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HEXA [lysosomal lumen]
Stable Identifier
R-BTA-1605799
Type
Protein [EntityWithAccessionedSequence]
Species
Bos taurus
Compartment
lysosomal lumen
Synonyms
HEXA(88-528), Q0V8R6
Locations in the PathwayBrowser
Expand all
Metabolism (Bos taurus)
Metabolism of carbohydrates (Bos taurus)
Glycosaminoglycan metabolism (Bos taurus)
Chondroitin sulfate/dermatan sulfate metabolism (Bos taurus)
CS/DS degradation (Bos taurus)
HEXA cleaves the terminal GalNAc from DS (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXA dimer [lysosomal lumen] (Bos taurus)
Mature HEXA [lysosomal lumen] (Bos taurus)
HEXA [lysosomal lumen] (Bos taurus)
Hyaluronan metabolism (Bos taurus)
Hyaluronan uptake and degradation (Bos taurus)
HEXA cleaves the terminal GalNAc from small HA fragments (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXA dimer [lysosomal lumen] (Bos taurus)
Mature HEXA [lysosomal lumen] (Bos taurus)
HEXA [lysosomal lumen] (Bos taurus)
Keratan sulfate/keratin metabolism (Bos taurus)
Keratan sulfate degradation (Bos taurus)
HEXA cleaves the terminal GalNAc from keratan sulfate (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXA dimer [lysosomal lumen] (Bos taurus)
Mature HEXA [lysosomal lumen] (Bos taurus)
HEXA [lysosomal lumen] (Bos taurus)
Metabolism of lipids (Bos taurus)
Sphingolipid metabolism (Bos taurus)
Glycosphingolipid metabolism (Bos taurus)
Glycosphingolipid catabolism (Bos taurus)
bHEXA hydrolyzes GM2A:GM2 to GM2A:GM3 (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXA dimer [lysosomal lumen] (Bos taurus)
Mature HEXA [lysosomal lumen] (Bos taurus)
HEXA [lysosomal lumen] (Bos taurus)
bHEXA,bHEXB hydrolyze GM2A:GA2 to GM2A:LacCer (Bos taurus)
bHEXA,bHEXB [lysosomal lumen] (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXA dimer [lysosomal lumen] (Bos taurus)
Mature HEXA [lysosomal lumen] (Bos taurus)
HEXA [lysosomal lumen] (Bos taurus)
bHEXA,bHEXB hydrolyze PSAP(195-273):Gb4Cer:PE (Bos taurus)
bHEXA,bHEXB [lysosomal lumen] (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXA dimer [lysosomal lumen] (Bos taurus)
Mature HEXA [lysosomal lumen] (Bos taurus)
HEXA [lysosomal lumen] (Bos taurus)
bHEXA,bHEXS hydrolyze GM2A:SM2 (Bos taurus)
bHEXA,bHEXS [lysosomal lumen] (Bos taurus)
bHEXA [lysosomal lumen] (Bos taurus)
HEXA dimer [lysosomal lumen] (Bos taurus)
Mature HEXA [lysosomal lumen] (Bos taurus)
HEXA [lysosomal lumen] (Bos taurus)
bHEXS [lysosomal lumen] (Bos taurus)
HEXA dimer [lysosomal lumen] (Bos taurus)
Mature HEXA [lysosomal lumen] (Bos taurus)
HEXA [lysosomal lumen] (Bos taurus)
External Reference Information
External Reference
UniProt:Q0V8R6
Gene Names
HEXA
Reference Genes
BioGPS Gene:504468 HEXA
ENSEMBL:ENSBTAG00000012981
ENSEMBL:ENSBTAG00000012981.4 HEXA
KEGG Gene (Bos taurus):504468 HEXA
Monarch:504468 HEXA
NCBI Gene:504468 HEXA
Reference Transcript
RefSeq:NM_001075164.2 HEXA
Other Identifiers
504468
GO:0001501
GO:0003824
GO:0004553
GO:0004563
GO:0005764
GO:0005773
GO:0005829
GO:0005975
GO:0006024
GO:0006629
GO:0006689
GO:0006790
GO:0007040
GO:0007605
GO:0007626
GO:0007628
GO:0008375
GO:0016020
GO:0016740
GO:0016787
GO:0019915
GO:0019953
GO:0023052
GO:0030154
GO:0030203
GO:0030209
GO:0030214
GO:0031410
GO:0042552
GO:0042582
GO:0043226
GO:0043231
GO:0046982
GO:0048667
GO:0048856
GO:0050877
GO:0050884
GO:0050885
GO:0051651
GO:0060395
GO:1901135
GO:1905379
Participates
as a component of
Mature HEXA [lysosomal lumen] (Bos taurus)
Other forms of this molecule
HEXA [lysosomal lumen]
Inferred From
HEXA(88-528) [lysosomal lumen]
(Homo sapiens)
Modified Residues
Name
Inter-chain Crosslink via L-cystine (cross-link) at 104 and 58 (in Homo sapiens)
Coordinate
104
PsiMod Name
L-cystine (cross-link)
PsiMod Definition
A protein modification that effectively cross-links two L-cysteine residues to form L-cystine.
Cross References
RefSeq
NP_001068632.1
OpenTargets
ENSG00000213614
Ensembl
ENSBTAT00000017261
,
ENSBTAG00000012981
,
ENSBTAP00000017261
PRO
Q0V8R6
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