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Ndufs3 [mitochondrial matrix]
Stable Identifier
R-MMU-163927
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial matrix
Synonyms
NDUFS3, Q9DCT2
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
The citric acid (TCA) cycle and respiratory electron transport (Mus musculus)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Mus musculus)
Respiratory electron transport (Mus musculus)
Complex I biogenesis (Mus musculus)
IP subcomplex binds NDUFAF3, NDUFAF4, TIMMDC1 to form Intermediate 1 (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
NDUF subunits bind to form the IP subcomplex (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
980kDa complex [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Mus musculus)
980kDa complex [mitochondrial inner membrane] (Mus musculus)
815kDa complex [mitochondrial inner membrane] (Mus musculus)
550kDa complex [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 [mitochondrial inner membrane] (Mus musculus)
IP subcomplex [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
Complex I [mitochondrial inner membrane] (Mus musculus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Mus musculus)
Complex I [mitochondrial inner membrane] (Mus musculus)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
Metabolism of proteins (Mus musculus)
Mitochondrial protein degradation (Mus musculus)
CLPXP binds mitochondrial matrix proteins (Mus musculus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
CLPXP degrades mitochondrial matrix proteins (Mus musculus)
CLPXP:substrate protein (mitochondrial matrix) [mitochondrial matrix] (Mus musculus)
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
Ndufs3 [mitochondrial matrix] (Mus musculus)
External Reference Information
External Reference
UniProt:Q9DCT2
Gene Names
Ndufs3
Reference Genes
BioGPS Gene:68349 Ndufs3
ENSEMBL:ENSMUSG00000005510
KEGG Gene (Mus musculus):68349 Ndufs3
Monarch:68349 Ndufs3
NCBI Gene:68349 Ndufs3
UCSC:Q9DCT2 Ndufs3
Reference Transcript
RefSeq:NM_026688.2 Ndufs3
Other Identifiers
10386171
10484912
1423737_at
17388074
4321135
4368119
4379564
4543774
4903151
5012081
5064020
5254079
5410108
5544463
68349
96899_at
A_51_P395014
A_55_P2106834
GE1449781
GE38302
GO:0003824
GO:0003954
GO:0005215
GO:0005515
GO:0005634
GO:0005654
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0007005
GO:0008137
GO:0009060
GO:0012501
GO:0016020
GO:0016491
GO:0016604
GO:0016651
GO:0023052
GO:0030308
GO:0031966
GO:0032981
GO:0042776
GO:0043209
GO:0043226
GO:0055086
GO:0065003
GO:0070469
GO:0072593
GO:1901135
GO:2001243
ILMN_2646125
ILMN_2747897
aa271399_s_at
mMC020554
Participates
as a member of
Substrate of CLPXP (mitrochondrial matrix) [mitochondrial matrix] (Mus musculus)
as an input of
NDUF subunits bind to form the IP subcomplex (Mus musculus)
as a component of
IP subcomplex [mitochondrial matrix] (Mus musculus)
Intermediate 1 (-NDUFAF3,4,7, TIMMDC1) [mitochondrial inner membrane] (Mus musculus)
Other forms of this molecule
Ndufs3 [cytosol]
Inferred From
NDUFS3 [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_080964.1
IntEnz
7.1.1.2
Ensembl
ENSMUST00000005647
,
ENSMUSG00000005510
,
ENSMUSP00000005647
PRO
Q9DCT2
MGI
1915599
PDB
6G2J
,
7AK6
,
7B93
,
7PSA
,
6ZR2
,
6ZTQ
,
6G72
,
7AK5
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