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Heparan sulfate chain(7) [lysosomal lumen]
Stable Identifier
R-ALL-2090070
Type
Chemical Compound [SimpleEntity]
Compartment
lysosomal lumen
Synonyms
alpha-D-GlcNS3S-(1->4)-beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Canis familiaris
Dictyostelium discoideum
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates and carbohydrate derivatives (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Heparan sulfate/heparin (HS-GAG) metabolism (Bos taurus)
HS-GAG degradation (Bos taurus)
IDUA hydrolyses Heparan sulfate chain(6) (Bos taurus)
Heparan sulfate chain(7) [lysosomal lumen]
SGSH hydrolyses Heparan sulfate chain(7) (Bos taurus)
Heparan sulfate chain(7) [lysosomal lumen]
Metabolism (Canis familiaris)
Metabolism of carbohydrates and carbohydrate derivatives (Canis familiaris)
Glycosaminoglycan metabolism (Canis familiaris)
Heparan sulfate/heparin (HS-GAG) metabolism (Canis familiaris)
HS-GAG degradation (Canis familiaris)
IDUA hydrolyses Heparan sulfate chain(6) (Canis familiaris)
Heparan sulfate chain(7) [lysosomal lumen]
SGSH hydrolyses Heparan sulfate chain(7) (Canis familiaris)
Heparan sulfate chain(7) [lysosomal lumen]
Metabolism (Dictyostelium discoideum)
Metabolism of carbohydrates and carbohydrate derivatives (Dictyostelium discoideum)
Glycosaminoglycan metabolism (Dictyostelium discoideum)
Heparan sulfate/heparin (HS-GAG) metabolism (Dictyostelium discoideum)
HS-GAG degradation (Dictyostelium discoideum)
IDUA hydrolyses Heparan sulfate chain(6) (Dictyostelium discoideum)
Heparan sulfate chain(7) [lysosomal lumen]
Metabolism (Drosophila melanogaster)
Metabolism of carbohydrates and carbohydrate derivatives (Drosophila melanogaster)
Glycosaminoglycan metabolism (Drosophila melanogaster)
Heparan sulfate/heparin (HS-GAG) metabolism (Drosophila melanogaster)
HS-GAG degradation (Drosophila melanogaster)
IDUA hydrolyses Heparan sulfate chain(6) (Drosophila melanogaster)
Heparan sulfate chain(7) [lysosomal lumen]
SGSH hydrolyses Heparan sulfate chain(7) (Drosophila melanogaster)
Heparan sulfate chain(7) [lysosomal lumen]
Metabolism (Gallus gallus)
Metabolism of carbohydrates and carbohydrate derivatives (Gallus gallus)
Glycosaminoglycan metabolism (Gallus gallus)
Heparan sulfate/heparin (HS-GAG) metabolism (Gallus gallus)
HS-GAG degradation (Gallus gallus)
IDUA hydrolyses Heparan sulfate chain(6) (Gallus gallus)
Heparan sulfate chain(7) [lysosomal lumen]
SGSH hydrolyses Heparan sulfate chain(7) (Gallus gallus)
Heparan sulfate chain(7) [lysosomal lumen]
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of carbohydrate metabolism (Homo sapiens)
Mucopolysaccharidoses (Homo sapiens)
MPS IIIA - Sanfilippo syndrome A (Homo sapiens)
Defective SGSH does not hydrolyse Heparan sulfate chain(7) (Homo sapiens)
Heparan sulfate chain(7) [lysosomal lumen]
Metabolism (Homo sapiens)
Metabolism of carbohydrates and carbohydrate derivatives (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Heparan sulfate/heparin (HS-GAG) metabolism (Homo sapiens)
HS-GAG degradation (Homo sapiens)
IDUA hydrolyses Heparan sulfate chain(6) (Homo sapiens)
Heparan sulfate chain(7) [lysosomal lumen]
SGSH hydrolyses Heparan sulfate chain(7) (Homo sapiens)
Heparan sulfate chain(7) [lysosomal lumen]
