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(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen]
Stable Identifier
R-HSA-5689430
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
endoplasmic reticulum lumen
Synonyms
Cathepsin C
Locations in the PathwayBrowser
Expand all
Metabolism of proteins (Homo sapiens)
Post-translational protein modification (Homo sapiens)
Asparagine N-linked glycosylation (Homo sapiens)
Transport to the Golgi and subsequent modification (Homo sapiens)
ER to Golgi Anterograde Transport (Homo sapiens)
COPII-mediated vesicle transport (Homo sapiens)
Inner coat assembly and cargo binding (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
Loss of SAR1B GTPase (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
SEC16 complex binds SAR1B:GTP:SEC23:SEC24 (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
SEC31:SEC13 and v-SNARE recruitment (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer:SEC13:SEC31:SEC23IP:v-SNARES [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
Vesicle budding (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer:SEC13:SEC31:SEC23IP:v-SNARES [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
Cargo concentration in the ER (Homo sapiens)
Inner coat assembly and cargo binding (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
LMAN family proteins bind glycosylated cargo (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
Vesicle-mediated transport (Homo sapiens)
Membrane Trafficking (Homo sapiens)
ER to Golgi Anterograde Transport (Homo sapiens)
COPII-mediated vesicle transport (Homo sapiens)
Inner coat assembly and cargo binding (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
Loss of SAR1B GTPase (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
SEC16 complex binds SAR1B:GTP:SEC23:SEC24 (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
SEC31:SEC13 and v-SNARE recruitment (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer:SEC13:SEC31:SEC23IP:v-SNARES [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
Vesicle budding (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer:SEC13:SEC31:SEC23IP:v-SNARES [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors:SAR1B:GTP:SEC23:SEC24:SEC16A:SEC16B:TFG hexamer [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
Cargo concentration in the ER (Homo sapiens)
Inner coat assembly and cargo binding (Homo sapiens)
COPII cargo receptors:SAR1B:GTP:SEC23:SEC24 [endoplasmic reticulum membrane] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
COPII cargo:receptors [endoplasmic reticulum membrane] (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
LMAN family proteins bind glycosylated cargo (Homo sapiens)
LMAN receptor:glycosylated cargo [endoplasmic reticulum membrane] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen] (Homo sapiens)
External Reference Information
External Reference
UniProt:P53634 CTSC
Gene Names
CTSC, CPPI
Chain
signal peptide:1-24, chain:25-134, propeptide:135-230, chain:231-394, chain:395-463
Reference Genes
BioGPS Gene:1075 CTSC
COSMIC (genes):CTSC CTSC
CTD Gene:1075 CTSC
dbSNP Gene:1075 CTSC
ENSEMBL:ENSG00000109861 CTSC
ENSEMBL_homo_sapiens_GENE:ENSG00000109861.17 CTSC
HGNC:2528 CTSC
KEGG Gene (Homo sapiens):1075 CTSC
Monarch:1075 CTSC
NCBI Gene:1075 CTSC
OMIM:602365 CTSC
UCSC:P53634 CTSC
Reference Transcript
RefSeq:NM_001814.5 CTSC
RefSeq:NM_001114173.2 CTSC
RefSeq:NM_148170.4 CTSC
Other Identifiers
1075
11715710_s_at
11731465_a_at
11731466_a_at
133_at
16743111
