Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
H+ [mitochondrial matrix]
Stable Identifier
R-ALL-113529
Type
Chemical Compound [SimpleEntity]
Compartment
mitochondrial matrix
Synonyms
hydron
Icon
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Plasmodium falciparum
Rattus norvegicus
Saccharomyces cerevisiae
Schizosaccharomyces pombe
Sus scrofa
Xenopus tropicalis
Expand all
Cellular responses to stimuli (Bos taurus)
Cellular responses to stress (Bos taurus)
Cellular response to chemical stress (Bos taurus)
Cytoprotection by HMOX1 (Bos taurus)
Electron transfer from reduced cytochrome c to molecular oxygen (Bos taurus)
H+ [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Bos taurus)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Bos taurus)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Bos taurus)
H+ [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Bos taurus)
H+ [mitochondrial matrix]
Gene expression (Transcription) (Bos taurus)
RNA Polymerase II Transcription (Bos taurus)
Generic Transcription Pathway (Bos taurus)
Transcriptional Regulation by TP53 (Bos taurus)
TP53 Regulates Metabolic Genes (Bos taurus)
Electron transfer from reduced cytochrome c to molecular oxygen (Bos taurus)
H+ [mitochondrial matrix]
Metabolism (Bos taurus)
Aerobic respiration and respiratory electron transport (Bos taurus)
Citric acid cycle (TCA cycle) (Bos taurus)
CS acetylates OA to citrate (Bos taurus)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Bos taurus)
H+ [mitochondrial matrix]
Maturation of TCA enzymes and regulation of TCA cycle (Bos taurus)
ACAT1 tetramer acetylates IDH2 dimer (Bos taurus)
H+ [mitochondrial matrix]
CSKMT methylates Citrate Synthase (Bos taurus)
H+ [mitochondrial matrix]
NNT dimer transfers proton from NADPH to NAD+ (Bos taurus)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Bos taurus)
DLD dimer dehydrogenates dihydrolipoyl (Bos taurus)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Bos taurus)
H+ [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Bos taurus)
Enzyme-bound ATP is released (Bos taurus)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Bos taurus)
AAC1 imports a proton (Bos taurus)
H+ [mitochondrial matrix]
UCP1 imports a proton (Bos taurus)
H+ [mitochondrial matrix]
Pyruvate metabolism (Bos taurus)
FAHD1 dimer hydrolyses OA to PYR (Bos taurus)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Bos taurus)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Bos taurus)
DLD dimer dehydrogenates dihydrolipoyl (Bos taurus)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Bos taurus)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Bos taurus)
Regulation of pyruvate dehydrogenase (PDH) complex (Bos taurus)
GSTZ1 dimer dehalogenates DCA (Bos taurus)
H+ [mitochondrial matrix]
PDK isozymes phosphorylate PDHC subunit E1 (Bos taurus)
H+ [mitochondrial matrix]
Respiratory electron transport (Bos taurus)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Bos taurus)
H+ [mitochondrial matrix]
Electron transfer from reduced cytochrome c to molecular oxygen (Bos taurus)
H+ [mitochondrial matrix]
Electron transfer from ubiquinol to cytochrome c of complex III (Bos taurus)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Bos taurus)
MDH2 dimer dehydrogenates MAL (Bos taurus)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Bos taurus)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Bos taurus)
H+ [mitochondrial matrix]
Biological oxidations (Bos taurus)
Phase I - Functionalization of compounds (Bos taurus)
Cytochrome P450 - arranged by substrate type (Bos taurus)
Endogenous sterols (Bos taurus)
CYP11A1 cleaves 20a,22b-DHCHOL (Bos taurus)
H+ [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Bos taurus)
H+ [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Bos taurus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Bos taurus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Bos taurus)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Bos taurus)
H+ [mitochondrial matrix]
Vitamins (Bos taurus)
CYP24A1 24-hydroxylates CTL (Bos taurus)
H+ [mitochondrial matrix]
Ethanol oxidation (Bos taurus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Bos taurus)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Bos taurus)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Bos taurus)
Aspartate and asparagine metabolism (Bos taurus)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Bos taurus)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Bos taurus)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Bos taurus)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Bos taurus)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Bos taurus)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Bos taurus)
H+ [mitochondrial matrix]
BCKDK phosphorylates BCKDH (Bos taurus)
H+ [mitochondrial matrix]
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Bos taurus)
H+ [mitochondrial matrix]
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Bos taurus)
H+ [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Bos taurus)
H+ [mitochondrial matrix]
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Bos taurus)
H+ [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Bos taurus)
H+ [mitochondrial matrix]
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Bos taurus)
H+ [mitochondrial matrix]
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Bos taurus)
H+ [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Bos taurus)
H+ [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Bos taurus)
H+ [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Bos taurus)
H+ [mitochondrial matrix]
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Bos taurus)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Bos taurus)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Bos taurus)
H+ [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Bos taurus)
H+ [mitochondrial matrix]
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Bos taurus)
H+ [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Bos taurus)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Bos taurus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Bos taurus)
H+ [mitochondrial matrix]
Glycine degradation (Bos taurus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Bos taurus)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Bos taurus)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Bos taurus)
H+ [mitochondrial matrix]
Lysine catabolism (Bos taurus)
HYKK phosphorylates 5HLYS (Bos taurus)
H+ [mitochondrial matrix]
OADH complex synthesizes glutaryl-CoA from 2-OA (Bos taurus)
DHTKD1 dimer decarboxylates 2-OA (Bos taurus)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Bos taurus)
H+ [mitochondrial matrix]
DLST transfers glutaryl to CoA (Bos taurus)
H+ [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Bos taurus)
H+ [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Bos taurus)
H+ [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Bos taurus)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Bos taurus)
H+ [mitochondrial matrix]
Proline catabolism (Bos taurus)
ALDH4A1 oxidises L-GluSS to Glu (Bos taurus)
H+ [mitochondrial matrix]
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Bos taurus)
H+ [mitochondrial matrix]
PRODH oxidises L-Pro to 1PYR-5COOH (Bos taurus)
H+ [mitochondrial matrix]
Sulfur amino acid metabolism (Bos taurus)
Degradation of cysteine and homocysteine (Bos taurus)
Sulfide oxidation to sulfate (Bos taurus)
Persulfide sulfur is dioxygenated (Bos taurus)
H+ [mitochondrial matrix]
Thiosulfate can transfer its sulfur atom to glutathione (Bos taurus)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Bos taurus)
Glucose metabolism (Bos taurus)
Gluconeogenesis (Bos taurus)
PC carboxylates PYR to OA (Bos taurus)
H+ [mitochondrial matrix]
Metabolism of lipids (Bos taurus)
Fatty acid metabolism (Bos taurus)
Fatty acyl-CoA biosynthesis (Bos taurus)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Bos taurus)
H+ [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Bos taurus)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Bos taurus)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Bos taurus)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Bos taurus)
H+ [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Bos taurus)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Bos taurus)
H+ [mitochondrial matrix]
MECR dimer reduces tdec2-CoA to DEC-CoA (Bos taurus)
H+ [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Bos taurus)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Bos taurus)
H+ [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Bos taurus)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Bos taurus)
H+ [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Bos taurus)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Bos taurus)
H+ [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Bos taurus)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Bos taurus)
H+ [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Bos taurus)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Bos taurus)
H+ [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Bos taurus)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Bos taurus)
H+ [mitochondrial matrix]
Ketone body metabolism (Bos taurus)
Synthesis of Ketone Bodies (Bos taurus)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Bos taurus)
H+ [mitochondrial matrix]
Utilization of Ketone Bodies (Bos taurus)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Bos taurus)
H+ [mitochondrial matrix]
Metabolism of steroids (Bos taurus)
Bile acid and bile salt metabolism (Bos taurus)
Synthesis of bile acids and bile salts (Bos taurus)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Bos taurus)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Bos taurus)
H+ [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Bos taurus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Bos taurus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Bos taurus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Bos taurus)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Bos taurus)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Bos taurus)
CYP27A1 27-hydroxylates CHOL (Bos taurus)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Bos taurus)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Bos taurus)
H+ [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Bos taurus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Bos taurus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Bos taurus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Bos taurus)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Bos taurus)
H+ [mitochondrial matrix]
Metabolism of steroid hormones (Bos taurus)
Estrogen biosynthesis (Bos taurus)
AKR1B15 reduces EST17b to E1 (Bos taurus)
H+ [mitochondrial matrix]
Glucocorticoid biosynthesis (Bos taurus)
CYP11B1 oxidises 11DCORT (Bos taurus)
H+ [mitochondrial matrix]
Mineralocorticoid biosynthesis (Bos taurus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Bos taurus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Bos taurus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Bos taurus)
H+ [mitochondrial matrix]
Pregnenolone biosynthesis (Bos taurus)
CYP11A1 cleaves 20a,22b-DHCHOL (Bos taurus)
H+ [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Bos taurus)
H+ [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Bos taurus)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Bos taurus)
Heme biosynthesis (Bos taurus)
ALAS condenses SUCC-CoA and Gly to form dALA (Bos taurus)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Bos taurus)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Bos taurus)
Metabolism of cofactors (Bos taurus)
Ubiquinol biosynthesis (Bos taurus)
COQ3 methylates DHDB (Bos taurus)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Bos taurus)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Bos taurus)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Bos taurus)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Bos taurus)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Bos taurus)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Bos taurus)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Bos taurus)
Cobalamin (Cbl) metabolism (Bos taurus)
MMAB adenosylates cob(I)alamin (Bos taurus)
H+ [mitochondrial matrix]
Metabolism of folate and pterines (Bos taurus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Bos taurus)
H+ [mitochondrial matrix]
Nicotinate metabolism (Bos taurus)
NADK2 dimer phosphorylates NAD+ to NADP+ (Bos taurus)
H+ [mitochondrial matrix]
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Bos taurus)
H+ [mitochondrial matrix]
Nicotinamide salvage (Bos taurus)
CARKD dehydrates S-NAD(P)HX to NADPH (Bos taurus)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Bos taurus)
Electron transport from NADPH to Ferredoxin (Bos taurus)
FDXR transfers electrons to FDX1,2 (FDX1L) (Bos taurus)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Bos taurus)
H+ [mitochondrial matrix]
Reversible hydration of carbon dioxide (Bos taurus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Bos taurus)
H+ [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Bos taurus)
H+ [mitochondrial matrix]
Metabolism of proteins (Bos taurus)
Post-translational protein modification (Bos taurus)
Protein lipoylation (Bos taurus)
LIAS synthesizes lipoyl-GCSH (Bos taurus)
H+ [mitochondrial matrix]
LIPT2 transfers octanoyl group to GCSH (Bos taurus)
H+ [mitochondrial matrix]
Neuronal System (Bos taurus)
Transmission across Chemical Synapses (Bos taurus)
Neurotransmitter clearance (Bos taurus)
Serotonin clearance from the synaptic cleft (Bos taurus)
Metabolism of serotonin (Bos taurus)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Bos taurus)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Bos taurus)
GABA synthesis, release, reuptake and degradation (Bos taurus)
Degradation of GABA (Bos taurus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Bos taurus)
H+ [mitochondrial matrix]
Signal Transduction (Bos taurus)
Signaling by Nuclear Receptors (Bos taurus)
Signaling by Retinoic Acid (Bos taurus)
PDK isozymes phosphorylate PDHC subunit E1 (Bos taurus)
H+ [mitochondrial matrix]
Transport of small molecules (Bos taurus)
Ion channel transport (Bos taurus)
Stimuli-sensing channels (Bos taurus)
SLC9B2 exchanges Na+ for H+ (Bos taurus)
H+ [mitochondrial matrix]
Iron uptake and transport (Bos taurus)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Bos taurus)
H+ [mitochondrial matrix]
SLC-mediated transmembrane transport (Bos taurus)
Transport of inorganic cations/anions and amino acids/oligopeptides (Bos taurus)
Organic anion transporters (Bos taurus)
SLC25A18,22 import L-Glu, H+ (Bos taurus)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Caenorhabditis elegans)
Cellular responses to stress (Caenorhabditis elegans)
Cellular response to chemical stress (Caenorhabditis elegans)
Detoxification of Reactive Oxygen Species (Caenorhabditis elegans)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Caenorhabditis elegans)
H+ [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Metabolism (Caenorhabditis elegans)
Aerobic respiration and respiratory electron transport (Caenorhabditis elegans)
Citric acid cycle (TCA cycle) (Caenorhabditis elegans)
CS acetylates OA to citrate (Caenorhabditis elegans)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Maturation of TCA enzymes and regulation of TCA cycle (Caenorhabditis elegans)
ACAT1 tetramer acetylates IDH2 dimer (Caenorhabditis elegans)
H+ [mitochondrial matrix]
NNT dimer transfers proton from NADPH to NAD+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Caenorhabditis elegans)
DLD dimer dehydrogenates dihydrolipoyl (Caenorhabditis elegans)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Caenorhabditis elegans)
Enzyme-bound ATP is released (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Caenorhabditis elegans)
AAC1 imports a proton (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Pyruvate metabolism (Caenorhabditis elegans)
FAHD1 dimer hydrolyses OA to PYR (Caenorhabditis elegans)
H+ [mitochondrial matrix]
LDHAL6B reduces PYR to LACT (Caenorhabditis elegans)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Caenorhabditis elegans)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Caenorhabditis elegans)
DLD dimer dehydrogenates dihydrolipoyl (Caenorhabditis elegans)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Caenorhabditis elegans)
Regulation of pyruvate dehydrogenase (PDH) complex (Caenorhabditis elegans)
GSTZ1 dimer dehalogenates DCA (Caenorhabditis elegans)
H+ [mitochondrial matrix]
PDK isozymes phosphorylate PDHC subunit E1 (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Respiratory electron transport (Caenorhabditis elegans)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Electron transfer from ubiquinol to cytochrome c of complex III (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Caenorhabditis elegans)
MDH2 dimer dehydrogenates MAL (Caenorhabditis elegans)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Caenorhabditis elegans)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Biological oxidations (Caenorhabditis elegans)
Phase I - Functionalization of compounds (Caenorhabditis elegans)
Ethanol oxidation (Caenorhabditis elegans)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Caenorhabditis elegans)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Caenorhabditis elegans)
Aspartate and asparagine metabolism (Caenorhabditis elegans)
SLC25A12,13 exchange L-Glu and L-Asp (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Caenorhabditis elegans)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Caenorhabditis elegans)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Caenorhabditis elegans)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Caenorhabditis elegans)
H+ [mitochondrial matrix]
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Caenorhabditis elegans)
H+ [mitochondrial matrix]
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Caenorhabditis elegans)
H+ [mitochondrial matrix]
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Caenorhabditis elegans)
H+ [mitochondrial matrix]
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Caenorhabditis elegans)
H+ [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Caenorhabditis elegans)
H+ [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Caenorhabditis elegans)
H+ [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Caenorhabditis elegans)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Caenorhabditis elegans)
H+ [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Caenorhabditis elegans)
H+ [mitochondrial matrix]
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Caenorhabditis elegans)
H+ [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Caenorhabditis elegans)
Glycine degradation (Caenorhabditis elegans)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Caenorhabditis elegans)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Caenorhabditis elegans)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Lysine catabolism (Caenorhabditis elegans)
OADH complex synthesizes glutaryl-CoA from 2-OA (Caenorhabditis elegans)
DHTKD1 dimer decarboxylates 2-OA (Caenorhabditis elegans)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Caenorhabditis elegans)
H+ [mitochondrial matrix]
DLST transfers glutaryl to CoA (Caenorhabditis elegans)
H+ [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Caenorhabditis elegans)
H+ [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Caenorhabditis elegans)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Proline catabolism (Caenorhabditis elegans)
PRODH oxidises L-Pro to 1PYR-5COOH (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Sulfur amino acid metabolism (Caenorhabditis elegans)
Degradation of cysteine and homocysteine (Caenorhabditis elegans)
Sulfide oxidation to sulfate (Caenorhabditis elegans)
Persulfide sulfur is dioxygenated (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Caenorhabditis elegans)
Glucose metabolism (Caenorhabditis elegans)
Gluconeogenesis (Caenorhabditis elegans)
PC carboxylates PYR to OA (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Metabolism of lipids (Caenorhabditis elegans)
Fatty acid metabolism (Caenorhabditis elegans)
Mitochondrial Fatty Acid Beta-Oxidation (Caenorhabditis elegans)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Caenorhabditis elegans)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Caenorhabditis elegans)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Caenorhabditis elegans)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Caenorhabditis elegans)
H+ [mitochondrial matrix]
MECR dimer reduces tdec2-CoA to DEC-CoA (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Caenorhabditis elegans)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Caenorhabditis elegans)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Caenorhabditis elegans)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Caenorhabditis elegans)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Caenorhabditis elegans)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Caenorhabditis elegans)
H+ [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Caenorhabditis elegans)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Metabolism of steroids (Caenorhabditis elegans)
Metabolism of steroid hormones (Caenorhabditis elegans)
Estrogen biosynthesis (Caenorhabditis elegans)
AKR1B15 reduces EST17b to E1 (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Caenorhabditis elegans)
Heme biosynthesis (Caenorhabditis elegans)
FECH binds Fe2+ to PRIN9 to form heme (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Caenorhabditis elegans)
Metabolism of cofactors (Caenorhabditis elegans)
Ubiquinol biosynthesis (Caenorhabditis elegans)
COQ3 methylates DHDB (Caenorhabditis elegans)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Caenorhabditis elegans)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Caenorhabditis elegans)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Caenorhabditis elegans)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Caenorhabditis elegans)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Caenorhabditis elegans)
Cobalamin (Cbl) metabolism (Caenorhabditis elegans)
MMAB adenosylates cob(I)alamin (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Metabolism of folate and pterines (Caenorhabditis elegans)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Nicotinate metabolism (Caenorhabditis elegans)
NADK2 dimer phosphorylates NAD+ to NADP+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Nicotinamide salvage (Caenorhabditis elegans)
CARKD dehydrates S-NAD(P)HX to NADPH (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Caenorhabditis elegans)
Electron transport from NADPH to Ferredoxin (Caenorhabditis elegans)
FDXR transfers electrons to FDX1,2 (FDX1L) (Caenorhabditis elegans)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Reversible hydration of carbon dioxide (Caenorhabditis elegans)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Metabolism of proteins (Caenorhabditis elegans)
Post-translational protein modification (Caenorhabditis elegans)
Protein lipoylation (Caenorhabditis elegans)
LIPT2 transfers octanoyl group to GCSH (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Neuronal System (Caenorhabditis elegans)
Transmission across Chemical Synapses (Caenorhabditis elegans)
Neurotransmitter clearance (Caenorhabditis elegans)
Serotonin clearance from the synaptic cleft (Caenorhabditis elegans)
Metabolism of serotonin (Caenorhabditis elegans)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Caenorhabditis elegans)
GABA synthesis, release, reuptake and degradation (Caenorhabditis elegans)
Degradation of GABA (Caenorhabditis elegans)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Signal Transduction (Caenorhabditis elegans)
Signaling by Nuclear Receptors (Caenorhabditis elegans)
Signaling by Retinoic Acid (Caenorhabditis elegans)
PDK isozymes phosphorylate PDHC subunit E1 (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Transport of small molecules (Caenorhabditis elegans)
Ion channel transport (Caenorhabditis elegans)
Stimuli-sensing channels (Caenorhabditis elegans)
SLC9B2 exchanges Na+ for H+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Iron uptake and transport (Caenorhabditis elegans)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Caenorhabditis elegans)
H+ [mitochondrial matrix]
SLC-mediated transmembrane transport (Caenorhabditis elegans)
Transport of inorganic cations/anions and amino acids/oligopeptides (Caenorhabditis elegans)
Organic anion transporters (Caenorhabditis elegans)
SLC25A18,22 import L-Glu, H+ (Caenorhabditis elegans)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Canis familiaris)
Cellular responses to stress (Canis familiaris)
Cellular response to chemical stress (Canis familiaris)
Cytoprotection by HMOX1 (Canis familiaris)
Electron transfer from reduced cytochrome c to molecular oxygen (Canis familiaris)
H+ [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Canis familiaris)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Canis familiaris)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Canis familiaris)
H+ [mitochondrial matrix]
Gene expression (Transcription) (Canis familiaris)
RNA Polymerase II Transcription (Canis familiaris)
Generic Transcription Pathway (Canis familiaris)
Transcriptional Regulation by TP53 (Canis familiaris)
TP53 Regulates Metabolic Genes (Canis familiaris)
Electron transfer from reduced cytochrome c to molecular oxygen (Canis familiaris)
H+ [mitochondrial matrix]
Metabolism (Canis familiaris)
Aerobic respiration and respiratory electron transport (Canis familiaris)
Citric acid cycle (TCA cycle) (Canis familiaris)
CS acetylates OA to citrate (Canis familiaris)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Canis familiaris)
H+ [mitochondrial matrix]
Maturation of TCA enzymes and regulation of TCA cycle (Canis familiaris)
ACAT1 tetramer acetylates IDH2 dimer (Canis familiaris)
H+ [mitochondrial matrix]
CSKMT methylates Citrate Synthase (Canis familiaris)
H+ [mitochondrial matrix]
NNT dimer transfers proton from NADPH to NAD+ (Canis familiaris)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Canis familiaris)
DLD dimer dehydrogenates dihydrolipoyl (Canis familiaris)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Canis familiaris)
H+ [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Canis familiaris)
Enzyme-bound ATP is released (Canis familiaris)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Canis familiaris)
AAC1 imports a proton (Canis familiaris)
H+ [mitochondrial matrix]
UCP1 imports a proton (Canis familiaris)
H+ [mitochondrial matrix]
Pyruvate metabolism (Canis familiaris)
FAHD1 dimer hydrolyses OA to PYR (Canis familiaris)
H+ [mitochondrial matrix]
LDHAL6B reduces PYR to LACT (Canis familiaris)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Canis familiaris)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Canis familiaris)
DLD dimer dehydrogenates dihydrolipoyl (Canis familiaris)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Canis familiaris)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Canis familiaris)
Regulation of pyruvate dehydrogenase (PDH) complex (Canis familiaris)
GSTZ1 dimer dehalogenates DCA (Canis familiaris)
H+ [mitochondrial matrix]
PDK isozymes phosphorylate PDHC subunit E1 (Canis familiaris)
H+ [mitochondrial matrix]
Respiratory electron transport (Canis familiaris)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Canis familiaris)
H+ [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Canis familiaris)
H+ [mitochondrial matrix]
Electron transfer from reduced cytochrome c to molecular oxygen (Canis familiaris)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Canis familiaris)
MDH2 dimer dehydrogenates MAL (Canis familiaris)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Canis familiaris)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Canis familiaris)
H+ [mitochondrial matrix]
Biological oxidations (Canis familiaris)
Phase I - Functionalization of compounds (Canis familiaris)
Cytochrome P450 - arranged by substrate type (Canis familiaris)
Endogenous sterols (Canis familiaris)
CYP11A1 cleaves 20a,22b-DHCHOL (Canis familiaris)
H+ [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Canis familiaris)
H+ [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Canis familiaris)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Canis familiaris)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Canis familiaris)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Canis familiaris)
H+ [mitochondrial matrix]
Vitamins (Canis familiaris)
CYP24A1 24-hydroxylates CTL (Canis familiaris)
H+ [mitochondrial matrix]
Ethanol oxidation (Canis familiaris)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Canis familiaris)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Canis familiaris)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Canis familiaris)
Aspartate and asparagine metabolism (Canis familiaris)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Canis familiaris)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Canis familiaris)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Canis familiaris)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Canis familiaris)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Canis familiaris)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Canis familiaris)
H+ [mitochondrial matrix]
BCKDK phosphorylates BCKDH (Canis familiaris)
H+ [mitochondrial matrix]
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Canis familiaris)
H+ [mitochondrial matrix]
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Canis familiaris)
H+ [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Canis familiaris)
H+ [mitochondrial matrix]
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Canis familiaris)
H+ [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Canis familiaris)
H+ [mitochondrial matrix]
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Canis familiaris)
H+ [mitochondrial matrix]
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Canis familiaris)
H+ [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Canis familiaris)
H+ [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Canis familiaris)
H+ [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Canis familiaris)
H+ [mitochondrial matrix]
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Canis familiaris)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Canis familiaris)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Canis familiaris)
H+ [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Canis familiaris)
H+ [mitochondrial matrix]
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Canis familiaris)
H+ [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Canis familiaris)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Canis familiaris)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Canis familiaris)
H+ [mitochondrial matrix]
Glycine degradation (Canis familiaris)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Canis familiaris)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Canis familiaris)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Canis familiaris)
H+ [mitochondrial matrix]
Lysine catabolism (Canis familiaris)
HYKK phosphorylates 5HLYS (Canis familiaris)
H+ [mitochondrial matrix]
