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DBT [mitochondrial matrix]
Stable Identifier
R-BTA-9859145
Type
Protein [EntityWithAccessionedSequence]
Species
Bos taurus
Compartment
mitochondrial matrix
Synonyms
2-Methylbutyryl-lipoH2-K105-DBT, P11181
Locations in the PathwayBrowser
Expand all
Metabolism (Bos taurus)
Metabolism of amino acids and derivatives (Bos taurus)
Branched-chain amino acid catabolism (Bos taurus)
BCKDH synthesizes BCAA-CoA from KIC, KMVA, KIV (Bos taurus)
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Bos taurus)
DBT [mitochondrial matrix] (Bos taurus)
DBT transfers BCAA to CoA (Bos taurus)
DBT [mitochondrial matrix] (Bos taurus)
External Reference Information
External Reference
UniProt:P11181
Gene Names
DBT
Reference Genes
BioGPS Gene:280759 DBT
ENSEMBL:ENSBTAG00000006320
KEGG:bta:280759 DBT
Monarch:280759 DBT
NCBI Gene:280759 DBT
UCSC:P11181 DBT
Reference Transcript
RefSeq:NM_173905.2 DBT
Other Identifiers
280759
Bt.426.1.S1_at
GO:0003824
GO:0005737
GO:0005739
GO:0005759
GO:0005829
GO:0005856
GO:0006520
GO:0008289
GO:0009083
GO:0015630
GO:0016407
GO:0016491
GO:0016740
GO:0016746
GO:0031405
GO:0031625
GO:0042645
GO:0043226
GO:0043754
GO:0047101
GO:0160157
Participates
as an output of
BCKDHA:BCKDHB tetramer decarboxylates KIC, KMVA, KIV (Bos taurus)
as an input of
DBT transfers BCAA to CoA (Bos taurus)
Other forms of this molecule
DBT [cytosol]
DBT [mitochondrial matrix]
DBT [mitochondrial matrix]
DBT [mitochondrial matrix]
DBT [mitochondrial matrix]
DBT [mitochondrial matrix]
Inferred From
BCAA-lipoH2-K105-DBT [mitochondrial matrix]
(Homo sapiens)
2-Methylbutyryl-lipoH2-K105-DBT [mitochondrial matrix]
(Homo sapiens)
Modified Residues
Name
N6-lipoyl-L-lysine ((R)-N6-(S8-2-methylbutyryldihydrolipoyl)-L-lysine residue) at 105 (in Homo sapiens)
Coordinate
105
Modification
(R)-N6-(S8-2-methylbutyryldihydrolipoyl)-L-lysine residue
PsiMod Name
N6-lipoyl-L-lysine [MOD:00127]
PsiMod Definition
A protein modification that effectively converts an L-lysine residue to N6-lipoyl-L-lysine.
Cross References
RefSeq
NP_776330.1
ENSEMBL
ENSBTAT00000008292
,
ENSBTAG00000006320
,
ENSBTAP00000008292
IntEnz
2.3.1.168
VGNC
27896
PDB
2IHW
,
2II4
,
2II5
,
2II3
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