201487_PM_at
201487_at
225646_PM_at
225646_at
225647_PM_s_at
225647_s_at
231234_PM_at
231234_at
2831981
3385770
3385771
3385774
3385776
3385777
3385778
3385779
3385780
3385781
3385782
3385783
3385788
3385791
3385794
3385795
3385796
3385805
63866_at
74213_at
7893937
7950906
A_24_P115762
A_33_P3268472
A_33_P3283480
GE61251
GE86110
GO:0001913
GO:0002376
GO:0003824
GO:0004197
GO:0004252
GO:0005515
GO:0005576
GO:0005615
GO:0005634
GO:0005654
GO:0005737
GO:0005764
GO:0005773
GO:0005783
GO:0005788
GO:0005813
GO:0005815
GO:0005856
GO:0006508
GO:0006915
GO:0006954
GO:0006955
GO:0008233
GO:0008234
GO:0008239
GO:0010033
GO:0012501
GO:0016020
GO:0016505
GO:0016787
GO:0019902
GO:0023052
GO:0030134
GO:0030163
GO:0030312
GO:0031012
GO:0031404
GO:0031410
GO:0031642
GO:0033116
GO:0035578
GO:0042802
GO:0043226
GO:0043231
GO:0043621
GO:0048856
GO:0050877
GO:0051087
GO:0051603
GO:0062023
GO:0070062
GO:0098772
GO:0140096
GO:1903052
GO:1903980
GO:2001235
HMNXSV003051709
Hs.10029.1.S1_3p_at
ILMN_1689086
ILMN_1696347
ILMN_1792885
ILMN_2242463
PH_hs_0022406
PH_hs_0035561
X87212_at
g4503140_3p_at
Participates
as a member of
glycosylated LMAN cargo [endoplasmic reticulum lumen] (Homo sapiens)
Other forms of this molecule
CTSC(25-134) [lysosomal lumen]
CTSC(25-134) [extracellular region]
CTSC(25-134) [azurophil granule lumen]
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum-Golgi intermediate compartment membrane]
(Glc)3(GlcNAc)2(Man)9-CTSC [COPII-coated ER to Golgi transport vesicle]
Inferred To
ctsc [endoplasmic reticulum lumen]
(Xenopus tropicalis)
CTSC [endoplasmic reticulum lumen]
(Bos taurus)
CTSC [endoplasmic reticulum lumen]
(Canis familiaris)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen]
(Gallus gallus)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen]
(Mus musculus)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen]
(Rattus norvegicus)
(Glc)3(GlcNAc)2(Man)9-CTSC [endoplasmic reticulum lumen]
(Sus scrofa)
ik:tdsubc_1h2 [endoplasmic reticulum lumen]
(Danio rerio)
gmsA [endoplasmic reticulum lumen]
(Dictyostelium discoideum)
Modified Residues
Name
N4-(N-acetylamino)glucosyl-L-asparagine (N-{alpha-Glc-(1->2)-alpha-Glc-(1->3)-alpha-Glc-(1->3)-alpha-Man-(1->2)-alpha-Man-(1->2)-alpha-Man-(1->3)-(alpha-Man-(1->2)-alpha-Man-(1->3)-(alpha-Man-(1->2)-alpha-Man-(1->6))-alpha-Man-(1->6))-beta-Man-(1->4)-beta-GlcNAc-(1->4)-beta-GlcNAc}-L-Asn residue (ChEBI:59084)) at unknown position
Modification
N-{alpha-Glc-(1->2)-alpha-Glc-(1->3)-alpha-Glc-(1->3)-alpha-Man-(1->2)-alpha-Man-(1->2)-alpha-Man-(1->3)-(alpha-Man-(1->2)-alpha-Man-(1->3)-(alpha-Man-(1->2)-alpha-Man-(1->6))-alpha-Man-(1->6))-beta-Man-(1->4)-beta-GlcNAc-(1->4)-beta-GlcNAc}-yl group (ChEBI:59084)
PsiMod Name
N4-(N-acetylamino)glucosyl-L-asparagine
PsiMod Definition
A protein modification that effectively converts an L-asparagine residue to N4-(N-acetylaminoglucosyl)-L-asparagine.
Cross References
RefSeq
NP_001805.3
,
NP_001107645.1
,
NP_680475.1
Guide to Pharmacology - Targets
2344
OpenTargets
ENSG00000109861
ZINC - Substances
CATC_HUMAN
ZINC target
P53634
PRO
P53634
PDB
2DJG
,
4OEL
,
4CDC
,
4CDE
,
4CDD
,
3PDF
,
4CDF
,
4OEM
,
2DJF
,
1K3B
GeneCards
P53634
HPA
ENSG00000109861-CTSC
Ensembl
ENST00000529974
,
ENST00000227266
,
ENST00000524463
,
ENSP00000504568
,
ENSP00000227266
,
ENSG00000109861
,
ENSP00000432541
,
ENST00000677106
,
ENSP00000433539
Pharos - Targets
P53634
Orphanet
15822
ZINC - Predictions - Purchasable
CATC_HUMAN
HMDB Protein
HMDBP08180
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