OADH complex synthesizes glutaryl-CoA from 2-OA (Canis familiaris)
DHTKD1 dimer decarboxylates 2-OA (Canis familiaris)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Canis familiaris)
H+ [mitochondrial matrix]
DLST transfers glutaryl to CoA (Canis familiaris)
H+ [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Canis familiaris)
H+ [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Canis familiaris)
H+ [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Canis familiaris)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Canis familiaris)
H+ [mitochondrial matrix]
Proline catabolism (Canis familiaris)
ALDH4A1 oxidises L-GluSS to Glu (Canis familiaris)
H+ [mitochondrial matrix]
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Canis familiaris)
H+ [mitochondrial matrix]
PRODH oxidises L-Pro to 1PYR-5COOH (Canis familiaris)
H+ [mitochondrial matrix]
Sulfur amino acid metabolism (Canis familiaris)
Degradation of cysteine and homocysteine (Canis familiaris)
Sulfide oxidation to sulfate (Canis familiaris)
Persulfide sulfur is dioxygenated (Canis familiaris)
H+ [mitochondrial matrix]
Thiosulfate can transfer its sulfur atom to glutathione (Canis familiaris)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Canis familiaris)
Glucose metabolism (Canis familiaris)
Gluconeogenesis (Canis familiaris)
PC carboxylates PYR to OA (Canis familiaris)
H+ [mitochondrial matrix]
Metabolism of lipids (Canis familiaris)
Fatty acid metabolism (Canis familiaris)
Fatty acyl-CoA biosynthesis (Canis familiaris)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Canis familiaris)
H+ [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Canis familiaris)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Canis familiaris)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Canis familiaris)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Canis familiaris)
H+ [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Canis familiaris)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Canis familiaris)
H+ [mitochondrial matrix]
MECR dimer reduces tdec2-CoA to DEC-CoA (Canis familiaris)
H+ [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Canis familiaris)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Canis familiaris)
H+ [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Canis familiaris)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Canis familiaris)
H+ [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Canis familiaris)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Canis familiaris)
H+ [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Canis familiaris)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Canis familiaris)
H+ [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Canis familiaris)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Canis familiaris)
H+ [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Canis familiaris)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Canis familiaris)
H+ [mitochondrial matrix]
Ketone body metabolism (Canis familiaris)
Synthesis of Ketone Bodies (Canis familiaris)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Canis familiaris)
H+ [mitochondrial matrix]
Utilization of Ketone Bodies (Canis familiaris)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Canis familiaris)
H+ [mitochondrial matrix]
Metabolism of steroids (Canis familiaris)
Bile acid and bile salt metabolism (Canis familiaris)
Synthesis of bile acids and bile salts (Canis familiaris)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Canis familiaris)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Canis familiaris)
H+ [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Canis familiaris)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Canis familiaris)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Canis familiaris)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Canis familiaris)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Canis familiaris)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Canis familiaris)
CYP27A1 27-hydroxylates CHOL (Canis familiaris)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Canis familiaris)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Canis familiaris)
H+ [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Canis familiaris)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Canis familiaris)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Canis familiaris)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Canis familiaris)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Canis familiaris)
H+ [mitochondrial matrix]
Metabolism of steroid hormones (Canis familiaris)
Glucocorticoid biosynthesis (Canis familiaris)
CYP11B1 oxidises 11DCORT (Canis familiaris)
H+ [mitochondrial matrix]
Mineralocorticoid biosynthesis (Canis familiaris)
CYP11B2 18-hydroxylates CORST to 18HCORST (Canis familiaris)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Canis familiaris)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Canis familiaris)
H+ [mitochondrial matrix]
Pregnenolone biosynthesis (Canis familiaris)
CYP11A1 cleaves 20a,22b-DHCHOL (Canis familiaris)
H+ [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Canis familiaris)
H+ [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Canis familiaris)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Canis familiaris)
Heme biosynthesis (Canis familiaris)
ALAS condenses SUCC-CoA and Gly to form dALA (Canis familiaris)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Canis familiaris)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Canis familiaris)
Metabolism of cofactors (Canis familiaris)
Ubiquinol biosynthesis (Canis familiaris)
COQ3 methylates DHDB (Canis familiaris)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Canis familiaris)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Canis familiaris)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Canis familiaris)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Canis familiaris)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Canis familiaris)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Canis familiaris)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Canis familiaris)
Cobalamin (Cbl) metabolism (Canis familiaris)
MMAB adenosylates cob(I)alamin (Canis familiaris)
H+ [mitochondrial matrix]
Metabolism of folate and pterines (Canis familiaris)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Canis familiaris)
H+ [mitochondrial matrix]
Nicotinate metabolism (Canis familiaris)
NADK2 dimer phosphorylates NAD+ to NADP+ (Canis familiaris)
H+ [mitochondrial matrix]
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Canis familiaris)
H+ [mitochondrial matrix]
Nicotinamide salvage (Canis familiaris)
CARKD dehydrates S-NAD(P)HX to NADPH (Canis familiaris)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Canis familiaris)
Electron transport from NADPH to Ferredoxin (Canis familiaris)
FDXR transfers electrons to FDX1,2 (FDX1L) (Canis familiaris)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Canis familiaris)
H+ [mitochondrial matrix]
Reversible hydration of carbon dioxide (Canis familiaris)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Canis familiaris)
H+ [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Canis familiaris)
H+ [mitochondrial matrix]
Metabolism of proteins (Canis familiaris)
Post-translational protein modification (Canis familiaris)
Protein lipoylation (Canis familiaris)
LIAS synthesizes lipoyl-GCSH (Canis familiaris)
H+ [mitochondrial matrix]
LIPT2 transfers octanoyl group to GCSH (Canis familiaris)
H+ [mitochondrial matrix]
Neuronal System (Canis familiaris)
Transmission across Chemical Synapses (Canis familiaris)
Neurotransmitter clearance (Canis familiaris)
Serotonin clearance from the synaptic cleft (Canis familiaris)
Metabolism of serotonin (Canis familiaris)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Canis familiaris)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Canis familiaris)
GABA synthesis, release, reuptake and degradation (Canis familiaris)
Degradation of GABA (Canis familiaris)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Canis familiaris)
H+ [mitochondrial matrix]
Signal Transduction (Canis familiaris)
Signaling by Nuclear Receptors (Canis familiaris)
Signaling by Retinoic Acid (Canis familiaris)
PDK isozymes phosphorylate PDHC subunit E1 (Canis familiaris)
H+ [mitochondrial matrix]
Transport of small molecules (Canis familiaris)
Ion channel transport (Canis familiaris)
Stimuli-sensing channels (Canis familiaris)
SLC9B2 exchanges Na+ for H+ (Canis familiaris)
H+ [mitochondrial matrix]
Iron uptake and transport (Canis familiaris)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Canis familiaris)
H+ [mitochondrial matrix]
SLC-mediated transmembrane transport (Canis familiaris)
Transport of inorganic cations/anions and amino acids/oligopeptides (Canis familiaris)
Organic anion transporters (Canis familiaris)
SLC25A18,22 import L-Glu, H+ (Canis familiaris)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Danio rerio)
Cellular responses to stress (Danio rerio)
Cellular response to chemical stress (Danio rerio)
Cytoprotection by HMOX1 (Danio rerio)
Electron transfer from reduced cytochrome c to molecular oxygen (Danio rerio)
H+ [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Danio rerio)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Danio rerio)
H+ [mitochondrial matrix]
Gene expression (Transcription) (Danio rerio)
RNA Polymerase II Transcription (Danio rerio)
Generic Transcription Pathway (Danio rerio)
Transcriptional Regulation by TP53 (Danio rerio)
TP53 Regulates Metabolic Genes (Danio rerio)
Electron transfer from reduced cytochrome c to molecular oxygen (Danio rerio)
H+ [mitochondrial matrix]
Metabolism (Danio rerio)
Aerobic respiration and respiratory electron transport (Danio rerio)
Citric acid cycle (TCA cycle) (Danio rerio)
CS acetylates OA to citrate (Danio rerio)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Danio rerio)
H+ [mitochondrial matrix]
Maturation of TCA enzymes and regulation of TCA cycle (Danio rerio)
ACAT1 tetramer acetylates IDH2 dimer (Danio rerio)
H+ [mitochondrial matrix]
CSKMT methylates Citrate Synthase (Danio rerio)
H+ [mitochondrial matrix]
NNT dimer transfers proton from NADPH to NAD+ (Danio rerio)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Danio rerio)
DLD dimer dehydrogenates dihydrolipoyl (Danio rerio)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Danio rerio)
H+ [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Danio rerio)
Enzyme-bound ATP is released (Danio rerio)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Danio rerio)
AAC1 imports a proton (Danio rerio)
H+ [mitochondrial matrix]
UCP1 imports a proton (Danio rerio)
H+ [mitochondrial matrix]
Pyruvate metabolism (Danio rerio)
FAHD1 dimer hydrolyses OA to PYR (Danio rerio)
H+ [mitochondrial matrix]
LDHAL6B reduces PYR to LACT (Danio rerio)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Danio rerio)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Danio rerio)
Regulation of pyruvate dehydrogenase (PDH) complex (Danio rerio)
GSTZ1 dimer dehalogenates DCA (Danio rerio)
H+ [mitochondrial matrix]
Respiratory electron transport (Danio rerio)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Danio rerio)
H+ [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Danio rerio)
H+ [mitochondrial matrix]
Electron transfer from reduced cytochrome c to molecular oxygen (Danio rerio)
H+ [mitochondrial matrix]
Electron transfer from ubiquinol to cytochrome c of complex III (Danio rerio)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Danio rerio)
MDH2 dimer dehydrogenates MAL (Danio rerio)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Danio rerio)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Danio rerio)
H+ [mitochondrial matrix]
Biological oxidations (Danio rerio)
Phase I - Functionalization of compounds (Danio rerio)
Cytochrome P450 - arranged by substrate type (Danio rerio)
Endogenous sterols (Danio rerio)
CYP11A1 cleaves 20a,22b-DHCHOL (Danio rerio)
H+ [mitochondrial matrix]
Vitamins (Danio rerio)
CYP24A1 24-hydroxylates CTL (Danio rerio)
H+ [mitochondrial matrix]
Ethanol oxidation (Danio rerio)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Danio rerio)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Danio rerio)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Danio rerio)
Aspartate and asparagine metabolism (Danio rerio)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Danio rerio)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Danio rerio)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Danio rerio)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Danio rerio)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Danio rerio)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Danio rerio)
H+ [mitochondrial matrix]
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Danio rerio)
H+ [mitochondrial matrix]
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Danio rerio)
H+ [mitochondrial matrix]
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Danio rerio)
H+ [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Danio rerio)
H+ [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Danio rerio)
H+ [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Danio rerio)
H+ [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Danio rerio)
H+ [mitochondrial matrix]
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Danio rerio)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Danio rerio)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Danio rerio)
H+ [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Danio rerio)
H+ [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Danio rerio)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Danio rerio)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Danio rerio)
H+ [mitochondrial matrix]
Glycine degradation (Danio rerio)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Danio rerio)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Danio rerio)
H+ [mitochondrial matrix]
Lysine catabolism (Danio rerio)
HYKK phosphorylates 5HLYS (Danio rerio)
H+ [mitochondrial matrix]
OADH complex synthesizes glutaryl-CoA from 2-OA (Danio rerio)
DHTKD1 dimer decarboxylates 2-OA (Danio rerio)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Danio rerio)
H+ [mitochondrial matrix]
DLST transfers glutaryl to CoA (Danio rerio)
H+ [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Danio rerio)
H+ [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Danio rerio)
H+ [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Danio rerio)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Danio rerio)
H+ [mitochondrial matrix]
Proline catabolism (Danio rerio)
ALDH4A1 oxidises L-GluSS to Glu (Danio rerio)
H+ [mitochondrial matrix]
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Danio rerio)
H+ [mitochondrial matrix]
Sulfur amino acid metabolism (Danio rerio)
Degradation of cysteine and homocysteine (Danio rerio)
Sulfide oxidation to sulfate (Danio rerio)
Persulfide sulfur is dioxygenated (Danio rerio)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Danio rerio)
Glucose metabolism (Danio rerio)
Gluconeogenesis (Danio rerio)
PC carboxylates PYR to OA (Danio rerio)
H+ [mitochondrial matrix]
Metabolism of lipids (Danio rerio)
Fatty acid metabolism (Danio rerio)
Fatty acyl-CoA biosynthesis (Danio rerio)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Danio rerio)
H+ [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Danio rerio)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Danio rerio)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Danio rerio)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Danio rerio)
H+ [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Danio rerio)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Danio rerio)
H+ [mitochondrial matrix]
MECR dimer reduces tdec2-CoA to DEC-CoA (Danio rerio)
H+ [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Danio rerio)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Danio rerio)
H+ [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Danio rerio)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Danio rerio)
H+ [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Danio rerio)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Danio rerio)
H+ [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Danio rerio)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Danio rerio)
H+ [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Danio rerio)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Danio rerio)
H+ [mitochondrial matrix]
Ketone body metabolism (Danio rerio)
Synthesis of Ketone Bodies (Danio rerio)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Danio rerio)
H+ [mitochondrial matrix]
Utilization of Ketone Bodies (Danio rerio)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Danio rerio)
H+ [mitochondrial matrix]
Metabolism of steroids (Danio rerio)
Metabolism of steroid hormones (Danio rerio)
Estrogen biosynthesis (Danio rerio)
AKR1B15 reduces EST17b to E1 (Danio rerio)
H+ [mitochondrial matrix]
Pregnenolone biosynthesis (Danio rerio)
CYP11A1 cleaves 20a,22b-DHCHOL (Danio rerio)
H+ [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Danio rerio)
H+ [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Danio rerio)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Danio rerio)
Heme biosynthesis (Danio rerio)
ALAS condenses SUCC-CoA and Gly to form dALA (Danio rerio)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Danio rerio)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Danio rerio)
Metabolism of cofactors (Danio rerio)
Ubiquinol biosynthesis (Danio rerio)
COQ3 methylates DHDB (Danio rerio)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Danio rerio)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Danio rerio)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Danio rerio)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Danio rerio)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Danio rerio)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Danio rerio)
Nicotinate metabolism (Danio rerio)
Nicotinamide salvage (Danio rerio)
CARKD dehydrates S-NAD(P)HX to NADPH (Danio rerio)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Danio rerio)
Electron transport from NADPH to Ferredoxin (Danio rerio)
FDXR transfers electrons to FDX1,2 (FDX1L) (Danio rerio)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Danio rerio)
H+ [mitochondrial matrix]
Reversible hydration of carbon dioxide (Danio rerio)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Danio rerio)
H+ [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Danio rerio)
H+ [mitochondrial matrix]
Metabolism of proteins (Danio rerio)
Post-translational protein modification (Danio rerio)
Protein lipoylation (Danio rerio)
LIAS synthesizes lipoyl-GCSH (Danio rerio)
H+ [mitochondrial matrix]
LIPT2 transfers octanoyl group to GCSH (Danio rerio)
H+ [mitochondrial matrix]
Neuronal System (Danio rerio)
Transmission across Chemical Synapses (Danio rerio)
Neurotransmitter clearance (Danio rerio)
Serotonin clearance from the synaptic cleft (Danio rerio)
Metabolism of serotonin (Danio rerio)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Danio rerio)
H+ [mitochondrial matrix]
Transport of small molecules (Danio rerio)
Iron uptake and transport (Danio rerio)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Danio rerio)
H+ [mitochondrial matrix]
SLC-mediated transmembrane transport (Danio rerio)
Transport of inorganic cations/anions and amino acids/oligopeptides (Danio rerio)
Organic anion transporters (Danio rerio)
SLC25A18,22 import L-Glu, H+ (Danio rerio)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Dictyostelium discoideum)
Cellular responses to stress (Dictyostelium discoideum)
Cellular response to chemical stress (Dictyostelium discoideum)
Detoxification of Reactive Oxygen Species (Dictyostelium discoideum)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Dictyostelium discoideum)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Metabolism (Dictyostelium discoideum)
Aerobic respiration and respiratory electron transport (Dictyostelium discoideum)
Citric acid cycle (TCA cycle) (Dictyostelium discoideum)
CS acetylates OA to citrate (Dictyostelium discoideum)
H+ [mitochondrial matrix]
NNT dimer transfers proton from NADPH to NAD+ (Dictyostelium discoideum)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Dictyostelium discoideum)
DLD dimer dehydrogenates dihydrolipoyl (Dictyostelium discoideum)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Dictyostelium discoideum)
AAC1 imports a proton (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Pyruvate metabolism (Dictyostelium discoideum)
FAHD1 dimer hydrolyses OA to PYR (Dictyostelium discoideum)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Dictyostelium discoideum)
DLD dimer dehydrogenates dihydrolipoyl (Dictyostelium discoideum)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Dictyostelium discoideum)
Regulation of pyruvate dehydrogenase (PDH) complex (Dictyostelium discoideum)
GSTZ1 dimer dehalogenates DCA (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Respiratory electron transport (Dictyostelium discoideum)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Electron transfer from ubiquinol to cytochrome c of complex III (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Dictyostelium discoideum)
SLC25A12,13 exchange L-Glu and L-Asp (Dictyostelium discoideum)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Biological oxidations (Dictyostelium discoideum)
Phase I - Functionalization of compounds (Dictyostelium discoideum)
Ethanol oxidation (Dictyostelium discoideum)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Dictyostelium discoideum)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Dictyostelium discoideum)
Aspartate and asparagine metabolism (Dictyostelium discoideum)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Dictyostelium discoideum)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Dictyostelium discoideum)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Dictyostelium discoideum)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Dictyostelium discoideum)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Dictyostelium discoideum)
H+ [mitochondrial matrix]
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Dictyostelium discoideum)
H+ [mitochondrial matrix]
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Dictyostelium discoideum)
H+ [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Dictyostelium discoideum)
H+ [mitochondrial matrix]
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Dictyostelium discoideum)
H+ [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Dictyostelium discoideum)
H+ [mitochondrial matrix]
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Dictyostelium discoideum)
H+ [mitochondrial matrix]
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Dictyostelium discoideum)
H+ [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Dictyostelium discoideum)
H+ [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Dictyostelium discoideum)
H+ [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Dictyostelium discoideum)
H+ [mitochondrial matrix]
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Dictyostelium discoideum)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Dictyostelium discoideum)
H+ [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Dictyostelium discoideum)
H+ [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Dictyostelium discoideum)
Glycine degradation (Dictyostelium discoideum)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Dictyostelium discoideum)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Dictyostelium discoideum)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Lysine catabolism (Dictyostelium discoideum)
OADH complex synthesizes glutaryl-CoA from 2-OA (Dictyostelium discoideum)
DHTKD1 dimer decarboxylates 2-OA (Dictyostelium discoideum)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Dictyostelium discoideum)
H+ [mitochondrial matrix]
DLST transfers glutaryl to CoA (Dictyostelium discoideum)
H+ [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Dictyostelium discoideum)
H+ [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Dictyostelium discoideum)
H+ [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Dictyostelium discoideum)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Proline catabolism (Dictyostelium discoideum)
PRODH oxidises L-Pro to 1PYR-5COOH (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Metabolism of lipids (Dictyostelium discoideum)
Fatty acid metabolism (Dictyostelium discoideum)
Fatty acyl-CoA biosynthesis (Dictyostelium discoideum)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Dictyostelium discoideum)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Dictyostelium discoideum)
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Dictyostelium discoideum)
MECR dimer reduces tdec2-CoA to DEC-CoA (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Metabolism of steroids (Dictyostelium discoideum)
Metabolism of steroid hormones (Dictyostelium discoideum)
Estrogen biosynthesis (Dictyostelium discoideum)
AKR1B15 reduces EST17b to E1 (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Dictyostelium discoideum)
Heme biosynthesis (Dictyostelium discoideum)
ALAS condenses SUCC-CoA and Gly to form dALA (Dictyostelium discoideum)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Dictyostelium discoideum)
Metabolism of cofactors (Dictyostelium discoideum)
Ubiquinol biosynthesis (Dictyostelium discoideum)
COQ3 methylates DHDB (Dictyostelium discoideum)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Dictyostelium discoideum)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Dictyostelium discoideum)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Dictyostelium discoideum)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Dictyostelium discoideum)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Dictyostelium discoideum)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Dictyostelium discoideum)
Cobalamin (Cbl) metabolism (Dictyostelium discoideum)
MMAB adenosylates cob(I)alamin (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Nicotinate metabolism (Dictyostelium discoideum)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Nicotinamide salvage (Dictyostelium discoideum)
CARKD dehydrates S-NAD(P)HX to NADPH (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Dictyostelium discoideum)
Electron transport from NADPH to Ferredoxin (Dictyostelium discoideum)
FDXR transfers electrons to FDX1,2 (FDX1L) (Dictyostelium discoideum)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Metabolism of proteins (Dictyostelium discoideum)
Post-translational protein modification (Dictyostelium discoideum)
Protein lipoylation (Dictyostelium discoideum)
LIPT2 transfers octanoyl group to GCSH (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Neuronal System (Dictyostelium discoideum)
Transmission across Chemical Synapses (Dictyostelium discoideum)
Neurotransmitter clearance (Dictyostelium discoideum)
Serotonin clearance from the synaptic cleft (Dictyostelium discoideum)
Metabolism of serotonin (Dictyostelium discoideum)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Transport of small molecules (Dictyostelium discoideum)
SLC-mediated transmembrane transport (Dictyostelium discoideum)
Transport of inorganic cations/anions and amino acids/oligopeptides (Dictyostelium discoideum)
Organic anion transporters (Dictyostelium discoideum)
SLC25A18,22 import L-Glu, H+ (Dictyostelium discoideum)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Drosophila melanogaster)
Cellular responses to stress (Drosophila melanogaster)
Cellular response to chemical stress (Drosophila melanogaster)
Cytoprotection by HMOX1 (Drosophila melanogaster)
Electron transfer from reduced cytochrome c to molecular oxygen (Drosophila melanogaster)
H+ [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Drosophila melanogaster)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Drosophila melanogaster)
H+ [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Drosophila melanogaster)
H+ [mitochondrial matrix]
Gene expression (Transcription) (Drosophila melanogaster)
RNA Polymerase II Transcription (Drosophila melanogaster)
Generic Transcription Pathway (Drosophila melanogaster)
Transcriptional Regulation by TP53 (Drosophila melanogaster)
TP53 Regulates Metabolic Genes (Drosophila melanogaster)
Electron transfer from reduced cytochrome c to molecular oxygen (Drosophila melanogaster)
H+ [mitochondrial matrix]
Metabolism (Drosophila melanogaster)
Aerobic respiration and respiratory electron transport (Drosophila melanogaster)
Citric acid cycle (TCA cycle) (Drosophila melanogaster)
CS acetylates OA to citrate (Drosophila melanogaster)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Drosophila melanogaster)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Drosophila melanogaster)
DLD dimer dehydrogenates dihydrolipoyl (Drosophila melanogaster)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Drosophila melanogaster)
H+ [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Drosophila melanogaster)
Enzyme-bound ATP is released (Drosophila melanogaster)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Drosophila melanogaster)
AAC1 imports a proton (Drosophila melanogaster)
H+ [mitochondrial matrix]
Pyruvate metabolism (Drosophila melanogaster)
FAHD1 dimer hydrolyses OA to PYR (Drosophila melanogaster)
H+ [mitochondrial matrix]
LDHAL6B reduces PYR to LACT (Drosophila melanogaster)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Drosophila melanogaster)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Drosophila melanogaster)
DLD dimer dehydrogenates dihydrolipoyl (Drosophila melanogaster)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Drosophila melanogaster)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Drosophila melanogaster)
Regulation of pyruvate dehydrogenase (PDH) complex (Drosophila melanogaster)
GSTZ1 dimer dehalogenates DCA (Drosophila melanogaster)
H+ [mitochondrial matrix]
PDK isozymes phosphorylate PDHC subunit E1 (Drosophila melanogaster)
H+ [mitochondrial matrix]
Respiratory electron transport (Drosophila melanogaster)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Drosophila melanogaster)
H+ [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Drosophila melanogaster)
H+ [mitochondrial matrix]
Electron transfer from reduced cytochrome c to molecular oxygen (Drosophila melanogaster)
H+ [mitochondrial matrix]
Electron transfer from ubiquinol to cytochrome c of complex III (Drosophila melanogaster)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Drosophila melanogaster)
MDH2 dimer dehydrogenates MAL (Drosophila melanogaster)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Drosophila melanogaster)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
Biological oxidations (Drosophila melanogaster)
Phase I - Functionalization of compounds (Drosophila melanogaster)
Ethanol oxidation (Drosophila melanogaster)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Drosophila melanogaster)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Drosophila melanogaster)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Drosophila melanogaster)
Aspartate and asparagine metabolism (Drosophila melanogaster)
