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ACAD9 [mitochondrial inner membrane]
Stable Identifier
R-HSA-5689049
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
Acyl-CoA dehydrogenase family member 9, mitochondrial, ACAD9_HUMAN
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
COA1:MT-ND2, TMEM186:MT-ND3, MT-ND6, NDUFB6 bind the MCIA complex to form a 370kDa subcomplex (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MCIA complex [mitochondrial inner membrane] (Homo sapiens)
ACAD9 [mitochondrial inner membrane] (Homo sapiens)
MCIA complex [mitochondrial inner membrane] (Homo sapiens)
ACAD9 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MCIA complex [mitochondrial inner membrane] (Homo sapiens)
ACAD9 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MCIA complex [mitochondrial inner membrane] (Homo sapiens)
ACAD9 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MCIA complex [mitochondrial inner membrane] (Homo sapiens)
ACAD9 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MCIA complex [mitochondrial inner membrane] (Homo sapiens)
ACAD9 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MCIA complex [mitochondrial inner membrane] (Homo sapiens)
ACAD9 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MCIA complex [mitochondrial inner membrane] (Homo sapiens)
ACAD9 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
370 kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
MCIA complex [mitochondrial inner membrane] (Homo sapiens)
ACAD9 [mitochondrial inner membrane] (Homo sapiens)
MCIA complex [mitochondrial inner membrane] (Homo sapiens)
ACAD9 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:Q9H845 ACAD9
Gene Names
ACAD9
Chain
transit peptide:1-37, chain:38-621
Reference Genes
BioGPS Gene:28976 ACAD9
COSMIC (genes):ACAD9 ACAD9
CTD Gene:28976 ACAD9
dbSNP Gene:28976 ACAD9
ENSEMBL:ENSG00000177646 ACAD9
ENSEMBL_homo_sapiens_GENE:ENSG00000177646.20 ACAD9
HGNC:21497 ACAD9
KEGG Gene (Homo sapiens):28976 ACAD9
Monarch:28976 ACAD9
NCBI Gene:28976 ACAD9
OMIM:611103 ACAD9
UCSC:Q9H845 ACAD9
Reference Transcript
RefSeq:NM_014049.4 ACAD9
Other Identifiers
11743539_a_at
11743540_s_at
11747330_s_at
11751634_a_at
16945254
224160_PM_s_at
224160_s_at
2641342
2641343
2641347
2641352
2641354
2641358
2641359
2641361
2641362
2641363
2641364
2641366
2641368
2641369
2641372
2641373
2641375
2641376
2641377
2641378
2641379
2641380
2641381
2641382
2641383
2641397
28976
54100_at
8082444
A_23_P132405
GE58551
GO:0001676
GO:0003824
GO:0003995
GO:0004466
GO:0005515
GO:0005634
GO:0005739
GO:0005743
GO:0006629
GO:0007005
GO:0016020
GO:0016491
GO:0016627
GO:0030425
GO:0031966
GO:0032981
GO:0043226
GO:0050660
GO:0051791
GO:0065003
GO:0070991
HMNXSV003014142
HMNXSV003033934
ILMN_1775579
PH_hs_0024787
TC03000684.hg
TC03002531.hg
g12804754_3p_a_at
Participates
as a component of
MCIA complex [mitochondrial inner membrane] (Homo sapiens)
Inferred To
acad9 [mitochondrial inner membrane]
(Xenopus tropicalis)
Acad9 [mitochondrial inner membrane]
(Mus musculus)
Acad9 [mitochondrial inner membrane]
(Rattus norvegicus)
acdh-13 [mitochondrial inner membrane]
(Caenorhabditis elegans)
zgc:136367 [mitochondrial inner membrane]
(Danio rerio)
ACAD9 [mitochondrial inner membrane]
(Bos taurus)
ACAD9 [mitochondrial inner membrane]
(Canis familiaris)
ACAD9 [mitochondrial inner membrane]
(Gallus gallus)
ACAD9 [mitochondrial inner membrane]
(Sus scrofa)
Ghost homologue of ACAD9 [mitochondrial inner membrane]
(Drosophila melanogaster)
Cross References
RefSeq
NP_054768.2
OpenTargets
ENSG00000177646
HPA
ENSG00000177646-ACAD9
GeneCards
Q9H845
Ensembl
ENST00000308982
,
ENSP00000506340
,
ENSG00000177646
,
ENST00000681583
,
ENSP00000312618
PRO
Q9H845
Pharos - Targets
Q9H845
Orphanet
16424
HMDB Protein
HMDBP05275
Interactors (5)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.643
6
UniProt:Q9BQ95 ECSIT
2
ECSIT [cytosol]
(R-HSA-168064)
ECSIT [mitochondrial inner membrane]
(R-HSA-5689047)
0.643
4
UniProt:Q9NPL8 TIMMDC1
1
TIMMDC1 [mitochondrial inner membrane]
(R-HSA-5689720)
0.527
3
UniProt:Q9P0J0 NDUFA13
8
NDUFA13 [mitochondrial inner membrane]
(R-HSA-59936)
NDUFA13(41-49) [mitochondrial inner membrane]
(R-HSA-9839958)
NDUFA13(100-108) [mitochondrial inner membrane]
(R-HSA-9839959)
NDUFA13(109-144) [mitochondrial inner membrane]
(R-HSA-9839968)
NDUFA13(2-19) [mitochondrial inner membrane]
(R-HSA-9839966)
NDUFA13(69-99) [mitochondrial inner membrane]
(R-HSA-9839964)
NDUFA13(20-40) [mitochondrial inner membrane]
(R-HSA-9839963)
NDUFA13(50-68) [mitochondrial inner membrane]
(R-HSA-9839961)
0.527
2
UniProt:Q8IWL3 HSCB
5
HSCB [mitochondrial matrix]
(R-HSA-1299438)
HSCB [mitochondrial inner membrane]
(R-HSA-1299447)
HSCB(1-235) [mitochondrial inner membrane]
(R-HSA-1299443)
HSCB(1-30) [mitochondrial matrix]
(R-HSA-8986120)
HSCB(1-235) [mitochondrial intermembrane space]
(R-HSA-1299456)
0.462
2
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