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NDUFA7 [mitochondrial inner membrane]
Stable Identifier
R-HSA-59858
Type
Protein [EntityWithAccessionedSequence]
Species
Homo sapiens
Compartment
mitochondrial inner membrane
Synonyms
NADH-ubiquinone oxidoreductase subunit B14.5a , Complex I-B14.5a, CI-B14.5a
Locations in the PathwayBrowser
Expand all
Metabolism (Homo sapiens)
The citric acid (TCA) cycle and respiratory electron transport (Homo sapiens)
Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. (Homo sapiens)
Respiratory electron transport (Homo sapiens)
Complex I biogenesis (Homo sapiens)
Intermediate 1 binds HP subcomplex to form Intermediate 2 (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 binds MT-ND1:NDUFAF5:NDUFAF6 to form a 315kDa subcomplex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
ND4, ND5 bind the 550kDa complex to form the 815kDa complex (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
Peripheral arm subunits bind the 815kDa complex to form a 980kDa complex (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
The 315kDa subcomplex binds the 370kDa subcomplex to form the 550kDa complex (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
The MCIA complex, NDUFAF2-7 all dissociate from the 980kDa complex, resulting in Complex I (Homo sapiens)
980kDa complex [mitochondrial inner membrane] (Homo sapiens)
815kDa complex [mitochondrial inner membrane] (Homo sapiens)
550kDa complex [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
Complex I oxidises NADH to NAD+, reduces CoQ to QH2 (Homo sapiens)
Complex I [mitochondrial inner membrane] (Homo sapiens)
815kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
550kDa complex (-MCIA, NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
315kDa subcomplex (-NDUFAF3,4,5,6,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
Intermediate 2 (-NDUFAF3,4,7,TIMMDC1) [mitochondrial inner membrane] (Homo sapiens)
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
NDUFA7 [mitochondrial inner membrane] (Homo sapiens)
External Reference Information
External Reference
UniProt:O95182 NDUFA7
Gene Names
NDUFA7
Chain
initiator methionine:, chain:2-113
Reference Genes
BioGPS Gene:4701 NDUFA7
COSMIC (genes):NDUFA7 NDUFA7
CTD Gene:4701 NDUFA7
dbSNP Gene:4701 NDUFA7
ENSEMBL:ENSG00000267855 NDUFA7
ENSEMBL_homo_sapiens_GENE:ENSG00000267855.6 NDUFA7
HGNC:7691 NDUFA7
KEGG Gene (Homo sapiens):4701 NDUFA7
Monarch:4701 NDUFA7
NCBI Gene:4701 NDUFA7
OMIM:602139 NDUFA7
UCSC:O95182 NDUFA7
Reference Transcript
RefSeq:NM_005001.4 NDUFA7
Other Identifiers
11720188_a_at
1557532_PM_at
1557532_at
16868138
202785_PM_at
202785_at
32752_at
3848886
3848889
3848890
3848891
3848892
3848896
3848898
4701
8033564
A_23_P108303
GE54497
GO:0003735
GO:0003824
GO:0005198
GO:0005215
GO:0005515
GO:0005739
GO:0005743
GO:0005747
GO:0005761
GO:0005840
GO:0006091
GO:0006120
GO:0008137
GO:0009060
GO:0016020
GO:0016491
GO:0032543
GO:0042773
GO:0042776
GO:0043226
GO:0055086
GO:0070469
GO:0140053
GO:1901135
HMNXSV003050965
ILMN_1675239
PH_hs_0001717
TC19001128.hg
g4826849_3p_at
Participates
as a component of
HP subcomplex [mitochondrial inner membrane] (Homo sapiens)
Inferred To
ND-B14.5A [mitochondrial inner membrane]
(Drosophila melanogaster)
zgc:92850 [mitochondrial inner membrane]
(Danio rerio)
NDUFA7 [mitochondrial inner membrane]
(Bos taurus)
NDUFA7 [mitochondrial inner membrane]
(Canis familiaris)
NDUFA7 [mitochondrial inner membrane]
(Gallus gallus)
NDUFA7 [mitochondrial inner membrane]
(Sus scrofa)
Ndufa7 [mitochondrial inner membrane]
(Mus musculus)
ndua-7 [mitochondrial inner membrane]
(Caenorhabditis elegans)
Ghost homologue of NDUFA7 [mitochondrial inner membrane]
(Xenopus tropicalis)
LOC120101567 [mitochondrial inner membrane]
(Rattus norvegicus)
Cross References
RefSeq
NP_004992.2
OpenTargets
ENSG00000267855
HPA
ENSG00000267855-NDUFA7
GeneCards
O95182
Ensembl
ENSP00000301457
,
ENST00000301457
,
ENST00000593729
,
ENSG00000267855
,
ENSP00000470962
PRO
O95182
Pharos - Targets
O95182
Orphanet
24740
PDB
5XTH
,
5XTB
,
5XTD
,
5XTI
HMDB Protein
HMDBP00157
Interactors (4)
Accession
#Entities
Entities
Confidence Score
Evidence (IntAct)
UniProt:O75489 NDUFS3
2
NDUFS3 [mitochondrial matrix]
(R-HSA-163927)
NDUFS3 [cytosol]
(R-HSA-9714751)
0.643
5
UniProt:Q5QGT7 RTP2
2
RTP2 [endoplasmic reticulum membrane]
(R-HSA-9752982)
RTP2 [plasma membrane]
(R-HSA-8939446)
0.556
3
UniProt:P49638 TTPA
1
TTPA [cytosol]
(R-HSA-2980979)
0.556
3
UniProt:O75380 NDUFS6
1
NDUFS6 [mitochondrial inner membrane]
(R-HSA-163922)
0.527
2
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