SLC25A12,13 exchange L-Glu and L-Asp (Drosophila melanogaster)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Drosophila melanogaster)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Drosophila melanogaster)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Drosophila melanogaster)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Drosophila melanogaster)
H+ [mitochondrial matrix]
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Drosophila melanogaster)
H+ [mitochondrial matrix]
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Drosophila melanogaster)
H+ [mitochondrial matrix]
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Drosophila melanogaster)
H+ [mitochondrial matrix]
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Drosophila melanogaster)
H+ [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Drosophila melanogaster)
H+ [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Drosophila melanogaster)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Drosophila melanogaster)
H+ [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Drosophila melanogaster)
H+ [mitochondrial matrix]
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Drosophila melanogaster)
H+ [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Drosophila melanogaster)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Drosophila melanogaster)
Glycine degradation (Drosophila melanogaster)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Drosophila melanogaster)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Drosophila melanogaster)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Drosophila melanogaster)
H+ [mitochondrial matrix]
Lysine catabolism (Drosophila melanogaster)
HYKK phosphorylates 5HLYS (Drosophila melanogaster)
H+ [mitochondrial matrix]
OADH complex synthesizes glutaryl-CoA from 2-OA (Drosophila melanogaster)
DHTKD1 dimer decarboxylates 2-OA (Drosophila melanogaster)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Drosophila melanogaster)
H+ [mitochondrial matrix]
DLST transfers glutaryl to CoA (Drosophila melanogaster)
H+ [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Drosophila melanogaster)
H+ [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Drosophila melanogaster)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
Proline catabolism (Drosophila melanogaster)
PRODH oxidises L-Pro to 1PYR-5COOH (Drosophila melanogaster)
H+ [mitochondrial matrix]
Sulfur amino acid metabolism (Drosophila melanogaster)
Degradation of cysteine and homocysteine (Drosophila melanogaster)
Sulfide oxidation to sulfate (Drosophila melanogaster)
Persulfide sulfur is dioxygenated (Drosophila melanogaster)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Drosophila melanogaster)
Glucose metabolism (Drosophila melanogaster)
Gluconeogenesis (Drosophila melanogaster)
PC carboxylates PYR to OA (Drosophila melanogaster)
H+ [mitochondrial matrix]
Metabolism of lipids (Drosophila melanogaster)
Fatty acid metabolism (Drosophila melanogaster)
Mitochondrial Fatty Acid Beta-Oxidation (Drosophila melanogaster)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Drosophila melanogaster)
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Drosophila melanogaster)
MECR dimer reduces tdec2-CoA to DEC-CoA (Drosophila melanogaster)
H+ [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Drosophila melanogaster)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Drosophila melanogaster)
H+ [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Drosophila melanogaster)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Drosophila melanogaster)
H+ [mitochondrial matrix]
Ketone body metabolism (Drosophila melanogaster)
Synthesis of Ketone Bodies (Drosophila melanogaster)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
Utilization of Ketone Bodies (Drosophila melanogaster)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
Metabolism of steroids (Drosophila melanogaster)
Metabolism of steroid hormones (Drosophila melanogaster)
Estrogen biosynthesis (Drosophila melanogaster)
AKR1B15 reduces EST17b to E1 (Drosophila melanogaster)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Drosophila melanogaster)
Heme biosynthesis (Drosophila melanogaster)
ALAS condenses SUCC-CoA and Gly to form dALA (Drosophila melanogaster)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Drosophila melanogaster)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Drosophila melanogaster)
Metabolism of cofactors (Drosophila melanogaster)
Ubiquinol biosynthesis (Drosophila melanogaster)
COQ3 methylates DHDB (Drosophila melanogaster)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Drosophila melanogaster)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Drosophila melanogaster)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Drosophila melanogaster)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Drosophila melanogaster)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Drosophila melanogaster)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Drosophila melanogaster)
Metabolism of folate and pterines (Drosophila melanogaster)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Drosophila melanogaster)
H+ [mitochondrial matrix]
Nicotinate metabolism (Drosophila melanogaster)
NADK2 dimer phosphorylates NAD+ to NADP+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Drosophila melanogaster)
H+ [mitochondrial matrix]
Nicotinamide salvage (Drosophila melanogaster)
CARKD dehydrates S-NAD(P)HX to NADPH (Drosophila melanogaster)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Drosophila melanogaster)
Electron transport from NADPH to Ferredoxin (Drosophila melanogaster)
FDXR transfers electrons to FDX1,2 (FDX1L) (Drosophila melanogaster)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Drosophila melanogaster)
H+ [mitochondrial matrix]
Reversible hydration of carbon dioxide (Drosophila melanogaster)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Drosophila melanogaster)
H+ [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Drosophila melanogaster)
H+ [mitochondrial matrix]
Metabolism of proteins (Drosophila melanogaster)
Post-translational protein modification (Drosophila melanogaster)
Protein lipoylation (Drosophila melanogaster)
LIAS synthesizes lipoyl-GCSH (Drosophila melanogaster)
H+ [mitochondrial matrix]
LIPT2 transfers octanoyl group to GCSH (Drosophila melanogaster)
H+ [mitochondrial matrix]
Neuronal System (Drosophila melanogaster)
Transmission across Chemical Synapses (Drosophila melanogaster)
Neurotransmitter clearance (Drosophila melanogaster)
Serotonin clearance from the synaptic cleft (Drosophila melanogaster)
Metabolism of serotonin (Drosophila melanogaster)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Drosophila melanogaster)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Drosophila melanogaster)
GABA synthesis, release, reuptake and degradation (Drosophila melanogaster)
Degradation of GABA (Drosophila melanogaster)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Drosophila melanogaster)
H+ [mitochondrial matrix]
Signal Transduction (Drosophila melanogaster)
Signaling by Nuclear Receptors (Drosophila melanogaster)
Signaling by Retinoic Acid (Drosophila melanogaster)
PDK isozymes phosphorylate PDHC subunit E1 (Drosophila melanogaster)
H+ [mitochondrial matrix]
Transport of small molecules (Drosophila melanogaster)
Ion channel transport (Drosophila melanogaster)
Stimuli-sensing channels (Drosophila melanogaster)
SLC9B2 exchanges Na+ for H+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
Iron uptake and transport (Drosophila melanogaster)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Drosophila melanogaster)
H+ [mitochondrial matrix]
SLC-mediated transmembrane transport (Drosophila melanogaster)
Transport of inorganic cations/anions and amino acids/oligopeptides (Drosophila melanogaster)
Organic anion transporters (Drosophila melanogaster)
SLC25A18,22 import L-Glu, H+ (Drosophila melanogaster)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Gallus gallus)
Cellular responses to stress (Gallus gallus)
Cellular response to chemical stress (Gallus gallus)
Cytoprotection by HMOX1 (Gallus gallus)
Electron transfer from reduced cytochrome c to molecular oxygen (Gallus gallus)
H+ [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Gallus gallus)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Gallus gallus)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Gallus gallus)
H+ [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Gallus gallus)
H+ [mitochondrial matrix]
Gene expression (Transcription) (Gallus gallus)
RNA Polymerase II Transcription (Gallus gallus)
Generic Transcription Pathway (Gallus gallus)
Transcriptional Regulation by TP53 (Gallus gallus)
TP53 Regulates Metabolic Genes (Gallus gallus)
Electron transfer from reduced cytochrome c to molecular oxygen (Gallus gallus)
H+ [mitochondrial matrix]
Metabolism (Gallus gallus)
Carbohydrate metabolism (Gallus gallus)
Gluconeogenesis (Gallus gallus)
oxaloacetate + NADH + H+ <=> malate + NAD+ (Gallus gallus)
H+ [mitochondrial matrix]
Heme synthesis (Gallus gallus)
protoporphyrin IX + Fe++ => heme + 2 H+ (Gallus gallus)
H+ [mitochondrial matrix]
Lipid metabolism (Gallus gallus)
oxaloacetate + NADH + H+ <=> malate + NAD+ (Gallus gallus)
H+ [mitochondrial matrix]
Pyruvate metabolism (Gallus gallus)
pyruvate + CoASH + NAD+ => acetylCoA + CO2 + NADH + H+ (Gallus gallus)
H+ [mitochondrial matrix]
pyruvate + H+ [cytosol] => pyruvate + H+ [mitochondrial matrix] (Gallus gallus)
H+ [mitochondrial matrix]
The tricarboxylic acid cycle (Gallus gallus)
2-oxoglutarate (alpha-ketoglutarate) + CoASH + NAD+ => succinylCoA + CO2 + NADH + H+ (Gallus gallus)
H+ [mitochondrial matrix]
isocitrate + NAD+ => 2-oxoglutarate (alpha-ketoglutarate) + CO2 + NADH + H+ (Gallus gallus)
H+ [mitochondrial matrix]
malate + NAD+ <=> oxaloacetate + NADH + H+ (Gallus gallus)
H+ [mitochondrial matrix]
Metabolism of proteins (Gallus gallus)
Post-translational protein modification (Gallus gallus)
Protein lipoylation (Gallus gallus)
LIAS synthesizes lipoyl-GCSH (Gallus gallus)
H+ [mitochondrial matrix]
LIPT2 transfers octanoyl group to GCSH (Gallus gallus)
H+ [mitochondrial matrix]
Neuronal System (Gallus gallus)
Transmission across Chemical Synapses (Gallus gallus)
Neurotransmitter clearance (Gallus gallus)
Serotonin clearance from the synaptic cleft (Gallus gallus)
Metabolism of serotonin (Gallus gallus)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Gallus gallus)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Gallus gallus)
GABA synthesis, release, reuptake and degradation (Gallus gallus)
Degradation of GABA (Gallus gallus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Gallus gallus)
H+ [mitochondrial matrix]
Signal Transduction (Gallus gallus)
Signaling by Nuclear Receptors (Gallus gallus)
Signaling by Retinoic Acid (Gallus gallus)
PDK isozymes phosphorylate PDHC subunit E1 (Gallus gallus)
H+ [mitochondrial matrix]
Transport of small molecules (Gallus gallus)
Ion channel transport (Gallus gallus)
Stimuli-sensing channels (Gallus gallus)
SLC9B2 exchanges Na+ for H+ (Gallus gallus)
H+ [mitochondrial matrix]
Iron uptake and transport (Gallus gallus)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Gallus gallus)
H+ [mitochondrial matrix]
SLC-mediated transmembrane transport (Gallus gallus)
Transport of inorganic cations/anions and amino acids/oligopeptides (Gallus gallus)
Organic anion transporters (Gallus gallus)
SLC25A18,22 import L-Glu, H+ (Gallus gallus)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Homo sapiens)
Cellular responses to stress (Homo sapiens)
Cellular response to chemical stress (Homo sapiens)
Cytoprotection by HMOX1 (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
H+ [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Homo sapiens)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Homo sapiens)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Homo sapiens)
H+ [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Homo sapiens)
H+ [mitochondrial matrix]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of branched-chain amino acid catabolism (Homo sapiens)
Maple Syrup Urine Disease (Homo sapiens)
Loss-of-function mutations in BCKDHA or BCKDHB cause MSUD (Homo sapiens)
BCKDHA or BCKDHB loss-of-function mutants don't synthesize BCAA-CoA (Homo sapiens)
H+ [mitochondrial matrix]
Metabolic disorders of biological oxidation enzymes (Homo sapiens)
Defective CYP11A1 causes AICSR (Homo sapiens)
Defective CYP11A1 does not cleave 20a,22b-DHCHOL (Homo sapiens)
H+ [mitochondrial matrix]
Defective CYP11B1 causes AH4 (Homo sapiens)
Defective CYP11B1 does not oxidise 11DCORT (Homo sapiens)
H+ [mitochondrial matrix]
Defective CYP11B2 causes CMO-1 deficiency (Homo sapiens)
Defective CYP11B2 does not oxidise 11DCORST (Homo sapiens)
H+ [mitochondrial matrix]
Defective CYP11B2 does not oxidise 18HCORST (Homo sapiens)
H+ [mitochondrial matrix]
Defective CYP11B2 does not oxidise CORST (Homo sapiens)
H+ [mitochondrial matrix]
Defective CYP24A1 causes HCAI (Homo sapiens)
Defective CYP24A1 does not 24-hydroxylate CALTOL (Homo sapiens)
H+ [mitochondrial matrix]
Defective CYP27A1 causes CTX (Homo sapiens)
CYP27A1 does not 27-hydroxylate 5bCHOL3a,7a,12a-triol (Homo sapiens)
H+ [mitochondrial matrix]
Defective CYP27A1 does not 27-hydroxylate 5β-CHOL3α,7α,24(s)-triol (Homo sapiens)
H+ [mitochondrial matrix]
Gene expression (Transcription) (Homo sapiens)
RNA Polymerase II Transcription (Homo sapiens)
Generic Transcription Pathway (Homo sapiens)
Transcriptional Regulation by TP53 (Homo sapiens)
TP53 Regulates Metabolic Genes (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
H+ [mitochondrial matrix]
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Citric acid cycle (TCA cycle) (Homo sapiens)
CS acetylates OA to citrate (Homo sapiens)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Homo sapiens)
H+ [mitochondrial matrix]
Maturation of TCA enzymes and regulation of TCA cycle (Homo sapiens)
ACAT1 tetramer acetylates IDH2 dimer (Homo sapiens)
H+ [mitochondrial matrix]
CSKMT methylates Citrate Synthase (Homo sapiens)
H+ [mitochondrial matrix]
NNT dimer transfers proton from NADPH to NAD+ (Homo sapiens)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Homo sapiens)
DLD dimer dehydrogenates dihydrolipoyl (Homo sapiens)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Homo sapiens)
H+ [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Homo sapiens)
Enzyme-bound ATP is released (Homo sapiens)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Homo sapiens)
AAC1 imports a proton (Homo sapiens)
H+ [mitochondrial matrix]
The fatty acid cycling model (Homo sapiens)
The proton is delivered to the matrix side (Homo sapiens)
H+ [mitochondrial matrix]
UCP1 imports a proton (Homo sapiens)
H+ [mitochondrial matrix]
Pyruvate metabolism (Homo sapiens)
FAHD1 dimer hydrolyses OA to PYR (Homo sapiens)
H+ [mitochondrial matrix]
LDHAL6B reduces PYR to LACT (Homo sapiens)
H+ [mitochondrial matrix]
MPC1:MPC2 imports PYR, H+ to mitochondrial matrix (Homo sapiens)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Homo sapiens)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Homo sapiens)
DLD dimer dehydrogenates dihydrolipoyl (Homo sapiens)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Homo sapiens)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Homo sapiens)
Regulation of pyruvate dehydrogenase (PDH) complex (Homo sapiens)
GS-MCA spontaneously hydrolyzes (Homo sapiens)
H+ [mitochondrial matrix]
GSTZ1 dimer dehalogenates DCA (Homo sapiens)
H+ [mitochondrial matrix]
PDK isozymes phosphorylate PDHC subunit E1 (Homo sapiens)
H+ [mitochondrial matrix]
Respiratory electron transport (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Homo sapiens)
H+ [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Homo sapiens)
H+ [mitochondrial matrix]
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
H+ [mitochondrial matrix]
Electron transfer from ubiquinol to cytochrome c of complex III (Homo sapiens)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Homo sapiens)
MDH2 dimer dehydrogenates MAL (Homo sapiens)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Homo sapiens)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Homo sapiens)
H+ [mitochondrial matrix]
Biological oxidations (Homo sapiens)
Phase I - Functionalization of compounds (Homo sapiens)
Cytochrome P450 - arranged by substrate type (Homo sapiens)
Endogenous sterols (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
H+ [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Homo sapiens)
H+ [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Homo sapiens)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Homo sapiens)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Homo sapiens)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Homo sapiens)
H+ [mitochondrial matrix]
Vitamins (Homo sapiens)
CYP24A1 24-hydroxylates CTL (Homo sapiens)
H+ [mitochondrial matrix]
Ethanol oxidation (Homo sapiens)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Homo sapiens)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Homo sapiens)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Homo sapiens)
Aspartate and asparagine metabolism (Homo sapiens)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Homo sapiens)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Homo sapiens)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Homo sapiens)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Homo sapiens)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Homo sapiens)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Homo sapiens)
H+ [mitochondrial matrix]
BCKDK phosphorylates BCKDH (Homo sapiens)
H+ [mitochondrial matrix]
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Homo sapiens)
H+ [mitochondrial matrix]
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Homo sapiens)
H+ [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Homo sapiens)
H+ [mitochondrial matrix]
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Homo sapiens)
H+ [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Homo sapiens)
H+ [mitochondrial matrix]
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Homo sapiens)
H+ [mitochondrial matrix]
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Homo sapiens)
H+ [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Homo sapiens)
H+ [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Homo sapiens)
H+ [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Homo sapiens)
H+ [mitochondrial matrix]
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Homo sapiens)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Homo sapiens)
L-glutamate gamma-semialdehyde <=> L-1-pyrroline-5-carboxylate (Homo sapiens)
H+ [mitochondrial matrix]
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Homo sapiens)
H+ [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Homo sapiens)
H+ [mitochondrial matrix]
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Homo sapiens)
H+ [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Homo sapiens)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Homo sapiens)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Homo sapiens)
H+ [mitochondrial matrix]
Glycine degradation (Homo sapiens)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Homo sapiens)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Homo sapiens)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Homo sapiens)
H+ [mitochondrial matrix]
Lysine catabolism (Homo sapiens)
HYKK phosphorylates 5HLYS (Homo sapiens)
H+ [mitochondrial matrix]
OADH complex synthesizes glutaryl-CoA from 2-OA (Homo sapiens)
DHTKD1 dimer decarboxylates 2-OA (Homo sapiens)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Homo sapiens)
H+ [mitochondrial matrix]
DLST transfers glutaryl to CoA (Homo sapiens)
H+ [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Homo sapiens)
H+ [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Homo sapiens)
H+ [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Homo sapiens)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Homo sapiens)
H+ [mitochondrial matrix]
Proline catabolism (Homo sapiens)
ALDH4A1 oxidises L-GluSS to Glu (Homo sapiens)
H+ [mitochondrial matrix]
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Homo sapiens)
H+ [mitochondrial matrix]
PRODH oxidises L-Pro to 1PYR-5COOH (Homo sapiens)
H+ [mitochondrial matrix]
Sulfur amino acid metabolism (Homo sapiens)
Degradation of cysteine and homocysteine (Homo sapiens)
Sulfide oxidation to sulfate (Homo sapiens)
Persulfide sulfur is dioxygenated (Homo sapiens)
H+ [mitochondrial matrix]
Thiosulfate can transfer its sulfur atom to glutathione (Homo sapiens)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Homo sapiens)
Glucose metabolism (Homo sapiens)
Gluconeogenesis (Homo sapiens)
PC carboxylates PYR to OA (Homo sapiens)
H+ [mitochondrial matrix]
Metabolism of lipids (Homo sapiens)
Fatty acid metabolism (Homo sapiens)
Fatty acyl-CoA biosynthesis (Homo sapiens)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Homo sapiens)
H+ [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Homo sapiens)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Homo sapiens)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Homo sapiens)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Homo sapiens)
H+ [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Homo sapiens)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Homo sapiens)
H+ [mitochondrial matrix]
MECR dimer reduces tdec2-CoA to DEC-CoA (Homo sapiens)
H+ [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Homo sapiens)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Homo sapiens)
H+ [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Homo sapiens)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Homo sapiens)
H+ [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Homo sapiens)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Homo sapiens)
H+ [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Homo sapiens)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Homo sapiens)
H+ [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Homo sapiens)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Homo sapiens)
H+ [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Homo sapiens)
Linoleoyl-CoA is converted to cis,cis-3,6- dodecadienoyl-CoA by three cycles of beta-oxidation (Homo sapiens)
H+ [mitochondrial matrix]
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Homo sapiens)
H+ [mitochondrial matrix]
Trans,cis-lauro-2,6-dienoyl-CoA is converted to cis,cis-3,6- 4-cis-decenoyl-CoA by one cycle of beta-oxidation (Homo sapiens)
H+ [mitochondrial matrix]
Ketone body metabolism (Homo sapiens)
Synthesis of Ketone Bodies (Homo sapiens)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Homo sapiens)
H+ [mitochondrial matrix]
Utilization of Ketone Bodies (Homo sapiens)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Homo sapiens)
H+ [mitochondrial matrix]
Metabolism of steroids (Homo sapiens)
Bile acid and bile salt metabolism (Homo sapiens)
Synthesis of bile acids and bile salts (Homo sapiens)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Homo sapiens)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Homo sapiens)
H+ [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Homo sapiens)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Homo sapiens)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Homo sapiens)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Homo sapiens)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Homo sapiens)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Homo sapiens)
CYP27A1 27-hydroxylates CHOL (Homo sapiens)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Homo sapiens)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Homo sapiens)
H+ [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Homo sapiens)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Homo sapiens)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Homo sapiens)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Homo sapiens)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Homo sapiens)
H+ [mitochondrial matrix]
Metabolism of steroid hormones (Homo sapiens)
Estrogen biosynthesis (Homo sapiens)
AKR1B15 reduces EST17b to E1 (Homo sapiens)
H+ [mitochondrial matrix]
Glucocorticoid biosynthesis (Homo sapiens)
CYP11B1 oxidises 11DCORT (Homo sapiens)
H+ [mitochondrial matrix]
Mineralocorticoid biosynthesis (Homo sapiens)
CYP11B2 18-hydroxylates CORST to 18HCORST (Homo sapiens)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Homo sapiens)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Homo sapiens)
H+ [mitochondrial matrix]
Pregnenolone biosynthesis (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
H+ [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Homo sapiens)
H+ [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Homo sapiens)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Homo sapiens)
Heme biosynthesis (Homo sapiens)
ALAS condenses SUCC-CoA and Gly to form dALA (Homo sapiens)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Homo sapiens)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Homo sapiens)
Metabolism of cofactors (Homo sapiens)
Ubiquinol biosynthesis (Homo sapiens)
COQ3 methylates DHDB (Homo sapiens)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Homo sapiens)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Homo sapiens)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Homo sapiens)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Homo sapiens)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Homo sapiens)
H+ [mitochondrial matrix]
Unknown dehydrogenase oxidizes 4-HBz (Homo sapiens)
H+ [mitochondrial matrix]
Unknown enzyme hydroxylates DMPhOH (Homo sapiens)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Homo sapiens)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Homo sapiens)
Cobalamin (Cbl) metabolism (Homo sapiens)
MMAB adenosylates cob(I)alamin (Homo sapiens)
H+ [mitochondrial matrix]
Metabolism of folate and pterines (Homo sapiens)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Homo sapiens)
H+ [mitochondrial matrix]
Nicotinate metabolism (Homo sapiens)
NADK2 dimer phosphorylates NAD+ to NADP+ (Homo sapiens)
H+ [mitochondrial matrix]
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Homo sapiens)
H+ [mitochondrial matrix]
Nicotinamide salvage (Homo sapiens)
CARKD dehydrates S-NAD(P)HX to NADPH (Homo sapiens)
H+ [mitochondrial matrix]
Vitamin B5 (pantothenate) metabolism (Homo sapiens)
NUDT8 hydrolyzes CoA-SH to PPANT (Homo sapiens)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Homo sapiens)
Electron transport from NADPH to Ferredoxin (Homo sapiens)
FDXR transfers electrons to FDX1,2 (FDX1L) (Homo sapiens)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Homo sapiens)
H+ [mitochondrial matrix]
Reversible hydration of carbon dioxide (Homo sapiens)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Homo sapiens)
H+ [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Homo sapiens)
H+ [mitochondrial matrix]
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
Protein lipoylation (Homo sapiens)
LIAS synthesizes lipoyl-GCSH (Homo sapiens)
H+ [mitochondrial matrix]
LIPT2 transfers octanoyl group to GCSH (Homo sapiens)
H+ [mitochondrial matrix]
Muscle contraction (Homo sapiens)
Smooth Muscle Contraction (Homo sapiens)
ALDH2 transforms GTN to NO (Homo sapiens)
H+ [mitochondrial matrix]
Neuronal System (Homo sapiens)
Transmission across Chemical Synapses (Homo sapiens)
Neurotransmitter clearance (Homo sapiens)
Serotonin clearance from the synaptic cleft (Homo sapiens)
Metabolism of serotonin (Homo sapiens)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Homo sapiens)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Homo sapiens)
GABA synthesis, release, reuptake and degradation (Homo sapiens)
Degradation of GABA (Homo sapiens)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Homo sapiens)
H+ [mitochondrial matrix]
Signal Transduction (Homo sapiens)
Signaling by Nuclear Receptors (Homo sapiens)
Signaling by Retinoic Acid (Homo sapiens)
PDK isozymes phosphorylate PDHC subunit E1 (Homo sapiens)
H+ [mitochondrial matrix]
Transport of small molecules (Homo sapiens)
Ion channel transport (Homo sapiens)
Stimuli-sensing channels (Homo sapiens)
SLC9B2 exchanges Na+ for H+ (Homo sapiens)
H+ [mitochondrial matrix]
Iron uptake and transport (Homo sapiens)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Homo sapiens)
H+ [mitochondrial matrix]
Mitochondrial calcium ion transport (Homo sapiens)
LETM1 exchanges protons (mitochondrial intermembrane space) for calcium (mitochondrial matrix) (Homo sapiens)
H+ [mitochondrial matrix]
SLC-mediated transmembrane transport (Homo sapiens)
Transport of inorganic cations/anions and amino acids/oligopeptides (Homo sapiens)
Organic anion transporters (Homo sapiens)
SLC25A18,22 import L-Glu, H+ (Homo sapiens)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Mus musculus)
Cellular responses to stress (Mus musculus)
Cellular response to chemical stress (Mus musculus)
Cytoprotection by HMOX1 (Mus musculus)
Electron transfer from reduced cytochrome c to molecular oxygen (Mus musculus)
H+ [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Mus musculus)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Mus musculus)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Mus musculus)
H+ [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Mus musculus)
H+ [mitochondrial matrix]
Gene expression (Transcription) (Mus musculus)
RNA Polymerase II Transcription (Mus musculus)
Generic Transcription Pathway (Mus musculus)
Transcriptional Regulation by TP53 (Mus musculus)
TP53 Regulates Metabolic Genes (Mus musculus)
Electron transfer from reduced cytochrome c to molecular oxygen (Mus musculus)
H+ [mitochondrial matrix]
Metabolism (Mus musculus)
Aerobic respiration and respiratory electron transport (Mus musculus)
Citric acid cycle (TCA cycle) (Mus musculus)
CS acetylates OA to citrate (Mus musculus)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Mus musculus)
H+ [mitochondrial matrix]
Maturation of TCA enzymes and regulation of TCA cycle (Mus musculus)
ACAT1 tetramer acetylates IDH2 dimer (Mus musculus)
H+ [mitochondrial matrix]
NNT dimer transfers proton from NADPH to NAD+ (Mus musculus)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Mus musculus)
DLD dimer dehydrogenates dihydrolipoyl (Mus musculus)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Mus musculus)
H+ [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Mus musculus)
Enzyme-bound ATP is released (Mus musculus)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Mus musculus)
AAC1 imports a proton (Mus musculus)
H+ [mitochondrial matrix]
UCP1 imports a proton (Mus musculus)
H+ [mitochondrial matrix]
Pyruvate metabolism (Mus musculus)
FAHD1 dimer hydrolyses OA to PYR (Mus musculus)
H+ [mitochondrial matrix]
LDHAL6B reduces PYR to LACT (Mus musculus)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Mus musculus)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Mus musculus)
DLD dimer dehydrogenates dihydrolipoyl (Mus musculus)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Mus musculus)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Mus musculus)
Regulation of pyruvate dehydrogenase (PDH) complex (Mus musculus)
GSTZ1 dimer dehalogenates DCA (Mus musculus)
H+ [mitochondrial matrix]
PDK isozymes phosphorylate PDHC subunit E1 (Mus musculus)
H+ [mitochondrial matrix]
Respiratory electron transport (Mus musculus)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Mus musculus)
