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CS/HS precursor [lysosomal lumen]
Stable Identifier
R-ALL-2065212
Type
Chemical Compound [SimpleEntity]
Compartment
lysosomal lumen
Synonyms
GlcA-Gal-Gal-Xyl linker chain, beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates and carbohydrate derivatives (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Chondroitin sulfate/dermatan sulfate metabolism (Bos taurus)
CS/DS degradation (Bos taurus)
HYAL1 hydrolyses Chondroitin chains (Bos taurus)
CS/HS precursor [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Bos taurus)
HS-GAG degradation (Bos taurus)
GUSB tetramer hydrolyses CS/HS precursor (Bos taurus)
CS/HS precursor [lysosomal lumen]
NAGLU hydrolyses heparan chain(2) (Bos taurus)
CS/HS precursor [lysosomal lumen]
Metabolism (Caenorhabditis elegans)
Metabolism of carbohydrates and carbohydrate derivatives (Caenorhabditis elegans)
Glycosaminoglycan metabolism (Caenorhabditis elegans)
Chondroitin sulfate/dermatan sulfate metabolism (Caenorhabditis elegans)
CS/DS degradation (Caenorhabditis elegans)
HYAL1 hydrolyses Chondroitin chains (Caenorhabditis elegans)
CS/HS precursor [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Caenorhabditis elegans)
HS-GAG degradation (Caenorhabditis elegans)
GUSB tetramer hydrolyses CS/HS precursor (Caenorhabditis elegans)
CS/HS precursor [lysosomal lumen]
NAGLU hydrolyses heparan chain(2) (Caenorhabditis elegans)
CS/HS precursor [lysosomal lumen]
Metabolism (Canis familiaris)
Metabolism of carbohydrates and carbohydrate derivatives (Canis familiaris)
Glycosaminoglycan metabolism (Canis familiaris)
Chondroitin sulfate/dermatan sulfate metabolism (Canis familiaris)
CS/DS degradation (Canis familiaris)
HYAL1 hydrolyses Chondroitin chains (Canis familiaris)
CS/HS precursor [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Canis familiaris)
HS-GAG degradation (Canis familiaris)
GUSB tetramer hydrolyses CS/HS precursor (Canis familiaris)
CS/HS precursor [lysosomal lumen]
NAGLU hydrolyses heparan chain(2) (Canis familiaris)
CS/HS precursor [lysosomal lumen]
Metabolism (Danio rerio)
Metabolism of carbohydrates and carbohydrate derivatives (Danio rerio)
Glycosaminoglycan metabolism (Danio rerio)
Chondroitin sulfate/dermatan sulfate metabolism (Danio rerio)
CS/DS degradation (Danio rerio)
HYAL1 hydrolyses Chondroitin chains (Danio rerio)
CS/HS precursor [lysosomal lumen]
Metabolism (Dictyostelium discoideum)
Metabolism of carbohydrates and carbohydrate derivatives (Dictyostelium discoideum)
Glycosaminoglycan metabolism (Dictyostelium discoideum)
Heparan sulfate/heparin (HS-GAG) metabolism (Dictyostelium discoideum)
HS-GAG degradation (Dictyostelium discoideum)
NAGLU hydrolyses heparan chain(2) (Dictyostelium discoideum)
CS/HS precursor [lysosomal lumen]
Metabolism (Drosophila melanogaster)
Metabolism of carbohydrates and carbohydrate derivatives (Drosophila melanogaster)
Glycosaminoglycan metabolism (Drosophila melanogaster)
Heparan sulfate/heparin (HS-GAG) metabolism (Drosophila melanogaster)
HS-GAG degradation (Drosophila melanogaster)
GUSB tetramer hydrolyses CS/HS precursor (Drosophila melanogaster)
CS/HS precursor [lysosomal lumen]
NAGLU hydrolyses heparan chain(2) (Drosophila melanogaster)
CS/HS precursor [lysosomal lumen]
Metabolism (Gallus gallus)
Metabolism of carbohydrates and carbohydrate derivatives (Gallus gallus)
Glycosaminoglycan metabolism (Gallus gallus)
Chondroitin sulfate/dermatan sulfate metabolism (Gallus gallus)
CS/DS degradation (Gallus gallus)
HYAL1 hydrolyses Chondroitin chains (Gallus gallus)
CS/HS precursor [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Gallus gallus)
HS-GAG degradation (Gallus gallus)
GUSB tetramer hydrolyses CS/HS precursor (Gallus gallus)
CS/HS precursor [lysosomal lumen]
NAGLU hydrolyses heparan chain(2) (Gallus gallus)
CS/HS precursor [lysosomal lumen]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of carbohydrate metabolism (Homo sapiens)
Mucopolysaccharidoses (Homo sapiens)
MPS VII - Sly syndrome (Homo sapiens)
Defective GUSB does not hydrolyse CS/HS precursor (Homo sapiens)
CS/HS precursor [lysosomal lumen]
Metabolism (Homo sapiens)
Metabolism of carbohydrates and carbohydrate derivatives (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
CS/DS degradation (Homo sapiens)
HYAL1 hydrolyses Chondroitin chains (Homo sapiens)
CS/HS precursor [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Homo sapiens)
