)
K497-NOP58-G97-SUMO1 [nucleoplasm]
(R-HSA-4570504)
K467-NOP58-G97-SUMO1 [nucleoplasm]
(R-HSA-4570462)
DNMT3B-G97-SUMO1 [nucleoplasm]
(R-HSA-4655444)
DNMT3A-G97-SUMO1 [nucleoplasm]
(R-HSA-4655383)
DNMT1-G97-SUMO1 [nucleoplasm]
(R-HSA-4655358)
K84-CBX5-G97-SUMO1 [nucleoplasm]
(R-HSA-4615838)
K-CBX5-G97-SUMO1 [nucleoplasm]
(R-HSA-4615955)
K476-HDAC1-G97-SUMO1 [nucleoplasm]
(R-HSA-4615867)
K444-HDAC1-G97-SUMO1 [nucleoplasm]
(R-HSA-4616028)
CBX4-G97-SUMO1 [nucleoplasm]
(R-HSA-4551756)
HDAC2-G97-SUMO1 [nucleoplasm]
(R-HSA-4616032)
SUZ12-G97-SUMO1 [nucleoplasm]
(R-HSA-4615961)
SATB1-G97-SUMO1 [nucleoplasm]
(R-HSA-4615877)
HDAC4-G97-SUMO1 [nucleoplasm]
(R-HSA-4615956)
K1971-CHD3-G97-SUMO1 [nucleoplasm]
(R-HSA-8956370)
HIST1H4-G97-SUMO1 [nucleoplasm]
(R-HSA-4570549)
BMI1-G97-SUMO1 [nucleoplasm]
(R-HSA-4551654)
TFAP2B-G97-SUMO1 [nucleoplasm]
(R-HSA-3730839)
TFAP2C-G97-SUMO1 [nucleoplasm]
(R-HSA-3730823)
TFAP2A-1-G97-SUMO1 [nucleoplasm]
(R-HSA-3730825)
UBE2I-G97-SUMO1 [cytosol]
(R-HSA-4656941)
RANGAP1-G97-SUMO1 [nucleoplasm]
(R-HSA-3730796)
SUMO1(2-101) [nucleoplasm]
(R-HSA-2990831)
SUMO1 [nucleoplasm]
(R-HSA-877304)
UBA2-G97-SUMO1 [nucleoplasm]
(R-HSA-3730616)
UBE2I-G97-SUMO1 [nucleoplasm]
(R-HSA-3730622)
HERC2-SUMO1 [nucleoplasm]
(R-HSA-4551761)
0.656
3
UniProt:P26367 PAX6
1
PAX6 [nucleoplasm]
(R-HSA-3009044)
0.556
3
UniProt:Q02548 PAX5
1
PAX5 [nucleoplasm]
(R-HSA-158583)
0.556
3
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