H+ [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Mus musculus)
H+ [mitochondrial matrix]
Electron transfer from reduced cytochrome c to molecular oxygen (Mus musculus)
H+ [mitochondrial matrix]
Electron transfer from ubiquinol to cytochrome c of complex III (Mus musculus)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Mus musculus)
MDH2 dimer dehydrogenates MAL (Mus musculus)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Mus musculus)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Mus musculus)
H+ [mitochondrial matrix]
Biological oxidations (Mus musculus)
Phase I - Functionalization of compounds (Mus musculus)
Cytochrome P450 - arranged by substrate type (Mus musculus)
Endogenous sterols (Mus musculus)
CYP11A1 cleaves 20a,22b-DHCHOL (Mus musculus)
H+ [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Mus musculus)
H+ [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Mus musculus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Mus musculus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Mus musculus)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Mus musculus)
H+ [mitochondrial matrix]
Vitamins (Mus musculus)
CYP24A1 24-hydroxylates CTL (Mus musculus)
H+ [mitochondrial matrix]
Ethanol oxidation (Mus musculus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Mus musculus)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Mus musculus)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Mus musculus)
Aspartate and asparagine metabolism (Mus musculus)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Mus musculus)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Mus musculus)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Mus musculus)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Mus musculus)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Mus musculus)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Mus musculus)
H+ [mitochondrial matrix]
BCKDK phosphorylates BCKDH (Mus musculus)
H+ [mitochondrial matrix]
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Mus musculus)
H+ [mitochondrial matrix]
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Mus musculus)
H+ [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Mus musculus)
H+ [mitochondrial matrix]
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Mus musculus)
H+ [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Mus musculus)
H+ [mitochondrial matrix]
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Mus musculus)
H+ [mitochondrial matrix]
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Mus musculus)
H+ [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Mus musculus)
H+ [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Mus musculus)
H+ [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Mus musculus)
H+ [mitochondrial matrix]
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Mus musculus)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Mus musculus)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Mus musculus)
H+ [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Mus musculus)
H+ [mitochondrial matrix]
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Mus musculus)
H+ [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Mus musculus)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Mus musculus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Mus musculus)
H+ [mitochondrial matrix]
Glycine degradation (Mus musculus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Mus musculus)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Mus musculus)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Mus musculus)
H+ [mitochondrial matrix]
Lysine catabolism (Mus musculus)
HYKK phosphorylates 5HLYS (Mus musculus)
H+ [mitochondrial matrix]
OADH complex synthesizes glutaryl-CoA from 2-OA (Mus musculus)
DHTKD1 dimer decarboxylates 2-OA (Mus musculus)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Mus musculus)
H+ [mitochondrial matrix]
DLST transfers glutaryl to CoA (Mus musculus)
H+ [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Mus musculus)
H+ [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Mus musculus)
H+ [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Mus musculus)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Mus musculus)
H+ [mitochondrial matrix]
Proline catabolism (Mus musculus)
ALDH4A1 oxidises L-GluSS to Glu (Mus musculus)
H+ [mitochondrial matrix]
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Mus musculus)
H+ [mitochondrial matrix]
PRODH oxidises L-Pro to 1PYR-5COOH (Mus musculus)
H+ [mitochondrial matrix]
Sulfur amino acid metabolism (Mus musculus)
Degradation of cysteine and homocysteine (Mus musculus)
Sulfide oxidation to sulfate (Mus musculus)
Persulfide sulfur is dioxygenated (Mus musculus)
H+ [mitochondrial matrix]
Thiosulfate can transfer its sulfur atom to glutathione (Mus musculus)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Mus musculus)
Glucose metabolism (Mus musculus)
Gluconeogenesis (Mus musculus)
PC carboxylates PYR to OA (Mus musculus)
H+ [mitochondrial matrix]
Metabolism of lipids (Mus musculus)
Fatty acid metabolism (Mus musculus)
Fatty acyl-CoA biosynthesis (Mus musculus)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Mus musculus)
H+ [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Mus musculus)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Mus musculus)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Mus musculus)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Mus musculus)
H+ [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Mus musculus)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Mus musculus)
H+ [mitochondrial matrix]
MECR dimer reduces tdec2-CoA to DEC-CoA (Mus musculus)
H+ [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Mus musculus)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Mus musculus)
H+ [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Mus musculus)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Mus musculus)
H+ [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Mus musculus)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Mus musculus)
H+ [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Mus musculus)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Mus musculus)
H+ [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Mus musculus)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Mus musculus)
H+ [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Mus musculus)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Mus musculus)
H+ [mitochondrial matrix]
Ketone body metabolism (Mus musculus)
Synthesis of Ketone Bodies (Mus musculus)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Mus musculus)
H+ [mitochondrial matrix]
Utilization of Ketone Bodies (Mus musculus)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Mus musculus)
H+ [mitochondrial matrix]
Metabolism of steroids (Mus musculus)
Bile acid and bile salt metabolism (Mus musculus)
Synthesis of bile acids and bile salts (Mus musculus)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Mus musculus)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Mus musculus)
H+ [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Mus musculus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Mus musculus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Mus musculus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Mus musculus)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Mus musculus)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Mus musculus)
CYP27A1 27-hydroxylates CHOL (Mus musculus)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Mus musculus)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Mus musculus)
H+ [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Mus musculus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Mus musculus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Mus musculus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Mus musculus)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Mus musculus)
H+ [mitochondrial matrix]
Metabolism of steroid hormones (Mus musculus)
Estrogen biosynthesis (Mus musculus)
AKR1B15 reduces EST17b to E1 (Mus musculus)
H+ [mitochondrial matrix]
Glucocorticoid biosynthesis (Mus musculus)
CYP11B1 oxidises 11DCORT (Mus musculus)
H+ [mitochondrial matrix]
Mineralocorticoid biosynthesis (Mus musculus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Mus musculus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Mus musculus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Mus musculus)
H+ [mitochondrial matrix]
Pregnenolone biosynthesis (Mus musculus)
CYP11A1 cleaves 20a,22b-DHCHOL (Mus musculus)
H+ [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Mus musculus)
H+ [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Mus musculus)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Mus musculus)
Heme biosynthesis (Mus musculus)
ALAS condenses SUCC-CoA and Gly to form dALA (Mus musculus)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Mus musculus)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Mus musculus)
Metabolism of cofactors (Mus musculus)
Ubiquinol biosynthesis (Mus musculus)
COQ3 methylates DHDB (Mus musculus)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Mus musculus)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Mus musculus)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Mus musculus)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Mus musculus)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Mus musculus)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Mus musculus)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Mus musculus)
Cobalamin (Cbl) metabolism (Mus musculus)
MMAB adenosylates cob(I)alamin (Mus musculus)
H+ [mitochondrial matrix]
Metabolism of folate and pterines (Mus musculus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Mus musculus)
H+ [mitochondrial matrix]
Nicotinate metabolism (Mus musculus)
NADK2 dimer phosphorylates NAD+ to NADP+ (Mus musculus)
H+ [mitochondrial matrix]
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Mus musculus)
H+ [mitochondrial matrix]
Nicotinamide salvage (Mus musculus)
CARKD dehydrates S-NAD(P)HX to NADPH (Mus musculus)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Mus musculus)
Electron transport from NADPH to Ferredoxin (Mus musculus)
FDXR transfers electrons to FDX1,2 (FDX1L) (Mus musculus)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Mus musculus)
H+ [mitochondrial matrix]
Reversible hydration of carbon dioxide (Mus musculus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Mus musculus)
H+ [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Mus musculus)
H+ [mitochondrial matrix]
Metabolism of proteins (Mus musculus)
Post-translational protein modification (Mus musculus)
Protein lipoylation (Mus musculus)
LIAS synthesizes lipoyl-GCSH (Mus musculus)
H+ [mitochondrial matrix]
LIPT2 transfers octanoyl group to GCSH (Mus musculus)
H+ [mitochondrial matrix]
Neuronal System (Mus musculus)
Transmission across Chemical Synapses (Mus musculus)
Neurotransmitter clearance (Mus musculus)
Serotonin clearance from the synaptic cleft (Mus musculus)
Metabolism of serotonin (Mus musculus)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Mus musculus)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Mus musculus)
GABA synthesis, release, reuptake and degradation (Mus musculus)
Degradation of GABA (Mus musculus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Mus musculus)
H+ [mitochondrial matrix]
Signal Transduction (Mus musculus)
Signaling by Nuclear Receptors (Mus musculus)
Signaling by Retinoic Acid (Mus musculus)
PDK isozymes phosphorylate PDHC subunit E1 (Mus musculus)
H+ [mitochondrial matrix]
Transport of small molecules (Mus musculus)
Ion channel transport (Mus musculus)
Stimuli-sensing channels (Mus musculus)
SLC9B2 exchanges Na+ for H+ (Mus musculus)
H+ [mitochondrial matrix]
Iron uptake and transport (Mus musculus)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Mus musculus)
H+ [mitochondrial matrix]
SLC-mediated transmembrane transport (Mus musculus)
Transport of inorganic cations/anions and amino acids/oligopeptides (Mus musculus)
Organic anion transporters (Mus musculus)
SLC25A18,22 import L-Glu, H+ (Mus musculus)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Plasmodium falciparum)
Cellular responses to stress (Plasmodium falciparum)
Cellular response to chemical stress (Plasmodium falciparum)
Detoxification of Reactive Oxygen Species (Plasmodium falciparum)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Plasmodium falciparum)
H+ [mitochondrial matrix]
Metabolism (Plasmodium falciparum)
Aerobic respiration and respiratory electron transport (Plasmodium falciparum)
Citric acid cycle (TCA cycle) (Plasmodium falciparum)
CS acetylates OA to citrate (Plasmodium falciparum)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Plasmodium falciparum)
H+ [mitochondrial matrix]
Maturation of TCA enzymes and regulation of TCA cycle (Plasmodium falciparum)
ACAT1 tetramer acetylates IDH2 dimer (Plasmodium falciparum)
H+ [mitochondrial matrix]
NNT dimer transfers proton from NADPH to NAD+ (Plasmodium falciparum)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Plasmodium falciparum)
DLD dimer dehydrogenates dihydrolipoyl (Plasmodium falciparum)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Plasmodium falciparum)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Plasmodium falciparum)
AAC1 imports a proton (Plasmodium falciparum)
H+ [mitochondrial matrix]
Respiratory electron transport (Plasmodium falciparum)
Malate-aspartate shuttle (Plasmodium falciparum)
MDH2 dimer dehydrogenates MAL (Plasmodium falciparum)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Plasmodium falciparum)
Aspartate and asparagine metabolism (Plasmodium falciparum)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Plasmodium falciparum)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Plasmodium falciparum)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Plasmodium falciparum)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Plasmodium falciparum)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Plasmodium falciparum)
H+ [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Plasmodium falciparum)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Plasmodium falciparum)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Plasmodium falciparum)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Plasmodium falciparum)
Glycine degradation (Plasmodium falciparum)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Plasmodium falciparum)
H+ [mitochondrial matrix]
Metabolism of lipids (Plasmodium falciparum)
Fatty acid metabolism (Plasmodium falciparum)
Fatty acyl-CoA biosynthesis (Plasmodium falciparum)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Plasmodium falciparum)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Plasmodium falciparum)
Heme biosynthesis (Plasmodium falciparum)
ALAS condenses SUCC-CoA and Gly to form dALA (Plasmodium falciparum)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Plasmodium falciparum)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Plasmodium falciparum)
Metabolism of water-soluble vitamins and cofactors (Plasmodium falciparum)
Nicotinate metabolism (Plasmodium falciparum)
NADK2 dimer phosphorylates NAD+ to NADP+ (Plasmodium falciparum)
H+ [mitochondrial matrix]
Nicotinamide salvage (Plasmodium falciparum)
CARKD dehydrates S-NAD(P)HX to NADPH (Plasmodium falciparum)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Plasmodium falciparum)
Electron transport from NADPH to Ferredoxin (Plasmodium falciparum)
FDXR transfers electrons to FDX1,2 (FDX1L) (Plasmodium falciparum)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Plasmodium falciparum)
H+ [mitochondrial matrix]
Reversible hydration of carbon dioxide (Plasmodium falciparum)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Plasmodium falciparum)
H+ [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Plasmodium falciparum)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Rattus norvegicus)
Cellular responses to stress (Rattus norvegicus)
Cellular response to chemical stress (Rattus norvegicus)
Cytoprotection by HMOX1 (Rattus norvegicus)
Electron transfer from reduced cytochrome c to molecular oxygen (Rattus norvegicus)
H+ [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Rattus norvegicus)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Rattus norvegicus)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Rattus norvegicus)
H+ [mitochondrial matrix]
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Rattus norvegicus)
H+ [mitochondrial matrix]
Gene expression (Transcription) (Rattus norvegicus)
RNA Polymerase II Transcription (Rattus norvegicus)
Generic Transcription Pathway (Rattus norvegicus)
Transcriptional Regulation by TP53 (Rattus norvegicus)
TP53 Regulates Metabolic Genes (Rattus norvegicus)
Electron transfer from reduced cytochrome c to molecular oxygen (Rattus norvegicus)
H+ [mitochondrial matrix]
Metabolism (Rattus norvegicus)
Aerobic respiration and respiratory electron transport (Rattus norvegicus)
Citric acid cycle (TCA cycle) (Rattus norvegicus)
CS acetylates OA to citrate (Rattus norvegicus)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Rattus norvegicus)
H+ [mitochondrial matrix]
Maturation of TCA enzymes and regulation of TCA cycle (Rattus norvegicus)
ACAT1 tetramer acetylates IDH2 dimer (Rattus norvegicus)
H+ [mitochondrial matrix]
NNT dimer transfers proton from NADPH to NAD+ (Rattus norvegicus)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Rattus norvegicus)
DLD dimer dehydrogenates dihydrolipoyl (Rattus norvegicus)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Rattus norvegicus)
H+ [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Rattus norvegicus)
Enzyme-bound ATP is released (Rattus norvegicus)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Rattus norvegicus)
AAC1 imports a proton (Rattus norvegicus)
H+ [mitochondrial matrix]
UCP1 imports a proton (Rattus norvegicus)
H+ [mitochondrial matrix]
Pyruvate metabolism (Rattus norvegicus)
FAHD1 dimer hydrolyses OA to PYR (Rattus norvegicus)
H+ [mitochondrial matrix]
LDHAL6B reduces PYR to LACT (Rattus norvegicus)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Rattus norvegicus)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Rattus norvegicus)
DLD dimer dehydrogenates dihydrolipoyl (Rattus norvegicus)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Rattus norvegicus)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Rattus norvegicus)
Regulation of pyruvate dehydrogenase (PDH) complex (Rattus norvegicus)
GSTZ1 dimer dehalogenates DCA (Rattus norvegicus)
H+ [mitochondrial matrix]
PDK isozymes phosphorylate PDHC subunit E1 (Rattus norvegicus)
H+ [mitochondrial matrix]
Respiratory electron transport (Rattus norvegicus)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Rattus norvegicus)
H+ [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Rattus norvegicus)
H+ [mitochondrial matrix]
Electron transfer from reduced cytochrome c to molecular oxygen (Rattus norvegicus)
H+ [mitochondrial matrix]
Electron transfer from ubiquinol to cytochrome c of complex III (Rattus norvegicus)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Rattus norvegicus)
MDH2 dimer dehydrogenates MAL (Rattus norvegicus)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Rattus norvegicus)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Rattus norvegicus)
H+ [mitochondrial matrix]
Biological oxidations (Rattus norvegicus)
Phase I - Functionalization of compounds (Rattus norvegicus)
Cytochrome P450 - arranged by substrate type (Rattus norvegicus)
Endogenous sterols (Rattus norvegicus)
CYP11A1 cleaves 20a,22b-DHCHOL (Rattus norvegicus)
H+ [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Rattus norvegicus)
H+ [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Rattus norvegicus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Rattus norvegicus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Rattus norvegicus)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Rattus norvegicus)
H+ [mitochondrial matrix]
Vitamins (Rattus norvegicus)
CYP24A1 24-hydroxylates CTL (Rattus norvegicus)
H+ [mitochondrial matrix]
Ethanol oxidation (Rattus norvegicus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Rattus norvegicus)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Rattus norvegicus)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Rattus norvegicus)
Aspartate and asparagine metabolism (Rattus norvegicus)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Rattus norvegicus)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Rattus norvegicus)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Rattus norvegicus)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Rattus norvegicus)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Rattus norvegicus)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Rattus norvegicus)
H+ [mitochondrial matrix]
BCKDK phosphorylates BCKDH (Rattus norvegicus)
H+ [mitochondrial matrix]
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Rattus norvegicus)
H+ [mitochondrial matrix]
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Rattus norvegicus)
H+ [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Rattus norvegicus)
H+ [mitochondrial matrix]
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Rattus norvegicus)
H+ [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Rattus norvegicus)
H+ [mitochondrial matrix]
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Rattus norvegicus)
H+ [mitochondrial matrix]
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Rattus norvegicus)
H+ [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Rattus norvegicus)
H+ [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Rattus norvegicus)
H+ [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Rattus norvegicus)
H+ [mitochondrial matrix]
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Rattus norvegicus)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Rattus norvegicus)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Rattus norvegicus)
H+ [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Rattus norvegicus)
H+ [mitochondrial matrix]
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Rattus norvegicus)
H+ [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Rattus norvegicus)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Rattus norvegicus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Rattus norvegicus)
H+ [mitochondrial matrix]
Glycine degradation (Rattus norvegicus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Rattus norvegicus)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Rattus norvegicus)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Rattus norvegicus)
H+ [mitochondrial matrix]
Lysine catabolism (Rattus norvegicus)
HYKK phosphorylates 5HLYS (Rattus norvegicus)
H+ [mitochondrial matrix]
OADH complex synthesizes glutaryl-CoA from 2-OA (Rattus norvegicus)
DHTKD1 dimer decarboxylates 2-OA (Rattus norvegicus)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Rattus norvegicus)
H+ [mitochondrial matrix]
DLST transfers glutaryl to CoA (Rattus norvegicus)
H+ [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Rattus norvegicus)
H+ [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Rattus norvegicus)
H+ [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Rattus norvegicus)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Rattus norvegicus)
H+ [mitochondrial matrix]
Proline catabolism (Rattus norvegicus)
ALDH4A1 oxidises L-GluSS to Glu (Rattus norvegicus)
H+ [mitochondrial matrix]
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Rattus norvegicus)
H+ [mitochondrial matrix]
PRODH oxidises L-Pro to 1PYR-5COOH (Rattus norvegicus)
H+ [mitochondrial matrix]
Sulfur amino acid metabolism (Rattus norvegicus)
Degradation of cysteine and homocysteine (Rattus norvegicus)
Sulfide oxidation to sulfate (Rattus norvegicus)
Persulfide sulfur is dioxygenated (Rattus norvegicus)
H+ [mitochondrial matrix]
Thiosulfate can transfer its sulfur atom to glutathione (Rattus norvegicus)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Rattus norvegicus)
Glucose metabolism (Rattus norvegicus)
Gluconeogenesis (Rattus norvegicus)
PC carboxylates PYR to OA (Rattus norvegicus)
H+ [mitochondrial matrix]
Metabolism of lipids (Rattus norvegicus)
Fatty acid metabolism (Rattus norvegicus)
Fatty acyl-CoA biosynthesis (Rattus norvegicus)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Rattus norvegicus)
H+ [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Rattus norvegicus)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Rattus norvegicus)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Rattus norvegicus)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Rattus norvegicus)
H+ [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Rattus norvegicus)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Rattus norvegicus)
H+ [mitochondrial matrix]
MECR dimer reduces tdec2-CoA to DEC-CoA (Rattus norvegicus)
H+ [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Rattus norvegicus)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Rattus norvegicus)
H+ [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Rattus norvegicus)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Rattus norvegicus)
H+ [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Rattus norvegicus)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Rattus norvegicus)
H+ [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Rattus norvegicus)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Rattus norvegicus)
H+ [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Rattus norvegicus)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Rattus norvegicus)
H+ [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Rattus norvegicus)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Rattus norvegicus)
H+ [mitochondrial matrix]
Ketone body metabolism (Rattus norvegicus)
Synthesis of Ketone Bodies (Rattus norvegicus)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Rattus norvegicus)
H+ [mitochondrial matrix]
Utilization of Ketone Bodies (Rattus norvegicus)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Rattus norvegicus)
H+ [mitochondrial matrix]
Metabolism of steroids (Rattus norvegicus)
Bile acid and bile salt metabolism (Rattus norvegicus)
Synthesis of bile acids and bile salts (Rattus norvegicus)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Rattus norvegicus)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Rattus norvegicus)
H+ [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Rattus norvegicus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Rattus norvegicus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Rattus norvegicus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Rattus norvegicus)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Rattus norvegicus)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Rattus norvegicus)
CYP27A1 27-hydroxylates CHOL (Rattus norvegicus)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Rattus norvegicus)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Rattus norvegicus)
H+ [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Rattus norvegicus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Rattus norvegicus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Rattus norvegicus)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Rattus norvegicus)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Rattus norvegicus)
H+ [mitochondrial matrix]
Metabolism of steroid hormones (Rattus norvegicus)
Estrogen biosynthesis (Rattus norvegicus)
AKR1B15 reduces EST17b to E1 (Rattus norvegicus)
H+ [mitochondrial matrix]
Glucocorticoid biosynthesis (Rattus norvegicus)
CYP11B1 oxidises 11DCORT (Rattus norvegicus)
H+ [mitochondrial matrix]
Mineralocorticoid biosynthesis (Rattus norvegicus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Rattus norvegicus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Rattus norvegicus)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Rattus norvegicus)
H+ [mitochondrial matrix]
Pregnenolone biosynthesis (Rattus norvegicus)
CYP11A1 cleaves 20a,22b-DHCHOL (Rattus norvegicus)
H+ [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Rattus norvegicus)
H+ [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Rattus norvegicus)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Rattus norvegicus)
Heme biosynthesis (Rattus norvegicus)
ALAS condenses SUCC-CoA and Gly to form dALA (Rattus norvegicus)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Rattus norvegicus)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Rattus norvegicus)
Metabolism of cofactors (Rattus norvegicus)
Ubiquinol biosynthesis (Rattus norvegicus)
COQ3 methylates DHDB (Rattus norvegicus)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Rattus norvegicus)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Rattus norvegicus)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Rattus norvegicus)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Rattus norvegicus)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Rattus norvegicus)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Rattus norvegicus)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Rattus norvegicus)
Cobalamin (Cbl) metabolism (Rattus norvegicus)
MMAB adenosylates cob(I)alamin (Rattus norvegicus)
H+ [mitochondrial matrix]
Metabolism of folate and pterines (Rattus norvegicus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Rattus norvegicus)
H+ [mitochondrial matrix]
Nicotinate metabolism (Rattus norvegicus)
NADK2 dimer phosphorylates NAD+ to NADP+ (Rattus norvegicus)
H+ [mitochondrial matrix]
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Rattus norvegicus)
H+ [mitochondrial matrix]
Nicotinamide salvage (Rattus norvegicus)
CARKD dehydrates S-NAD(P)HX to NADPH (Rattus norvegicus)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Rattus norvegicus)
Electron transport from NADPH to Ferredoxin (Rattus norvegicus)
FDXR transfers electrons to FDX1,2 (FDX1L) (Rattus norvegicus)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Rattus norvegicus)
H+ [mitochondrial matrix]
Reversible hydration of carbon dioxide (Rattus norvegicus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Rattus norvegicus)
H+ [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Rattus norvegicus)
H+ [mitochondrial matrix]
Metabolism of proteins (Rattus norvegicus)
Post-translational protein modification (Rattus norvegicus)
Protein lipoylation (Rattus norvegicus)
LIAS synthesizes lipoyl-GCSH (Rattus norvegicus)
H+ [mitochondrial matrix]
LIPT2 transfers octanoyl group to GCSH (Rattus norvegicus)
H+ [mitochondrial matrix]
Neuronal System (Rattus norvegicus)
Transmission across Chemical Synapses (Rattus norvegicus)
Neurotransmitter clearance (Rattus norvegicus)
Serotonin clearance from the synaptic cleft (Rattus norvegicus)
Metabolism of serotonin (Rattus norvegicus)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Rattus norvegicus)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Rattus norvegicus)
GABA synthesis, release, reuptake and degradation (Rattus norvegicus)
Degradation of GABA (Rattus norvegicus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Rattus norvegicus)
H+ [mitochondrial matrix]
Signal Transduction (Rattus norvegicus)
Signaling by Nuclear Receptors (Rattus norvegicus)
