Toggle navigation
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
About
What is Reactome ?
News
Team
Scientific Advisory Board
Funding
Editorial Calendar
Release Calendar
Statistics
Our Logo
License Agreement
Privacy Notice
Disclaimer
Digital Preservation
Contact us
Content
Table of Contents
DOIs
Data Schema
Reactome Research Spotlight
ORCID Integration Project
COVID-19 Disease Pathways
Docs
Userguide
Pathway Browser
How do I search ?
Details Panel
Analysis Tools
Analysis Data
Analysis Gene Expression
Species Comparison
Tissue Distribution
Diseases
Cytomics
Review Status of Reactome Events
ReactomeFIViz
Developer's Zone
Graph Database
Analysis Service
Content Service
Pathways Overview
Pathway Diagrams
Icon Info
EHLD Specs & Guidelines
Icon Library Guidelines
Data Model
Curator Guide
Release Documentation
Computationally inferred events
FAQ
Linking to Us
Citing us
Tools
Pathway Browser
Analyse gene list
Analyse gene expression
Species Comparison
Tissue Distribution
Analysis Service
Content Service
ReactomeFIViz
Advanced Data Search
Site Search
Community
Contribute Pathway Knowledge
Icon Library
Outreach
Events
Publications
Partners
Contributors
Resources Guide
Download
Search ...
Go!
misfolded CFTR [endoplasmic reticulum membrane]
Stable Identifier
R-DRE-8868730
Type
Protein [EntityWithAccessionedSequence]
Species
Danio rerio
Compartment
endoplasmic reticulum membrane
Synonyms
Q1LX78
Locations in the PathwayBrowser
Expand all
Autophagy (Danio rerio)
Macroautophagy (Danio rerio)
Selective autophagy (Danio rerio)
Aggrephagy (Danio rerio)
Parkin transfers Ub to misfolded proteins (Danio rerio)
Ub:Misfolded proteins:PRKN:UBE2N:UBE2V1 [cytosol] (Danio rerio)
Ub-Misfolded Proteins [cytosol] (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
PolyUb-Misfolded Proteins:HDAC6 bind dynein motor (Danio rerio)
PolyUb-Misfolded Proteins:HDAC6 [cytosol] (Danio rerio)
PolyUb-Misfolded Proteins [cytosol] (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
PolyUb-Misfolded Proteins:HDAC6:Dynein complex [cytosol] (Danio rerio)
PolyUb-Misfolded Proteins:HDAC6 [cytosol] (Danio rerio)
PolyUb-Misfolded Proteins [cytosol] (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
PolyUb-Misfolded proteins bind vimentin to form aggresome (Danio rerio)
Poly-vimentin:PolyUb-Misfolded Proteins:HDAC6:Microtubule:Dynein complex [microtubule organizing center] (Danio rerio)
PolyUb-Misfolded Proteins:HDAC6:Microtubule:Dynein complex [microtubule organizing center] (Danio rerio)
PolyUb-Misfolded Proteins:HDAC6:Dynein complex [cytosol] (Danio rerio)
PolyUb-Misfolded Proteins:HDAC6 [cytosol] (Danio rerio)
PolyUb-Misfolded Proteins [cytosol] (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
PolyUb-Misfolded Proteins:HDAC6:Microtubule:Dynein complex [microtubule organizing center] (Danio rerio)
PolyUb-Misfolded Proteins:HDAC6:Dynein complex [cytosol] (Danio rerio)
PolyUb-Misfolded Proteins:HDAC6 [cytosol] (Danio rerio)
PolyUb-Misfolded Proteins [cytosol] (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
PolyUb:misfolded proteins dissociate from PRKN:UBE2N:UBE2V1 (Danio rerio)
PolyUb-Misfolded Proteins [cytosol] (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
PolyUb:Misfolded proteins:PRKN:UBE2N:UBE2V1 [cytosol] (Danio rerio)
PolyUb-Misfolded Proteins [cytosol] (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
Ub:misfolded proteins polymerize to PolyUb:misfolded proteins (Danio rerio)
PolyUb:Misfolded proteins:PRKN:UBE2N:UBE2V1 [cytosol] (Danio rerio)
PolyUb-Misfolded Proteins [cytosol] (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
Ub:Misfolded proteins:PRKN:UBE2N:UBE2V1 [cytosol] (Danio rerio)
Ub-Misfolded Proteins [cytosol] (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
Transport of small molecules (Danio rerio)
ABC-family proteins mediated transport (Danio rerio)
CFTR transits to the plasma membrane (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
RNF5 and RNF185 ubiquitinate misfolded CFTR (Danio rerio)
Ub-misfolded nascent CFTR:ERAD complex [endoplasmic reticulum membrane] (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
misfolded CFTR:ERAD complex [endoplasmic reticulum membrane] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
misfolded CFTR is degraded by the 26S proteasome (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
misfolded CFTR [endoplasmic reticulum membrane] (Danio rerio)
External Reference Information
External Reference
UniProt:Q1LX78
Reference Genes
BioGPS Gene:559080
ENSEMBL:ENSDARG00000041107
KEGG:dre:559080
Monarch:559080
NCBI Gene:559080
UCSC:Q1LX78
Reference Transcript
RefSeq:NM_001044883.1
Other Identifiers
13058035
559080
A_15_P150461
CUST_3489_PI428451958
DRER08123
ENSDART00000060243
ENSDART00000060243_1
ENSDART00000060243_2
ENSDART00000100729
GO:0002376
GO:0002679
GO:0003824
GO:0005215
GO:0005254
GO:0005260
GO:0005524
GO:0005768
GO:0005783
GO:0005789
GO:0005829
GO:0005886
GO:0006811
GO:0006821
GO:0007507
GO:0008354
GO:0015106
GO:0015108
GO:0015701
GO:0016020
GO:0016324
GO:0016787
GO:0016853
GO:0016887
GO:0030154
GO:0030217
GO:0031016
GO:0031410
GO:0031901
GO:0034220
GO:0034707
GO:0035162
GO:0035377
GO:0042626
GO:0042742
GO:0043226
GO:0045087
GO:0048856
GO:0048870
GO:0050891
GO:0055038
GO:0055085
GO:0060063
GO:0070121
GO:0090022
GO:0097535
GO:0098542
GO:0140359
GO:0140657
GO:1902476
GO:1904322
GT_Spec_NM_001044883.1_106682
MADDr01006105
NM_001044883
OTTDART00000016385
Participates
as a component of
misfolded CFTR:ERAD complex [endoplasmic reticulum membrane] (Danio rerio)
Ub-misfolded nascent CFTR [cytosol] (Danio rerio)
as an input of
CFTR transits to the plasma membrane (Danio rerio)
Other forms of this molecule
PolyUb-CFTR [plasma membrane]
CFTR [lysosomal membrane]
CFTR [Golgi-associated vesicle membrane]
CFTR [plasma membrane]
Inferred From
CFTR [endoplasmic reticulum membrane]
(Homo sapiens)
misfolded CFTR [endoplasmic reticulum membrane]
(Homo sapiens)
Cross References
RefSeq
NP_001038348.1
ENSEMBL
ENSDART00000060243
,
ENSDARG00000041107
,
ENSDARP00000060242
ZFIN
ZDB-GENE-050517-20
PRO
Q1LX78
PDB
5UAR
,
5W81
© 2025
Reactome
Cite Us!
Cite Us!
Cite Us!
Warning!
Unable to extract citation. Please try again later.
Download As:
BibTeX
RIS
Text