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Heparan sulfate chain(4) [lysosomal lumen]
Stable Identifier
R-ALL-2090069
Type
Chemical Compound [SimpleEntity]
Compartment
lysosomal lumen
Synonyms
alpha-D-GlcNAc-(1->4)-beta-D-IdoA2S-(1->4)-alpha-D-GlcNS3S-(1->4)-beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Heparan sulfate/heparin (HS-GAG) metabolism (Bos taurus)
HS-GAG degradation (Bos taurus)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Bos taurus)
Heparan sulfate chain(4) [lysosomal lumen]
NAGLU hydrolyses Heparan sulfate chain(4) (Bos taurus)
Heparan sulfate chain(4) [lysosomal lumen]
Metabolism (Caenorhabditis elegans)
Metabolism of carbohydrates (Caenorhabditis elegans)
Glycosaminoglycan metabolism (Caenorhabditis elegans)
Heparan sulfate/heparin (HS-GAG) metabolism (Caenorhabditis elegans)
HS-GAG degradation (Caenorhabditis elegans)
NAGLU hydrolyses Heparan sulfate chain(4) (Caenorhabditis elegans)
Heparan sulfate chain(4) [lysosomal lumen]
Metabolism (Canis familiaris)
Metabolism of carbohydrates (Canis familiaris)
Glycosaminoglycan metabolism (Canis familiaris)
Heparan sulfate/heparin (HS-GAG) metabolism (Canis familiaris)
HS-GAG degradation (Canis familiaris)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Canis familiaris)
Heparan sulfate chain(4) [lysosomal lumen]
NAGLU hydrolyses Heparan sulfate chain(4) (Canis familiaris)
Heparan sulfate chain(4) [lysosomal lumen]
Metabolism (Dictyostelium discoideum)
Metabolism of carbohydrates (Dictyostelium discoideum)
Glycosaminoglycan metabolism (Dictyostelium discoideum)
Heparan sulfate/heparin (HS-GAG) metabolism (Dictyostelium discoideum)
HS-GAG degradation (Dictyostelium discoideum)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Dictyostelium discoideum)
Heparan sulfate chain(4) [lysosomal lumen]
NAGLU hydrolyses Heparan sulfate chain(4) (Dictyostelium discoideum)
Heparan sulfate chain(4) [lysosomal lumen]
Metabolism (Drosophila melanogaster)
Metabolism of carbohydrates (Drosophila melanogaster)
Glycosaminoglycan metabolism (Drosophila melanogaster)
Heparan sulfate/heparin (HS-GAG) metabolism (Drosophila melanogaster)
HS-GAG degradation (Drosophila melanogaster)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Drosophila melanogaster)
Heparan sulfate chain(4) [lysosomal lumen]
NAGLU hydrolyses Heparan sulfate chain(4) (Drosophila melanogaster)
Heparan sulfate chain(4) [lysosomal lumen]
Metabolism (Gallus gallus)
Metabolism of carbohydrates (Gallus gallus)
Glycosaminoglycan metabolism (Gallus gallus)
Heparan sulfate/heparin (HS-GAG) metabolism (Gallus gallus)
HS-GAG degradation (Gallus gallus)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Gallus gallus)
Heparan sulfate chain(4) [lysosomal lumen]
NAGLU hydrolyses Heparan sulfate chain(4) (Gallus gallus)
Heparan sulfate chain(4) [lysosomal lumen]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of carbohydrate metabolism (Homo sapiens)
Mucopolysaccharidoses (Homo sapiens)
MPS IIIB - Sanfilippo syndrome B (Homo sapiens)
Defective NAGLU does not hydrolyse Heparan sulfate chain(4) (Homo sapiens)
Heparan sulfate chain(4) [lysosomal lumen]
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Heparan sulfate/heparin (HS-GAG) metabolism (Homo sapiens)
HS-GAG degradation (Homo sapiens)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Homo sapiens)
Heparan sulfate chain(4) [lysosomal lumen]
NAGLU hydrolyses Heparan sulfate chain(4) (Homo sapiens)
Heparan sulfate chain(4) [lysosomal lumen]
Metabolism (Mus musculus)
Metabolism of carbohydrates (Mus musculus)
Glycosaminoglycan metabolism (Mus musculus)
Heparan sulfate/heparin (HS-GAG) metabolism (Mus musculus)
HS-GAG degradation (Mus musculus)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Mus musculus)
Heparan sulfate chain(4) [lysosomal lumen]
NAGLU hydrolyses Heparan sulfate chain(4) (Mus musculus)
Heparan sulfate chain(4) [lysosomal lumen]
Metabolism (Rattus norvegicus)
Metabolism of carbohydrates (Rattus norvegicus)
Glycosaminoglycan metabolism (Rattus norvegicus)
Heparan sulfate/heparin (HS-GAG) metabolism (Rattus norvegicus)
HS-GAG degradation (Rattus norvegicus)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Rattus norvegicus)
Heparan sulfate chain(4) [lysosomal lumen]
NAGLU hydrolyses Heparan sulfate chain(4) (Rattus norvegicus)
Heparan sulfate chain(4) [lysosomal lumen]
Metabolism (Sus scrofa)
Metabolism of carbohydrates (Sus scrofa)
Glycosaminoglycan metabolism (Sus scrofa)
Heparan sulfate/heparin (HS-GAG) metabolism (Sus scrofa)
HS-GAG degradation (Sus scrofa)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Sus scrofa)
Heparan sulfate chain(4) [lysosomal lumen]
NAGLU hydrolyses Heparan sulfate chain(4) (Sus scrofa)
Heparan sulfate chain(4) [lysosomal lumen]
Metabolism (Xenopus tropicalis)
Metabolism of carbohydrates (Xenopus tropicalis)
Glycosaminoglycan metabolism (Xenopus tropicalis)
Heparan sulfate/heparin (HS-GAG) metabolism (Xenopus tropicalis)
HS-GAG degradation (Xenopus tropicalis)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Xenopus tropicalis)
Heparan sulfate chain(4) [lysosomal lumen]
External Reference Information
External Reference
alpha-D-GlcNAc-(1->4)-beta-D-IdoA2S-(1->4)-alpha-D-GlcNS3S-(1->4)-beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group [ChEBI:63807]
Participates
as an input of
Defective NAGLU does not hydrolyse Heparan sulfate chain(4) (Homo sapiens)
NAGLU hydrolyses Heparan sulfate chain(4) (Dictyostelium discoideum)
NAGLU hydrolyses Heparan sulfate chain(4) (Caenorhabditis elegans)
NAGLU hydrolyses Heparan sulfate chain(4) (Drosophila melanogaster)
NAGLU hydrolyses Heparan sulfate chain(4) (Gallus gallus)
NAGLU hydrolyses Heparan sulfate chain(4) (Sus scrofa)
NAGLU hydrolyses Heparan sulfate chain(4) (Bos taurus)
NAGLU hydrolyses Heparan sulfate chain(4) (Canis familiaris)
NAGLU hydrolyses Heparan sulfate chain(4) (Rattus norvegicus)
NAGLU hydrolyses Heparan sulfate chain(4) (Mus musculus)
NAGLU hydrolyses Heparan sulfate chain(4) (Homo sapiens)
as an output of
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Dictyostelium discoideum)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Drosophila melanogaster)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Gallus gallus)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Xenopus tropicalis)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Sus scrofa)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Bos taurus)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Canis familiaris)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Rattus norvegicus)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Mus musculus)
HGSNAT oligomer acetylates Heparan sulfate chain(3) (Homo sapiens)
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