Signaling by Retinoic Acid (Rattus norvegicus)
PDK isozymes phosphorylate PDHC subunit E1 (Rattus norvegicus)
H+ [mitochondrial matrix]
Transport of small molecules (Rattus norvegicus)
Iron uptake and transport (Rattus norvegicus)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Rattus norvegicus)
H+ [mitochondrial matrix]
SLC-mediated transmembrane transport (Rattus norvegicus)
Transport of inorganic cations/anions and amino acids/oligopeptides (Rattus norvegicus)
Organic anion transporters (Rattus norvegicus)
SLC25A18,22 import L-Glu, H+ (Rattus norvegicus)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Saccharomyces cerevisiae)
Cellular responses to stress (Saccharomyces cerevisiae)
Cellular response to chemical stress (Saccharomyces cerevisiae)
Detoxification of Reactive Oxygen Species (Saccharomyces cerevisiae)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Metabolism (Saccharomyces cerevisiae)
Aerobic respiration and respiratory electron transport (Saccharomyces cerevisiae)
Citric acid cycle (TCA cycle) (Saccharomyces cerevisiae)
CS acetylates OA to citrate (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Saccharomyces cerevisiae)
DLD dimer dehydrogenates dihydrolipoyl (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Saccharomyces cerevisiae)
AAC1 imports a proton (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Pyruvate metabolism (Saccharomyces cerevisiae)
FAHD1 dimer hydrolyses OA to PYR (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Saccharomyces cerevisiae)
DLD dimer dehydrogenates dihydrolipoyl (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Respiratory electron transport (Saccharomyces cerevisiae)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Electron transfer from ubiquinol to cytochrome c of complex III (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Saccharomyces cerevisiae)
MDH2 dimer dehydrogenates MAL (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Biological oxidations (Saccharomyces cerevisiae)
Phase I - Functionalization of compounds (Saccharomyces cerevisiae)
Ethanol oxidation (Saccharomyces cerevisiae)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Saccharomyces cerevisiae)
Aspartate and asparagine metabolism (Saccharomyces cerevisiae)
SLC25A12,13 exchange L-Glu and L-Asp (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Saccharomyces cerevisiae)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Saccharomyces cerevisiae)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Saccharomyces cerevisiae)
Glycine degradation (Saccharomyces cerevisiae)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Lysine catabolism (Saccharomyces cerevisiae)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Proline catabolism (Saccharomyces cerevisiae)
PRODH oxidises L-Pro to 1PYR-5COOH (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Saccharomyces cerevisiae)
Glucose metabolism (Saccharomyces cerevisiae)
Gluconeogenesis (Saccharomyces cerevisiae)
PC carboxylates PYR to OA (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Metabolism of lipids (Saccharomyces cerevisiae)
Fatty acid metabolism (Saccharomyces cerevisiae)
Fatty acyl-CoA biosynthesis (Saccharomyces cerevisiae)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Saccharomyces cerevisiae)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Saccharomyces cerevisiae)
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Saccharomyces cerevisiae)
MECR dimer reduces tdec2-CoA to DEC-CoA (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Metabolism of steroids (Saccharomyces cerevisiae)
Metabolism of steroid hormones (Saccharomyces cerevisiae)
Estrogen biosynthesis (Saccharomyces cerevisiae)
AKR1B15 reduces EST17b to E1 (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Saccharomyces cerevisiae)
Heme biosynthesis (Saccharomyces cerevisiae)
ALAS condenses SUCC-CoA and Gly to form dALA (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Saccharomyces cerevisiae)
Metabolism of cofactors (Saccharomyces cerevisiae)
Ubiquinol biosynthesis (Saccharomyces cerevisiae)
COQ3 methylates DHDB (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Saccharomyces cerevisiae)
Nicotinate metabolism (Saccharomyces cerevisiae)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Nicotinamide salvage (Saccharomyces cerevisiae)
CARKD dehydrates S-NAD(P)HX to NADPH (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Saccharomyces cerevisiae)
Electron transport from NADPH to Ferredoxin (Saccharomyces cerevisiae)
FDXR transfers electrons to FDX1,2 (FDX1L) (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Metabolism of proteins (Saccharomyces cerevisiae)
Post-translational protein modification (Saccharomyces cerevisiae)
Protein lipoylation (Saccharomyces cerevisiae)
LIPT2 transfers octanoyl group to GCSH (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Neuronal System (Saccharomyces cerevisiae)
Transmission across Chemical Synapses (Saccharomyces cerevisiae)
Neurotransmitter clearance (Saccharomyces cerevisiae)
Serotonin clearance from the synaptic cleft (Saccharomyces cerevisiae)
Metabolism of serotonin (Saccharomyces cerevisiae)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Saccharomyces cerevisiae)
GABA synthesis, release, reuptake and degradation (Saccharomyces cerevisiae)
Degradation of GABA (Saccharomyces cerevisiae)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Transport of small molecules (Saccharomyces cerevisiae)
SLC-mediated transmembrane transport (Saccharomyces cerevisiae)
Transport of inorganic cations/anions and amino acids/oligopeptides (Saccharomyces cerevisiae)
Organic anion transporters (Saccharomyces cerevisiae)
SLC25A18,22 import L-Glu, H+ (Saccharomyces cerevisiae)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Schizosaccharomyces pombe)
Cellular responses to stress (Schizosaccharomyces pombe)
Cellular response to chemical stress (Schizosaccharomyces pombe)
Detoxification of Reactive Oxygen Species (Schizosaccharomyces pombe)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Metabolism (Schizosaccharomyces pombe)
Aerobic respiration and respiratory electron transport (Schizosaccharomyces pombe)
Citric acid cycle (TCA cycle) (Schizosaccharomyces pombe)
CS acetylates OA to citrate (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Schizosaccharomyces pombe)
DLD dimer dehydrogenates dihydrolipoyl (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Schizosaccharomyces pombe)
AAC1 imports a proton (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Pyruvate metabolism (Schizosaccharomyces pombe)
FAHD1 dimer hydrolyses OA to PYR (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Schizosaccharomyces pombe)
DLD dimer dehydrogenates dihydrolipoyl (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Schizosaccharomyces pombe)
Regulation of pyruvate dehydrogenase (PDH) complex (Schizosaccharomyces pombe)
PDK isozymes phosphorylate PDHC subunit E1 (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Respiratory electron transport (Schizosaccharomyces pombe)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Electron transfer from ubiquinol to cytochrome c of complex III (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Schizosaccharomyces pombe)
MDH2 dimer dehydrogenates MAL (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Biological oxidations (Schizosaccharomyces pombe)
Phase I - Functionalization of compounds (Schizosaccharomyces pombe)
Ethanol oxidation (Schizosaccharomyces pombe)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Schizosaccharomyces pombe)
Branched-chain amino acid catabolism (Schizosaccharomyces pombe)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Schizosaccharomyces pombe)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Schizosaccharomyces pombe)
Glycine degradation (Schizosaccharomyces pombe)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Lysine catabolism (Schizosaccharomyces pombe)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Proline catabolism (Schizosaccharomyces pombe)
PRODH oxidises L-Pro to 1PYR-5COOH (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Schizosaccharomyces pombe)
Glucose metabolism (Schizosaccharomyces pombe)
Gluconeogenesis (Schizosaccharomyces pombe)
PC carboxylates PYR to OA (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Metabolism of lipids (Schizosaccharomyces pombe)
Fatty acid metabolism (Schizosaccharomyces pombe)
Fatty acyl-CoA biosynthesis (Schizosaccharomyces pombe)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Schizosaccharomyces pombe)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Schizosaccharomyces pombe)
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Schizosaccharomyces pombe)
MECR dimer reduces tdec2-CoA to DEC-CoA (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Ketone body metabolism (Schizosaccharomyces pombe)
Synthesis of Ketone Bodies (Schizosaccharomyces pombe)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Utilization of Ketone Bodies (Schizosaccharomyces pombe)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Metabolism of steroids (Schizosaccharomyces pombe)
Metabolism of steroid hormones (Schizosaccharomyces pombe)
Estrogen biosynthesis (Schizosaccharomyces pombe)
AKR1B15 reduces EST17b to E1 (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Schizosaccharomyces pombe)
Heme biosynthesis (Schizosaccharomyces pombe)
ALAS condenses SUCC-CoA and Gly to form dALA (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Schizosaccharomyces pombe)
Metabolism of cofactors (Schizosaccharomyces pombe)
Ubiquinol biosynthesis (Schizosaccharomyces pombe)
COQ3 methylates DHDB (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Schizosaccharomyces pombe)
Nicotinate metabolism (Schizosaccharomyces pombe)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Nicotinamide salvage (Schizosaccharomyces pombe)
CARKD dehydrates S-NAD(P)HX to NADPH (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Schizosaccharomyces pombe)
Electron transport from NADPH to Ferredoxin (Schizosaccharomyces pombe)
NADPH transfers electrons to FDXR (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Metabolism of proteins (Schizosaccharomyces pombe)
Post-translational protein modification (Schizosaccharomyces pombe)
Protein lipoylation (Schizosaccharomyces pombe)
LIPT2 transfers octanoyl group to GCSH (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Neuronal System (Schizosaccharomyces pombe)
Transmission across Chemical Synapses (Schizosaccharomyces pombe)
Neurotransmitter clearance (Schizosaccharomyces pombe)
Serotonin clearance from the synaptic cleft (Schizosaccharomyces pombe)
Metabolism of serotonin (Schizosaccharomyces pombe)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Schizosaccharomyces pombe)
GABA synthesis, release, reuptake and degradation (Schizosaccharomyces pombe)
Degradation of GABA (Schizosaccharomyces pombe)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Signal Transduction (Schizosaccharomyces pombe)
Signaling by Nuclear Receptors (Schizosaccharomyces pombe)
Signaling by Retinoic Acid (Schizosaccharomyces pombe)
PDK isozymes phosphorylate PDHC subunit E1 (Schizosaccharomyces pombe)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Sus scrofa)
Cellular responses to stress (Sus scrofa)
Cellular response to chemical stress (Sus scrofa)
Cytoprotection by HMOX1 (Sus scrofa)
Electron transfer from reduced cytochrome c to molecular oxygen (Sus scrofa)
H+ [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Sus scrofa)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Sus scrofa)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Sus scrofa)
H+ [mitochondrial matrix]
Gene expression (Transcription) (Sus scrofa)
RNA Polymerase II Transcription (Sus scrofa)
Generic Transcription Pathway (Sus scrofa)
Transcriptional Regulation by TP53 (Sus scrofa)
TP53 Regulates Metabolic Genes (Sus scrofa)
Electron transfer from reduced cytochrome c to molecular oxygen (Sus scrofa)
H+ [mitochondrial matrix]
Metabolism (Sus scrofa)
Aerobic respiration and respiratory electron transport (Sus scrofa)
Citric acid cycle (TCA cycle) (Sus scrofa)
CS acetylates OA to citrate (Sus scrofa)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Sus scrofa)
H+ [mitochondrial matrix]
Maturation of TCA enzymes and regulation of TCA cycle (Sus scrofa)
ACAT1 tetramer acetylates IDH2 dimer (Sus scrofa)
H+ [mitochondrial matrix]
CSKMT methylates Citrate Synthase (Sus scrofa)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Sus scrofa)
DLD dimer dehydrogenates dihydrolipoyl (Sus scrofa)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Sus scrofa)
H+ [mitochondrial matrix]
Formation of ATP by chemiosmotic coupling (Sus scrofa)
Enzyme-bound ATP is released (Sus scrofa)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Sus scrofa)
AAC1 imports a proton (Sus scrofa)
H+ [mitochondrial matrix]
Pyruvate metabolism (Sus scrofa)
FAHD1 dimer hydrolyses OA to PYR (Sus scrofa)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Sus scrofa)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Sus scrofa)
DLD dimer dehydrogenates dihydrolipoyl (Sus scrofa)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Sus scrofa)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Sus scrofa)
Regulation of pyruvate dehydrogenase (PDH) complex (Sus scrofa)
GSTZ1 dimer dehalogenates DCA (Sus scrofa)
H+ [mitochondrial matrix]
PDK isozymes phosphorylate PDHC subunit E1 (Sus scrofa)
H+ [mitochondrial matrix]
Respiratory electron transport (Sus scrofa)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Sus scrofa)
H+ [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Sus scrofa)
H+ [mitochondrial matrix]
Electron transfer from reduced cytochrome c to molecular oxygen (Sus scrofa)
H+ [mitochondrial matrix]
Electron transfer from ubiquinol to cytochrome c of complex III (Sus scrofa)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Sus scrofa)
MDH2 dimer dehydrogenates MAL (Sus scrofa)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Sus scrofa)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Sus scrofa)
H+ [mitochondrial matrix]
Biological oxidations (Sus scrofa)
Phase I - Functionalization of compounds (Sus scrofa)
Cytochrome P450 - arranged by substrate type (Sus scrofa)
Endogenous sterols (Sus scrofa)
CYP11A1 cleaves 20a,22b-DHCHOL (Sus scrofa)
H+ [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Sus scrofa)
H+ [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Sus scrofa)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Sus scrofa)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Sus scrofa)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates CHOL (Sus scrofa)
H+ [mitochondrial matrix]
Vitamins (Sus scrofa)
CYP24A1 24-hydroxylates CTL (Sus scrofa)
H+ [mitochondrial matrix]
Ethanol oxidation (Sus scrofa)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Sus scrofa)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Sus scrofa)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Sus scrofa)
Aspartate and asparagine metabolism (Sus scrofa)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Sus scrofa)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Sus scrofa)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Sus scrofa)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Sus scrofa)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Sus scrofa)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Sus scrofa)
H+ [mitochondrial matrix]
BCKDK phosphorylates BCKDH (Sus scrofa)
H+ [mitochondrial matrix]
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Sus scrofa)
H+ [mitochondrial matrix]
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Sus scrofa)
H+ [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Sus scrofa)
H+ [mitochondrial matrix]
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Sus scrofa)
H+ [mitochondrial matrix]
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Sus scrofa)
H+ [mitochondrial matrix]
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Sus scrofa)
H+ [mitochondrial matrix]
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Sus scrofa)
H+ [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Sus scrofa)
H+ [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Sus scrofa)
H+ [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Sus scrofa)
H+ [mitochondrial matrix]
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Sus scrofa)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Sus scrofa)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Sus scrofa)
H+ [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Sus scrofa)
H+ [mitochondrial matrix]
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Sus scrofa)
H+ [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Sus scrofa)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Sus scrofa)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Sus scrofa)
H+ [mitochondrial matrix]
Glycine degradation (Sus scrofa)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Sus scrofa)
H+ [mitochondrial matrix]
PXLP-K754-GLDC dimer decarboxylates Gly (Sus scrofa)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Sus scrofa)
H+ [mitochondrial matrix]
Lysine catabolism (Sus scrofa)
HYKK phosphorylates 5HLYS (Sus scrofa)
H+ [mitochondrial matrix]
OADH complex synthesizes glutaryl-CoA from 2-OA (Sus scrofa)
DHTKD1 dimer decarboxylates 2-OA (Sus scrofa)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Sus scrofa)
H+ [mitochondrial matrix]
DLST transfers glutaryl to CoA (Sus scrofa)
H+ [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Sus scrofa)
H+ [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Sus scrofa)
H+ [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Sus scrofa)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Sus scrofa)
H+ [mitochondrial matrix]
Proline catabolism (Sus scrofa)
ALDH4A1 oxidises L-GluSS to Glu (Sus scrofa)
H+ [mitochondrial matrix]
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Sus scrofa)
H+ [mitochondrial matrix]
PRODH oxidises L-Pro to 1PYR-5COOH (Sus scrofa)
H+ [mitochondrial matrix]
Sulfur amino acid metabolism (Sus scrofa)
Degradation of cysteine and homocysteine (Sus scrofa)
Sulfide oxidation to sulfate (Sus scrofa)
Persulfide sulfur is dioxygenated (Sus scrofa)
H+ [mitochondrial matrix]
Thiosulfate can transfer its sulfur atom to glutathione (Sus scrofa)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Sus scrofa)
Glucose metabolism (Sus scrofa)
Gluconeogenesis (Sus scrofa)
PC carboxylates PYR to OA (Sus scrofa)
H+ [mitochondrial matrix]
Metabolism of lipids (Sus scrofa)
Fatty acid metabolism (Sus scrofa)
Fatty acyl-CoA biosynthesis (Sus scrofa)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Sus scrofa)
H+ [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Sus scrofa)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Sus scrofa)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Sus scrofa)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Sus scrofa)
H+ [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Sus scrofa)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Sus scrofa)
H+ [mitochondrial matrix]
MECR dimer reduces tdec2-CoA to DEC-CoA (Sus scrofa)
H+ [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Sus scrofa)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Sus scrofa)
H+ [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Sus scrofa)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Sus scrofa)
H+ [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Sus scrofa)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Sus scrofa)
H+ [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Sus scrofa)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Sus scrofa)
H+ [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Sus scrofa)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Sus scrofa)
H+ [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Sus scrofa)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Sus scrofa)
H+ [mitochondrial matrix]
Ketone body metabolism (Sus scrofa)
Synthesis of Ketone Bodies (Sus scrofa)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Sus scrofa)
H+ [mitochondrial matrix]
Utilization of Ketone Bodies (Sus scrofa)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Sus scrofa)
H+ [mitochondrial matrix]
Metabolism of steroids (Sus scrofa)
Bile acid and bile salt metabolism (Sus scrofa)
Synthesis of bile acids and bile salts (Sus scrofa)
Synthesis of bile acids and bile salts via 24-hydroxycholesterol (Sus scrofa)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Sus scrofa)
H+ [mitochondrial matrix]
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Sus scrofa)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Sus scrofa)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Sus scrofa)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Sus scrofa)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Sus scrofa)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 27-hydroxycholesterol (Sus scrofa)
CYP27A1 27-hydroxylates CHOL (Sus scrofa)
H+ [mitochondrial matrix]
Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol (Sus scrofa)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Sus scrofa)
H+ [mitochondrial matrix]
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Sus scrofa)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Sus scrofa)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Sus scrofa)
H+ [mitochondrial matrix]
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Sus scrofa)
H+ [mitochondrial matrix]
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Sus scrofa)
H+ [mitochondrial matrix]
Metabolism of steroid hormones (Sus scrofa)
Glucocorticoid biosynthesis (Sus scrofa)
CYP11B1 oxidises 11DCORT (Sus scrofa)
H+ [mitochondrial matrix]
Mineralocorticoid biosynthesis (Sus scrofa)
CYP11B2 18-hydroxylates CORST to 18HCORST (Sus scrofa)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Sus scrofa)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Sus scrofa)
H+ [mitochondrial matrix]
Pregnenolone biosynthesis (Sus scrofa)
CYP11A1 cleaves 20a,22b-DHCHOL (Sus scrofa)
H+ [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Sus scrofa)
H+ [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Sus scrofa)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Sus scrofa)
Heme biosynthesis (Sus scrofa)
ALAS condenses SUCC-CoA and Gly to form dALA (Sus scrofa)
H+ [mitochondrial matrix]
FECH binds Fe2+ to PRIN9 to form heme (Sus scrofa)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Sus scrofa)
Metabolism of cofactors (Sus scrofa)
Ubiquinol biosynthesis (Sus scrofa)
COQ3 methylates DHDB (Sus scrofa)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Sus scrofa)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Sus scrofa)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Sus scrofa)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Sus scrofa)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Sus scrofa)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Sus scrofa)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Sus scrofa)
Cobalamin (Cbl) metabolism (Sus scrofa)
MMAB adenosylates cob(I)alamin (Sus scrofa)
H+ [mitochondrial matrix]
Metabolism of folate and pterines (Sus scrofa)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Sus scrofa)
H+ [mitochondrial matrix]
Nicotinate metabolism (Sus scrofa)
NADK2 dimer phosphorylates NAD+ to NADP+ (Sus scrofa)
H+ [mitochondrial matrix]
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Sus scrofa)
H+ [mitochondrial matrix]
Nicotinamide salvage (Sus scrofa)
CARKD dehydrates S-NAD(P)HX to NADPH (Sus scrofa)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Sus scrofa)
Electron transport from NADPH to Ferredoxin (Sus scrofa)
FDXR transfers electrons to FDX1,2 (FDX1L) (Sus scrofa)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Sus scrofa)
H+ [mitochondrial matrix]
Reversible hydration of carbon dioxide (Sus scrofa)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Sus scrofa)
H+ [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Sus scrofa)
H+ [mitochondrial matrix]
Metabolism of proteins (Sus scrofa)
Post-translational protein modification (Sus scrofa)
Protein lipoylation (Sus scrofa)
LIAS synthesizes lipoyl-GCSH (Sus scrofa)
H+ [mitochondrial matrix]
LIPT2 transfers octanoyl group to GCSH (Sus scrofa)
H+ [mitochondrial matrix]
Neuronal System (Sus scrofa)
Transmission across Chemical Synapses (Sus scrofa)
Neurotransmitter clearance (Sus scrofa)
Serotonin clearance from the synaptic cleft (Sus scrofa)
Metabolism of serotonin (Sus scrofa)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Sus scrofa)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Sus scrofa)
GABA synthesis, release, reuptake and degradation (Sus scrofa)
Degradation of GABA (Sus scrofa)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Sus scrofa)
H+ [mitochondrial matrix]
Signal Transduction (Sus scrofa)
Signaling by Nuclear Receptors (Sus scrofa)
Signaling by Retinoic Acid (Sus scrofa)
PDK isozymes phosphorylate PDHC subunit E1 (Sus scrofa)
H+ [mitochondrial matrix]
Transport of small molecules (Sus scrofa)
Ion channel transport (Sus scrofa)
Stimuli-sensing channels (Sus scrofa)
SLC9B2 exchanges Na+ for H+ (Sus scrofa)
H+ [mitochondrial matrix]
Iron uptake and transport (Sus scrofa)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Sus scrofa)
H+ [mitochondrial matrix]
SLC-mediated transmembrane transport (Sus scrofa)
Transport of inorganic cations/anions and amino acids/oligopeptides (Sus scrofa)
Organic anion transporters (Sus scrofa)
SLC25A18,22 import L-Glu, H+ (Sus scrofa)
H+ [mitochondrial matrix]
Cellular responses to stimuli (Xenopus tropicalis)
Cellular responses to stress (Xenopus tropicalis)
Cellular response to chemical stress (Xenopus tropicalis)
Cytoprotection by HMOX1 (Xenopus tropicalis)
Electron transfer from reduced cytochrome c to molecular oxygen (Xenopus tropicalis)
H+ [mitochondrial matrix]
Detoxification of Reactive Oxygen Species (Xenopus tropicalis)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Xenopus tropicalis)
H+ [mitochondrial matrix]
Gene expression (Transcription) (Xenopus tropicalis)
RNA Polymerase II Transcription (Xenopus tropicalis)
Generic Transcription Pathway (Xenopus tropicalis)
Transcriptional Regulation by TP53 (Xenopus tropicalis)
TP53 Regulates Metabolic Genes (Xenopus tropicalis)
Electron transfer from reduced cytochrome c to molecular oxygen (Xenopus tropicalis)
H+ [mitochondrial matrix]
Metabolism (Xenopus tropicalis)
Aerobic respiration and respiratory electron transport (Xenopus tropicalis)
Citric acid cycle (TCA cycle) (Xenopus tropicalis)
CS acetylates OA to citrate (Xenopus tropicalis)
H+ [mitochondrial matrix]
MDH2 dimer dehydrogenates MAL (Xenopus tropicalis)
H+ [mitochondrial matrix]
Maturation of TCA enzymes and regulation of TCA cycle (Xenopus tropicalis)
ACAT1 tetramer acetylates IDH2 dimer (Xenopus tropicalis)
H+ [mitochondrial matrix]
NNT dimer transfers proton from NADPH to NAD+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
OGDH complex synthesizes succinyl-CoA from 2-OG (Xenopus tropicalis)
DLD dimer dehydrogenates dihydrolipoyl (Xenopus tropicalis)
H+ [mitochondrial matrix]
OGDH dimer decarboxylates 2-OG (Xenopus tropicalis)
H+ [mitochondrial matrix]
Mitochondrial Uncoupling (Xenopus tropicalis)
AAC1 imports a proton (Xenopus tropicalis)
H+ [mitochondrial matrix]
UCP1 imports a proton (Xenopus tropicalis)
H+ [mitochondrial matrix]
Pyruvate metabolism (Xenopus tropicalis)
FAHD1 dimer hydrolyses OA to PYR (Xenopus tropicalis)
H+ [mitochondrial matrix]
LDHAL6B reduces PYR to LACT (Xenopus tropicalis)
H+ [mitochondrial matrix]
PC carboxylates PYR to OA (Xenopus tropicalis)
H+ [mitochondrial matrix]
PDH complex synthesizes acetyl-CoA from PYR (Xenopus tropicalis)
DLD dimer dehydrogenates dihydrolipoyl (Xenopus tropicalis)
H+ [mitochondrial matrix]
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Xenopus tropicalis)
H+ [mitochondrial matrix]
Regulation of pyruvate metabolism (Xenopus tropicalis)
Regulation of pyruvate dehydrogenase (PDH) complex (Xenopus tropicalis)
GSTZ1 dimer dehalogenates DCA (Xenopus tropicalis)
H+ [mitochondrial matrix]
PDK isozymes phosphorylate PDHC subunit E1 (Xenopus tropicalis)
H+ [mitochondrial matrix]
Respiratory electron transport (Xenopus tropicalis)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Xenopus tropicalis)
H+ [mitochondrial matrix]
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Xenopus tropicalis)
H+ [mitochondrial matrix]
Electron transfer from reduced cytochrome c to molecular oxygen (Xenopus tropicalis)
H+ [mitochondrial matrix]
Malate-aspartate shuttle (Xenopus tropicalis)
MDH2 dimer dehydrogenates MAL (Xenopus tropicalis)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Xenopus tropicalis)
H+ [mitochondrial matrix]
SLC25A18,22 import L-Glu, H+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
Biological oxidations (Xenopus tropicalis)
Phase I - Functionalization of compounds (Xenopus tropicalis)
Cytochrome P450 - arranged by substrate type (Xenopus tropicalis)
Endogenous sterols (Xenopus tropicalis)
CYP11A1 cleaves 20a,22b-DHCHOL (Xenopus tropicalis)
H+ [mitochondrial matrix]
CYP11B1 oxidises 11DCORT (Xenopus tropicalis)
H+ [mitochondrial matrix]
CYP11B2 18-hydroxylates CORST to 18HCORST (Xenopus tropicalis)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Xenopus tropicalis)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Xenopus tropicalis)
H+ [mitochondrial matrix]
Ethanol oxidation (Xenopus tropicalis)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Xenopus tropicalis)
H+ [mitochondrial matrix]
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Xenopus tropicalis)
H+ [mitochondrial matrix]
Metabolism of amino acids and derivatives (Xenopus tropicalis)
Aspartate and asparagine metabolism (Xenopus tropicalis)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Xenopus tropicalis)
H+ [mitochondrial matrix]
SLC25A12,13 exchange L-Glu and L-Asp (Xenopus tropicalis)
H+ [mitochondrial matrix]
Branched-chain amino acid catabolism (Xenopus tropicalis)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Xenopus tropicalis)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Xenopus tropicalis)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Xenopus tropicalis)
H+ [mitochondrial matrix]
BCKDK phosphorylates BCKDH (Xenopus tropicalis)
H+ [mitochondrial matrix]
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Xenopus tropicalis)
H+ [mitochondrial matrix]
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Xenopus tropicalis)
H+ [mitochondrial matrix]
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Xenopus tropicalis)
H+ [mitochondrial matrix]
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Xenopus tropicalis)
H+ [mitochondrial matrix]
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Xenopus tropicalis)
H+ [mitochondrial matrix]
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
Glutamate and glutamine metabolism (Xenopus tropicalis)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Xenopus tropicalis)
H+ [mitochondrial matrix]
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Xenopus tropicalis)
H+ [mitochondrial matrix]
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Xenopus tropicalis)
H+ [mitochondrial matrix]
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Xenopus tropicalis)
H+ [mitochondrial matrix]
Glyoxylate metabolism and glycine degradation (Xenopus tropicalis)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Xenopus tropicalis)
H+ [mitochondrial matrix]
Glycine degradation (Xenopus tropicalis)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Xenopus tropicalis)
