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lomitapide [endoplasmic reticulum lumen]
Stable Identifier
R-ALL-9737774
Type
ChemicalDrug
Compartment
endoplasmic reticulum lumen
Locations in the PathwayBrowser
for Species:
Homo sapiens
Bos taurus
Caenorhabditis elegans
Canis familiaris
Danio rerio
Drosophila melanogaster
Gallus gallus
Mus musculus
Rattus norvegicus
Sus scrofa
Xenopus tropicalis
Expand all
Transport of small molecules (Bos taurus)
Plasma lipoprotein assembly, remodeling, and clearance (Bos taurus)
Plasma lipoprotein assembly (Bos taurus)
VLDL assembly (Bos taurus)
MTTP lipidates APOB-100, forming a pre-VLDL (Bos taurus)
MTTP:lomitapide [endoplasmic reticulum lumen] (Bos taurus)
lomitapide [endoplasmic reticulum lumen]
Plasma lipoprotein remodeling (Bos taurus)
LDL remodeling (Bos taurus)
MTTP binds lomitapide (Bos taurus)
lomitapide [endoplasmic reticulum lumen]
MTTP:lomitapide [endoplasmic reticulum lumen] (Bos taurus)
lomitapide [endoplasmic reticulum lumen]
Transport of small molecules (Caenorhabditis elegans)
Plasma lipoprotein assembly, remodeling, and clearance (Caenorhabditis elegans)
Plasma lipoprotein remodeling (Caenorhabditis elegans)
LDL remodeling (Caenorhabditis elegans)
MTTP binds lomitapide (Caenorhabditis elegans)
lomitapide [endoplasmic reticulum lumen]
MTTP:lomitapide [endoplasmic reticulum lumen] (Caenorhabditis elegans)
lomitapide [endoplasmic reticulum lumen]
Transport of small molecules (Canis familiaris)
Plasma lipoprotein assembly, remodeling, and clearance (Canis familiaris)
Plasma lipoprotein assembly (Canis familiaris)
VLDL assembly (Canis familiaris)
MTTP lipidates APOB-100, forming a pre-VLDL (Canis familiaris)
MTTP:lomitapide [endoplasmic reticulum lumen] (Canis familiaris)
lomitapide [endoplasmic reticulum lumen]
Plasma lipoprotein remodeling (Canis familiaris)
LDL remodeling (Canis familiaris)
MTTP binds lomitapide (Canis familiaris)
lomitapide [endoplasmic reticulum lumen]
MTTP:lomitapide [endoplasmic reticulum lumen] (Canis familiaris)
lomitapide [endoplasmic reticulum lumen]
Transport of small molecules (Danio rerio)
Plasma lipoprotein assembly, remodeling, and clearance (Danio rerio)
Plasma lipoprotein remodeling (Danio rerio)
LDL remodeling (Danio rerio)
MTTP binds lomitapide (Danio rerio)
lomitapide [endoplasmic reticulum lumen]
MTTP:lomitapide [endoplasmic reticulum lumen] (Danio rerio)
lomitapide [endoplasmic reticulum lumen]
Transport of small molecules (Drosophila melanogaster)
Plasma lipoprotein assembly, remodeling, and clearance (Drosophila melanogaster)
Plasma lipoprotein remodeling (Drosophila melanogaster)
LDL remodeling (Drosophila melanogaster)
MTTP binds lomitapide (Drosophila melanogaster)
lomitapide [endoplasmic reticulum lumen]
MTTP:lomitapide [endoplasmic reticulum lumen] (Drosophila melanogaster)
lomitapide [endoplasmic reticulum lumen]
Transport of small molecules (Gallus gallus)
Plasma lipoprotein assembly, remodeling, and clearance (Gallus gallus)
Plasma lipoprotein assembly (Gallus gallus)
VLDL assembly (Gallus gallus)
MTTP lipidates APOB-100, forming a pre-VLDL (Gallus gallus)
MTTP:lomitapide [endoplasmic reticulum lumen] (Gallus gallus)
lomitapide [endoplasmic reticulum lumen]
Plasma lipoprotein remodeling (Gallus gallus)
LDL remodeling (Gallus gallus)
MTTP binds lomitapide (Gallus gallus)
lomitapide [endoplasmic reticulum lumen]
MTTP:lomitapide [endoplasmic reticulum lumen] (Gallus gallus)
lomitapide [endoplasmic reticulum lumen]
Transport of small molecules (Homo sapiens)
Plasma lipoprotein assembly, remodeling, and clearance (Homo sapiens)
Plasma lipoprotein assembly (Homo sapiens)
VLDL assembly (Homo sapiens)
MTTP lipidates APOB-100, forming a pre-VLDL (Homo sapiens)
MTTP:lomitapide [endoplasmic reticulum lumen] (Homo sapiens)
lomitapide [endoplasmic reticulum lumen]
Plasma lipoprotein remodeling (Homo sapiens)
LDL remodeling (Homo sapiens)
MTTP binds lomitapide (Homo sapiens)
lomitapide [endoplasmic reticulum lumen]