Metabolism (Mus musculus)
Metabolism of carbohydrates and carbohydrate derivatives (Mus musculus)
Glycosaminoglycan metabolism (Mus musculus)
Heparan sulfate/heparin (HS-GAG) metabolism (Mus musculus)
HS-GAG degradation (Mus musculus)
IDUA hydrolyses Heparan sulfate chain(6) (Mus musculus)
Heparan sulfate chain(7) [lysosomal lumen]
SGSH hydrolyses Heparan sulfate chain(7) (Mus musculus)
Heparan sulfate chain(7) [lysosomal lumen]
Metabolism (Rattus norvegicus)
Metabolism of carbohydrates and carbohydrate derivatives (Rattus norvegicus)
Glycosaminoglycan metabolism (Rattus norvegicus)
Heparan sulfate/heparin (HS-GAG) metabolism (Rattus norvegicus)
HS-GAG degradation (Rattus norvegicus)
IDUA hydrolyses Heparan sulfate chain(6) (Rattus norvegicus)
Heparan sulfate chain(7) [lysosomal lumen]
SGSH hydrolyses Heparan sulfate chain(7) (Rattus norvegicus)
Heparan sulfate chain(7) [lysosomal lumen]
Metabolism (Sus scrofa)
Metabolism of carbohydrates and carbohydrate derivatives (Sus scrofa)
Glycosaminoglycan metabolism (Sus scrofa)
Heparan sulfate/heparin (HS-GAG) metabolism (Sus scrofa)
HS-GAG degradation (Sus scrofa)
IDUA hydrolyses Heparan sulfate chain(6) (Sus scrofa)
Heparan sulfate chain(7) [lysosomal lumen]
SGSH hydrolyses Heparan sulfate chain(7) (Sus scrofa)
Heparan sulfate chain(7) [lysosomal lumen]
Metabolism (Xenopus tropicalis)
Metabolism of carbohydrates and carbohydrate derivatives (Xenopus tropicalis)
Glycosaminoglycan metabolism (Xenopus tropicalis)
Heparan sulfate/heparin (HS-GAG) metabolism (Xenopus tropicalis)
HS-GAG degradation (Xenopus tropicalis)
IDUA hydrolyses Heparan sulfate chain(6) (Xenopus tropicalis)
Heparan sulfate chain(7) [lysosomal lumen]
SGSH hydrolyses Heparan sulfate chain(7) (Xenopus tropicalis)
Heparan sulfate chain(7) [lysosomal lumen]
External Reference Information
External Reference
alpha-D-GlcNS3S-(1->4)-beta-D-GlcA-(1->3)-beta-D-Gal-(1->3)-beta-D-Gal-(1->4)-beta-D-Xyl-yl group [ChEBI:63810]
Participates
as an input of
Defective SGSH does not hydrolyse Heparan sulfate chain(7) (Homo sapiens)
SGSH hydrolyses Heparan sulfate chain(7) (Drosophila melanogaster)
SGSH hydrolyses Heparan sulfate chain(7) (Gallus gallus)
SGSH hydrolyses Heparan sulfate chain(7) (Xenopus tropicalis)
SGSH hydrolyses Heparan sulfate chain(7) (Sus scrofa)
SGSH hydrolyses Heparan sulfate chain(7) (Bos taurus)
SGSH hydrolyses Heparan sulfate chain(7) (Rattus norvegicus)
SGSH hydrolyses Heparan sulfate chain(7) (Mus musculus)
SGSH hydrolyses Heparan sulfate chain(7) (Homo sapiens)
SGSH hydrolyses Heparan sulfate chain(7) (Canis familiaris)
as an output of
IDUA hydrolyses Heparan sulfate chain(6) (Dictyostelium discoideum)
IDUA hydrolyses Heparan sulfate chain(6) (Drosophila melanogaster)
IDUA hydrolyses Heparan sulfate chain(6) (Gallus gallus)
IDUA hydrolyses Heparan sulfate chain(6) (Xenopus tropicalis)
IDUA hydrolyses Heparan sulfate chain(6) (Sus scrofa)
IDUA hydrolyses Heparan sulfate chain(6) (Bos taurus)
IDUA hydrolyses Heparan sulfate chain(6) (Rattus norvegicus)
IDUA hydrolyses Heparan sulfate chain(6) (Mus musculus)
IDUA hydrolyses Heparan sulfate chain(6) (Homo sapiens)
IDUA hydrolyses Heparan sulfate chain(6) (Canis familiaris)
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