H+ [mitochondrial matrix]
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Xenopus tropicalis)
H+ [mitochondrial matrix]
Lysine catabolism (Xenopus tropicalis)
HYKK phosphorylates 5HLYS (Xenopus tropicalis)
H+ [mitochondrial matrix]
OADH complex synthesizes glutaryl-CoA from 2-OA (Xenopus tropicalis)
DHTKD1 dimer decarboxylates 2-OA (Xenopus tropicalis)
H+ [mitochondrial matrix]
DLD dimer dehydrogenates dihydrolipoyl (Xenopus tropicalis)
H+ [mitochondrial matrix]
DLST transfers glutaryl to CoA (Xenopus tropicalis)
H+ [mitochondrial matrix]
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Xenopus tropicalis)
H+ [mitochondrial matrix]
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Xenopus tropicalis)
H+ [mitochondrial matrix]
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
Proline catabolism (Xenopus tropicalis)
ALDH4A1 oxidises L-GluSS to Glu (Xenopus tropicalis)
H+ [mitochondrial matrix]
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Xenopus tropicalis)
H+ [mitochondrial matrix]
PRODH oxidises L-Pro to 1PYR-5COOH (Xenopus tropicalis)
H+ [mitochondrial matrix]
Sulfur amino acid metabolism (Xenopus tropicalis)
Degradation of cysteine and homocysteine (Xenopus tropicalis)
Sulfide oxidation to sulfate (Xenopus tropicalis)
Persulfide sulfur is dioxygenated (Xenopus tropicalis)
H+ [mitochondrial matrix]
Thiosulfate can transfer its sulfur atom to glutathione (Xenopus tropicalis)
H+ [mitochondrial matrix]
Metabolism of carbohydrates and carbohydrate derivatives (Xenopus tropicalis)
Glucose metabolism (Xenopus tropicalis)
Gluconeogenesis (Xenopus tropicalis)
PC carboxylates PYR to OA (Xenopus tropicalis)
H+ [mitochondrial matrix]
Metabolism of lipids (Xenopus tropicalis)
Fatty acid metabolism (Xenopus tropicalis)
Fatty acyl-CoA biosynthesis (Xenopus tropicalis)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Xenopus tropicalis)
H+ [mitochondrial matrix]
Mitochondrial Fatty Acid Beta-Oxidation (Xenopus tropicalis)
mitochondrial fatty acid beta-oxidation of saturated fatty acids (Xenopus tropicalis)
Beta oxidation of butanoyl-CoA to acetyl-CoA (Xenopus tropicalis)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Xenopus tropicalis)
H+ [mitochondrial matrix]
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA (Xenopus tropicalis)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Xenopus tropicalis)
H+ [mitochondrial matrix]
MECR dimer reduces tdec2-CoA to DEC-CoA (Xenopus tropicalis)
H+ [mitochondrial matrix]
Beta oxidation of hexanoyl-CoA to butanoyl-CoA (Xenopus tropicalis)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Xenopus tropicalis)
H+ [mitochondrial matrix]
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA (Xenopus tropicalis)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Xenopus tropicalis)
H+ [mitochondrial matrix]
Beta oxidation of myristoyl-CoA to lauroyl-CoA (Xenopus tropicalis)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Xenopus tropicalis)
H+ [mitochondrial matrix]
Beta oxidation of octanoyl-CoA to hexanoyl-CoA (Xenopus tropicalis)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Xenopus tropicalis)
H+ [mitochondrial matrix]
Beta oxidation of palmitoyl-CoA to myristoyl-CoA (Xenopus tropicalis)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Xenopus tropicalis)
H+ [mitochondrial matrix]
mitochondrial fatty acid beta-oxidation of unsaturated fatty acids (Xenopus tropicalis)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Xenopus tropicalis)
H+ [mitochondrial matrix]
Ketone body metabolism (Xenopus tropicalis)
Synthesis of Ketone Bodies (Xenopus tropicalis)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
Utilization of Ketone Bodies (Xenopus tropicalis)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
Metabolism of steroids (Xenopus tropicalis)
Metabolism of steroid hormones (Xenopus tropicalis)
Estrogen biosynthesis (Xenopus tropicalis)
AKR1B15 reduces EST17b to E1 (Xenopus tropicalis)
H+ [mitochondrial matrix]
Glucocorticoid biosynthesis (Xenopus tropicalis)
CYP11B1 oxidises 11DCORT (Xenopus tropicalis)
H+ [mitochondrial matrix]
Mineralocorticoid biosynthesis (Xenopus tropicalis)
CYP11B2 18-hydroxylates CORST to 18HCORST (Xenopus tropicalis)
H+ [mitochondrial matrix]
CYP11B2 oxidises 11DCORST to CORST (Xenopus tropicalis)
H+ [mitochondrial matrix]
CYP11B2 oxidises 18HCORST to ALDO (Xenopus tropicalis)
H+ [mitochondrial matrix]
Pregnenolone biosynthesis (Xenopus tropicalis)
CYP11A1 cleaves 20a,22b-DHCHOL (Xenopus tropicalis)
H+ [mitochondrial matrix]
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Xenopus tropicalis)
H+ [mitochondrial matrix]
Oxidation of cholesterol to 22beta-hydroxycholesterol (Xenopus tropicalis)
H+ [mitochondrial matrix]
Metabolism of porphyrins (Xenopus tropicalis)
Heme biosynthesis (Xenopus tropicalis)
ALAS condenses SUCC-CoA and Gly to form dALA (Xenopus tropicalis)
H+ [mitochondrial matrix]
Metabolism of vitamins and cofactors (Xenopus tropicalis)
Metabolism of cofactors (Xenopus tropicalis)
Ubiquinol biosynthesis (Xenopus tropicalis)
COQ3 methylates DHDB (Xenopus tropicalis)
H+ [mitochondrial matrix]
COQ3 methylates DeMQ10H2 (Xenopus tropicalis)
H+ [mitochondrial matrix]
COQ4 decarboxylates MHDB (Xenopus tropicalis)
H+ [mitochondrial matrix]
COQ5 methylates MDMQ10H2 (Xenopus tropicalis)
H+ [mitochondrial matrix]
COQ6 hydroxylates DHB (Xenopus tropicalis)
H+ [mitochondrial matrix]
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Xenopus tropicalis)
H+ [mitochondrial matrix]
Metabolism of water-soluble vitamins and cofactors (Xenopus tropicalis)
Cobalamin (Cbl, vitamin B12) transport and metabolism (Xenopus tropicalis)
Cobalamin (Cbl) metabolism (Xenopus tropicalis)
MMAB adenosylates cob(I)alamin (Xenopus tropicalis)
H+ [mitochondrial matrix]
Metabolism of folate and pterines (Xenopus tropicalis)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Xenopus tropicalis)
H+ [mitochondrial matrix]
Nicotinate metabolism (Xenopus tropicalis)
NADK2 dimer phosphorylates NAD+ to NADP+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
Nicotinamide salvage (Xenopus tropicalis)
CARKD dehydrates S-NAD(P)HX to NADPH (Xenopus tropicalis)
H+ [mitochondrial matrix]
Mitochondrial iron-sulfur cluster biogenesis (Xenopus tropicalis)
Electron transport from NADPH to Ferredoxin (Xenopus tropicalis)
FDXR transfers electrons to FDX1,2 (FDX1L) (Xenopus tropicalis)
H+ [mitochondrial matrix]
NADPH transfers electrons to FDXR (Xenopus tropicalis)
H+ [mitochondrial matrix]
Reversible hydration of carbon dioxide (Xenopus tropicalis)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Xenopus tropicalis)
H+ [mitochondrial matrix]
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Xenopus tropicalis)
H+ [mitochondrial matrix]
Metabolism of proteins (Xenopus tropicalis)
Post-translational protein modification (Xenopus tropicalis)
Protein lipoylation (Xenopus tropicalis)
LIPT2 transfers octanoyl group to GCSH (Xenopus tropicalis)
H+ [mitochondrial matrix]
Neuronal System (Xenopus tropicalis)
Transmission across Chemical Synapses (Xenopus tropicalis)
Neurotransmitter clearance (Xenopus tropicalis)
Serotonin clearance from the synaptic cleft (Xenopus tropicalis)
Metabolism of serotonin (Xenopus tropicalis)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Xenopus tropicalis)
H+ [mitochondrial matrix]
Neurotransmitter release cycle (Xenopus tropicalis)
GABA synthesis, release, reuptake and degradation (Xenopus tropicalis)
Degradation of GABA (Xenopus tropicalis)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Xenopus tropicalis)
H+ [mitochondrial matrix]
Signal Transduction (Xenopus tropicalis)
Signaling by Nuclear Receptors (Xenopus tropicalis)
Signaling by Retinoic Acid (Xenopus tropicalis)
PDK isozymes phosphorylate PDHC subunit E1 (Xenopus tropicalis)
H+ [mitochondrial matrix]
Transport of small molecules (Xenopus tropicalis)
Ion channel transport (Xenopus tropicalis)
Stimuli-sensing channels (Xenopus tropicalis)
SLC9B2 exchanges Na+ for H+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
Iron uptake and transport (Xenopus tropicalis)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Xenopus tropicalis)
H+ [mitochondrial matrix]
SLC-mediated transmembrane transport (Xenopus tropicalis)
Transport of inorganic cations/anions and amino acids/oligopeptides (Xenopus tropicalis)
Organic anion transporters (Xenopus tropicalis)
SLC25A18,22 import L-Glu, H+ (Xenopus tropicalis)
H+ [mitochondrial matrix]
External Reference Information
External Reference
hydron [ChEBI:15378]
Participates
as an input of
oxaloacetate + NADH + H+ <=> malate + NAD+ (Gallus gallus)
ALDH2 transforms GTN to NO (Homo sapiens)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Schizosaccharomyces pombe)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Drosophila melanogaster)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Gallus gallus)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Xenopus tropicalis)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Danio rerio)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Sus scrofa)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Bos taurus)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Canis familiaris)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Rattus norvegicus)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Mus musculus)
acetoacetic acid + NADH + H+ <=> beta-hydroxybutyrate + NAD+ (Homo sapiens)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Plasmodium falciparum)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Caenorhabditis elegans)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Drosophila melanogaster)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Gallus gallus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Xenopus tropicalis)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Danio rerio)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Sus scrofa)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Bos taurus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Canis familiaris)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Rattus norvegicus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Mus musculus)
Carbonic anhydrase dehydrates bicarbonate (mitochondria) (Homo sapiens)
BCKDHA or BCKDHB loss-of-function mutants don't synthesize BCAA-CoA (Homo sapiens)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Sus scrofa)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Bos taurus)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Canis familiaris)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Rattus norvegicus)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Mus musculus)
3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestanoate (THCA) (Homo sapiens)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Sus scrofa)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Bos taurus)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Canis familiaris)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Rattus norvegicus)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Mus musculus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Sus scrofa)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Bos taurus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Canis familiaris)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Rattus norvegicus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Mus musculus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Sus scrofa)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Bos taurus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Canis familiaris)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Rattus norvegicus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Mus musculus)
5beta-cholestan-3alpha,7alpha,12alpha,24(S)-tetrol is hydroxylated to 5beta-cholestan-3alpha,7alpha,12alpha,24(S), 27-pentol (Homo sapiens)
5beta-cholestan-3alpha,7alpha,12alpha,24(S),27-pentol is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al (Homo sapiens)
3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,12alpha,24(S)-tetrahydroxy-5beta-cholestanoate (TetraHCA) (Homo sapiens)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Sus scrofa)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Bos taurus)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Canis familiaris)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Rattus norvegicus)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Mus musculus)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Sus scrofa)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Bos taurus)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Canis familiaris)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Rattus norvegicus)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Mus musculus)
5beta-cholestan-3alpha, 7alpha-diol is hydroxylated to 5beta-cholestan-3alpha, 7alpha, 26-triol (Homo sapiens)
3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestanoate (DHCA) (Homo sapiens)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Sus scrofa)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Bos taurus)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Canis familiaris)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Rattus norvegicus)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Mus musculus)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Sus scrofa)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Bos taurus)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Canis familiaris)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Rattus norvegicus)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Mus musculus)
5beta-cholestan-3alpha,7alpha,24(S),27-tetrol is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al (Homo sapiens)
3alpha,7alpha,24(S)-trihydroxy-5beta-cholestan-27-al is oxidized to 3alpha,7alpha,24(S)-trihydroxy-5beta-cholestanoate (3,7,24THCA) (Homo sapiens)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Sus scrofa)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Bos taurus)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Canis familiaris)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Rattus norvegicus)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Mus musculus)
CYP27A1 27-hydroxylates 5bCHOL3a,7a,12a-triol (Homo sapiens)
CYP27A1 does not 27-hydroxylate 5bCHOL3a,7a,12a-triol (Homo sapiens)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Sus scrofa)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Bos taurus)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Canis familiaris)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Rattus norvegicus)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Mus musculus)
CYP27A1 27-hydroxylates 5β-CHOL3α,7α,24(s)-triol (Homo sapiens)
Defective CYP27A1 does not 27-hydroxylate 5β-CHOL3α,7α,24(s)-triol (Homo sapiens)
Defective CYP11B1 does not oxidise 11DCORT (Homo sapiens)
Defective CYP24A1 does not 24-hydroxylate CALTOL (Homo sapiens)
Defective CYP11B2 does not oxidise 18HCORST (Homo sapiens)
Defective CYP11B2 does not oxidise CORST (Homo sapiens)
Defective CYP11B2 does not oxidise 11DCORST (Homo sapiens)
Defective CYP11A1 does not cleave 20a,22b-DHCHOL (Homo sapiens)
CYP24A1 24-hydroxylates CTL (Danio rerio)
CYP24A1 24-hydroxylates CTL (Sus scrofa)
CYP24A1 24-hydroxylates CTL (Bos taurus)
CYP24A1 24-hydroxylates CTL (Canis familiaris)
CYP24A1 24-hydroxylates CTL (Rattus norvegicus)
CYP24A1 24-hydroxylates CTL (Mus musculus)
CYP24A1 24-hydroxylates CTL (Homo sapiens)
CYP27A1 27-hydroxylates CHOL (Sus scrofa)
CYP27A1 27-hydroxylates CHOL (Bos taurus)
CYP27A1 27-hydroxylates CHOL (Canis familiaris)
CYP27A1 27-hydroxylates CHOL (Rattus norvegicus)
CYP27A1 27-hydroxylates CHOL (Mus musculus)
CYP27A1 27-hydroxylates CHOL (Homo sapiens)
CYP11B2 oxidises 18HCORST to ALDO (Xenopus tropicalis)
CYP11B2 oxidises 18HCORST to ALDO (Sus scrofa)
CYP11B2 oxidises 18HCORST to ALDO (Bos taurus)
CYP11B2 oxidises 18HCORST to ALDO (Canis familiaris)
CYP11B2 oxidises 18HCORST to ALDO (Rattus norvegicus)
CYP11B2 oxidises 18HCORST to ALDO (Mus musculus)
CYP11B2 oxidises 18HCORST to ALDO (Homo sapiens)
CYP11B2 18-hydroxylates CORST to 18HCORST (Xenopus tropicalis)
CYP11B2 18-hydroxylates CORST to 18HCORST (Sus scrofa)
CYP11B2 18-hydroxylates CORST to 18HCORST (Bos taurus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Canis familiaris)
CYP11B2 18-hydroxylates CORST to 18HCORST (Rattus norvegicus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Mus musculus)
CYP11B2 18-hydroxylates CORST to 18HCORST (Homo sapiens)
CYP11B2 oxidises 11DCORST to CORST (Xenopus tropicalis)
CYP11B2 oxidises 11DCORST to CORST (Sus scrofa)
CYP11B2 oxidises 11DCORST to CORST (Bos taurus)
CYP11B2 oxidises 11DCORST to CORST (Canis familiaris)
CYP11B2 oxidises 11DCORST to CORST (Rattus norvegicus)
CYP11B2 oxidises 11DCORST to CORST (Mus musculus)
CYP11B2 oxidises 11DCORST to CORST (Homo sapiens)
CYP11B1 oxidises 11DCORT (Xenopus tropicalis)
CYP11B1 oxidises 11DCORT (Sus scrofa)
CYP11B1 oxidises 11DCORT (Bos taurus)
CYP11B1 oxidises 11DCORT (Canis familiaris)
CYP11B1 oxidises 11DCORT (Rattus norvegicus)
CYP11B1 oxidises 11DCORT (Mus musculus)
CYP11B1 oxidises 11DCORT (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Gallus gallus)
CYP11A1 cleaves 20a,22b-DHCHOL (Xenopus tropicalis)
CYP11A1 cleaves 20a,22b-DHCHOL (Danio rerio)
CYP11A1 cleaves 20a,22b-DHCHOL (Sus scrofa)
CYP11A1 cleaves 20a,22b-DHCHOL (Bos taurus)
CYP11A1 cleaves 20a,22b-DHCHOL (Canis familiaris)
CYP11A1 cleaves 20a,22b-DHCHOL (Rattus norvegicus)
CYP11A1 cleaves 20a,22b-DHCHOL (Mus musculus)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Gallus gallus)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Xenopus tropicalis)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Danio rerio)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Sus scrofa)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Bos taurus)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Canis familiaris)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Rattus norvegicus)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Mus musculus)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Gallus gallus)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Xenopus tropicalis)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Danio rerio)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Sus scrofa)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Bos taurus)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Canis familiaris)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Rattus norvegicus)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Mus musculus)
Oxidation of cholesterol to 22beta-hydroxycholesterol (Homo sapiens)
Oxidation of 22beta-hydroxycholesterol to 20alpha,22beta-hydroxycholesterol (Homo sapiens)
CYP11A1 cleaves 20a,22b-DHCHOL (Homo sapiens)
SLC9B2 exchanges Na+ for H+ (Caenorhabditis elegans)
SLC9B2 exchanges Na+ for H+ (Drosophila melanogaster)
SLC9B2 exchanges Na+ for H+ (Gallus gallus)
SLC9B2 exchanges Na+ for H+ (Xenopus tropicalis)
SLC9B2 exchanges Na+ for H+ (Sus scrofa)
SLC9B2 exchanges Na+ for H+ (Bos taurus)
SLC9B2 exchanges Na+ for H+ (Canis familiaris)
SLC9B2 exchanges Na+ for H+ (Mus musculus)
SLC9B2 exchanges Na+ for H+ (Homo sapiens)
ALAS condenses SUCC-CoA and Gly to form dALA (Plasmodium falciparum)
ALAS condenses SUCC-CoA and Gly to form dALA (Saccharomyces cerevisiae)
ALAS condenses SUCC-CoA and Gly to form dALA (Schizosaccharomyces pombe)
ALAS condenses SUCC-CoA and Gly to form dALA (Dictyostelium discoideum)
ALAS condenses SUCC-CoA and Gly to form dALA (Drosophila melanogaster)
ALAS condenses SUCC-CoA and Gly to form dALA (Gallus gallus)
ALAS condenses SUCC-CoA and Gly to form dALA (Xenopus tropicalis)
ALAS condenses SUCC-CoA and Gly to form dALA (Danio rerio)
ALAS condenses SUCC-CoA and Gly to form dALA (Sus scrofa)
ALAS condenses SUCC-CoA and Gly to form dALA (Bos taurus)
ALAS condenses SUCC-CoA and Gly to form dALA (Canis familiaris)
ALAS condenses SUCC-CoA and Gly to form dALA (Rattus norvegicus)
ALAS condenses SUCC-CoA and Gly to form dALA (Mus musculus)
ALAS condenses SUCC-CoA and Gly to form dALA (Homo sapiens)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Saccharomyces cerevisiae)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Schizosaccharomyces pombe)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Dictyostelium discoideum)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Caenorhabditis elegans)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Drosophila melanogaster)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Gallus gallus)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Sus scrofa)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Bos taurus)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Canis familiaris)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Rattus norvegicus)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Mus musculus)
NMNAT3 transfers an adenylyl group from ATP to NAMN to yield NAAD (Homo sapiens)
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Dictyostelium discoideum)
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Caenorhabditis elegans)
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Drosophila melanogaster)
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Gallus gallus)
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Xenopus tropicalis)
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Sus scrofa)
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Canis familiaris)
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Rattus norvegicus)
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Mus musculus)
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Homo sapiens)
beta-methylglutaconyl-CoA + ADP + orthophosphate <=> beta-methylcrotonyl-CoA + ATP + HCO3- (MCCA) (Bos taurus)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Dictyostelium discoideum)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Caenorhabditis elegans)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Drosophila melanogaster)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Gallus gallus)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Xenopus tropicalis)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Danio rerio)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Sus scrofa)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Canis familiaris)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Rattus norvegicus)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Mus musculus)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Homo sapiens)
isovaleryl-CoA + FAD => beta-methylcrotonyl-CoA + FADH2 (Bos taurus)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Plasmodium falciparum)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Saccharomyces cerevisiae)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Schizosaccharomyces pombe)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Dictyostelium discoideum)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Caenorhabditis elegans)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Gallus gallus)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Xenopus tropicalis)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Sus scrofa)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Bos taurus)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Canis familiaris)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Rattus norvegicus)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Homo sapiens)
GSR catalyzes glutathione (oxidized) + NADPH + H+ => 2 glutathione (reduced) + NADP+ (Mus musculus)
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Caenorhabditis elegans)
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Drosophila melanogaster)
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Gallus gallus)
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Bos taurus)
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Rattus norvegicus)
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Homo sapiens)
TXNRD2 catalyzes the reduction of TXN2 by NADPH (Mus musculus)
MECR dimer reduces tdec2-CoA to DEC-CoA (Saccharomyces cerevisiae)
MECR dimer reduces tdec2-CoA to DEC-CoA (Schizosaccharomyces pombe)
MECR dimer reduces tdec2-CoA to DEC-CoA (Dictyostelium discoideum)
MECR dimer reduces tdec2-CoA to DEC-CoA (Caenorhabditis elegans)
MECR dimer reduces tdec2-CoA to DEC-CoA (Drosophila melanogaster)
MECR dimer reduces tdec2-CoA to DEC-CoA (Gallus gallus)
MECR dimer reduces tdec2-CoA to DEC-CoA (Xenopus tropicalis)
MECR dimer reduces tdec2-CoA to DEC-CoA (Danio rerio)
MECR dimer reduces tdec2-CoA to DEC-CoA (Sus scrofa)
MECR dimer reduces tdec2-CoA to DEC-CoA (Bos taurus)
MECR dimer reduces tdec2-CoA to DEC-CoA (Canis familiaris)
MECR dimer reduces tdec2-CoA to DEC-CoA (Rattus norvegicus)
MECR dimer reduces tdec2-CoA to DEC-CoA (Homo sapiens)
MECR dimer reduces tdec2-CoA to DEC-CoA (Mus musculus)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Saccharomyces cerevisiae)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Schizosaccharomyces pombe)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Dictyostelium discoideum)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Caenorhabditis elegans)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Drosophila melanogaster)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Gallus gallus)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Xenopus tropicalis)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Danio rerio)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Sus scrofa)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Bos taurus)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Canis familiaris)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Rattus norvegicus)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Mus musculus)
SOD2 catalyzes 2H+ + 2O2.- => O2 + H2O2 (mitochondrial matrix) (Homo sapiens)
PXLP-K754-GLDC dimer decarboxylates Gly (Saccharomyces cerevisiae)
PXLP-K754-GLDC dimer decarboxylates Gly (Schizosaccharomyces pombe)
PXLP-K754-GLDC dimer decarboxylates Gly (Dictyostelium discoideum)
PXLP-K754-GLDC dimer decarboxylates Gly (Caenorhabditis elegans)
PXLP-K754-GLDC dimer decarboxylates Gly (Drosophila melanogaster)
PXLP-K754-GLDC dimer decarboxylates Gly (Gallus gallus)
PXLP-K754-GLDC dimer decarboxylates Gly (Danio rerio)
PXLP-K754-GLDC dimer decarboxylates Gly (Sus scrofa)
PXLP-K754-GLDC dimer decarboxylates Gly (Bos taurus)
PXLP-K754-GLDC dimer decarboxylates Gly (Canis familiaris)
PXLP-K754-GLDC dimer decarboxylates Gly (Rattus norvegicus)
PXLP-K754-GLDC dimer decarboxylates Gly (Mus musculus)
PXLP-K754-GLDC dimer decarboxylates Gly (Homo sapiens)
LIAS synthesizes lipoyl-GCSH (Sus scrofa)
LIAS synthesizes lipoyl-GCSH (Drosophila melanogaster)
LIAS synthesizes lipoyl-GCSH (Gallus gallus)
LIAS synthesizes lipoyl-GCSH (Danio rerio)
LIAS synthesizes lipoyl-GCSH (Bos taurus)
LIAS synthesizes lipoyl-GCSH (Canis familiaris)
LIAS synthesizes lipoyl-GCSH (Rattus norvegicus)
LIAS synthesizes lipoyl-GCSH (Mus musculus)
LIAS synthesizes lipoyl-GCSH (Homo sapiens)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Plasmodium falciparum)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Saccharomyces cerevisiae)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Schizosaccharomyces pombe)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Dictyostelium discoideum)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Xenopus tropicalis)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Danio rerio)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Sus scrofa)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Bos taurus)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Canis familiaris)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Rattus norvegicus)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Mus musculus)
2xHSD17B8:2xCBR4 reduces 3OA-ACP to 3HA-ACP (Homo sapiens)
Thiosulfate can transfer its sulfur atom to glutathione (Xenopus tropicalis)
Thiosulfate can transfer its sulfur atom to glutathione (Sus scrofa)
Thiosulfate can transfer its sulfur atom to glutathione (Bos taurus)
Thiosulfate can transfer its sulfur atom to glutathione (Canis familiaris)
Thiosulfate can transfer its sulfur atom to glutathione (Rattus norvegicus)
Thiosulfate can transfer its sulfur atom to glutathione (Mus musculus)
Thiosulfate can transfer its sulfur atom to glutathione (Homo sapiens)
Electron transfer from ubiquinol to cytochrome c of complex III (Saccharomyces cerevisiae)
Electron transfer from ubiquinol to cytochrome c of complex III (Schizosaccharomyces pombe)
Electron transfer from ubiquinol to cytochrome c of complex III (Dictyostelium discoideum)
Electron transfer from ubiquinol to cytochrome c of complex III (Caenorhabditis elegans)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Drosophila melanogaster)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Xenopus tropicalis)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Canis familiaris)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Gallus gallus)
Electron transfer from ubiquinol to cytochrome c of complex III (Gallus gallus)
Electron transfer from reduced cytochrome c to molecular oxygen (Gallus gallus)
Electron transfer from reduced cytochrome c to molecular oxygen (Xenopus tropicalis)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Danio rerio)
Electron transfer from ubiquinol to cytochrome c of complex III (Danio rerio)
Electron transfer from reduced cytochrome c to molecular oxygen (Danio rerio)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Sus scrofa)
Electron transfer from ubiquinol to cytochrome c of complex III (Sus scrofa)
Electron transfer from reduced cytochrome c to molecular oxygen (Sus scrofa)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Bos taurus)
Electron transfer from ubiquinol to cytochrome c of complex III (Bos taurus)
Electron transfer from reduced cytochrome c to molecular oxygen (Bos taurus)
Electron transfer from reduced cytochrome c to molecular oxygen (Canis familiaris)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Rattus norvegicus)
Electron transfer from ubiquinol to cytochrome c of complex III (Rattus norvegicus)
Electron transfer from reduced cytochrome c to molecular oxygen (Rattus norvegicus)
Electron transfer from reduced cytochrome c to molecular oxygen (Homo sapiens)
Electron transfer from reduced cytochrome c to molecular oxygen (Mus musculus)
Electron transfer from ubiquinol to cytochrome c of complex III (Mus musculus)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Mus musculus)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Dictyostelium discoideum)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Caenorhabditis elegans)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Drosophila melanogaster)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Gallus gallus)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Xenopus tropicalis)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Danio rerio)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Sus scrofa)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Bos taurus)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Canis familiaris)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Rattus norvegicus)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Mus musculus)
DHTKD1 dimer decarboxylates 2-OA (Dictyostelium discoideum)
DLST transfers glutaryl to CoA (Dictyostelium discoideum)
