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SUCLA2 [mitochondrial matrix]
Stable Identifier
R-HSA-156624
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial matrix
Synonyms
Succinyl-CoA synthetase, betaA chain
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Citric acid cycle (TCA cycle) (Homo sapiens)
SUCLG1/A2 cleaves succinyl-CoA (Homo sapiens)
SUCLA2:SUCLG1 [mitochondrial matrix] (Homo sapiens)
SUCLA2:Mg2+ [mitochondrial matrix] (Homo sapiens)
SUCLA2 [mitochondrial matrix] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9P2R7 SUCLA2
Gene Names
SUCLA2
Chain
transit peptide:1-52, chain:53-463
Reference Genes
BioGPS Gene:8803 SUCLA2
COSMIC (genes):SUCLA2 SUCLA2
CTD Gene:8803 SUCLA2
dbSNP Gene:8803 SUCLA2
ENSEMBL:ENSG00000136143 SUCLA2
ENSEMBL_homo_sapiens_GENE:ENSG00000136143.16 SUCLA2
HGNC:11448 SUCLA2
KEGG Gene (Homo sapiens):8803 SUCLA2
Monarch:8803 SUCLA2
NCBI Gene:8803 SUCLA2
OMIM:603921 SUCLA2
UCSC:Q9P2R7 SUCLA2
Reference Transcript
RefSeq:NM_003850.2 SUCLA2
Other Identifiers
11748619_a_at
11748620_x_at
11755266_x_at
11755492_a_at
11759519_a_at
16778956
16778959
202930_PM_s_at
202930_s_at
2544609
2901605
3513309
3513310
3513323
3513324
3513325
3513326
3513327
3513328
3513332
3513333
3513334
3513336
3513340
3513343
3513347
3513348
3513351
3513352
3513353
3513356
3513357
3513372
3513373
3513377
3513379
3513381
40893_at
7971541
84409_i_at
8803
A_21_P0011228
A_23_P117157
GE683287
GO:0000166
GO:0000287
GO:0003824
GO:0004775
GO:0005515
GO:0005524
GO:0005576
GO:0005615
GO:0005737
GO:0005739
GO:0005759
GO:0006091
GO:0006099
GO:0006104
GO:0006105
GO:0006781
GO:0006790
GO:0009361
GO:0016874
GO:0042709
GO:0043226
GO:0046872
GO:0055086
GO:0070062
GO:1901135
GO:1901289
HMNXSV003007310
HMNXSV003050089
ILMN_1660787
PH_hs_0010761
TC13000651.hg
TC13000652.hg
g11321582_3p_a_at
p4039
Participates
as a component of
SUCLA2:Mg2+ [mitochondrial matrix] (Homo sapiens)
Inferred To
SUCLA2 [mitochondrial matrix]
(Bos taurus)
SUCLA2 [mitochondrial matrix]
(Caenorhabditis elegans)
SUCLA2 [mitochondrial matrix]
(Canis familiaris)
SUCLA2 [mitochondrial matrix]
(Danio rerio)
SUCLA2 [mitochondrial matrix]
(Dictyostelium discoideum)
SUCLA2 [mitochondrial matrix]
(Drosophila melanogaster)
SUCLA2 [mitochondrial matrix]
(Gallus gallus)
SUCLA2 [mitochondrial matrix]
(Mus musculus)
SUCLA2 [mitochondrial matrix]
(Plasmodium falciparum)
SUCLA2 [mitochondrial matrix]
(Rattus norvegicus)
SUCLA2 [mitochondrial matrix]
(Saccharomyces cerevisiae)
SUCLA2 [mitochondrial matrix]
(Schizosaccharomyces pombe)
SUCLA2 [mitochondrial matrix]
(Sus scrofa)
SUCLA2 [mitochondrial matrix]
(Xenopus tropicalis)
Cross References
RefSeq
NP_003841.1
OpenTargets
ENSG00000136143
GeneCards
Q9P2R7
HPA
ENSG00000136143-SUCLA2
Ensembl
ENST00000646932
,
ENSP00000494360
,
ENSP00000494987
,
ENSG00000136143
,
ENST00000643584
PRO
Q9P2R7
Pharos - Targets
Q9P2R7
Orphanet
15568
HMDB Protein
HMDBP00971
PDB
6G4Q
Interactors (4)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:Q96CV9 OPTN
5
OPTN [recycling endosome membrane]
(R-HSA-8854141)
OPTN [Golgi membrane]
(R-HSA-2161111)
p-S177-OPTN [nucleoplasm]
(R-HSA-2562595)
p-S177-OPTN [cytosol]
(R-HSA-2562525)
OPTN [cytosol]
(R-HSA-9687907)
0.556
3
UniProt:Q9UBN6 TNFRSF10D
1
TNFRSF10D [plasma membrane]
(R-HSA-5633374)
0.556
3
UniProt:Q15436 SEC23A
4
p-S738,T744 SEC23A [cytosol]
(R-HSA-5685740)
SEC23A [ER to Golgi transport vesicle membrane]
(R-HSA-204024)
SEC23A [cytosol]
(R-HSA-203972)
SEC23A [endoplasmic reticulum membrane]
(R-HSA-203976)
0.556
3
UniProt:P13569 CFTR
17
PolyUb-CFTR [clathrin-coated endocytic vesicle membrane]
(R-HSA-8869104)
PolyUb-CFTR [plasma membrane]
(R-HSA-8867595)
CFTR [lysosomal membrane]
(R-HSA-5627279)
CFTR [Golgi-associated vesicle membrane]
(R-HSA-5627079)
CFTR [endosome membrane]
(R-HSA-6782965)
PolyUb-CFTR [endosome membrane]
(R-HSA-6782976)
CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866834)
ub-CFTR F508del [cytosol]
(R-HSA-8866838)
ub-CFTR F508del [endoplasmic reticulum membrane]
(R-HSA-8866842)
CFTR G542* [plasma membrane]
(R-HSA-5678986)
CFTR G551D [plasma membrane]
(R-HSA-5678977)
CFTR W1282* [plasma membrane]
(R-HSA-5678976)
CFTR F508del [plasma membrane]
(R-HSA-5678978)
CFTR N1303K [plasma membrane]
(R-HSA-5678983)
CFTR [plasma membrane]
(R-HSA-383188)
CFTR [endoplasmic reticulum membrane]
(R-HSA-8866837)
misfolded CFTR [endoplasmic reticulum membrane]
(R-HSA-8868730)
0.483
8
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