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mccc1 [mitochondrial matrix]
Stable Identifier
R-XTR-70748
Type
Protein [EntityWithAccessionedSequence]
Species
Xenopus tropicalis
Compartment
mitochondrial matrix
Synonyms
Btn-MCCC1, Q6DIZ7
Locations in the PathwayBrowser
Expand all
Metabolism (Xenopus tropicalis)
Metabolism of amino acids and derivatives (Xenopus tropicalis)
Branched-chain amino acid catabolism (Xenopus tropicalis)
beta-methylcrotonyl-CoA + ATP + CO2 <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O [MCCA] (Xenopus tropicalis)
6x(Btn-MCCC1:MCCC2) [mitochondrial matrix] (Xenopus tropicalis)
mccc1 [mitochondrial matrix] (Xenopus tropicalis)
beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O <=> beta-methylcrotonyl-CoA + ATP + CO2 [MCCA] (Xenopus tropicalis)
6x(Btn-MCCC1:MCCC2) [mitochondrial matrix] (Xenopus tropicalis)
mccc1 [mitochondrial matrix] (Xenopus tropicalis)
Metabolism of vitamins and cofactors (Xenopus tropicalis)
Metabolism of water-soluble vitamins and cofactors (Xenopus tropicalis)
Biotin transport and metabolism (Xenopus tropicalis)
Cytoslic carboxylases translocate to mitochondrial matrix (Xenopus tropicalis)
hCBXs [mitochondrial matrix] (Xenopus tropicalis)
6x(Btn-MCCC1:MCCC2) [mitochondrial matrix] (Xenopus tropicalis)
mccc1 [mitochondrial matrix] (Xenopus tropicalis)
External Reference Information
External Reference
UniProt:Q6DIZ7
Gene Names
mccc1
Reference Genes
BioGPS Gene:448313 mccc1
ENSEMBL:ENSXETG00000016826
KEGG Gene (Xenopus tropicalis):448313 mccc1
Monarch:448313 mccc1
NCBI Gene:448313 mccc1
Reference Transcript
RefSeq:NM_001006690.1 mccc1
Participates
as a component of
6x(Btn-MCCC1:MCCC2) [mitochondrial matrix] (Xenopus tropicalis)
Other forms of this molecule
mccc1 [cytosol]
mccc1 [cytosol]
Inferred From
Btn-MCCC1 [mitochondrial matrix]
(Homo sapiens)
Modified Residues
Name
N6-biotinyl-L-lysine at 681 (in Homo sapiens)
Coordinate
681
PsiMod Name
N6-biotinyl-L-lysine [MOD:00126]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-biotinyl-L-lysine.
Cross References
RefSeq
NP_001006691.1
Xenbase
XB-GENE-967301
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