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Dbt [mitochondrial matrix]
Stable Identifier
R-MMU-9859145
Type
Protein [EntityWithAccessionedSequence]
Species
Mus musculus
Compartment
mitochondrial matrix
Synonyms
2-Methylbutyryl-lipoH2-K105-DBT, P53395
Locations in the PathwayBrowser
Expand all
Metabolism (Mus musculus)
Metabolism of amino acids and derivatives (Mus musculus)
Branched-chain amino acid catabolism (Mus musculus)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Mus musculus)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Mus musculus)
Dbt [mitochondrial matrix] (Mus musculus)
DBT transfers BCAA to CoA (Mus musculus)
Dbt [mitochondrial matrix] (Mus musculus)
External Reference Information
External Reference
UniProt:P53395
Gene Names
Dbt
Reference Genes
BioGPS Gene:13171 Dbt
ENSEMBL:ENSMUSG00000000340
KEGG:mmu:13171 Dbt
Monarch:13171 Dbt
NCBI Gene:13171 Dbt
UCSC:P53395 Dbt
Reference Transcript
RefSeq:NM_010022.5 Dbt
Other Identifiers
10495549
115077_f_at
115078_r_at
13171
1449118_at
17402025
4517199
4520140
4647933
4676434
4743621
4844976
4853570
4932514
5165398
5217184
5240871
5264295
5304831
5435253
98966_at
A_52_P569348
GE35295
GO:0005739
GO:0005759
GO:0005829
GO:0005856
GO:0006520
GO:0009083
GO:0015630
GO:0016740
GO:0016746
GO:0031625
GO:0042645
GO:0043754
GO:0120552
GO:0160157
ILMN_1242012
ILMN_2417061
ILMN_2662920
L42996_s_at
mMC008698
mMR001410
Participates
as an output of
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Mus musculus)
as an input of
DBT transfers BCAA to CoA (Mus musculus)
Other forms of this molecule
Dbt [cytosol]
Dbt [mitochondrial matrix]
Dbt [mitochondrial matrix]
Dbt [mitochondrial matrix]
Dbt [mitochondrial matrix]
Dbt [mitochondrial matrix]
Inferred From
BCAA-lipoH2-K105-DBT [mitochondrial matrix]
(Homo sapiens)
2-Methylbutyryl-lipoH2-K105-DBT [mitochondrial matrix]
(Homo sapiens)
Modified Residues
Name
N6-lipoyl-L-lysine ((R)-N6-(S8-2-methylbutyryldihydrolipoyl)-L-lysine residue) at 105 (in Homo sapiens)
Coordinate
105
Modification
(R)-N6-(S8-2-methylbutyryldihydrolipoyl)-L-lysine residue
PsiMod Name
N6-lipoyl-L-lysine [MOD:00127]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-lipoyl-L-lysine.
Cross References
RefSeq
NP_034152.2
ENSEMBL
ENSMUST00000000349
,
ENSMUSG00000000340
,
ENSMUSP00000000349
IntEnz
2.3.1.168
PRO
P53395
MGI
105386
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