DHTKD1 dimer decarboxylates 2-OA (Caenorhabditis elegans)
DLST transfers glutaryl to CoA (Caenorhabditis elegans)
DHTKD1 dimer decarboxylates 2-OA (Drosophila melanogaster)
DLST transfers glutaryl to CoA (Drosophila melanogaster)
DHTKD1 dimer decarboxylates 2-OA (Gallus gallus)
DLST transfers glutaryl to CoA (Gallus gallus)
DHTKD1 dimer decarboxylates 2-OA (Xenopus tropicalis)
DLST transfers glutaryl to CoA (Xenopus tropicalis)
DHTKD1 dimer decarboxylates 2-OA (Danio rerio)
DLST transfers glutaryl to CoA (Danio rerio)
DHTKD1 dimer decarboxylates 2-OA (Sus scrofa)
DLST transfers glutaryl to CoA (Sus scrofa)
DHTKD1 dimer decarboxylates 2-OA (Bos taurus)
DLST transfers glutaryl to CoA (Bos taurus)
DHTKD1 dimer decarboxylates 2-OA (Canis familiaris)
DLST transfers glutaryl to CoA (Canis familiaris)
DHTKD1 dimer decarboxylates 2-OA (Rattus norvegicus)
DLST transfers glutaryl to CoA (Rattus norvegicus)
DHTKD1 dimer decarboxylates 2-OA (Mus musculus)
DLST transfers glutaryl to CoA (Mus musculus)
DHTKD1 dimer decarboxylates 2-OA (Homo sapiens)
DLST transfers glutaryl to CoA (Homo sapiens)
glutaryl-CoA + FAD => crotonyl-CoA + FADH2 + CO2 (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Homo sapiens)
Electron transfer from ubiquinol to cytochrome c of complex III (Homo sapiens)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Caenorhabditis elegans)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Gallus gallus)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Xenopus tropicalis)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Sus scrofa)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Bos taurus)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Canis familiaris)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Rattus norvegicus)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Mus musculus)
Reduction of 2-trans-4-cis-decadienoyl-CoA to form 3-trans-decenoyl-CoA (Homo sapiens)
Electron transfer from ubiquinol to cytochrome c of complex III (Drosophila melanogaster)
Electron transfer from reduced cytochrome c to molecular oxygen (Drosophila melanogaster)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Drosophila melanogaster)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Gallus gallus)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Xenopus tropicalis)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Danio rerio)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Sus scrofa)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Bos taurus)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Canis familiaris)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Rattus norvegicus)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Mus musculus)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Homo sapiens)
FTMT 24mer oxidises 4Fe2+ to 4Fe(3+)O(OH) (Caenorhabditis elegans)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Saccharomyces cerevisiae)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Schizosaccharomyces pombe)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Dictyostelium discoideum)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Drosophila melanogaster)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Gallus gallus)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Xenopus tropicalis)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Danio rerio)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Sus scrofa)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Bos taurus)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Canis familiaris)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Rattus norvegicus)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Mus musculus)
HMPhOH is hydroxylated to MDMQ6H2 by HMPhOH monooxygenase (Saccharomyces cerevisiae)
COQ4 decarboxylates MHDB (Saccharomyces cerevisiae)
COQ4 decarboxylates MHDB (Schizosaccharomyces pombe)
COQ4 decarboxylates MHDB (Dictyostelium discoideum)
COQ4 decarboxylates MHDB (Caenorhabditis elegans)
COQ4 decarboxylates MHDB (Drosophila melanogaster)
COQ4 decarboxylates MHDB (Gallus gallus)
COQ4 decarboxylates MHDB (Xenopus tropicalis)
COQ4 decarboxylates MHDB (Danio rerio)
COQ4 decarboxylates MHDB (Sus scrofa)
COQ4 decarboxylates MHDB (Bos taurus)
COQ4 decarboxylates MHDB (Canis familiaris)
COQ4 decarboxylates MHDB (Rattus norvegicus)
COQ4 decarboxylates MHDB (Mus musculus)
COQ4 decarboxylates MHDB (Homo sapiens)
Unknown enzyme hydroxylates DMPhOH (Homo sapiens)
COQ7:COQ9 octamer hydroxylates DMQ10H2 (Homo sapiens)
COQ6 hydroxylates DHB (Saccharomyces cerevisiae)
COQ6 hydroxylates DHB (Schizosaccharomyces pombe)
COQ6 hydroxylates DHB (Dictyostelium discoideum)
COQ6 hydroxylates DHB (Drosophila melanogaster)
COQ6 hydroxylates DHB (Gallus gallus)
COQ6 hydroxylates DHB (Xenopus tropicalis)
COQ6 hydroxylates DHB (Danio rerio)
COQ6 hydroxylates DHB (Sus scrofa)
COQ6 hydroxylates DHB (Bos taurus)
COQ6 hydroxylates DHB (Canis familiaris)
COQ6 hydroxylates DHB (Rattus norvegicus)
COQ6 hydroxylates DHB (Mus musculus)
COQ6 hydroxylates DHB (Homo sapiens)
COQ6 hydroxylates DHB (Caenorhabditis elegans)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Caenorhabditis elegans)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Drosophila melanogaster)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Saccharomyces cerevisiae)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Schizosaccharomyces pombe)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Xenopus tropicalis)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Rattus norvegicus)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Gallus gallus)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Canis familiaris)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Sus scrofa)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Bos taurus)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Mus musculus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Dictyostelium discoideum)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Caenorhabditis elegans)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Drosophila melanogaster)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Gallus gallus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Xenopus tropicalis)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Danio rerio)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Sus scrofa)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Bos taurus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Canis familiaris)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Rattus norvegicus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Mus musculus)
alpha-ketoglutarate + NH4+ + NAD(P)H + H+ <=> glutamate + NAD(P)+ (GLUD1,2) (Homo sapiens)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Plasmodium falciparum)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Saccharomyces cerevisiae)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Schizosaccharomyces pombe)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Dictyostelium discoideum)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Caenorhabditis elegans)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Drosophila melanogaster)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Gallus gallus)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Xenopus tropicalis)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Danio rerio)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Sus scrofa)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Bos taurus)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Canis familiaris)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Rattus norvegicus)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Mus musculus)
PYCR1 decamer reduces (S)-1-pyrroline-5-carboxylate to L-Pro (Homo sapiens)
glutamate + ATP + NADPH + H+ => L-glutamate gamma-semialdehyde + NADP+ + ADP + orthophosphate [P5CS] (Homo sapiens)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Saccharomyces cerevisiae)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Schizosaccharomyces pombe)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Caenorhabditis elegans)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Drosophila melanogaster)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Danio rerio)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Rattus norvegicus)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Dictyostelium discoideum)
OGDH dimer decarboxylates 2-OG (Plasmodium falciparum)
OGDH dimer decarboxylates 2-OG (Dictyostelium discoideum)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Caenorhabditis elegans)
LDHAL6B reduces PYR to LACT (Caenorhabditis elegans)
LDHAL6B reduces PYR to LACT (Drosophila melanogaster)
LDHAL6B reduces PYR to LACT (Gallus gallus)
LDHAL6B reduces PYR to LACT (Xenopus tropicalis)
LDHAL6B reduces PYR to LACT (Danio rerio)
LDHAL6B reduces PYR to LACT (Canis familiaris)
LDHAL6B reduces PYR to LACT (Rattus norvegicus)
LDHAL6B reduces PYR to LACT (Mus musculus)
LDHAL6B reduces PYR to LACT (Homo sapiens)
OGDH dimer decarboxylates 2-OG (Saccharomyces cerevisiae)
FAHD1 dimer hydrolyses OA to PYR (Saccharomyces cerevisiae)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Saccharomyces cerevisiae)
OGDH dimer decarboxylates 2-OG (Schizosaccharomyces pombe)
FAHD1 dimer hydrolyses OA to PYR (Schizosaccharomyces pombe)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Schizosaccharomyces pombe)
FAHD1 dimer hydrolyses OA to PYR (Dictyostelium discoideum)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Dictyostelium discoideum)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Xenopus tropicalis)
FAHD1 dimer hydrolyses OA to PYR (Drosophila melanogaster)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Drosophila melanogaster)
FAHD1 dimer hydrolyses OA to PYR (Gallus gallus)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Gallus gallus)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Sus scrofa)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Bos taurus)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Canis familiaris)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Rattus norvegicus)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Mus musculus)
PDH E1 decarboxylates PYR, transferring acetyl to DLAT (Homo sapiens)
FAHD1 dimer hydrolyses OA to PYR (Caenorhabditis elegans)
OGDH dimer decarboxylates 2-OG (Caenorhabditis elegans)
OGDH dimer decarboxylates 2-OG (Drosophila melanogaster)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Gallus gallus)
OGDH dimer decarboxylates 2-OG (Gallus gallus)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Xenopus tropicalis)
OGDH dimer decarboxylates 2-OG (Xenopus tropicalis)
NADPH transfers electrons to FDXR (Plasmodium falciparum)
NADPH transfers electrons to FDXR (Saccharomyces cerevisiae)
NADPH transfers electrons to FDXR (Schizosaccharomyces pombe)
NADPH transfers electrons to FDXR (Dictyostelium discoideum)
NADPH transfers electrons to FDXR (Caenorhabditis elegans)
NADPH transfers electrons to FDXR (Drosophila melanogaster)
NADPH transfers electrons to FDXR (Gallus gallus)
NADPH transfers electrons to FDXR (Xenopus tropicalis)
NADPH transfers electrons to FDXR (Danio rerio)
NADPH transfers electrons to FDXR (Sus scrofa)
NADPH transfers electrons to FDXR (Bos taurus)
NADPH transfers electrons to FDXR (Canis familiaris)
NADPH transfers electrons to FDXR (Rattus norvegicus)
NADPH transfers electrons to FDXR (Mus musculus)
NADPH transfers electrons to FDXR (Homo sapiens)
FAHD1 dimer hydrolyses OA to PYR (Xenopus tropicalis)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Sus scrofa)
FAHD1 dimer hydrolyses OA to PYR (Sus scrofa)
FAHD1 dimer hydrolyses OA to PYR (Rattus norvegicus)
FAHD1 dimer hydrolyses OA to PYR (Mus musculus)
FAHD1 dimer hydrolyses OA to PYR (Homo sapiens)
FAHD1 dimer hydrolyses OA to PYR (Danio rerio)
OGDH dimer decarboxylates 2-OG (Danio rerio)
OGDH dimer decarboxylates 2-OG (Homo sapiens)
OGDH dimer decarboxylates 2-OG (Sus scrofa)
OGDH dimer decarboxylates 2-OG (Canis familiaris)
FAHD1 dimer hydrolyses OA to PYR (Canis familiaris)
OGDH dimer decarboxylates 2-OG (Mus musculus)
OGDH dimer decarboxylates 2-OG (Bos taurus)
FAHD1 dimer hydrolyses OA to PYR (Bos taurus)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Bos taurus)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Mus musculus)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Homo sapiens)
lysine + alpha-ketoglutarate +NADPH + H+ => saccharopine + NADP+ + H2O (Canis familiaris)
OGDH dimer decarboxylates 2-OG (Rattus norvegicus)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Dictyostelium discoideum)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Caenorhabditis elegans)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Drosophila melanogaster)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Gallus gallus)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Xenopus tropicalis)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Sus scrofa)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Bos taurus)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Canis familiaris)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Rattus norvegicus)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Mus musculus)
alpha-methylbutyryl-CoA + FAD => tiglyl-CoA + FADH2 (Homo sapiens)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Dictyostelium discoideum)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Caenorhabditis elegans)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Drosophila melanogaster)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Gallus gallus)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Xenopus tropicalis)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Danio rerio)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Sus scrofa)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Bos taurus)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Canis familiaris)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Rattus norvegicus)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Mus musculus)
alpha-methylacetoacetyl-CoA + NADH + H+ <=> alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ (Homo sapiens)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Dictyostelium discoideum)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Caenorhabditis elegans)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Drosophila melanogaster)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Gallus gallus)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Xenopus tropicalis)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Danio rerio)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Sus scrofa)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Bos taurus)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Canis familiaris)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Rattus norvegicus)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Mus musculus)
methylmalonyl semialdehyde + NADH + H+ <=> beta-hydroxyisobutyrate + NAD+ (Homo sapiens)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Dictyostelium discoideum)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Caenorhabditis elegans)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Gallus gallus)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Xenopus tropicalis)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Danio rerio)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Sus scrofa)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Bos taurus)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Canis familiaris)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Mus musculus)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Homo sapiens)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Plasmodium falciparum)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Dictyostelium discoideum)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Caenorhabditis elegans)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Drosophila melanogaster)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Gallus gallus)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Xenopus tropicalis)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Danio rerio)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Sus scrofa)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Bos taurus)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Canis familiaris)
isobutyryl-CoA + FAD => methacrylyl-CoA + FADH2 (Rattus norvegicus)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Rattus norvegicus)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Homo sapiens)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Mus musculus)
as an output of
protoporphyrin IX + Fe++ => heme + 2 H+ (Gallus gallus)
pyruvate + H+ [cytosol] => pyruvate + H+ [mitochondrial matrix] (Gallus gallus)
pyruvate + CoASH + NAD+ => acetylCoA + CO2 + NADH + H+ (Gallus gallus)
isocitrate + NAD+ => 2-oxoglutarate (alpha-ketoglutarate) + CO2 + NADH + H+ (Gallus gallus)
2-oxoglutarate (alpha-ketoglutarate) + CoASH + NAD+ => succinylCoA + CO2 + NADH + H+ (Gallus gallus)
malate + NAD+ <=> oxaloacetate + NADH + H+ (Gallus gallus)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Schizosaccharomyces pombe)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Homo sapiens)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Drosophila melanogaster)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Gallus gallus)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Xenopus tropicalis)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Danio rerio)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Sus scrofa)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Bos taurus)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Canis familiaris)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Rattus norvegicus)
D-beta hydroxybutyrate+NAD+ <=> acetoacetate+NADH+H+ (Mus musculus)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Plasmodium falciparum)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Caenorhabditis elegans)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Drosophila melanogaster)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Gallus gallus)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Xenopus tropicalis)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Danio rerio)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Sus scrofa)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Bos taurus)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Canis familiaris)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Rattus norvegicus)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Mus musculus)
Carbonic anhydrase hydrates carbon dioxide (mitochondria) (Homo sapiens)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Saccharomyces cerevisiae)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Schizosaccharomyces pombe)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Dictyostelium discoideum)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Caenorhabditis elegans)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Drosophila melanogaster)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Gallus gallus)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Xenopus tropicalis)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Danio rerio)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Sus scrofa)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Bos taurus)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Canis familiaris)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Rattus norvegicus)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Mus musculus)
5-hydroxyindole acetaldehyde to 5-hydroxyindole acetic acid (Homo sapiens)
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Sus scrofa)
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Bos taurus)
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Canis familiaris)
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Rattus norvegicus)
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Mus musculus)
5beta-cholestan-3alpha,7alpha,12alpha,27-tetrol is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-27-al (Homo sapiens)
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Sus scrofa)
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Bos taurus)
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Canis familiaris)
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Rattus norvegicus)
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Mus musculus)
5beta-cholestan-3alpha, 7alpha, 26-triol is oxidized to 3alpha, 7alpha-dihydroxy-5beta-cholestan-26-al (Homo sapiens)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Saccharomyces cerevisiae)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Schizosaccharomyces pombe)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Dictyostelium discoideum)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Caenorhabditis elegans)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Drosophila melanogaster)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Xenopus tropicalis)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Danio rerio)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Sus scrofa)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Bos taurus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Canis familiaris)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Rattus norvegicus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Mus musculus)
ALDH1B1 tetramer oxidises CH3CHO to CH3COOH (Homo sapiens)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Saccharomyces cerevisiae)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Schizosaccharomyces pombe)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Dictyostelium discoideum)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Caenorhabditis elegans)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Drosophila melanogaster)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Gallus gallus)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Xenopus tropicalis)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Danio rerio)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Sus scrofa)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Bos taurus)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Canis familiaris)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Rattus norvegicus)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Mus musculus)
acetaldehyde + NAD+ => acetate + NADH + H+ [mitochondrial] (Homo sapiens)
AKR1B15 reduces EST17b to E1 (Saccharomyces cerevisiae)
AKR1B15 reduces EST17b to E1 (Schizosaccharomyces pombe)
AKR1B15 reduces EST17b to E1 (Dictyostelium discoideum)
AKR1B15 reduces EST17b to E1 (Caenorhabditis elegans)
AKR1B15 reduces EST17b to E1 (Drosophila melanogaster)
AKR1B15 reduces EST17b to E1 (Gallus gallus)
AKR1B15 reduces EST17b to E1 (Xenopus tropicalis)
AKR1B15 reduces EST17b to E1 (Danio rerio)
AKR1B15 reduces EST17b to E1 (Bos taurus)
AKR1B15 reduces EST17b to E1 (Rattus norvegicus)
AKR1B15 reduces EST17b to E1 (Mus musculus)
AKR1B15 reduces EST17b to E1 (Homo sapiens)
Nudt8 hydrolyzes CoA-SH to PPANT (Mus musculus)
NUDT8 hydrolyzes CoA-SH to PPANT (Homo sapiens)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Caenorhabditis elegans)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Drosophila melanogaster)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Gallus gallus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Xenopus tropicalis)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Sus scrofa)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Bos taurus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Canis familiaris)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Rattus norvegicus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Mus musculus)
ALDH1L2 dehydrogenates 10-formyl-THFPG to THFPG (Homo sapiens)
Letm1 exchanges protons (mitochondrial intermembrane space) for calcium (mitochondrial matrix) (Mus musculus)
LETM1 exchanges protons (mitochondrial intermembrane space) for calcium (mitochondrial matrix) (Homo sapiens)
FECH binds Fe2+ to PRIN9 to form heme (Plasmodium falciparum)
FECH binds Fe2+ to PRIN9 to form heme (Saccharomyces cerevisiae)
FECH binds Fe2+ to PRIN9 to form heme (Schizosaccharomyces pombe)
FECH binds Fe2+ to PRIN9 to form heme (Dictyostelium discoideum)
FECH binds Fe2+ to PRIN9 to form heme (Caenorhabditis elegans)
FECH binds Fe2+ to PRIN9 to form heme (Drosophila melanogaster)
FECH binds Fe2+ to PRIN9 to form heme (Gallus gallus)
FECH binds Fe2+ to PRIN9 to form heme (Danio rerio)
FECH binds Fe2+ to PRIN9 to form heme (Bos taurus)
FECH binds Fe2+ to PRIN9 to form heme (Canis familiaris)
FECH binds Fe2+ to PRIN9 to form heme (Rattus norvegicus)
FECH binds Fe2+ to PRIN9 to form heme (Mus musculus)
FECH binds Fe2+ to PRIN9 to form heme (Homo sapiens)
FECH binds Fe2+ to PRIN9 to form heme (Sus scrofa)
AAC1 imports a proton (Plasmodium falciparum)
AAC1 imports a proton (Saccharomyces cerevisiae)
AAC1 imports a proton (Schizosaccharomyces pombe)
AAC1 imports a proton (Dictyostelium discoideum)
AAC1 imports a proton (Caenorhabditis elegans)
AAC1 imports a proton (Drosophila melanogaster)
AAC1 imports a proton (Gallus gallus)
AAC1 imports a proton (Xenopus tropicalis)
AAC1 imports a proton (Danio rerio)
AAC1 imports a proton (Sus scrofa)
AAC1 imports a proton (Bos taurus)
AAC1 imports a proton (Canis familiaris)
AAC1 imports a proton (Rattus norvegicus)
AAC1 imports a proton (Mus musculus)
AAC1 imports a proton (Homo sapiens)
UCP1 imports a proton (Xenopus tropicalis)
UCP1 imports a proton (Danio rerio)
UCP1 imports a proton (Bos taurus)
UCP1 imports a proton (Canis familiaris)
UCP1 imports a proton (Rattus norvegicus)
UCP1 imports a proton (Mus musculus)
UCP1 imports a proton (Homo sapiens)
The proton is delivered to the matrix side (Homo sapiens)
NADK2 dimer phosphorylates NAD+ to NADP+ (Plasmodium falciparum)
NADK2 dimer phosphorylates NAD+ to NADP+ (Caenorhabditis elegans)
NADK2 dimer phosphorylates NAD+ to NADP+ (Drosophila melanogaster)
NADK2 dimer phosphorylates NAD+ to NADP+ (Gallus gallus)
NADK2 dimer phosphorylates NAD+ to NADP+ (Xenopus tropicalis)
NADK2 dimer phosphorylates NAD+ to NADP+ (Sus scrofa)
NADK2 dimer phosphorylates NAD+ to NADP+ (Bos taurus)
NADK2 dimer phosphorylates NAD+ to NADP+ (Canis familiaris)
NADK2 dimer phosphorylates NAD+ to NADP+ (Rattus norvegicus)
NADK2 dimer phosphorylates NAD+ to NADP+ (Mus musculus)
NADK2 dimer phosphorylates NAD+ to NADP+ (Homo sapiens)
CARKD dehydrates S-NAD(P)HX to NADPH (Plasmodium falciparum)
CARKD dehydrates S-NAD(P)HX to NADPH (Saccharomyces cerevisiae)
CARKD dehydrates S-NAD(P)HX to NADPH (Schizosaccharomyces pombe)
CARKD dehydrates S-NAD(P)HX to NADPH (Dictyostelium discoideum)
CARKD dehydrates S-NAD(P)HX to NADPH (Caenorhabditis elegans)
CARKD dehydrates S-NAD(P)HX to NADPH (Drosophila melanogaster)
CARKD dehydrates S-NAD(P)HX to NADPH (Gallus gallus)
CARKD dehydrates S-NAD(P)HX to NADPH (Xenopus tropicalis)
CARKD dehydrates S-NAD(P)HX to NADPH (Danio rerio)
CARKD dehydrates S-NAD(P)HX to NADPH (Sus scrofa)
CARKD dehydrates S-NAD(P)HX to NADPH (Bos taurus)
CARKD dehydrates S-NAD(P)HX to NADPH (Canis familiaris)
CARKD dehydrates S-NAD(P)HX to NADPH (Rattus norvegicus)
CARKD dehydrates S-NAD(P)HX to NADPH (Mus musculus)
CARKD dehydrates S-NAD(P)HX to NADPH (Homo sapiens)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Gallus gallus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Xenopus tropicalis)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Danio rerio)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Sus scrofa)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Bos taurus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Canis familiaris)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Rattus norvegicus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Mus musculus)
ALDH4A1 oxidizes 1PYR-3OH-5COOH (Homo sapiens)
ALDH4A1 oxidises L-GluSS to Glu (Gallus gallus)
ALDH4A1 oxidises L-GluSS to Glu (Xenopus tropicalis)
ALDH4A1 oxidises L-GluSS to Glu (Danio rerio)
ALDH4A1 oxidises L-GluSS to Glu (Sus scrofa)
ALDH4A1 oxidises L-GluSS to Glu (Bos taurus)
ALDH4A1 oxidises L-GluSS to Glu (Canis familiaris)
ALDH4A1 oxidises L-GluSS to Glu (Rattus norvegicus)
ALDH4A1 oxidises L-GluSS to Glu (Mus musculus)
ALDH4A1 oxidises L-GluSS to Glu (Homo sapiens)
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Dictyostelium discoideum)
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Caenorhabditis elegans)
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Drosophila melanogaster)
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Gallus gallus)
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Xenopus tropicalis)
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Sus scrofa)
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Bos taurus)
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Canis familiaris)
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Rattus norvegicus)
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Mus musculus)
beta-methylcrotonyl-CoA + ATP + HCO3- <=> beta-methylglutaconyl-CoA + ADP + orthophosphate + H2O (MCCA) (Homo sapiens)
Enzyme-bound ATP is released (Caenorhabditis elegans)
Enzyme-bound ATP is released (Drosophila melanogaster)
Enzyme-bound ATP is released (Gallus gallus)
Enzyme-bound ATP is released (Danio rerio)
Enzyme-bound ATP is released (Sus scrofa)
Enzyme-bound ATP is released (Bos taurus)
Enzyme-bound ATP is released (Canis familiaris)
Enzyme-bound ATP is released (Mus musculus)
Enzyme-bound ATP is released (Homo sapiens)
Enzyme-bound ATP is released (Rattus norvegicus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Plasmodium falciparum)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Xenopus tropicalis)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Saccharomyces cerevisiae)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Schizosaccharomyces pombe)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Dictyostelium discoideum)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Caenorhabditis elegans)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Drosophila melanogaster)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Gallus gallus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Danio rerio)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Sus scrofa)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Bos taurus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Canis familiaris)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Rattus norvegicus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Mus musculus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Homo sapiens)
GSTZ1 dimer dehalogenates DCA (Dictyostelium discoideum)
GSTZ1 dimer dehalogenates DCA (Caenorhabditis elegans)
GSTZ1 dimer dehalogenates DCA (Drosophila melanogaster)
GSTZ1 dimer dehalogenates DCA (Gallus gallus)
GSTZ1 dimer dehalogenates DCA (Xenopus tropicalis)
GSTZ1 dimer dehalogenates DCA (Danio rerio)
GSTZ1 dimer dehalogenates DCA (Sus scrofa)
GSTZ1 dimer dehalogenates DCA (Bos taurus)
GSTZ1 dimer dehalogenates DCA (Canis familiaris)
GSTZ1 dimer dehalogenates DCA (Rattus norvegicus)
GSTZ1 dimer dehalogenates DCA (Mus musculus)
GSTZ1 dimer dehalogenates DCA (Homo sapiens)
