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NDUFB2 [mitochondrial inner membrane]
Stable Identifier
R-HSA-163941
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase AGGG subunit
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to CoQH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB2 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O95178 NDUFB2
Gene Names
NDUFB2
Chain
transit peptide:1-33, chain:34-105
Reference Genes
BioGPS Gene:4708 NDUFB2
COSMIC (genes):NDUFB2 NDUFB2
CTD Gene:4708 NDUFB2
dbSNP Gene:4708 NDUFB2
ENSEMBL:ENSG00000090266 NDUFB2
HGNC:7697 NDUFB2
KEGG:hsa:4708 NDUFB2
Monarch:4708 NDUFB2
NCBI Gene:4708 NDUFB2
OMIM:603838 NDUFB2
UCSC:O95178 NDUFB2
Reference Transcript
RefSeq:NM_004546.2 NDUFB2
Other Identifiers
11744822_a_at
218200_PM_s_at
218200_s_at
218201_PM_at
218201_at
240391_PM_at
240391_at
3027524
3027534
3027539
3027540
3027541
3027542
3027543
3027544
3027545
3027546
3027547
3027548
3027549
3027550
3027551
3027552
3027553
3027554
3027555
3027560
3027561
3027562
3027563
3027564
43135_at
4708
68790_at
78713_at
8136602
A_14_P136649
A_14_P200232
A_24_P406301
GE61360
GO:0003824
GO:0005215
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0008137
GO:0009060
GO:0016491
GO:0032981
GO:0042776
GO:0043226
GO:0045271
GO:0055085
GO:0055086
GO:0065003
GO:1901135
GO:1902600
HMNXSV003030403
Hs.188521.0.A1_3p_at
Hs.27262.2.S1_3p_a_at
ILMN_2117330
PH_hs_0022069
RNA94981|RNS_63_197
TC07000885.hg
g4758777_3p_a_at
p26446
Participates
as a component of
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
Inferred To
NDUFB2 [mitochondrial inner membrane]
(Bos taurus)
NDUFB2 [mitochondrial inner membrane]
(Caenorhabditis elegans)
NDUFB2 [mitochondrial inner membrane]
(Canis familiaris)
NDUFB2 [mitochondrial inner membrane]
(Gallus gallus)
NDUFB2 [mitochondrial inner membrane]
(Sus scrofa)
Ndufb2 [mitochondrial inner membrane]
(Mus musculus)
Ndufb2 [mitochondrial inner membrane]
(Rattus norvegicus)
ND-AGGG [mitochondrial inner membrane]
(Drosophila melanogaster)
ndufb2 [mitochondrial inner membrane]
(Danio rerio)
ndufb2 [mitochondrial inner membrane]
(Xenopus tropicalis)
Cross References
ENSEMBL
ENST00000465506
,
ENST00000247866
,
ENSP00000419357
,
ENST00000476279
,
ENSP00000419087
,
ENSP00000247866
OpenTargets
ENSG00000090266
HPA
ENSG00000090266-NDUFB2
PRO
O95178
Pharos - Targets
O95178
HMDB Protein
HMDBP00136
PDB
5XTI
,
5XTH
,
5XTD
,
5XTC
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