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CPOX(132-454) [mitochondrial intermembrane space]
Stable Identifier
R-HSA-189448
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial intermembrane space
Synonyms
Coproporphyrinogen III oxidase, mitochondrial, HEM6_HUMAN, CPOX
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
Metabolism of porphyrins (Homo sapiens)
Heme biosynthesis (Homo sapiens)
CPO transforms COPRO3 to PPGEN9 (Homo sapiens)
2xCPO [mitochondrial intermembrane space] (Homo sapiens)
CPOX(132-454) [mitochondrial intermembrane space] (Homo sapiens)
External Reference Information
External Reference
UniProt:P36551 CPOX
Gene Names
CPOX, CPO, CPX
Chain
transit peptide:1-110, chain:111-454
Reference Genes
BioGPS Gene:1371 CPOX
COSMIC (genes):CPOX CPOX
CTD Gene:1371 CPOX
dbSNP Gene:1371 CPOX
ENSEMBL:ENSG00000080819 CPOX
ENSEMBL_homo_sapiens_GENE:ENSG00000080819.9 CPOX
HGNC:2321 CPOX
KEGG Gene (Homo sapiens):1371 CPOX
Monarch:1371 CPOX
NCBI Gene:1371 CPOX
OMIM:612732 CPOX
UCSC:P36551 CPOX
Reference Transcript
RefSeq:NM_000097.5 CPOX
Other Identifiers
11739371_a_at
11746292_a_at
11755686_a_at
1371
16956691
204172_PM_at
204172_at
2685954
2685955
2685956
2685957
2685960
2685964
2685972
2685976
2685977
2685978
2685979
2685980
2685981
37999_at
8089072
A_23_P144179
A_33_P3301025
D16611_s_at
GE57101
GO:0003824
GO:0004109
GO:0005198
GO:0005212
GO:0005737
GO:0005739
GO:0005758
GO:0005829
GO:0006779
GO:0006782
GO:0006783
GO:0016020
GO:0016491
GO:0042803
GO:0043226
HMNXSV003026826
HMNXSV003042557
PH_hs_0005026
TC03003340.hg
g4503016_3p_at
Participates
as a component of
2xCPO [mitochondrial intermembrane space] (Homo sapiens)
Inferred To
CPOX [mitochondrial intermembrane space]
(Bos taurus)
CPOX [mitochondrial intermembrane space]
(Canis familiaris)
CPOX [mitochondrial intermembrane space]
(Sus scrofa)
wu:fc43a01 [mitochondrial intermembrane space]
(Danio rerio)
cpox [mitochondrial intermembrane space]
(Xenopus tropicalis)
CPOX(132-454) [mitochondrial intermembrane space]
(Dictyostelium discoideum)
CPOX(132-454) [mitochondrial intermembrane space]
(Drosophila melanogaster)
CPOX(132-454) [mitochondrial intermembrane space]
(Gallus gallus)
CPOX(132-454) [mitochondrial intermembrane space]
(Mus musculus)
CPOX(132-454) [mitochondrial intermembrane space]
(Plasmodium falciparum)
CPOX(132-454) [mitochondrial intermembrane space]
(Rattus norvegicus)
CPOX(132-454) [mitochondrial intermembrane space]
(Saccharomyces cerevisiae)
CPOX(132-454) [mitochondrial intermembrane space]
(Schizosaccharomyces pombe)
Cross References
RefSeq
NP_000088.3
OpenTargets
ENSG00000080819
IntEnz
1.3.3.3
GeneCards
P36551
HPA
ENSG00000080819-CPOX
ZINC target
P36551
Ensembl
ENST00000647941
,
ENSP00000497326
,
ENSG00000080819
PRO
P36551
Pharos - Targets
P36551
Orphanet
15793
HMDB Protein
HMDBP00251
PDB
2AEX
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