GS-MCA spontaneously hydrolyzes (Homo sapiens)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Gallus gallus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Xenopus tropicalis)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Danio rerio)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Sus scrofa)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Bos taurus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Canis familiaris)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Rattus norvegicus)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Mus musculus)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Saccharomyces cerevisiae)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Schizosaccharomyces pombe)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Dictyostelium discoideum)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Caenorhabditis elegans)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Drosophila melanogaster)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Xenopus tropicalis)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Sus scrofa)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Bos taurus)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Canis familiaris)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Rattus norvegicus)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Mus musculus)
PRODH2:FAD dimer dehydrogenates HPRO to 1-pyrroline-3-hydroxy-5-carboxylate (Homo sapiens)
ALDH4A1 converts 1PYR-3OH-5COOH to 4-OH-L-glutamate (Homo sapiens)
LIPT2 transfers octanoyl group to GCSH (Saccharomyces cerevisiae)
LIPT2 transfers octanoyl group to GCSH (Schizosaccharomyces pombe)
LIPT2 transfers octanoyl group to GCSH (Dictyostelium discoideum)
LIPT2 transfers octanoyl group to GCSH (Caenorhabditis elegans)
LIPT2 transfers octanoyl group to GCSH (Xenopus tropicalis)
LIPT2 transfers octanoyl group to GCSH (Sus scrofa)
LIPT2 transfers octanoyl group to GCSH (Drosophila melanogaster)
LIPT2 transfers octanoyl group to GCSH (Gallus gallus)
LIPT2 transfers octanoyl group to GCSH (Danio rerio)
LIPT2 transfers octanoyl group to GCSH (Bos taurus)
LIPT2 transfers octanoyl group to GCSH (Canis familiaris)
LIPT2 transfers octanoyl group to GCSH (Rattus norvegicus)
LIPT2 transfers octanoyl group to GCSH (Mus musculus)
LIPT2 transfers octanoyl group to GCSH (Homo sapiens)
ACAT1 tetramer acetylates IDH2 dimer (Plasmodium falciparum)
ACAT1 tetramer acetylates IDH2 dimer (Caenorhabditis elegans)
ACAT1 tetramer acetylates IDH2 dimer (Gallus gallus)
ACAT1 tetramer acetylates IDH2 dimer (Xenopus tropicalis)
ACAT1 tetramer acetylates IDH2 dimer (Danio rerio)
ACAT1 tetramer acetylates IDH2 dimer (Sus scrofa)
ACAT1 tetramer acetylates IDH2 dimer (Bos taurus)
ACAT1 tetramer acetylates IDH2 dimer (Canis familiaris)
ACAT1 tetramer acetylates IDH2 dimer (Rattus norvegicus)
ACAT1 tetramer acetylates IDH2 dimer (Homo sapiens)
ACAT1 tetramer acetylates IDH2 dimer (Mus musculus)
Thiosulfate can transfer its sulfur atom to glutathione (Xenopus tropicalis)
Thiosulfate can transfer its sulfur atom to glutathione (Sus scrofa)
Thiosulfate can transfer its sulfur atom to glutathione (Bos taurus)
Thiosulfate can transfer its sulfur atom to glutathione (Canis familiaris)
Thiosulfate can transfer its sulfur atom to glutathione (Rattus norvegicus)
Thiosulfate can transfer its sulfur atom to glutathione (Mus musculus)
Thiosulfate can transfer its sulfur atom to glutathione (Homo sapiens)
Persulfide sulfur is dioxygenated (Caenorhabditis elegans)
Persulfide sulfur is dioxygenated (Drosophila melanogaster)
Persulfide sulfur is dioxygenated (Xenopus tropicalis)
Persulfide sulfur is dioxygenated (Danio rerio)
Persulfide sulfur is dioxygenated (Sus scrofa)
Persulfide sulfur is dioxygenated (Bos taurus)
Persulfide sulfur is dioxygenated (Canis familiaris)
Persulfide sulfur is dioxygenated (Rattus norvegicus)
Persulfide sulfur is dioxygenated (Mus musculus)
Persulfide sulfur is dioxygenated (Homo sapiens)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Xenopus tropicalis)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Canis familiaris)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Saccharomyces cerevisiae)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Schizosaccharomyces pombe)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Dictyostelium discoideum)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Caenorhabditis elegans)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Mus musculus)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Danio rerio)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Sus scrofa)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Rattus norvegicus)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Caenorhabditis elegans)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Gallus gallus)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Xenopus tropicalis)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Danio rerio)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Sus scrofa)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Bos taurus)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Canis familiaris)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Rattus norvegicus)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Mus musculus)
DLD dimer dehydrogenates dihydrolipoyl (Dictyostelium discoideum)
DLD dimer dehydrogenates dihydrolipoyl (Caenorhabditis elegans)
DLD dimer dehydrogenates dihydrolipoyl (Drosophila melanogaster)
DLD dimer dehydrogenates dihydrolipoyl (Gallus gallus)
DLD dimer dehydrogenates dihydrolipoyl (Xenopus tropicalis)
DLD dimer dehydrogenates dihydrolipoyl (Danio rerio)
DLD dimer dehydrogenates dihydrolipoyl (Sus scrofa)
DLD dimer dehydrogenates dihydrolipoyl (Bos taurus)
DLD dimer dehydrogenates dihydrolipoyl (Canis familiaris)
DLD dimer dehydrogenates dihydrolipoyl (Rattus norvegicus)
DLD dimer dehydrogenates dihydrolipoyl (Mus musculus)
DLD dimer dehydrogenates dihydrolipoyl (Homo sapiens)
(S)-Hydroxybutanoyl-CoA+NAD<=>Acetoacetyl-CoA+NADH+H (Homo sapiens)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Homo sapiens)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Caenorhabditis elegans)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Gallus gallus)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Xenopus tropicalis)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Danio rerio)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Sus scrofa)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Bos taurus)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Canis familiaris)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Rattus norvegicus)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Mus musculus)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Caenorhabditis elegans)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Gallus gallus)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Xenopus tropicalis)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Danio rerio)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Sus scrofa)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Bos taurus)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Canis familiaris)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Rattus norvegicus)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Mus musculus)
(S)-Hydroxyoctanoyl-CoA+NAD<=>3-Oxooctanoyl-CoA+NADH+H (Homo sapiens)
(S)-Hydroxyhexanoyl-CoA+NAD<=>3-Oxohexanoyl-CoA+NADH+H (Homo sapiens)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Caenorhabditis elegans)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Gallus gallus)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Xenopus tropicalis)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Danio rerio)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Sus scrofa)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Bos taurus)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Canis familiaris)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Rattus norvegicus)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Mus musculus)
Linoleoyl-CoA is converted to cis,cis-3,6- dodecadienoyl-CoA by three cycles of beta-oxidation (Homo sapiens)
Trans,cis-lauro-2,6-dienoyl-CoA is converted to cis,cis-3,6- 4-cis-decenoyl-CoA by one cycle of beta-oxidation (Homo sapiens)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Caenorhabditis elegans)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Gallus gallus)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Xenopus tropicalis)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Danio rerio)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Sus scrofa)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Bos taurus)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Canis familiaris)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Rattus norvegicus)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Mus musculus)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Caenorhabditis elegans)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Drosophila melanogaster)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Gallus gallus)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Xenopus tropicalis)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Danio rerio)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Sus scrofa)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Bos taurus)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Canis familiaris)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Rattus norvegicus)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Mus musculus)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Caenorhabditis elegans)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Drosophila melanogaster)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Gallus gallus)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Xenopus tropicalis)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Danio rerio)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Sus scrofa)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Bos taurus)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Canis familiaris)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Rattus norvegicus)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Mus musculus)
(S)-3-Hydroxyhexadecanoyl-CoA+NAD<=>3-Oxopalmitoyl-CoA+NADH+H (Homo sapiens)
(S)-3-Hydroxytetradecanoyl-CoA+NAD<=>3-Oxotetradecanoyl-CoA+NADH+H (Homo sapiens)
(S)-3-Hydroxydodecanoyl-CoA+NAD<=>3-Oxododecanoyl-CoA+NADH+H (Homo sapiens)
(S)-Hydroxydecanoyl-CoA+NAD<=>3-Oxodecanoyl-CoA+NADH+H (Homo sapiens)
ETFDH oxidises ETF (reduced) to ETF, reduces CoQ to CoQH2 (Drosophila melanogaster)
COQ3 methylates DeMQ10H2 (Saccharomyces cerevisiae)
COQ3 methylates DeMQ10H2 (Schizosaccharomyces pombe)
COQ3 methylates DeMQ10H2 (Dictyostelium discoideum)
COQ3 methylates DeMQ10H2 (Drosophila melanogaster)
COQ3 methylates DeMQ10H2 (Gallus gallus)
COQ3 methylates DeMQ10H2 (Xenopus tropicalis)
COQ3 methylates DeMQ10H2 (Danio rerio)
COQ3 methylates DeMQ10H2 (Sus scrofa)
COQ3 methylates DeMQ10H2 (Bos taurus)
COQ3 methylates DeMQ10H2 (Canis familiaris)
COQ3 methylates DeMQ10H2 (Rattus norvegicus)
COQ3 methylates DeMQ10H2 (Mus musculus)
COQ5 methylates MDMQ10H2 (Saccharomyces cerevisiae)
COQ5 methylates MDMQ10H2 (Schizosaccharomyces pombe)
COQ5 methylates MDMQ10H2 (Dictyostelium discoideum)
COQ5 methylates MDMQ10H2 (Caenorhabditis elegans)
COQ5 methylates MDMQ10H2 (Drosophila melanogaster)
COQ5 methylates MDMQ10H2 (Gallus gallus)
COQ5 methylates MDMQ10H2 (Xenopus tropicalis)
COQ5 methylates MDMQ10H2 (Danio rerio)
COQ5 methylates MDMQ10H2 (Sus scrofa)
COQ5 methylates MDMQ10H2 (Bos taurus)
COQ5 methylates MDMQ10H2 (Canis familiaris)
COQ5 methylates MDMQ10H2 (Rattus norvegicus)
COQ5 methylates MDMQ10H2 (Mus musculus)
COQ3 methylates DHDB (Saccharomyces cerevisiae)
COQ3 methylates DHDB (Schizosaccharomyces pombe)
COQ3 methylates DHDB (Dictyostelium discoideum)
COQ3 methylates DHDB (Caenorhabditis elegans)
COQ3 methylates DHDB (Drosophila melanogaster)
COQ3 methylates DHDB (Gallus gallus)
COQ3 methylates DHDB (Xenopus tropicalis)
COQ3 methylates DHDB (Danio rerio)
COQ3 methylates DHDB (Sus scrofa)
COQ3 methylates DHDB (Bos taurus)
COQ3 methylates DHDB (Canis familiaris)
COQ3 methylates DHDB (Rattus norvegicus)
COQ3 methylates DHDB (Mus musculus)
COQ3 methylates DHDB (Homo sapiens)
COQ5 methylates MDMQ10H2 (Homo sapiens)
COQ3 methylates DeMQ10H2 (Homo sapiens)
COQ3 methylates DeMQ10H2 (Caenorhabditis elegans)
Unknown dehydrogenase oxidizes 4-HBz (Homo sapiens)
PRODH oxidises L-Pro to 1PYR-5COOH (Saccharomyces cerevisiae)
PRODH oxidises L-Pro to 1PYR-5COOH (Schizosaccharomyces pombe)
PRODH oxidises L-Pro to 1PYR-5COOH (Dictyostelium discoideum)
PRODH oxidises L-Pro to 1PYR-5COOH (Caenorhabditis elegans)
PRODH oxidises L-Pro to 1PYR-5COOH (Drosophila melanogaster)
PRODH oxidises L-Pro to 1PYR-5COOH (Gallus gallus)
PRODH oxidises L-Pro to 1PYR-5COOH (Xenopus tropicalis)
PRODH oxidises L-Pro to 1PYR-5COOH (Sus scrofa)
PRODH oxidises L-Pro to 1PYR-5COOH (Bos taurus)
PRODH oxidises L-Pro to 1PYR-5COOH (Canis familiaris)
PRODH oxidises L-Pro to 1PYR-5COOH (Rattus norvegicus)
PRODH oxidises L-Pro to 1PYR-5COOH (Mus musculus)
PRODH oxidises L-Pro to 1PYR-5COOH (Homo sapiens)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Dictyostelium discoideum)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Caenorhabditis elegans)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Drosophila melanogaster)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Gallus gallus)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Xenopus tropicalis)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Danio rerio)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Sus scrofa)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Bos taurus)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Canis familiaris)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Rattus norvegicus)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Mus musculus)
glutamate + NAD(P)+ => alpha-ketoglutarate + NH4+ + NAD(P)H + H+ (GLUD1,2) (Homo sapiens)
L-glutamate gamma-semialdehyde <=> L-1-pyrroline-5-carboxylate (Homo sapiens)
SLC25A18,22 import L-Glu, H+ (Saccharomyces cerevisiae)
SLC25A12,13 exchange L-Glu and L-Asp (Saccharomyces cerevisiae)
SLC25A12,13 exchange L-Glu and L-Asp (Rattus norvegicus)
Cytosolic PYR is transported to the mitochondrial matrix (Rattus norvegicus)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Dictyostelium discoideum)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Caenorhabditis elegans)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Drosophila melanogaster)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Gallus gallus)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Xenopus tropicalis)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Danio rerio)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Sus scrofa)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Bos taurus)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Canis familiaris)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Rattus norvegicus)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Mus musculus)
HYKK phosphorylates 5HLYS (Drosophila melanogaster)
HYKK phosphorylates 5HLYS (Gallus gallus)
HYKK phosphorylates 5HLYS (Xenopus tropicalis)
HYKK phosphorylates 5HLYS (Danio rerio)
HYKK phosphorylates 5HLYS (Sus scrofa)
HYKK phosphorylates 5HLYS (Bos taurus)
HYKK phosphorylates 5HLYS (Canis familiaris)
HYKK phosphorylates 5HLYS (Rattus norvegicus)
HYKK phosphorylates 5HLYS (Mus musculus)
HYKK phosphorylates 5HLYS (Homo sapiens)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Saccharomyces cerevisiae)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Schizosaccharomyces pombe)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Caenorhabditis elegans)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Drosophila melanogaster)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Danio rerio)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Rattus norvegicus)
SLC25A12,13 exchange L-Glu and L-Asp (Dictyostelium discoideum)
SLC25A18,22 import L-Glu, H+ (Dictyostelium discoideum)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Dictyostelium discoideum)
SLC25A12,13 exchange L-Glu and L-Asp (Canis familiaris)
SLC25A18,22 import L-Glu, H+ (Canis familiaris)
NNT dimer transfers proton from NADPH to NAD+ (Danio rerio)
CS acetylates OA to citrate (Danio rerio)
SLC25A18,22 import L-Glu, H+ (Danio rerio)
DLD dimer dehydrogenates dihydrolipoyl (Gallus gallus)
CS acetylates OA to citrate (Gallus gallus)
NNT dimer transfers proton from NADPH to NAD+ (Gallus gallus)
NNT dimer transfers proton from NADPH to NAD+ (Plasmodium falciparum)
CS acetylates OA to citrate (Plasmodium falciparum)
DLD dimer dehydrogenates dihydrolipoyl (Plasmodium falciparum)
MDH2 dimer dehydrogenates MAL (Plasmodium falciparum)
DLD dimer dehydrogenates dihydrolipoyl (Dictyostelium discoideum)
NNT dimer transfers proton from NADPH to NAD+ (Dictyostelium discoideum)
CS acetylates OA to citrate (Dictyostelium discoideum)
CS acetylates OA to citrate (Drosophila melanogaster)
DLD dimer dehydrogenates dihydrolipoyl (Drosophila melanogaster)
SLC25A12,13 exchange L-Glu and L-Asp (Drosophila melanogaster)
DLD dimer dehydrogenates dihydrolipoyl (Caenorhabditis elegans)
SLC25A18,22 import L-Glu, H+ (Caenorhabditis elegans)
PDK isozymes phosphorylate PDHC subunit E1 (Schizosaccharomyces pombe)
PDK isozymes phosphorylate PDHC subunit E1 (Xenopus tropicalis)
PC carboxylates PYR to OA (Saccharomyces cerevisiae)
CS acetylates OA to citrate (Saccharomyces cerevisiae)
DLD dimer dehydrogenates dihydrolipoyl (Saccharomyces cerevisiae)
MDH2 dimer dehydrogenates MAL (Saccharomyces cerevisiae)
DLD dimer dehydrogenates dihydrolipoyl (Saccharomyces cerevisiae)
PC carboxylates PYR to OA (Schizosaccharomyces pombe)
CS acetylates OA to citrate (Schizosaccharomyces pombe)
DLD dimer dehydrogenates dihydrolipoyl (Schizosaccharomyces pombe)
MDH2 dimer dehydrogenates MAL (Schizosaccharomyces pombe)
DLD dimer dehydrogenates dihydrolipoyl (Schizosaccharomyces pombe)
DLD dimer dehydrogenates dihydrolipoyl (Dictyostelium discoideum)
DLD dimer dehydrogenates dihydrolipoyl (Caenorhabditis elegans)
DLD dimer dehydrogenates dihydrolipoyl (Xenopus tropicalis)
DLD dimer dehydrogenates dihydrolipoyl (Drosophila melanogaster)
PDK isozymes phosphorylate PDHC subunit E1 (Drosophila melanogaster)
DLD dimer dehydrogenates dihydrolipoyl (Gallus gallus)
PDK isozymes phosphorylate PDHC subunit E1 (Gallus gallus)
DLD dimer dehydrogenates dihydrolipoyl (Sus scrofa)
PDK isozymes phosphorylate PDHC subunit E1 (Sus scrofa)
DLD dimer dehydrogenates dihydrolipoyl (Bos taurus)
PDK isozymes phosphorylate PDHC subunit E1 (Bos taurus)
DLD dimer dehydrogenates dihydrolipoyl (Canis familiaris)
PDK isozymes phosphorylate PDHC subunit E1 (Canis familiaris)
DLD dimer dehydrogenates dihydrolipoyl (Rattus norvegicus)
PDK isozymes phosphorylate PDHC subunit E1 (Rattus norvegicus)
DLD dimer dehydrogenates dihydrolipoyl (Mus musculus)
PDK isozymes phosphorylate PDHC subunit E1 (Mus musculus)
DLD dimer dehydrogenates dihydrolipoyl (Homo sapiens)
PDK isozymes phosphorylate PDHC subunit E1 (Homo sapiens)
PDK isozymes phosphorylate PDHC subunit E1 (Caenorhabditis elegans)
PC carboxylates PYR to OA (Caenorhabditis elegans)
SLC25A12,13 exchange L-Glu and L-Asp (Caenorhabditis elegans)
MDH2 dimer dehydrogenates MAL (Caenorhabditis elegans)
CS acetylates OA to citrate (Caenorhabditis elegans)
NNT dimer transfers proton from NADPH to NAD+ (Caenorhabditis elegans)
PC carboxylates PYR to OA (Drosophila melanogaster)
SLC25A18,22 import L-Glu, H+ (Drosophila melanogaster)
MDH2 dimer dehydrogenates MAL (Drosophila melanogaster)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Gallus gallus)
SLC25A12,13 exchange L-Glu and L-Asp (Gallus gallus)
SLC25A18,22 import L-Glu, H+ (Gallus gallus)
MDH2 dimer dehydrogenates MAL (Gallus gallus)
DLD dimer dehydrogenates dihydrolipoyl (Xenopus tropicalis)
NNT dimer transfers proton from NADPH to NAD+ (Xenopus tropicalis)
SLC25A18,22 import L-Glu, H+ (Xenopus tropicalis)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Xenopus tropicalis)
SLC25A12,13 exchange L-Glu and L-Asp (Xenopus tropicalis)
MDH2 dimer dehydrogenates MAL (Xenopus tropicalis)
CS acetylates OA to citrate (Xenopus tropicalis)
FDXR transfers electrons to FDX1,2 (FDX1L) (Plasmodium falciparum)
FDXR transfers electrons to FDX1,2 (FDX1L) (Saccharomyces cerevisiae)
FDXR transfers electrons to FDX1,2 (FDX1L) (Dictyostelium discoideum)
FDXR transfers electrons to FDX1,2 (FDX1L) (Caenorhabditis elegans)
FDXR transfers electrons to FDX1,2 (FDX1L) (Drosophila melanogaster)
FDXR transfers electrons to FDX1,2 (FDX1L) (Gallus gallus)
FDXR transfers electrons to FDX1,2 (FDX1L) (Xenopus tropicalis)
FDXR transfers electrons to FDX1,2 (FDX1L) (Danio rerio)
FDXR transfers electrons to FDX1,2 (FDX1L) (Sus scrofa)
FDXR transfers electrons to FDX1,2 (FDX1L) (Bos taurus)
FDXR transfers electrons to FDX1,2 (FDX1L) (Canis familiaris)
FDXR transfers electrons to FDX1,2 (FDX1L) (Rattus norvegicus)
FDXR transfers electrons to FDX1,2 (FDX1L) (Mus musculus)
FDXR transfers electrons to FDX1,2 (FDX1L) (Homo sapiens)
PC carboxylates PYR to OA (Xenopus tropicalis)
SLC25A12,13 exchange L-Glu and L-Asp (Sus scrofa)
SLC25A18,22 import L-Glu, H+ (Sus scrofa)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Sus scrofa)
MDH2 dimer dehydrogenates MAL (Sus scrofa)
MDH2 dimer dehydrogenates MAL (Mus musculus)
PC carboxylates PYR to OA (Danio rerio)
SLC25A12,13 exchange L-Glu and L-Asp (Danio rerio)
MDH2 dimer dehydrogenates MAL (Danio rerio)
DLD dimer dehydrogenates dihydrolipoyl (Danio rerio)
DLD dimer dehydrogenates dihydrolipoyl (Bos taurus)
DLD dimer dehydrogenates dihydrolipoyl (Canis familiaris)
DLD dimer dehydrogenates dihydrolipoyl (Rattus norvegicus)
DLD dimer dehydrogenates dihydrolipoyl (Mus musculus)
DLD dimer dehydrogenates dihydrolipoyl (Homo sapiens)
DLD dimer dehydrogenates dihydrolipoyl (Sus scrofa)
PC carboxylates PYR to OA (Sus scrofa)
CS acetylates OA to citrate (Sus scrofa)
NNT dimer transfers proton from NADPH to NAD+ (Mus musculus)
NNT dimer transfers proton from NADPH to NAD+ (Homo sapiens)
NNT dimer transfers proton from NADPH to NAD+ (Canis familiaris)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Saccharomyces cerevisiae)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Schizosaccharomyces pombe)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Caenorhabditis elegans)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Drosophila melanogaster)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Gallus gallus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Xenopus tropicalis)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Sus scrofa)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Bos taurus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Rattus norvegicus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Mus musculus)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Homo sapiens)
ALDH5A1 dehydrogenates SUCCSA to SUCCA (Canis familiaris)
MDH2 dimer dehydrogenates MAL (Canis familiaris)
PC carboxylates PYR to OA (Canis familiaris)
CS acetylates OA to citrate (Canis familiaris)
PC carboxylates PYR to OA (Mus musculus)
CS acetylates OA to citrate (Mus musculus)
CSKMT methylates Citrate Synthase (Danio rerio)
CSKMT methylates Citrate Synthase (Sus scrofa)
CSKMT methylates Citrate Synthase (Canis familiaris)
CSKMT methylates Citrate Synthase (Homo sapiens)
CSKMT methylates Citrate Synthase (Bos taurus)
CS acetylates OA to citrate (Bos taurus)
NNT dimer transfers proton from NADPH to NAD+ (Bos taurus)
MDH2 dimer dehydrogenates MAL (Bos taurus)
PC carboxylates PYR to OA (Bos taurus)
SLC25A12,13 exchange L-Glu and L-Asp (Bos taurus)
SLC25A18,22 import L-Glu, H+ (Bos taurus)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Bos taurus)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Mus musculus)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Homo sapiens)
alpha-aminoadipoate semialdehyde + NAD+ => alpha-aminoadipate + NADH + H+ (Homo sapiens)
saccharopine + NAD+ + H2O => alpha-aminoadipic semialdehyde + glutamate + NADH + H+ (Canis familiaris)
MPC1:MPC2 imports PYR, H+ to mitochondrial matrix (Homo sapiens)
PC carboxylates PYR to OA (Homo sapiens)
CS acetylates OA to citrate (Homo sapiens)
MDH2 dimer dehydrogenates MAL (Rattus norvegicus)
CS acetylates OA to citrate (Rattus norvegicus)
NNT dimer transfers proton from NADPH to NAD+ (Rattus norvegicus)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Dictyostelium discoideum)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Caenorhabditis elegans)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Drosophila melanogaster)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Gallus gallus)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Xenopus tropicalis)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Danio rerio)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Sus scrofa)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Bos taurus)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Canis familiaris)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Mus musculus)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Homo sapiens)
alpha-methyl-beta-hydroxybutyryl-CoA + NAD+ <=> alpha-methylacetoacetyl-CoA + NADH + H+ (Rattus norvegicus)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Dictyostelium discoideum)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Caenorhabditis elegans)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Drosophila melanogaster)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Gallus gallus)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Xenopus tropicalis)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Danio rerio)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Sus scrofa)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Bos taurus)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Canis familiaris)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Mus musculus)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Homo sapiens)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Dictyostelium discoideum)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Caenorhabditis elegans)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Drosophila melanogaster)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Gallus gallus)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Xenopus tropicalis)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Danio rerio)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Sus scrofa)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Bos taurus)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Canis familiaris)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Mus musculus)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Homo sapiens)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Plasmodium falciparum)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Saccharomyces cerevisiae)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Schizosaccharomyces pombe)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Dictyostelium discoideum)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Caenorhabditis elegans)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Drosophila melanogaster)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Gallus gallus)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Danio rerio)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Sus scrofa)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Bos taurus)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Canis familiaris)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Mus musculus)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Homo sapiens)
DLD dimer dehydrogenates dihydrolipoyl (Plasmodium falciparum)
DLD dimer dehydrogenates dihydrolipoyl (Dictyostelium discoideum)
DLD dimer dehydrogenates dihydrolipoyl (Caenorhabditis elegans)
DLD dimer dehydrogenates dihydrolipoyl (Drosophila melanogaster)
DLD dimer dehydrogenates dihydrolipoyl (Gallus gallus)
DLD dimer dehydrogenates dihydrolipoyl (Xenopus tropicalis)
DLD dimer dehydrogenates dihydrolipoyl (Danio rerio)
DLD dimer dehydrogenates dihydrolipoyl (Sus scrofa)
DLD dimer dehydrogenates dihydrolipoyl (Bos taurus)
DLD dimer dehydrogenates dihydrolipoyl (Canis familiaris)
SLC25A12,13 exchange L-Glu and L-Asp (Mus musculus)
SLC25A18,22 import L-Glu, H+ (Mus musculus)
SLC25A18,22 import L-Glu, H+ (Homo sapiens)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Homo sapiens)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Mus musculus)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Rattus norvegicus)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Canis familiaris)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Bos taurus)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Sus scrofa)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Danio rerio)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Xenopus tropicalis)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Gallus gallus)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Dictyostelium discoideum)
NAT8L transfers acetyl group from Ac-CoA to L-Asp, forming NAASP (Plasmodium falciparum)
SLC25A12,13 exchange L-Glu and L-Asp (Homo sapiens)
MDH2 dimer dehydrogenates MAL (Homo sapiens)
SLC25A18,22 import L-Glu, H+ (Rattus norvegicus)
PC carboxylates PYR to OA (Rattus norvegicus)
MMAB adenosylates cob(I)alamin (Rattus norvegicus)
MMAB adenosylates cob(I)alamin (Homo sapiens)
MMAB adenosylates cob(I)alamin (Mus musculus)
MMAB adenosylates cob(I)alamin (Canis familiaris)
MMAB adenosylates cob(I)alamin (Bos taurus)
MMAB adenosylates cob(I)alamin (Sus scrofa)
MMAB adenosylates cob(I)alamin (Xenopus tropicalis)
MMAB adenosylates cob(I)alamin (Gallus gallus)
MMAB adenosylates cob(I)alamin (Caenorhabditis elegans)
MMAB adenosylates cob(I)alamin (Dictyostelium discoideum)
methylmalonate semialdehyde + NAD+ + CoA + H2O => propionyl-CoA + HCO3- + NADH + H+ (Rattus norvegicus)
beta-hydroxyisobutyrate + NAD+ <=> methylmalonyl semialdehyde + NADH + H+ (Rattus norvegicus)
beta-hydroxyisobutyryl-CoA + H2O => beta-hydroxyisobutyrate + CoA (Rattus norvegicus)
BCKDK phosphorylates BCKDH (Homo sapiens)
BCKDK phosphorylates BCKDH (Mus musculus)
BCKDK phosphorylates BCKDH (Rattus norvegicus)
BCKDK phosphorylates BCKDH (Canis familiaris)
BCKDK phosphorylates BCKDH (Bos taurus)
BCKDK phosphorylates BCKDH (Sus scrofa)
BCKDK phosphorylates BCKDH (Xenopus tropicalis)
DLD dimer dehydrogenates dihydrolipoyl (Rattus norvegicus)
DLD dimer dehydrogenates dihydrolipoyl (Homo sapiens)
DLD dimer dehydrogenates dihydrolipoyl (Mus musculus)
Other forms of this molecule
H+ [early endosome]
H+ [synaptic vesicle lumen]
H+ [platelet dense tubular network lumen]
H+ [sperm flagellum]
H+ [melanosome lumen]
H+ [nuclear envelope]
H+ [mitochondrial inner membrane]
H+ [synaptic vesicle]
H+ [late endosome lumen]
H+ [early endosome lumen]
H+ [Golgi lumen]
H+ [endocytic vesicle lumen]
H+ [phagolysosome]
H+ [cytoplasm]
H+ [phagocytic vesicle lumen]
H+ [clathrin-sculpted acetylcholine transport vesicle lumen]
H+ [endolysosome lumen]
H+ [endoplasmic reticulum lumen]
H+ [endoplasmic reticulum-Golgi intermediate compartment]
H+ [endosome lumen]
H+ [extracellular region]
H+ [clathrin-sculpted monoamine transport vesicle lumen]
H+ [mitochondrial intermembrane space]
H+ [peroxisomal matrix]
H+ [lysosomal lumen]
H+ [cytosol]
H+ [nucleoplasm]
Cross References
COMPOUND
C00080
PubChem Substance
8145820
HMDB Metabolite
HMDB0059597
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text