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NDUFB5 [mitochondrial inner membrane]
Stable Identifier
R-HSA-163944
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase SGDH subunit
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Aerobic respiration and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFB5 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O43674 NDUFB5
Gene Names
NDUFB5
Chain
transit peptide:1-46, chain:47-189
Reference Genes
BioGPS Gene:4711 NDUFB5
COSMIC (genes):NDUFB5 NDUFB5
CTD Gene:4711 NDUFB5
dbSNP Gene:4711 NDUFB5
ENSEMBL:ENSG00000136521 NDUFB5
ENSEMBL_homo_sapiens_GENE:ENSG00000136521.13 NDUFB5
HGNC:7700 NDUFB5
KEGG Gene (Homo sapiens):4711 NDUFB5
Monarch:4711 NDUFB5
NCBI Gene:4711 NDUFB5
OMIM:603841 NDUFB5
UCSC:O43674 NDUFB5
Reference Transcript
RefSeq:NM_001199958.1 NDUFB5
RefSeq:NM_002492.3 NDUFB5
RefSeq:NM_001199957.1 NDUFB5
Other Identifiers
11727026_a_at
11757567_x_at
16948304
203621_PM_at
203621_at
2654072
2654075
2654078
2654079
2654081
2654082
2654083
2654084
2654085
2654086
32232_at
4711
8084092
85340_f_at
A_33_P3296682
A_33_P3340164
GE547769
GE61409
GO:0003824
GO:0005215
GO:0005515
GO:0005634
GO:0005654
GO:0005739
GO:0005743
GO:0005747
GO:0006091
GO:0006120
GO:0007005
GO:0008137
GO:0009060
GO:0016020
GO:0016491
GO:0032981
GO:0042776
GO:0043226
GO:0055086
GO:0065003
GO:0070469
GO:1901135
HMNXSV003025832
ILMN_1807397
PH_hs_0001694
g4505362_3p_at
Participates
as a component of
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
Inferred To
ndufb5 [mitochondrial inner membrane]
(Xenopus tropicalis)
hm:zeh0024 [mitochondrial inner membrane]
(Danio rerio)
ndub-5 [mitochondrial inner membrane]
(Caenorhabditis elegans)
NDUFB5 [mitochondrial inner membrane]
(Bos taurus)
NDUFB5 [mitochondrial inner membrane]
(Canis familiaris)
NDUFB5 [mitochondrial inner membrane]
(Gallus gallus)
NDUFB5 [mitochondrial inner membrane]
(Sus scrofa)
Ndufb5 [mitochondrial inner membrane]
(Mus musculus)
Ndufb5 [mitochondrial inner membrane]
(Rattus norvegicus)
ND-SGDH [mitochondrial inner membrane]
(Drosophila melanogaster)
Cross References
RefSeq
NP_001186886.1
,
NP_001186887.1
,
NP_002483.1
OpenTargets
ENSG00000136521
HPA
ENSG00000136521-NDUFB5
GeneCards
O43674
Ensembl
ENST00000259037
,
ENSG00000136521
,
ENSP00000419656
,
ENSP00000259037
,
ENST00000493866
PRO
O43674
Pharos - Targets
O43674
Orphanet
24746
HMDB Protein
HMDBP00163
PDB
5XTI
,
5XTD
,
5XTC
,
5XTH
Interactors (1)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.527
3
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