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GCSH [mitochondrial matrix]
Stable Identifier
R-BTA-5693951
Type
Protein [EntityWithAccessionedSequence]
Species
Bos taurus
Compartment
mitochondrial matrix
Synonyms
GCSH, P20821
Locations in the PathwayBrowser
Expand all
Metabolism (Bos taurus)
Metabolism of amino acids and derivatives (Bos taurus)
Glyoxylate metabolism and glycine degradation (Bos taurus)
Glycine degradation (Bos taurus)
AMT transfers NH2CH2 from GCSH:SAMDLL to THF (Bos taurus)
GCSH:DHLL [mitochondrial matrix] (Bos taurus)
GCSH [mitochondrial matrix] (Bos taurus)
GCSH:SAMDLL [mitochondrial matrix] (Bos taurus)
GCSH [mitochondrial matrix] (Bos taurus)
DLD dimer:2xFAD oxidises GCSH:DHLL to GCSH:lipoate (Bos taurus)
GCSH:DHLL [mitochondrial matrix] (Bos taurus)
GCSH [mitochondrial matrix] (Bos taurus)
PXLP-K754-GLDC dimer decarboxylates Gly (Bos taurus)
GCSH:SAMDLL [mitochondrial matrix] (Bos taurus)
GCSH [mitochondrial matrix] (Bos taurus)
Metabolism of proteins (Bos taurus)
Post-translational protein modification (Bos taurus)
Protein lipoylation (Bos taurus)
LIPT1 transfers lipoyl group from lipoyl-GCSH to DBT/DLST (Bos taurus)
GCSH [mitochondrial matrix] (Bos taurus)
LIPT1 transfers lipoyl group from lipoyl-GCSH to DLAT (Bos taurus)
GCSH [mitochondrial matrix] (Bos taurus)
LIPT2 transfers octanoyl group to GCSH (Bos taurus)
GCSH [mitochondrial matrix] (Bos taurus)
External Reference Information
External Reference
UniProt:P20821
Gene Names
GCSH
Reference Genes
BioGPS Gene:317723 GCSH
ENSEMBL:ENSBTAG00000006795
ENSEMBL:ENSBTAG00000006795.2 GCSH
KEGG Gene (Bos taurus):317723 GCSH
Monarch:317723 GCSH
NCBI Gene:317723 GCSH
Reference Transcript
RefSeq:NM_174844.1 GCSH
RefSeq:XM_005218384.2 GCSH
Other Identifiers
317723
GO:0005960
GO:0006520
GO:0019464
Participates
as a component of
GCSH:DHLL [mitochondrial matrix] (Bos taurus)
GCSH:SAMDLL [mitochondrial matrix] (Bos taurus)
as an output of
LIPT1 transfers lipoyl group from lipoyl-GCSH to DLAT (Bos taurus)
LIPT1 transfers lipoyl group from lipoyl-GCSH to DBT/DLST (Bos taurus)
as an input of
LIPT2 transfers octanoyl group to GCSH (Bos taurus)
Other forms of this molecule
GCSH [mitochondrial matrix]
GCSH [mitochondrial matrix]
Inferred From
GCSH [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
XP_005218441.1
,
NP_777269.1
OpenTargets
ENSG00000140905
Ensembl
ENSBTAG00000006795
,
ENSBTAT00000008936
,
ENSBTAP00000008936
PDB
3KLR
,
3WDN
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