MTTP:lomitapide [endoplasmic reticulum lumen] (Homo sapiens)
lomitapide [endoplasmic reticulum lumen]
Transport of small molecules (Mus musculus)
Plasma lipoprotein assembly, remodeling, and clearance (Mus musculus)
Plasma lipoprotein assembly (Mus musculus)
VLDL assembly (Mus musculus)
MTTP lipidates APOB-100, forming a pre-VLDL (Mus musculus)
MTTP:lomitapide [endoplasmic reticulum lumen] (Mus musculus)
lomitapide [endoplasmic reticulum lumen]
Plasma lipoprotein remodeling (Mus musculus)
LDL remodeling (Mus musculus)
MTTP binds lomitapide (Mus musculus)
lomitapide [endoplasmic reticulum lumen]
MTTP:lomitapide [endoplasmic reticulum lumen] (Mus musculus)
lomitapide [endoplasmic reticulum lumen]
Transport of small molecules (Rattus norvegicus)
Plasma lipoprotein assembly, remodeling, and clearance (Rattus norvegicus)
Plasma lipoprotein assembly (Rattus norvegicus)
VLDL assembly (Rattus norvegicus)
MTTP lipidates APOB-100, forming a pre-VLDL (Rattus norvegicus)
MTTP:lomitapide [endoplasmic reticulum lumen] (Rattus norvegicus)
lomitapide [endoplasmic reticulum lumen]
Plasma lipoprotein remodeling (Rattus norvegicus)
LDL remodeling (Rattus norvegicus)
MTTP binds lomitapide (Rattus norvegicus)
lomitapide [endoplasmic reticulum lumen]
MTTP:lomitapide [endoplasmic reticulum lumen] (Rattus norvegicus)
lomitapide [endoplasmic reticulum lumen]
Transport of small molecules (Sus scrofa)
Plasma lipoprotein assembly, remodeling, and clearance (Sus scrofa)
Plasma lipoprotein assembly (Sus scrofa)
VLDL assembly (Sus scrofa)
MTTP lipidates APOB-100, forming a pre-VLDL (Sus scrofa)
MTTP:lomitapide [endoplasmic reticulum lumen] (Sus scrofa)
lomitapide [endoplasmic reticulum lumen]
Plasma lipoprotein remodeling (Sus scrofa)
LDL remodeling (Sus scrofa)
MTTP binds lomitapide (Sus scrofa)
lomitapide [endoplasmic reticulum lumen]
MTTP:lomitapide [endoplasmic reticulum lumen] (Sus scrofa)
lomitapide [endoplasmic reticulum lumen]
Transport of small molecules (Xenopus tropicalis)
Plasma lipoprotein assembly, remodeling, and clearance (Xenopus tropicalis)
Plasma lipoprotein remodeling (Xenopus tropicalis)
LDL remodeling (Xenopus tropicalis)
MTTP binds lomitapide (Xenopus tropicalis)
lomitapide [endoplasmic reticulum lumen]
MTTP:lomitapide [endoplasmic reticulum lumen] (Xenopus tropicalis)
lomitapide [endoplasmic reticulum lumen]
External Reference Information
External Reference
lomitapide [Guide to Pharmacology:7439]
Participates
as an input of
MTTP binds lomitapide (Caenorhabditis elegans)
MTTP binds lomitapide (Drosophila melanogaster)
MTTP binds lomitapide (Gallus gallus)
MTTP binds lomitapide (Xenopus tropicalis)
MTTP binds lomitapide (Danio rerio)
MTTP binds lomitapide (Sus scrofa)
MTTP binds lomitapide (Bos taurus)
MTTP binds lomitapide (Canis familiaris)
MTTP binds lomitapide (Rattus norvegicus)
MTTP binds lomitapide (Mus musculus)
MTTP binds lomitapide (Homo sapiens)
as a component of
MTTP:lomitapide [endoplasmic reticulum lumen] (Danio rerio)
MTTP:lomitapide [endoplasmic reticulum lumen] (Caenorhabditis elegans)
MTTP:lomitapide [endoplasmic reticulum lumen] (Gallus gallus)
MTTP:lomitapide [endoplasmic reticulum lumen] (Rattus norvegicus)
MTTP:lomitapide [endoplasmic reticulum lumen] (Drosophila melanogaster)
MTTP:lomitapide [endoplasmic reticulum lumen] (Canis familiaris)
MTTP:lomitapide [endoplasmic reticulum lumen] (Xenopus tropicalis)
MTTP:lomitapide [endoplasmic reticulum lumen] (Sus scrofa)
MTTP:lomitapide [endoplasmic reticulum lumen] (Bos taurus)
MTTP:lomitapide [endoplasmic reticulum lumen] (Mus musculus)
MTTP:lomitapide [endoplasmic reticulum lumen] (Homo sapiens)
Disease
Name
Identifier
Synonyms
familial hypercholesterolemia
DOID:13810
Fredrickson type IIa hyperlipoproteinemia, type II hyperlipidemia, hyperbetalipoproteinemia, familial hypercholesteremia, familial hyperbetalipoproteinaemia, Fredrickson type IIa lipidaemia
Cross References
PharmacoDB
PDBC03003
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