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dermatan-core proteins [Golgi lumen]
Stable Identifier
R-HSA-5607515
Type
Set [DefinedSet]
Species
Homo sapiens
Compartment
Golgi lumen
Locations in the PathwayBrowser
Expand all
Disease (Homo sapiens)
Diseases of metabolism (Homo sapiens)
Diseases of glycosylation (Homo sapiens)
Diseases associated with glycosaminoglycan metabolism (Homo sapiens)
Defective CHST14 causes EDS, musculocontractural type (Homo sapiens)
Defective CHST14 does not transfer SO4(2-) to GalNAc in dermatan or DS (Homo sapiens)
CHST14 substrates [Golgi lumen] (Homo sapiens)
dermatan-core proteins [Golgi lumen] (Homo sapiens)
Metabolism (Homo sapiens)
Metabolism of carbohydrates (Homo sapiens)
Glycosaminoglycan metabolism (Homo sapiens)
Chondroitin sulfate/dermatan sulfate metabolism (Homo sapiens)
Dermatan sulfate biosynthesis (Homo sapiens)
CHST14 transfers SO4(2-) to GalNAc in dermatan or DS (Homo sapiens)
CHST14 substrates [Golgi lumen] (Homo sapiens)
dermatan-core proteins [Golgi lumen] (Homo sapiens)
Dermatan-sulfate epimerase (DSE) converts chondroitin sulfate (CS) to dermatan sulfate (DS) (Homo sapiens)
DSE,DSEL products [Golgi lumen] (Homo sapiens)
dermatan-core proteins [Golgi lumen] (Homo sapiens)
Participants
members
dermatan-BCAN [Golgi lumen]
(Homo sapiens)
dermatan-BGN [Golgi lumen]
(Homo sapiens)
dermatan-CSPG4 [Golgi lumen]
(Homo sapiens)
dermatan-CSPG5 [Golgi lumen]
(Homo sapiens)
dermatan-DCN [Golgi lumen]
(Homo sapiens)
dermatan-NCAN [Golgi lumen]
(Homo sapiens)
dermatan-VCAN [Golgi lumen]
(Homo sapiens)
Participates
as a member of
DSE,DSEL products [Golgi lumen] (Homo sapiens)
CHST14 substrates [Golgi lumen] (Homo sapiens)
Inferred To
dermatan-core proteins [Golgi lumen]
(Bos taurus)
dermatan-core proteins [Golgi lumen]
(Canis familiaris)
dermatan-core proteins [Golgi lumen]
(Danio rerio)
dermatan-core proteins [Golgi lumen]
(Drosophila melanogaster)
dermatan-core proteins [Golgi lumen]
(Gallus gallus)
dermatan-core proteins [Golgi lumen]
(Mus musculus)
dermatan-core proteins [Golgi lumen]
(Rattus norvegicus)
dermatan-core proteins [Golgi lumen]
(Sus scrofa)
dermatan-core proteins [Golgi lumen]
(Xenopus tropicalis)
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