HS-GAG degradation (Homo sapiens)
GUSB tetramer hydrolyses CS/HS precursor (Homo sapiens)
CS/HS precursor [lysosomal lumen]
NAGLU hydrolyses heparan chain(2) (Homo sapiens)
CS/HS precursor [lysosomal lumen]
Metabolism (Mus musculus)
Metabolism of carbohydrates and carbohydrate derivatives (Mus musculus)
Glycosaminoglycan metabolism (Mus musculus)
Chondroitin sulfate/dermatan sulfate metabolism (Mus musculus)
CS/DS degradation (Mus musculus)
HYAL1 hydrolyses Chondroitin chains (Mus musculus)
CS/HS precursor [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Mus musculus)
HS-GAG degradation (Mus musculus)
GUSB tetramer hydrolyses CS/HS precursor (Mus musculus)
CS/HS precursor [lysosomal lumen]
NAGLU hydrolyses heparan chain(2) (Mus musculus)
CS/HS precursor [lysosomal lumen]
Metabolism (Rattus norvegicus)
Metabolism of carbohydrates and carbohydrate derivatives (Rattus norvegicus)
Glycosaminoglycan metabolism (Rattus norvegicus)
Chondroitin sulfate/dermatan sulfate metabolism (Rattus norvegicus)
CS/DS degradation (Rattus norvegicus)
HYAL1 hydrolyses Chondroitin chains (Rattus norvegicus)
CS/HS precursor [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Rattus norvegicus)
HS-GAG degradation (Rattus norvegicus)
GUSB tetramer hydrolyses CS/HS precursor (Rattus norvegicus)
CS/HS precursor [lysosomal lumen]
NAGLU hydrolyses heparan chain(2) (Rattus norvegicus)
CS/HS precursor [lysosomal lumen]
Metabolism (Sus scrofa)
Metabolism of carbohydrates and carbohydrate derivatives (Sus scrofa)
Glycosaminoglycan metabolism (Sus scrofa)
Chondroitin sulfate/dermatan sulfate metabolism (Sus scrofa)
CS/DS degradation (Sus scrofa)
HYAL1 hydrolyses Chondroitin chains (Sus scrofa)
CS/HS precursor [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Sus scrofa)
HS-GAG degradation (Sus scrofa)
GUSB tetramer hydrolyses CS/HS precursor (Sus scrofa)
CS/HS precursor [lysosomal lumen]
NAGLU hydrolyses heparan chain(2) (Sus scrofa)
CS/HS precursor [lysosomal lumen]
Metabolism (Xenopus tropicalis)
Metabolism of carbohydrates and carbohydrate derivatives (Xenopus tropicalis)
Glycosaminoglycan metabolism (Xenopus tropicalis)
Chondroitin sulfate/dermatan sulfate metabolism (Xenopus tropicalis)
CS/DS degradation (Xenopus tropicalis)
HYAL1 hydrolyses Chondroitin chains (Xenopus tropicalis)
CS/HS precursor [lysosomal lumen]
Heparan sulfate/heparin (HS-GAG) metabolism (Xenopus tropicalis)
HS-GAG degradation (Xenopus tropicalis)
GUSB tetramer hydrolyses CS/HS precursor (Xenopus tropicalis)
CS/HS precursor [lysosomal lumen]
External Reference Information
External Reference
beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group [ChEBI:63505]
Participates
as an input of
Defective GUSB does not hydrolyse CS/HS precursor (Homo sapiens)
GUSB tetramer hydrolyses CS/HS precursor (Caenorhabditis elegans)
GUSB tetramer hydrolyses CS/HS precursor (Drosophila melanogaster)
GUSB tetramer hydrolyses CS/HS precursor (Gallus gallus)
GUSB tetramer hydrolyses CS/HS precursor (Xenopus tropicalis)
GUSB tetramer hydrolyses CS/HS precursor (Sus scrofa)
GUSB tetramer hydrolyses CS/HS precursor (Bos taurus)
GUSB tetramer hydrolyses CS/HS precursor (Rattus norvegicus)
GUSB tetramer hydrolyses CS/HS precursor (Mus musculus)
GUSB tetramer hydrolyses CS/HS precursor (Homo sapiens)
GUSB tetramer hydrolyses CS/HS precursor (Canis familiaris)
as an output of
HYAL1 hydrolyses Chondroitin chains (Caenorhabditis elegans)
HYAL1 hydrolyses Chondroitin chains (Gallus gallus)
HYAL1 hydrolyses Chondroitin chains (Xenopus tropicalis)
HYAL1 hydrolyses Chondroitin chains (Danio rerio)
HYAL1 hydrolyses Chondroitin chains (Sus scrofa)
HYAL1 hydrolyses Chondroitin chains (Bos taurus)
HYAL1 hydrolyses Chondroitin chains (Rattus norvegicus)
HYAL1 hydrolyses Chondroitin chains (Mus musculus)
HYAL1 hydrolyses Chondroitin chains (Homo sapiens)
HYAL1 hydrolyses Chondroitin chains (Canis familiaris)
NAGLU hydrolyses heparan chain(2) (Dictyostelium discoideum)
NAGLU hydrolyses heparan chain(2) (Caenorhabditis elegans)
NAGLU hydrolyses heparan chain(2) (Drosophila melanogaster)
NAGLU hydrolyses heparan chain(2) (Gallus gallus)
NAGLU hydrolyses heparan chain(2) (Sus scrofa)
NAGLU hydrolyses heparan chain(2) (Bos taurus)
NAGLU hydrolyses heparan chain(2) (Rattus norvegicus)
NAGLU hydrolyses heparan chain(2) (Mus musculus)
NAGLU hydrolyses heparan chain(2) (Homo sapiens)
NAGLU hydrolyses heparan chain(2) (Canis familiaris)
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