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PXLP-ALAS1 [mitochondrial matrix]
Stable Identifier
R-RNO-1022086
Type
Protein [EntityWithAccessionedSequence]
Species
Rattus norvegicus
Compartment
mitochondrial matrix
Synonyms
P13195
Locations in the PathwayBrowser
Expand all
Metabolism (Rattus norvegicus)
Metabolism of porphyrins (Rattus norvegicus)
Heme biosynthesis (Rattus norvegicus)
ALAS condenses SUCC-CoA and Gly to form dALA (Rattus norvegicus)
ALAS1,2 [mitochondrial matrix] (Rattus norvegicus)
ALAS1 homodimer (pyridoxal phosphate cofactor) [mitochondrial matrix] (Rattus norvegicus)
PXLP-ALAS1 [mitochondrial matrix] (Rattus norvegicus)
External Reference Information
External Reference
UniProt:P13195
Reference Genes
BioGPS Gene:65155
ENSEMBL:ENSRNOG00000056596
ENSEMBL:ENSRNOG00055012998
ENSEMBL:ENSRNOG00060030062
ENSEMBL:ENSRNOG00065008399
KEGG Gene (Rattus norvegicus):65155
Monarch:65155
NCBI Gene:65155
Reference Transcript
RefSeq:NM_024484.2
Participates
as a component of
ALAS1 homodimer (pyridoxal phosphate cofactor) [mitochondrial matrix] (Rattus norvegicus)
Other forms of this molecule
ALAS1 [mitochondrial matrix]
Inferred From
PXLP-ALAS1 [mitochondrial matrix]
(Homo sapiens)
Modified Residues
Name
N6-pyridoxal phosphate-L-lysine at unknown position
PsiMod Name
N6-pyridoxal phosphate-L-lysine [MOD:00128]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-pyridoxal phosphate-L-lysine.
Cross References
RefSeq
NP_077810.2
PRO
P13195
RGD
68392
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