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NDUFV3 [mitochondrial inner membrane]
Stable Identifier
R-HSA-163943
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase 9 kDa subunit
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
NDUF subunits bind to form the FP subcomplex (Homo sapiens)
FP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFV3 [mitochondrial inner membrane] (Homo sapiens)
NDUFV3 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
FP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFV3 [mitochondrial inner membrane] (Homo sapiens)
FP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFV3 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
FP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFV3 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
FP subcomplex (-NDUFAF2) [mitochondrial inner membrane] (Homo sapiens)
NDUFV3 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
FP subcomplex (-NDUFAF2) [mitochondrial inner membrane] (Homo sapiens)
NDUFV3 [mitochondrial inner membrane] (Homo sapiens)
Metabolism of proteins (Homo sapiens)
Mitochondrial protein degradation (Homo sapiens)
LONP1 binds mitochondrial inner membrane proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial inner membrane) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
NDUFV3 [mitochondrial inner membrane] (Homo sapiens)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
NDUFV3 [mitochondrial inner membrane] (Homo sapiens)
LONP1 degrades mitochondrial inner membrane proteins (Homo sapiens)
LONP1:substrate protein (mitochondrial inner membrane) [mitochondrial matrix] (Homo sapiens)
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
NDUFV3 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:P56181 NDUFV3
Gene Names
NDUFV3
Chain
transit peptide:1-34, chain:35-108
Reference Genes
BioGPS Gene:4731 NDUFV3
COSMIC (genes):NDUFV3 NDUFV3
CTD Gene:4731 NDUFV3
dbSNP Gene:4731 NDUFV3
ENSEMBL:ENSG00000160194 NDUFV3
ENSEMBL_homo_sapiens_GENE:ENSG00000160194.18 NDUFV3
HGNC:7719 NDUFV3
KEGG Gene (Homo sapiens):4731 NDUFV3
Monarch:4731 NDUFV3
NCBI Gene:4731 NDUFV3
OMIM:602184 NDUFV3
UCSC:P56181 NDUFV3
Reference Transcript
RefSeq:NM_001001503.1 NDUFV3
RefSeq:NM_021075.3 NDUFV3
Other Identifiers
11723072_x_at
11723449_a_at
11745460_at
226209_PM_at
226209_at
226616_PM_s_at
226616_s_at
2406606
3922930
3922931
3922935
3922937
3922938
3922944
3922945
3922946
3922947
3922948
3922957
3922959
4731
8068857
91619_s_at
91622_at
A_23_P211285
A_24_P241995
A_24_P416951
A_32_P1360
GE60222
GO:0003723
GO:0003824
GO:0005215
GO:0005515
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0008137
GO:0009060
GO:0016020
GO:0016491
GO:0042775
GO:0042776
GO:0043226
GO:0055086
GO:0070469
GO:1901135
HMNXSV003025528
Hs.59745.1.S1_3p_a_at
ILMN_1765500
ILMN_2387731
PH_hs_0022967
PH_hs_0032130
TC21001063.hg
X99728_at
Participates
as a member of
Substrate of LONP1 (mitochondrial inner membrane) [mitochondrial inner membrane] (Homo sapiens)
as a component of
FP subcomplex [mitochondrial inner membrane] (Homo sapiens)
FP subcomplex (-NDUFAF2) [mitochondrial inner membrane] (Homo sapiens)
as an input of
NDUF subunits bind to form the FP subcomplex (Homo sapiens)
Inferred To
Ghost homologue of NDUFV3 [mitochondrial inner membrane]
(Caenorhabditis elegans)
Ghost homologue of NDUFV3 [mitochondrial inner membrane]
(Canis familiaris)
Ghost homologue of NDUFV3 [mitochondrial inner membrane]
(Danio rerio)
Ghost homologue of NDUFV3 [mitochondrial inner membrane]
(Drosophila melanogaster)
Ghost homologue of NDUFV3 [mitochondrial inner membrane]
(Sus scrofa)
Ndufv3 [mitochondrial inner membrane]
(Mus musculus)
Ndufv3 [mitochondrial inner membrane]
(Rattus norvegicus)
NDUFV3 [mitochondrial inner membrane]
(Bos taurus)
NDUFV3 [mitochondrial inner membrane]
(Gallus gallus)
Homologues of NDUFV3 [mitochondrial inner membrane]
(Bos taurus)
ndufv3 [mitochondrial inner membrane]
(Xenopus tropicalis)
Cross References
RefSeq
NP_066553.3
,
NP_001001503.1
OpenTargets
ENSG00000160194
GeneCards
P56181
HPA
ENSG00000160194-NDUFV3
Ensembl
ENST00000354250
,
ENSG00000160194
,
ENSP00000342895
,
ENSP00000346196
,
ENST00000340344
PRO
P56181
Pharos - Targets
P56181
Orphanet
24753
HMDB Protein
HMDBP00148
PDB
5XTD
,
5XTB
,
5XTH
,
5XTI
Interactors (2)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:P49821 NDUFV1
1
NDUFV1 [mitochondrial inner membrane]
(R-HSA-163926)
0.564
2
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.527
3
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