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frh-1 [mitochondrial matrix]
Stable Identifier
R-CEL-1362390
Type
Protein [EntityWithAccessionedSequence]
Species
Caenorhabditis elegans
Compartment
mitochondrial matrix
Synonyms
FXN(81-210), Q9TY03
Locations in the PathwayBrowser
Expand all
Metabolism (Caenorhabditis elegans)
Aerobic respiration and respiratory electron transport (Caenorhabditis elegans)
Citric acid cycle (TCA cycle) (Caenorhabditis elegans)
Maturation of TCA enzymes and regulation of TCA cycle (Caenorhabditis elegans)
Frataxin transfers Fe2+ to ACO2 (Caenorhabditis elegans)
2 Iron:FXN [mitochondrial matrix] (Caenorhabditis elegans)
frh-1 [mitochondrial matrix] (Caenorhabditis elegans)
frh-1 [mitochondrial matrix] (Caenorhabditis elegans)
Mitochondrial iron-sulfur cluster biogenesis (Caenorhabditis elegans)
FXN:NFS1:ISD11:ISCU assembles 2Fe-2S iron-sulfur cluster (Caenorhabditis elegans)
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Caenorhabditis elegans)
2 Iron:FXN [mitochondrial matrix] (Caenorhabditis elegans)
frh-1 [mitochondrial matrix] (Caenorhabditis elegans)
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Caenorhabditis elegans)
frh-1 [mitochondrial matrix] (Caenorhabditis elegans)
Frataxin binds iron (Caenorhabditis elegans)
2 Iron:FXN:NFS1:ISD11:ISCU [mitochondrial matrix] (Caenorhabditis elegans)
2 Iron:FXN [mitochondrial matrix] (Caenorhabditis elegans)
frh-1 [mitochondrial matrix] (Caenorhabditis elegans)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Caenorhabditis elegans)
frh-1 [mitochondrial matrix] (Caenorhabditis elegans)
External Reference Information
External Reference
UniProt:Q9TY03
Gene Names
frh-1
Reference Genes
BioGPS Gene:174002 frh-1
ENSEMBL:WBGene00001486
KEGG:cel:CELE_F59G1.7 frh-1
Monarch:174002 frh-1
NCBI Gene:174002 frh-1
UCSC:Q9TY03 frh-1
Wormbase:WBGene00001486
Reference Transcript
RefSeq:NM_062782.3 frh-1
Other Identifiers
174002
18485685
187488_at
A_12_P120338
CE19476
CE_WBGene00001486_A
CE_WBGene00001486_B
CE_WBGene00001486_C
CGZ0025688
F59G1.7
F59G1.7_107-166_0.917_7_B
F59G1.7_252-311_0.946_4_A
F59G1.7_315-374_0.969_1_C
F59G1_7P00036
F59G1_7P00168
F59G1_7P00304
GO:0000303
GO:0003824
GO:0004322
GO:0005739
GO:0006783
GO:0006826
GO:0006879
GO:0008198
GO:0008199
GO:0008340
GO:0016226
GO:0016491
GO:0018283
GO:0034986
GO:0042542
GO:0043226
GO:0051537
GO:0140104
WBGene00001486
cea2.c.13123
Participates
as an output of
Frataxin transfers Fe2+ to ACO2 (Caenorhabditis elegans)
as a component of
FXN:NFS1:ISD11:ISCU:2Fe-2S Cluster [mitochondrial matrix] (Caenorhabditis elegans)
2 Iron:FXN [mitochondrial matrix] (Caenorhabditis elegans)
FXN:ISD11:NFS1:ISCU [mitochondrial matrix] (Caenorhabditis elegans)
Inferred From
FXN(81-210) [mitochondrial matrix]
(Homo sapiens)
Cross References
RefSeq
NP_495183.1
ENSEMBL
F59G1.7.1
PRO
Q9TY03
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q19289
6
phospho-ifb-1 [nucleoplasm]
(R-CEL-5229018-7)
phospho-ifb-1 [nucleoplasm]
(R-CEL-5228738-7)
ifb-1 [cytosol]
(R-CEL-2995384-7)
ifb-1 [nuclear envelope]
(R-CEL-352248-7)
ifb-1 [nuclear envelope]
(R-CEL-352244-7)
ifb-1 [nucleoplasm]
(R-CEL-264867-7)
0.488
2
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